2023 ICD-10-CM Index
'A' Terms
Index Terms Starting With 'A' (Agenesis)

Index Terms Starting With 'A' (Agenesis)

Agenesis
- adrenal Q89.1
  (gland)
  ICD-10-CM Diagnosis Code Q89.1
  Congenital malformations of adrenal gland
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Type 1 Excludes
  adrenogenital disorders (E25.-)
  congenital adrenal hyperplasia (E25.0)
- alimentary tract (complete) (partial) Q45.8
  ICD-10-CM Diagnosis Code Q45.8
  Other specified congenital malformations of digestive system
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence (complete) (partial) of alimentary tract NOS
  Duplication of digestive system
  Malposition, congenital of digestive system
  - upper Q40.8
    ICD-10-CM Diagnosis Code Q40.8
    Other specified congenital malformations of upper alimentary tract
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- anus, anal (canal) Q42.3
  ICD-10-CM Diagnosis Code Q42.3
  Congenital absence, atresia and stenosis of anus without fistula
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Imperforate anus
  - with fistula Q42.2
    ICD-10-CM Diagnosis Code Q42.2
    Congenital absence, atresia and stenosis of anus with fistula
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- aorta Q25.41
  ICD-10-CM Diagnosis Code Q25.41
  Absence and aplasia of aorta
  2017 - New Code 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- appendix Q42.8
  ICD-10-CM Diagnosis Code Q42.8
  Congenital absence, atresia and stenosis of other parts of large intestine
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- arm (complete) Q71.0-
  ICD-10-CM Diagnosis Code Q71.0-
  Congenital complete absence of upper limb
  2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
  - with hand present Q71.1-
    ICD-10-CM Diagnosis Code Q71.1-
    Congenital absence of upper arm and forearm with hand present
    2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
- artery (peripheral) Q27.9
  ICD-10-CM Diagnosis Code Q27.9
  Congenital malformation of peripheral vascular system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Anomaly of artery or vein NOS
  - brain Q28.3
    ICD-10-CM Diagnosis Code Q28.3
    Other malformations of cerebral vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital cerebral aneurysm (nonruptured)
    Congenital malformation of cerebral vessels NOS
    Developmental venous anomaly
  - coronary Q24.5
    ICD-10-CM Diagnosis Code Q24.5
    Malformation of coronary vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital coronary (artery) aneurysm
  - pulmonary Q25.79
    ICD-10-CM Diagnosis Code Q25.79
    Other congenital malformations of pulmonary artery
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Aberrant pulmonary artery
    Agenesis of pulmonary artery
    Congenital aneurysm of pulmonary artery
    Congenital anomaly of pulmonary artery
    Hypoplasia of pulmonary artery
  - specified NEC Q27.8
    ICD-10-CM Diagnosis Code Q27.8
    Other specified congenital malformations of peripheral vascular system
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Absence of peripheral vascular system
    Atresia of peripheral vascular system
    Congenital aneurysm (peripheral)
    Congenital stricture, artery
    Congenital varix
    Type 1 Excludes
    arteriovenous malformation (Q27.3-)
  - umbilical Q27.0
    ICD-10-CM Diagnosis Code Q27.0
    Congenital absence and hypoplasia of umbilical artery
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Single umbilical artery
- auditory Q16.1
  (canal) (external)
  ICD-10-CM Diagnosis Code Q16.1
  Congenital absence, atresia and stricture of auditory canal (external)
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital atresia or stricture of osseous meatus
- auricle Q16.0
  (ear)
  ICD-10-CM Diagnosis Code Q16.0
  Congenital absence of (ear) auricle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- bile duct or passage Q44.5
  ICD-10-CM Diagnosis Code Q44.5
  Other congenital malformations of bile ducts
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory hepatic duct
  Biliary duct duplication
  Congenital malformation of bile duct NOS
  Cystic duct duplication
- bladder Q64.5
  ICD-10-CM Diagnosis Code Q64.5
  Congenital absence of bladder and urethra
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- bone Q79.9
  ICD-10-CM Diagnosis Code Q79.9
  Congenital malformation of musculoskeletal system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of musculoskeletal system NOS
  Congenital deformity of musculoskeletal system NOS
- brain Q00.0
  ICD-10-CM Diagnosis Code Q00.0
  Anencephaly
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Acephaly
  Acrania
  Amyelencephaly
  Hemianencephaly
  Hemicephaly
  - part of Q04.3
    ICD-10-CM Diagnosis Code Q04.3
    Other reduction deformities of brain
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Absence of part of brain
    Agenesis of part of brain
    Agyria
    Aplasia of part of brain
    Hydranencephaly
    Hypoplasia of part of brain
    Lissencephaly
    Microgyria
    Pachygyria
    Type 1 Excludes
    congenital malformations of corpus callosum (Q04.0)
- breast (with nipple present) Q83.8
  ICD-10-CM Diagnosis Code Q83.8
  Other congenital malformations of breast
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - with absent nipple Q83.0
    ICD-10-CM Diagnosis Code Q83.0
    Congenital absence of breast with absent nipple
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- bronchus Q32.4
  ICD-10-CM Diagnosis Code Q32.4
  Other congenital malformations of bronchus
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of bronchus
  Agenesis of bronchus
  Atresia of bronchus
  Congenital diverticulum of bronchus
  Congenital malformation of bronchus NOS
- canaliculus lacrimalis Q10.4
  ICD-10-CM Diagnosis Code Q10.4
  Absence and agenesis of lacrimal apparatus
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of punctum lacrimale
- carpus - see Agenesis, hand
- cartilage Q79.9
  ICD-10-CM Diagnosis Code Q79.9
  Congenital malformation of musculoskeletal system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of musculoskeletal system NOS
  Congenital deformity of musculoskeletal system NOS
- cecum Q42.8
  ICD-10-CM Diagnosis Code Q42.8
  Congenital absence, atresia and stenosis of other parts of large intestine
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- cerebellum Q04.3
  ICD-10-CM Diagnosis Code Q04.3
  Other reduction deformities of brain
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of part of brain
  Agenesis of part of brain
  Agyria
  Aplasia of part of brain
  Hydranencephaly
  Hypoplasia of part of brain
  Lissencephaly
  Microgyria
  Pachygyria
  Type 1 Excludes
  congenital malformations of corpus callosum (Q04.0)
- cervix Q51.5
  ICD-10-CM Diagnosis Code Q51.5
  Agenesis and aplasia of cervix
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Congenital absence of cervix
- chin Q18.8
  ICD-10-CM Diagnosis Code Q18.8
  Other specified congenital malformations of face and neck
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Medial cyst of face and neck
  Medial fistula of face and neck
  Medial sinus of face and neck
- cilia Q10.3
  ICD-10-CM Diagnosis Code Q10.3
  Other congenital malformations of eyelid
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Ablepharon
  Blepharophimosis, congenital
  Coloboma of eyelid
  Congenital absence or agenesis of cilia
  Congenital absence or agenesis of eyelid
  Congenital accessory eyelid
  Congenital accessory eye muscle
  Congenital malformation of eyelid NOS
- circulatory system, part NOS Q28.9
  ICD-10-CM Diagnosis Code Q28.9
  Congenital malformation of circulatory system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- clavicle Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- clitoris Q52.6
  ICD-10-CM Diagnosis Code Q52.6
  Congenital malformation of clitoris
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
- coccyx Q76.49
  ICD-10-CM Diagnosis Code Q76.49
  Other congenital malformations of spine, not associated with scoliosis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of vertebra NOS
  Congenital fusion of spine NOS
  Congenital malformation of lumbosacral (joint) (region) NOS
  Congenital malformation of spine NOS
  Hemivertebra NOS
  Malformation of spine NOS
  Platyspondylisis NOS
  Supernumerary vertebra NOS
- colon Q42.9
  ICD-10-CM Diagnosis Code Q42.9
  Congenital absence, atresia and stenosis of large intestine, part unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - specified NEC Q42.8
    ICD-10-CM Diagnosis Code Q42.8
    Congenital absence, atresia and stenosis of other parts of large intestine
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- corpus callosum Q04.0
  ICD-10-CM Diagnosis Code Q04.0
  Congenital malformations of corpus callosum
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Agenesis of corpus callosum
- cricoid cartilage Q31.8
  ICD-10-CM Diagnosis Code Q31.8
  Other congenital malformations of larynx
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of larynx
  Agenesis of larynx
  Atresia of larynx
  Congenital cleft thyroid cartilage
  Congenital fissure of epiglottis
  Congenital stenosis of larynx NEC
  Posterior cleft of cricoid cartilage
- diaphragm Q79.1
  (with hernia)
  ICD-10-CM Diagnosis Code Q79.1
  Other congenital malformations of diaphragm
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of diaphragm
  Congenital malformation of diaphragm NOS
  Eventration of diaphragm
- digestive organ(s) or tract (complete) (partial) Q45.8
  ICD-10-CM Diagnosis Code Q45.8
  Other specified congenital malformations of digestive system
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence (complete) (partial) of alimentary tract NOS
  Duplication of digestive system
  Malposition, congenital of digestive system
  - upper Q40.8
    ICD-10-CM Diagnosis Code Q40.8
    Other specified congenital malformations of upper alimentary tract
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- ductus arteriosus Q28.8
  ICD-10-CM Diagnosis Code Q28.8
  Other specified congenital malformations of circulatory system
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital aneurysm, specified site NEC
  Spinal vessel anomaly
- duodenum Q41.0
  ICD-10-CM Diagnosis Code Q41.0
  Congenital absence, atresia and stenosis of duodenum
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- ear Q16.9
  ICD-10-CM Diagnosis Code Q16.9
  Congenital malformation of ear causing impairment of hearing, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of ear NOS
  - auricle Q16.0
    ICD-10-CM Diagnosis Code Q16.0
    Congenital absence of (ear) auricle
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - lobe Q17.8
    ICD-10-CM Diagnosis Code Q17.8
    Other specified congenital malformations of ear
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital absence of lobe of ear
- ejaculatory duct Q55.4
  ICD-10-CM Diagnosis Code Q55.4
  Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
  Applicable To
  Absence or aplasia of prostate
  Absence or aplasia of spermatic cord
  Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
- endocrine Q89.2
  (gland)
  ICD-10-CM Diagnosis Code Q89.2
  Congenital malformations of other endocrine glands
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of parathyroid or thyroid gland
  Persistent thyroglossal duct
  Thyroglossal cyst
  Type 1 Excludes
  congenital goiter (E03.0)
  congenital hypothyroidism (E03.1)
- epiglottis Q31.8
  ICD-10-CM Diagnosis Code Q31.8
  Other congenital malformations of larynx
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of larynx
  Agenesis of larynx
  Atresia of larynx
  Congenital cleft thyroid cartilage
  Congenital fissure of epiglottis
  Congenital stenosis of larynx NEC
  Posterior cleft of cricoid cartilage
- esophagus Q39.8
  ICD-10-CM Diagnosis Code Q39.8
  Other congenital malformations of esophagus
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of esophagus
  Congenital displacement of esophagus
  Congenital duplication of esophagus
- eustachian tube Q16.2
  ICD-10-CM Diagnosis Code Q16.2
  Absence of eustachian tube
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- eye Q11.1
  ICD-10-CM Diagnosis Code Q11.1
  Other anophthalmos
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Anophthalmos NOS
  Agenesis of eye
  Aplasia of eye
  - adnexa Q15.8
    ICD-10-CM Diagnosis Code Q15.8
    Other specified congenital malformations of eye
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- eyelid Q10.3
  (fold)
  ICD-10-CM Diagnosis Code Q10.3
  Other congenital malformations of eyelid
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Ablepharon
  Blepharophimosis, congenital
  Coloboma of eyelid
  Congenital absence or agenesis of cilia
  Congenital absence or agenesis of eyelid
  Congenital accessory eyelid
  Congenital accessory eye muscle
  Congenital malformation of eyelid NOS
- face
  - bones NEC Q75.8
    ICD-10-CM Diagnosis Code Q75.8
    Other specified congenital malformations of skull and face bones
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Absence of skull bone, congenital
    Congenital deformity of forehead
    Platybasia
  - specified part NEC Q18.8
    ICD-10-CM Diagnosis Code Q18.8
    Other specified congenital malformations of face and neck
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Medial cyst of face and neck
    Medial fistula of face and neck
    Medial sinus of face and neck
- fallopian tube Q50.6
  ICD-10-CM Diagnosis Code Q50.6
  Other congenital malformations of fallopian tube and broad ligament
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Absence of fallopian tube and broad ligament
  Accessory fallopian tube and broad ligament
  Atresia of fallopian tube and broad ligament
  Congenital malformation of fallopian tube or broad ligament NOS
- femur - see Defect, reduction, lower limb, longitudinal, femur
- fibula - see Defect, reduction, lower limb, longitudinal, fibula
- finger (complete) (partial) - see Agenesis, hand
- foot Q72.3-
  (and toes) (complete) (partial)
  ICD-10-CM Diagnosis Code Q72.3-
  Congenital absence of foot and toe(s)
  2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
- forearm (with hand present) - see Agenesis, arm, with hand present
  - and hand Q71.2-
    ICD-10-CM Diagnosis Code Q71.2-
    Congenital absence of both forearm and hand
    2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
- gallbladder Q44.0
  ICD-10-CM Diagnosis Code Q44.0
  Agenesis, aplasia and hypoplasia of gallbladder
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of gallbladder
- gastric Q40.2
  ICD-10-CM Diagnosis Code Q40.2
  Other specified congenital malformations of stomach
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital displacement of stomach
  Congenital diverticulum of stomach
  Congenital hourglass stomach
  Congenital duplication of stomach
  Megalogastria
  Microgastria
- genitalia, genital (organ(s))
  - female Q52.8
    ICD-10-CM Diagnosis Code Q52.8
    Other specified congenital malformations of female genitalia
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
    - external Q52.71
      ICD-10-CM Diagnosis Code Q52.71
      Congenital absence of vulva
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
    - internal NEC Q52.8
      ICD-10-CM Diagnosis Code Q52.8
      Other specified congenital malformations of female genitalia
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  - male Q55.8
    ICD-10-CM Diagnosis Code Q55.8
    Other specified congenital malformations of male genital organs
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
- glottis Q31.8
  ICD-10-CM Diagnosis Code Q31.8
  Other congenital malformations of larynx
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of larynx
  Agenesis of larynx
  Atresia of larynx
  Congenital cleft thyroid cartilage
  Congenital fissure of epiglottis
  Congenital stenosis of larynx NEC
  Posterior cleft of cricoid cartilage
- hair Q84.0
  ICD-10-CM Diagnosis Code Q84.0
  Congenital alopecia
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital atrichosis
- hand Q71.3-
  (and fingers) (complete) (partial)
  ICD-10-CM Diagnosis Code Q71.3-
  Congenital absence of hand and finger
  2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
- heart Q24.8
  ICD-10-CM Diagnosis Code Q24.8
  Other specified congenital malformations of heart
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital diverticulum of left ventricle
  Congenital malformation of myocardium
  Congenital malformation of pericardium
  Malposition of heart
  Uhl's disease
  - valve NEC Q24.8
    ICD-10-CM Diagnosis Code Q24.8
    Other specified congenital malformations of heart
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital diverticulum of left ventricle
    Congenital malformation of myocardium
    Congenital malformation of pericardium
    Malposition of heart
    Uhl's disease
    - pulmonary Q22.0
      ICD-10-CM Diagnosis Code Q22.0
      Pulmonary valve atresia
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- hepatic Q44.7
  ICD-10-CM Diagnosis Code Q44.7
  Other congenital malformations of liver
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory liver
  Alagille's syndrome
  Congenital absence of liver
  Congenital hepatomegaly
  Congenital malformation of liver NOS
- humerus - see Defect, reduction, upper limb
- hymen Q52.4
  ICD-10-CM Diagnosis Code Q52.4
  Other congenital malformations of vagina
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Canal of Nuck cyst, congenital
  Congenital malformation of vagina NOS
  Embryonic vaginal cyst
  Gartner's duct cyst
- ileum Q41.2
  ICD-10-CM Diagnosis Code Q41.2
  Congenital absence, atresia and stenosis of ileum
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- incus Q16.3
  ICD-10-CM Diagnosis Code Q16.3
  Congenital malformation of ear ossicles
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of ear ossicles
- intestine (small) Q41.9
  ICD-10-CM Diagnosis Code Q41.9
  Congenital absence, atresia and stenosis of small intestine, part unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence, atresia and stenosis of intestine NOS
  - large Q42.9
    ICD-10-CM Diagnosis Code Q42.9
    Congenital absence, atresia and stenosis of large intestine, part unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    - specified NEC Q42.8
      ICD-10-CM Diagnosis Code Q42.8
      Congenital absence, atresia and stenosis of other parts of large intestine
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- iris Q13.1
  (dilator fibers)
  ICD-10-CM Diagnosis Code Q13.1
  Absence of iris
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Aniridia
  Use Additional
  code for associated glaucoma (H42)
- jaw M26.09
  ICD-10-CM Diagnosis Code M26.09
  Other specified anomalies of jaw size
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
- jejunum Q41.1
  ICD-10-CM Diagnosis Code Q41.1
  Congenital absence, atresia and stenosis of jejunum
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Apple peel syndrome
  Imperforate jejunum
- kidney(s) (partial) Q60.2
  ICD-10-CM Diagnosis Code Q60.2
  Renal agenesis, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - bilateral Q60.1
    ICD-10-CM Diagnosis Code Q60.1
    Renal agenesis, bilateral
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - unilateral Q60.0
    ICD-10-CM Diagnosis Code Q60.0
    Renal agenesis, unilateral
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- labium Q52.71
  (majus) (minus)
  ICD-10-CM Diagnosis Code Q52.71
  Congenital absence of vulva
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
- labyrinth, membranous Q16.5
  ICD-10-CM Diagnosis Code Q16.5
  Congenital malformation of inner ear
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of membranous labyrinth
  Congenital anomaly of organ of Corti
- lacrimal apparatus Q10.4
  ICD-10-CM Diagnosis Code Q10.4
  Absence and agenesis of lacrimal apparatus
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of punctum lacrimale
- larynx Q31.8
  ICD-10-CM Diagnosis Code Q31.8
  Other congenital malformations of larynx
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of larynx
  Agenesis of larynx
  Atresia of larynx
  Congenital cleft thyroid cartilage
  Congenital fissure of epiglottis
  Congenital stenosis of larynx NEC
  Posterior cleft of cricoid cartilage
- leg (complete) Q72.0-
  ICD-10-CM Diagnosis Code Q72.0-
  Congenital complete absence of lower limb
  2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
  - lower leg (with foot present) - see Agenesis, leg, with foot present
    - and foot Q72.2-
      ICD-10-CM Diagnosis Code Q72.2-
      Congenital absence of both lower leg and foot
      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
  - with foot present Q72.1-
    ICD-10-CM Diagnosis Code Q72.1-
    Congenital absence of thigh and lower leg with foot present
    2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
- lens Q12.3
  ICD-10-CM Diagnosis Code Q12.3
  Congenital aphakia
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- limb (complete) Q73.0
  ICD-10-CM Diagnosis Code Q73.0
  Congenital absence of unspecified limb(s)
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Amelia NOS
  - lower - see Agenesis, leg
  - upper - see Agenesis, arm
- lip Q38.0
  ICD-10-CM Diagnosis Code Q38.0
  Congenital malformations of lips, not elsewhere classified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fistula of lip
  Congenital malformation of lip NOS
  Van der Woude's syndrome
  Type 1 Excludes
  cleft lip (Q36.-)
  cleft lip with cleft palate (Q37.-)
  macrocheilia (Q18.6)
  microcheilia (Q18.7)
- liver Q44.7
  ICD-10-CM Diagnosis Code Q44.7
  Other congenital malformations of liver
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory liver
  Alagille's syndrome
  Congenital absence of liver
  Congenital hepatomegaly
  Congenital malformation of liver NOS
- lung Q33.3
  (fissure) (lobe) (bilateral) (unilateral)
  ICD-10-CM Diagnosis Code Q33.3
  Agenesis of lung
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of lung (lobe)
- mandible, maxilla M26.09
  ICD-10-CM Diagnosis Code M26.09
  Other specified anomalies of jaw size
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
- metacarpus - see Agenesis, hand
- metatarsus - see Agenesis, foot
- muscle Q79.8
  ICD-10-CM Diagnosis Code Q79.8
  Other congenital malformations of musculoskeletal system
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of muscle
  Absence of tendon
  Accessory muscle
  Amyotrophia congenita
  Congenital constricting bands
  Congenital shortening of tendon
  Poland syndrome
  - eyelid Q10.3
    ICD-10-CM Diagnosis Code Q10.3
    Other congenital malformations of eyelid
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Ablepharon
    Blepharophimosis, congenital
    Coloboma of eyelid
    Congenital absence or agenesis of cilia
    Congenital absence or agenesis of eyelid
    Congenital accessory eyelid
    Congenital accessory eye muscle
    Congenital malformation of eyelid NOS
  - ocular Q15.8
    ICD-10-CM Diagnosis Code Q15.8
    Other specified congenital malformations of eye
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- musculoskeletal system NEC Q79.8
  ICD-10-CM Diagnosis Code Q79.8
  Other congenital malformations of musculoskeletal system
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of muscle
  Absence of tendon
  Accessory muscle
  Amyotrophia congenita
  Congenital constricting bands
  Congenital shortening of tendon
  Poland syndrome
- nail Q84.3
  (s)
  ICD-10-CM Diagnosis Code Q84.3
  Anonychia
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Type 1 Excludes
  nail patella syndrome (Q87.2)
- neck, part Q18.8
  ICD-10-CM Diagnosis Code Q18.8
  Other specified congenital malformations of face and neck
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Medial cyst of face and neck
  Medial fistula of face and neck
  Medial sinus of face and neck
- nerve Q07.8
  ICD-10-CM Diagnosis Code Q07.8
  Other specified congenital malformations of nervous system
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Agenesis of nerve
  Displacement of brachial plexus
  Jaw-winking syndrome
  Marcus Gunn's syndrome
- nervous system, part NEC Q07.8
  ICD-10-CM Diagnosis Code Q07.8
  Other specified congenital malformations of nervous system
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Agenesis of nerve
  Displacement of brachial plexus
  Jaw-winking syndrome
  Marcus Gunn's syndrome
- nipple Q83.2
  ICD-10-CM Diagnosis Code Q83.2
  Absent nipple
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- nose Q30.1
  ICD-10-CM Diagnosis Code Q30.1
  Agenesis and underdevelopment of nose
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absent of nose
- nuclear Q07.8
  ICD-10-CM Diagnosis Code Q07.8
  Other specified congenital malformations of nervous system
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Agenesis of nerve
  Displacement of brachial plexus
  Jaw-winking syndrome
  Marcus Gunn's syndrome
- organ
  - of Corti Q16.5
    ICD-10-CM Diagnosis Code Q16.5
    Congenital malformation of inner ear
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital anomaly of membranous labyrinth
    Congenital anomaly of organ of Corti
  - or site not listed - see Anomaly, by site
- osseous meatus Q16.1
  (ear)
  ICD-10-CM Diagnosis Code Q16.1
  Congenital absence, atresia and stricture of auditory canal (external)
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital atresia or stricture of osseous meatus
- ovary
  - bilateral Q50.02
    ICD-10-CM Diagnosis Code Q50.02
    Congenital absence of ovary, bilateral
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  - unilateral Q50.01
    ICD-10-CM Diagnosis Code Q50.01
    Congenital absence of ovary, unilateral
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
- oviduct Q50.6
  ICD-10-CM Diagnosis Code Q50.6
  Other congenital malformations of fallopian tube and broad ligament
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Absence of fallopian tube and broad ligament
  Accessory fallopian tube and broad ligament
  Atresia of fallopian tube and broad ligament
  Congenital malformation of fallopian tube or broad ligament NOS
- pancreas Q45.0
  ICD-10-CM Diagnosis Code Q45.0
  Agenesis, aplasia and hypoplasia of pancreas
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of pancreas
- parathyroid Q89.2
  (gland)
  ICD-10-CM Diagnosis Code Q89.2
  Congenital malformations of other endocrine glands
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of parathyroid or thyroid gland
  Persistent thyroglossal duct
  Thyroglossal cyst
  Type 1 Excludes
  congenital goiter (E03.0)
  congenital hypothyroidism (E03.1)
- parotid gland Q38.4
  (s)
  ICD-10-CM Diagnosis Code Q38.4
  Congenital malformations of salivary glands and ducts
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Atresia of salivary glands and ducts
  Congenital absence of salivary glands and ducts
  Congenital accessory salivary glands and ducts
  Congenital fistula of salivary gland
- patella Q74.1
  ICD-10-CM Diagnosis Code Q74.1
  Congenital malformation of knee
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of patella
  Congenital dislocation of patella
  Congenital genu valgum
  Congenital genu varum
  Rudimentary patella
  Type 1 Excludes
  congenital dislocation of knee (Q68.2)
  congenital genu recurvatum (Q68.2)
  nail patella syndrome (Q87.2)
- pelvic girdle Q74.2
  (complete) (partial)
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- penis Q55.5
  ICD-10-CM Diagnosis Code Q55.5
  Congenital absence and aplasia of penis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
- pericardium Q24.8
  ICD-10-CM Diagnosis Code Q24.8
  Other specified congenital malformations of heart
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital diverticulum of left ventricle
  Congenital malformation of myocardium
  Congenital malformation of pericardium
  Malposition of heart
  Uhl's disease
- pituitary Q89.2
  (gland)
  ICD-10-CM Diagnosis Code Q89.2
  Congenital malformations of other endocrine glands
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of parathyroid or thyroid gland
  Persistent thyroglossal duct
  Thyroglossal cyst
  Type 1 Excludes
  congenital goiter (E03.0)
  congenital hypothyroidism (E03.1)
- prostate Q55.4
  ICD-10-CM Diagnosis Code Q55.4
  Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
  Applicable To
  Absence or aplasia of prostate
  Absence or aplasia of spermatic cord
  Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
- punctum lacrimale Q10.4
  ICD-10-CM Diagnosis Code Q10.4
  Absence and agenesis of lacrimal apparatus
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of punctum lacrimale
- radioulnar - see Defect, reduction, upper limb
- radius - see Defect, reduction, upper limb, longitudinal, radius
- rectum Q42.1
  ICD-10-CM Diagnosis Code Q42.1
  Congenital absence, atresia and stenosis of rectum without fistula
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Imperforate rectum
  - with fistula Q42.0
    ICD-10-CM Diagnosis Code Q42.0
    Congenital absence, atresia and stenosis of rectum with fistula
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- renal Q60.2
  ICD-10-CM Diagnosis Code Q60.2
  Renal agenesis, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - bilateral Q60.1
    ICD-10-CM Diagnosis Code Q60.1
    Renal agenesis, bilateral
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - unilateral Q60.0
    ICD-10-CM Diagnosis Code Q60.0
    Renal agenesis, unilateral
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- respiratory organ NEC Q34.8
  ICD-10-CM Diagnosis Code Q34.8
  Other specified congenital malformations of respiratory system
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Atresia of nasopharynx
- rib Q76.6
  ICD-10-CM Diagnosis Code Q76.6
  Other congenital malformations of ribs
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory rib
  Congenital absence of rib
  Congenital fusion of ribs
  Congenital malformation of ribs NOS
  Type 1 Excludes
  short rib syndrome (Q77.2)
- roof of orbit Q75.8
  ICD-10-CM Diagnosis Code Q75.8
  Other specified congenital malformations of skull and face bones
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of skull bone, congenital
  Congenital deformity of forehead
  Platybasia
- round ligament Q52.8
  ICD-10-CM Diagnosis Code Q52.8
  Other specified congenital malformations of female genitalia
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
- sacrum Q76.49
  ICD-10-CM Diagnosis Code Q76.49
  Other congenital malformations of spine, not associated with scoliosis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of vertebra NOS
  Congenital fusion of spine NOS
  Congenital malformation of lumbosacral (joint) (region) NOS
  Congenital malformation of spine NOS
  Hemivertebra NOS
  Malformation of spine NOS
  Platyspondylisis NOS
  Supernumerary vertebra NOS
- salivary gland Q38.4
  ICD-10-CM Diagnosis Code Q38.4
  Congenital malformations of salivary glands and ducts
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Atresia of salivary glands and ducts
  Congenital absence of salivary glands and ducts
  Congenital accessory salivary glands and ducts
  Congenital fistula of salivary gland
- scapula Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- scrotum Q55.29
  ICD-10-CM Diagnosis Code Q55.29
  Other congenital malformations of testis and scrotum
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
- seminal vesicles Q55.4
  ICD-10-CM Diagnosis Code Q55.4
  Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
  Applicable To
  Absence or aplasia of prostate
  Absence or aplasia of spermatic cord
  Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
- septum
  - atrial Q21.19
    ICD-10-CM Diagnosis Code Q21.19
    Other specified atrial septal defect
    2023 - New Code Billable/Specific Code POA Exempt
    Applicable To
    Common atrium
    Other specified atrial septal abnormality
  - between aorta and pulmonary artery Q21.4
    ICD-10-CM Diagnosis Code Q21.4
    Aortopulmonary septal defect
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Aortic septal defect
    Aortopulmonary window
  - ventricular Q20.4
    ICD-10-CM Diagnosis Code Q20.4
    Double inlet ventricle
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Common ventricle
    Cor triloculare biatriatum
    Single ventricle
- shoulder girdle Q74.0
  (complete) (partial)
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- skull (bone) Q75.8
  ICD-10-CM Diagnosis Code Q75.8
  Other specified congenital malformations of skull and face bones
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of skull bone, congenital
  Congenital deformity of forehead
  Platybasia
  - with
    - anencephaly Q00.0
      ICD-10-CM Diagnosis Code Q00.0
      Anencephaly
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Acephaly
      Acrania
      Amyelencephaly
      Hemianencephaly
      Hemicephaly
    - encephalocele - see Encephalocele
    - hydrocephalus Q03.9
      ICD-10-CM Diagnosis Code Q03.9
      Congenital hydrocephalus, unspecified
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      - with spina bifida - see Spina bifida, by site, with hydrocephalus
    - microcephaly Q02
      ICD-10-CM Diagnosis Code Q02
      Microcephaly
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Code First
      , if applicable, congenital Zika virus disease
      Includes
      hydromicrocephaly
      micrencephalon
      Type 1 Excludes
      Meckel-Gruber syndrome (Q61.9)
- spermatic cord Q55.4
  ICD-10-CM Diagnosis Code Q55.4
  Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
  Applicable To
  Absence or aplasia of prostate
  Absence or aplasia of spermatic cord
  Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
- spinal cord Q06.0
  ICD-10-CM Diagnosis Code Q06.0
  Amyelia
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- spine Q76.49
  ICD-10-CM Diagnosis Code Q76.49
  Other congenital malformations of spine, not associated with scoliosis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of vertebra NOS
  Congenital fusion of spine NOS
  Congenital malformation of lumbosacral (joint) (region) NOS
  Congenital malformation of spine NOS
  Hemivertebra NOS
  Malformation of spine NOS
  Platyspondylisis NOS
  Supernumerary vertebra NOS
- spleen Q89.01
  ICD-10-CM Diagnosis Code Q89.01
  Asplenia (congenital)
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- sternum Q76.7
  ICD-10-CM Diagnosis Code Q76.7
  Congenital malformation of sternum
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of sternum
  Sternum bifidum
- stomach Q40.2
  ICD-10-CM Diagnosis Code Q40.2
  Other specified congenital malformations of stomach
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital displacement of stomach
  Congenital diverticulum of stomach
  Congenital hourglass stomach
  Congenital duplication of stomach
  Megalogastria
  Microgastria
- submaxillary gland Q38.4
  (s) (congenital)
  ICD-10-CM Diagnosis Code Q38.4
  Congenital malformations of salivary glands and ducts
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Atresia of salivary glands and ducts
  Congenital absence of salivary glands and ducts
  Congenital accessory salivary glands and ducts
  Congenital fistula of salivary gland
- tarsus - see Agenesis, foot
- tendon Q79.8
  ICD-10-CM Diagnosis Code Q79.8
  Other congenital malformations of musculoskeletal system
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of muscle
  Absence of tendon
  Accessory muscle
  Amyotrophia congenita
  Congenital constricting bands
  Congenital shortening of tendon
  Poland syndrome
- testicle Q55.0
  ICD-10-CM Diagnosis Code Q55.0
  Absence and aplasia of testis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
  Applicable To
  Monorchism
- thymus Q89.2
  (gland)
  ICD-10-CM Diagnosis Code Q89.2
  Congenital malformations of other endocrine glands
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of parathyroid or thyroid gland
  Persistent thyroglossal duct
  Thyroglossal cyst
  Type 1 Excludes
  congenital goiter (E03.0)
  congenital hypothyroidism (E03.1)
- thyroid (gland) E03.1
  ICD-10-CM Diagnosis Code E03.1
  Congenital hypothyroidism without goiter
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Aplasia of thyroid (with myxedema)
  Congenital atrophy of thyroid
  Congenital hypothyroidism NOS
  - cartilage Q31.8
    ICD-10-CM Diagnosis Code Q31.8
    Other congenital malformations of larynx
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Absence of larynx
    Agenesis of larynx
    Atresia of larynx
    Congenital cleft thyroid cartilage
    Congenital fissure of epiglottis
    Congenital stenosis of larynx NEC
    Posterior cleft of cricoid cartilage
- tibia - see Defect, reduction, lower limb, longitudinal, tibia
- tibiofibular - see Defect, reduction, lower limb, specified type NEC
- toe (and foot) (complete) (partial) - see Agenesis, foot
- tongue Q38.3
  ICD-10-CM Diagnosis Code Q38.3
  Other congenital malformations of tongue
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Aglossia
  Bifid tongue
  Congenital adhesion of tongue
  Congenital fissure of tongue
  Congenital malformation of tongue NOS
  Double tongue
  Hypoglossia
  Hypoplasia of tongue
  Microglossia
- trachea Q32.1
  (cartilage)
  ICD-10-CM Diagnosis Code Q32.1
  Other congenital malformations of trachea
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Atresia of trachea
  Congenital anomaly of tracheal cartilage
  Congenital dilatation of trachea
  Congenital malformation of trachea
  Congenital stenosis of trachea
  Congenital tracheocele
- ulna - see Defect, reduction, upper limb, longitudinal, ulna
- upper limb - see Agenesis, arm
- ureter Q62.4
  ICD-10-CM Diagnosis Code Q62.4
  Agenesis of ureter
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence ureter
- urethra Q64.5
  ICD-10-CM Diagnosis Code Q64.5
  Congenital absence of bladder and urethra
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- urinary tract NEC Q64.8
  ICD-10-CM Diagnosis Code Q64.8
  Other specified congenital malformations of urinary system
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- uterus Q51.0
  ICD-10-CM Diagnosis Code Q51.0
  Agenesis and aplasia of uterus
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Congenital absence of uterus
- uvula Q38.5
  ICD-10-CM Diagnosis Code Q38.5
  Congenital malformations of palate, not elsewhere classified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of uvula
  Congenital malformation of palate NOS
  Congenital high arched palate
  Type 1 Excludes
  cleft palate (Q35.-)
  cleft palate with cleft lip (Q37.-)
- vagina Q52.0
  ICD-10-CM Diagnosis Code Q52.0
  Congenital absence of vagina
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Vaginal agenesis, total or partial
- vas deferens Q55.4
  ICD-10-CM Diagnosis Code Q55.4
  Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
  Applicable To
  Absence or aplasia of prostate
  Absence or aplasia of spermatic cord
  Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
- vein(s) (peripheral) Q27.9
  ICD-10-CM Diagnosis Code Q27.9
  Congenital malformation of peripheral vascular system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Anomaly of artery or vein NOS
  - brain Q28.3
    ICD-10-CM Diagnosis Code Q28.3
    Other malformations of cerebral vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital cerebral aneurysm (nonruptured)
    Congenital malformation of cerebral vessels NOS
    Developmental venous anomaly
  - great NEC Q26.8
    ICD-10-CM Diagnosis Code Q26.8
    Other congenital malformations of great veins
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Absence of vena cava (inferior) (superior)
    Azygos continuation of inferior vena cava
    Persistent left posterior cardinal vein
    Scimitar syndrome
  - portal Q26.5
    ICD-10-CM Diagnosis Code Q26.5
    Anomalous portal venous connection
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- vena cava Q26.8
  (inferior) (superior)
  ICD-10-CM Diagnosis Code Q26.8
  Other congenital malformations of great veins
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of vena cava (inferior) (superior)
  Azygos continuation of inferior vena cava
  Persistent left posterior cardinal vein
  Scimitar syndrome
- vermis of cerebellum Q04.3
  ICD-10-CM Diagnosis Code Q04.3
  Other reduction deformities of brain
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of part of brain
  Agenesis of part of brain
  Agyria
  Aplasia of part of brain
  Hydranencephaly
  Hypoplasia of part of brain
  Lissencephaly
  Microgyria
  Pachygyria
  Type 1 Excludes
  congenital malformations of corpus callosum (Q04.0)
- vertebra Q76.49
  ICD-10-CM Diagnosis Code Q76.49
  Other congenital malformations of spine, not associated with scoliosis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of vertebra NOS
  Congenital fusion of spine NOS
  Congenital malformation of lumbosacral (joint) (region) NOS
  Congenital malformation of spine NOS
  Hemivertebra NOS
  Malformation of spine NOS
  Platyspondylisis NOS
  Supernumerary vertebra NOS
- vulva Q52.71
  ICD-10-CM Diagnosis Code Q52.71
  Congenital absence of vulva
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt

Index Terms Starting With 'A' (Agenesis)

Agenesis

Congenital malformations of adrenal gland

Other specified congenital malformations of digestive system

Other specified congenital malformations of upper alimentary tract

Congenital absence, atresia and stenosis of anus without fistula

Congenital absence, atresia and stenosis of anus with fistula

Absence and aplasia of aorta

Congenital absence, atresia and stenosis of other parts of large intestine

Congenital complete absence of upper limb

Congenital absence of upper arm and forearm with hand present

Congenital malformation of peripheral vascular system, unspecified

Other malformations of cerebral vessels

Malformation of coronary vessels

Other congenital malformations of pulmonary artery

Other specified congenital malformations of peripheral vascular system

Congenital absence and hypoplasia of umbilical artery

Congenital absence, atresia and stricture of auditory canal (external)

Congenital absence of (ear) auricle

Other congenital malformations of bile ducts

Congenital absence of bladder and urethra

Congenital malformation of musculoskeletal system, unspecified

Anencephaly

Other reduction deformities of brain

Other congenital malformations of breast

Congenital absence of breast with absent nipple

Other congenital malformations of bronchus

Absence and agenesis of lacrimal apparatus

Congenital malformation of musculoskeletal system, unspecified

Congenital absence, atresia and stenosis of other parts of large intestine

Other reduction deformities of brain

Agenesis and aplasia of cervix

Other specified congenital malformations of face and neck

Other congenital malformations of eyelid

Congenital malformation of circulatory system, unspecified

Other congenital malformations of upper limb(s), including shoulder girdle

Congenital malformation of clitoris

Other congenital malformations of spine, not associated with scoliosis

Congenital absence, atresia and stenosis of large intestine, part unspecified

Congenital absence, atresia and stenosis of other parts of large intestine

Congenital malformations of corpus callosum

Other congenital malformations of larynx

Other congenital malformations of diaphragm

Other specified congenital malformations of digestive system

Other specified congenital malformations of upper alimentary tract

Other specified congenital malformations of circulatory system

Congenital absence, atresia and stenosis of duodenum

Congenital malformation of ear causing impairment of hearing, unspecified

Congenital absence of (ear) auricle

Other specified congenital malformations of ear

Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate

Congenital malformations of other endocrine glands

Other congenital malformations of larynx

Other congenital malformations of esophagus

Absence of eustachian tube

Other anophthalmos

Other specified congenital malformations of eye

Other congenital malformations of eyelid

Other specified congenital malformations of skull and face bones

Other specified congenital malformations of face and neck

Other congenital malformations of fallopian tube and broad ligament

Congenital absence of foot and toe(s)

Congenital absence of both forearm and hand

Agenesis, aplasia and hypoplasia of gallbladder

Other specified congenital malformations of stomach

Other specified congenital malformations of female genitalia

Congenital absence of vulva

Other specified congenital malformations of female genitalia

Other specified congenital malformations of male genital organs

Other congenital malformations of larynx

Congenital alopecia

Congenital absence of hand and finger

Other specified congenital malformations of heart

Other specified congenital malformations of heart

Pulmonary valve atresia

Other congenital malformations of liver

Other congenital malformations of vagina

Congenital absence, atresia and stenosis of ileum

Congenital malformation of ear ossicles

Congenital absence, atresia and stenosis of small intestine, part unspecified