• Agenesis

    • adrenal Q89.1
      (gland)
      ICD-10-CM Diagnosis Code Q89.1

      Congenital malformations of adrenal gland

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Type 1 Excludes
      • adrenogenital disorders (E25.-)
      • congenital adrenal hyperplasia (E25.0)
    • alimentary tract (complete) (partial) Q45.8
      ICD-10-CM Diagnosis Code Q45.8

      Other specified congenital malformations of digestive system

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence (complete) (partial) of alimentary tract NOS
      • Duplication of digestive system
      • Malposition, congenital of digestive system
      • upper Q40.8
        ICD-10-CM Diagnosis Code Q40.8

        Other specified congenital malformations of upper alimentary tract

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • anus, anal (canal) Q42.3
      ICD-10-CM Diagnosis Code Q42.3

      Congenital absence, atresia and stenosis of anus without fistula

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Imperforate anus
      • with fistula Q42.2
        ICD-10-CM Diagnosis Code Q42.2

        Congenital absence, atresia and stenosis of anus with fistula

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • aorta Q25.41
      ICD-10-CM Diagnosis Code Q25.41

      Absence and aplasia of aorta

        2017 - New Code 2018 2019 2020 Billable/Specific Code POA Exempt
    • appendix Q42.8
      ICD-10-CM Diagnosis Code Q42.8

      Congenital absence, atresia and stenosis of other parts of large intestine

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • arm (complete) Q71.0-
      ICD-10-CM Diagnosis Code Q71.0-

      Congenital complete absence of upper limb

        2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
      • with hand present Q71.1-
        ICD-10-CM Diagnosis Code Q71.1-

        Congenital absence of upper arm and forearm with hand present

          2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    • artery (peripheral) Q27.9
      ICD-10-CM Diagnosis Code Q27.9

      Congenital malformation of peripheral vascular system, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Anomaly of artery or vein NOS
      • brain Q28.3
        ICD-10-CM Diagnosis Code Q28.3

        Other malformations of cerebral vessels

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital cerebral aneurysm (nonruptured)
        • Congenital malformation of cerebral vessels NOS
        • Developmental venous anomaly
      • coronary Q24.5
        ICD-10-CM Diagnosis Code Q24.5

        Malformation of coronary vessels

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital coronary (artery) aneurysm
      • pulmonary Q25.79
        ICD-10-CM Diagnosis Code Q25.79

        Other congenital malformations of pulmonary artery

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Aberrant pulmonary artery
        • Agenesis of pulmonary artery
        • Congenital aneurysm of pulmonary artery
        • Congenital anomaly of pulmonary artery
        • Hypoplasia of pulmonary artery
      • specified NEC Q27.8
        ICD-10-CM Diagnosis Code Q27.8

        Other specified congenital malformations of peripheral vascular system

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Absence of peripheral vascular system
        • Atresia of peripheral vascular system
        • Congenital aneurysm (peripheral)
        • Congenital stricture, artery
        • Congenital varix
        Type 1 Excludes
        • arteriovenous malformation (Q27.3-)
      • umbilical Q27.0
        ICD-10-CM Diagnosis Code Q27.0

        Congenital absence and hypoplasia of umbilical artery

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Single umbilical artery
    • auditory Q16.1
      (canal) (external)
      ICD-10-CM Diagnosis Code Q16.1

      Congenital absence, atresia and stricture of auditory canal (external)

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital atresia or stricture of osseous meatus
    • auricle Q16.0
      (ear)
      ICD-10-CM Diagnosis Code Q16.0

      Congenital absence of (ear) auricle

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • bile duct or passage Q44.5
      ICD-10-CM Diagnosis Code Q44.5

      Other congenital malformations of bile ducts

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Accessory hepatic duct
      • Biliary duct duplication
      • Congenital malformation of bile duct NOS
      • Cystic duct duplication
    • bladder Q64.5
      ICD-10-CM Diagnosis Code Q64.5

      Congenital absence of bladder and urethra

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • bone Q79.9
      ICD-10-CM Diagnosis Code Q79.9

      Congenital malformation of musculoskeletal system, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of musculoskeletal system NOS
      • Congenital deformity of musculoskeletal system NOS
    • brain Q00.0
      ICD-10-CM Diagnosis Code Q00.0

      Anencephaly

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Acephaly
      • Acrania
      • Amyelencephaly
      • Hemianencephaly
      • Hemicephaly
      • part of Q04.3
        ICD-10-CM Diagnosis Code Q04.3

        Other reduction deformities of brain

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Absence of part of brain
        • Agenesis of part of brain
        • Agyria
        • Aplasia of part of brain
        • Hydranencephaly
        • Hypoplasia of part of brain
        • Lissencephaly
        • Microgyria
        • Pachygyria
        Type 1 Excludes
        • congenital malformations of corpus callosum (Q04.0)
    • breast (with nipple present) Q83.8
      ICD-10-CM Diagnosis Code Q83.8

      Other congenital malformations of breast

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • with absent nipple Q83.0
        ICD-10-CM Diagnosis Code Q83.0

        Congenital absence of breast with absent nipple

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • bronchus Q32.4
      ICD-10-CM Diagnosis Code Q32.4

      Other congenital malformations of bronchus

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of bronchus
      • Agenesis of bronchus
      • Atresia of bronchus
      • Congenital diverticulum of bronchus
      • Congenital malformation of bronchus NOS
    • canaliculus lacrimalis Q10.4
      ICD-10-CM Diagnosis Code Q10.4

      Absence and agenesis of lacrimal apparatus

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of punctum lacrimale
    • carpus - see Agenesis, hand
    • cartilage Q79.9
      ICD-10-CM Diagnosis Code Q79.9

      Congenital malformation of musculoskeletal system, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of musculoskeletal system NOS
      • Congenital deformity of musculoskeletal system NOS
    • cecum Q42.8
      ICD-10-CM Diagnosis Code Q42.8

      Congenital absence, atresia and stenosis of other parts of large intestine

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • cerebellum Q04.3
      ICD-10-CM Diagnosis Code Q04.3

      Other reduction deformities of brain

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of part of brain
      • Agenesis of part of brain
      • Agyria
      • Aplasia of part of brain
      • Hydranencephaly
      • Hypoplasia of part of brain
      • Lissencephaly
      • Microgyria
      • Pachygyria
      Type 1 Excludes
      • congenital malformations of corpus callosum (Q04.0)
    • cervix Q51.5
      ICD-10-CM Diagnosis Code Q51.5

      Agenesis and aplasia of cervix

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of cervix
    • chin Q18.8
      ICD-10-CM Diagnosis Code Q18.8

      Other specified congenital malformations of face and neck

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Medial cyst of face and neck
      • Medial fistula of face and neck
      • Medial sinus of face and neck
    • cilia Q10.3
      ICD-10-CM Diagnosis Code Q10.3

      Other congenital malformations of eyelid

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Ablepharon
      • Blepharophimosis, congenital
      • Coloboma of eyelid
      • Congenital absence or agenesis of cilia
      • Congenital absence or agenesis of eyelid
      • Congenital accessory eyelid
      • Congenital accessory eye muscle
      • Congenital malformation of eyelid NOS
    • circulatory system, part NOS Q28.9
      ICD-10-CM Diagnosis Code Q28.9

      Congenital malformation of circulatory system, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • clavicle Q74.0
      ICD-10-CM Diagnosis Code Q74.0

      Other congenital malformations of upper limb(s), including shoulder girdle

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Accessory carpal bones
      • Cleidocranial dysostosis
      • Congenital pseudarthrosis of clavicle
      • Macrodactylia (fingers)
      • Madelung's deformity
      • Radioulnar synostosis
      • Sprengel's deformity
      • Triphalangeal thumb
    • clitoris Q52.6
      ICD-10-CM Diagnosis Code Q52.6

      Congenital malformation of clitoris

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • coccyx Q76.49
      ICD-10-CM Diagnosis Code Q76.49

      Other congenital malformations of spine, not associated with scoliosis

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of vertebra NOS
      • Congenital fusion of spine NOS
      • Congenital malformation of lumbosacral (joint) (region) NOS
      • Congenital malformation of spine NOS
      • Hemivertebra NOS
      • Malformation of spine NOS
      • Platyspondylisis NOS
      • Supernumerary vertebra NOS
    • colon Q42.9
      ICD-10-CM Diagnosis Code Q42.9

      Congenital absence, atresia and stenosis of large intestine, part unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • specified NEC Q42.8
        ICD-10-CM Diagnosis Code Q42.8

        Congenital absence, atresia and stenosis of other parts of large intestine

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • corpus callosum Q04.0
      ICD-10-CM Diagnosis Code Q04.0

      Congenital malformations of corpus callosum

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Agenesis of corpus callosum
    • cricoid cartilage Q31.8
      ICD-10-CM Diagnosis Code Q31.8

      Other congenital malformations of larynx

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of larynx
      • Agenesis of larynx
      • Atresia of larynx
      • Congenital cleft thyroid cartilage
      • Congenital fissure of epiglottis
      • Congenital stenosis of larynx NEC
      • Posterior cleft of cricoid cartilage
    • diaphragm Q79.1
      (with hernia)
      ICD-10-CM Diagnosis Code Q79.1

      Other congenital malformations of diaphragm

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of diaphragm
      • Congenital malformation of diaphragm NOS
      • Eventration of diaphragm
    • digestive organ(s) or tract (complete) (partial) Q45.8
      ICD-10-CM Diagnosis Code Q45.8

      Other specified congenital malformations of digestive system

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence (complete) (partial) of alimentary tract NOS
      • Duplication of digestive system
      • Malposition, congenital of digestive system
      • upper Q40.8
        ICD-10-CM Diagnosis Code Q40.8

        Other specified congenital malformations of upper alimentary tract

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • ductus arteriosus Q28.8
      ICD-10-CM Diagnosis Code Q28.8

      Other specified congenital malformations of circulatory system

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital aneurysm, specified site NEC
      • Spinal vessel anomaly
    • duodenum Q41.0
      ICD-10-CM Diagnosis Code Q41.0

      Congenital absence, atresia and stenosis of duodenum

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • ear Q16.9
      ICD-10-CM Diagnosis Code Q16.9

      Congenital malformation of ear causing impairment of hearing, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of ear NOS
      • auricle Q16.0
        ICD-10-CM Diagnosis Code Q16.0

        Congenital absence of (ear) auricle

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • lobe Q17.8
        ICD-10-CM Diagnosis Code Q17.8

        Other specified congenital malformations of ear

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital absence of lobe of ear
    • ejaculatory duct Q55.4
      ICD-10-CM Diagnosis Code Q55.4

      Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate

        2016 2017 2018 2019 2020 Billable/Specific Code Male Dx POA Exempt
      Applicable To
      • Absence or aplasia of prostate
      • Absence or aplasia of spermatic cord
      • Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
    • endocrine Q89.2
      (gland)
      ICD-10-CM Diagnosis Code Q89.2

      Congenital malformations of other endocrine glands

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of parathyroid or thyroid gland
      • Persistent thyroglossal duct
      • Thyroglossal cyst
      Type 1 Excludes
      • congenital goiter (E03.0)
      • congenital hypothyroidism (E03.1)
    • epiglottis Q31.8
      ICD-10-CM Diagnosis Code Q31.8

      Other congenital malformations of larynx

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of larynx
      • Agenesis of larynx
      • Atresia of larynx
      • Congenital cleft thyroid cartilage
      • Congenital fissure of epiglottis
      • Congenital stenosis of larynx NEC
      • Posterior cleft of cricoid cartilage
    • esophagus Q39.8
      ICD-10-CM Diagnosis Code Q39.8

      Other congenital malformations of esophagus

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of esophagus
      • Congenital displacement of esophagus
      • Congenital duplication of esophagus
    • eustachian tube Q16.2
      ICD-10-CM Diagnosis Code Q16.2

      Absence of eustachian tube

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • eye Q11.1
      ICD-10-CM Diagnosis Code Q11.1

      Other anophthalmos

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Anophthalmos NOS
      • Agenesis of eye
      • Aplasia of eye
      • adnexa Q15.8
        ICD-10-CM Diagnosis Code Q15.8

        Other specified congenital malformations of eye

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • eyelid Q10.3
      (fold)
      ICD-10-CM Diagnosis Code Q10.3

      Other congenital malformations of eyelid

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Ablepharon
      • Blepharophimosis, congenital
      • Coloboma of eyelid
      • Congenital absence or agenesis of cilia
      • Congenital absence or agenesis of eyelid
      • Congenital accessory eyelid
      • Congenital accessory eye muscle
      • Congenital malformation of eyelid NOS
    • face
      • bones NEC Q75.8
        ICD-10-CM Diagnosis Code Q75.8

        Other specified congenital malformations of skull and face bones

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Absence of skull bone, congenital
        • Congenital deformity of forehead
        • Platybasia
      • specified part NEC Q18.8
        ICD-10-CM Diagnosis Code Q18.8

        Other specified congenital malformations of face and neck

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Medial cyst of face and neck
        • Medial fistula of face and neck
        • Medial sinus of face and neck
    • fallopian tube Q50.6
      ICD-10-CM Diagnosis Code Q50.6

      Other congenital malformations of fallopian tube and broad ligament

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of fallopian tube and broad ligament
      • Accessory fallopian tube and broad ligament
      • Atresia of fallopian tube and broad ligament
      • Congenital malformation of fallopian tube or broad ligament NOS
    • femur - see Defect, reduction, lower limb, longitudinal, femur
    • fibula - see Defect, reduction, lower limb, longitudinal, fibula
    • finger (complete) (partial) - see Agenesis, hand
    • foot Q72.3-
      (and toes) (complete) (partial)
      ICD-10-CM Diagnosis Code Q72.3-

      Congenital absence of foot and toe(s)

        2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    • forearm (with hand present) - see Agenesis, arm, with hand present
      • and hand Q71.2-
        ICD-10-CM Diagnosis Code Q71.2-

        Congenital absence of both forearm and hand

          2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    • gallbladder Q44.0
      ICD-10-CM Diagnosis Code Q44.0

      Agenesis, aplasia and hypoplasia of gallbladder

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of gallbladder
    • gastric Q40.2
      ICD-10-CM Diagnosis Code Q40.2

      Other specified congenital malformations of stomach

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital displacement of stomach
      • Congenital diverticulum of stomach
      • Congenital hourglass stomach
      • Congenital duplication of stomach
      • Megalogastria
      • Microgastria
    • genitalia, genital (organ(s))
      • female Q52.8
        ICD-10-CM Diagnosis Code Q52.8

        Other specified congenital malformations of female genitalia

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        • external Q52.71
          ICD-10-CM Diagnosis Code Q52.71

          Congenital absence of vulva

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        • internal NEC Q52.8
          ICD-10-CM Diagnosis Code Q52.8

          Other specified congenital malformations of female genitalia

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • male Q55.8
        ICD-10-CM Diagnosis Code Q55.8

        Other specified congenital malformations of male genital organs

          2016 2017 2018 2019 2020 Billable/Specific Code Male Dx POA Exempt
    • glottis Q31.8
      ICD-10-CM Diagnosis Code Q31.8

      Other congenital malformations of larynx

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of larynx
      • Agenesis of larynx
      • Atresia of larynx
      • Congenital cleft thyroid cartilage
      • Congenital fissure of epiglottis
      • Congenital stenosis of larynx NEC
      • Posterior cleft of cricoid cartilage
    • hair Q84.0
      ICD-10-CM Diagnosis Code Q84.0

      Congenital alopecia

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital atrichosis
    • hand Q71.3-
      (and fingers) (complete) (partial)
      ICD-10-CM Diagnosis Code Q71.3-

      Congenital absence of hand and finger

        2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    • heart Q24.8
      ICD-10-CM Diagnosis Code Q24.8

      Other specified congenital malformations of heart

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital diverticulum of left ventricle
      • Congenital malformation of myocardium
      • Congenital malformation of pericardium
      • Malposition of heart
      • Uhl's disease
      • valve NEC Q24.8
        ICD-10-CM Diagnosis Code Q24.8

        Other specified congenital malformations of heart

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital diverticulum of left ventricle
        • Congenital malformation of myocardium
        • Congenital malformation of pericardium
        • Malposition of heart
        • Uhl's disease
        • pulmonary Q22.0
          ICD-10-CM Diagnosis Code Q22.0

          Pulmonary valve atresia

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • hepatic Q44.7
      ICD-10-CM Diagnosis Code Q44.7

      Other congenital malformations of liver

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Accessory liver
      • Alagille's syndrome
      • Congenital absence of liver
      • Congenital hepatomegaly
      • Congenital malformation of liver NOS
    • humerus - see Defect, reduction, upper limb
    • hymen Q52.4
      ICD-10-CM Diagnosis Code Q52.4

      Other congenital malformations of vagina

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Canal of Nuck cyst, congenital
      • Congenital malformation of vagina NOS
      • Embryonic vaginal cyst
      • Gartner's duct cyst
    • ileum Q41.2
      ICD-10-CM Diagnosis Code Q41.2

      Congenital absence, atresia and stenosis of ileum

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • incus Q16.3
      ICD-10-CM Diagnosis Code Q16.3

      Congenital malformation of ear ossicles

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital fusion of ear ossicles
    • intestine (small) Q41.9
      ICD-10-CM Diagnosis Code Q41.9

      Congenital absence, atresia and stenosis of small intestine, part unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence, atresia and stenosis of intestine NOS
      • large Q42.9
        ICD-10-CM Diagnosis Code Q42.9

        Congenital absence, atresia and stenosis of large intestine, part unspecified

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        • specified NEC Q42.8
          ICD-10-CM Diagnosis Code Q42.8

          Congenital absence, atresia and stenosis of other parts of large intestine

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • iris Q13.1
      (dilator fibers)
      ICD-10-CM Diagnosis Code Q13.1

      Absence of iris

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Aniridia
      Use Additional
      • code for associated glaucoma (H42)
    • jaw M26.09
      ICD-10-CM Diagnosis Code M26.09

      Other specified anomalies of jaw size

        2016 2017 2018 2019 2020 Billable/Specific Code
    • jejunum Q41.1
      ICD-10-CM Diagnosis Code Q41.1

      Congenital absence, atresia and stenosis of jejunum

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Apple peel syndrome
      • Imperforate jejunum
    • kidney(s) (partial) Q60.2
      ICD-10-CM Diagnosis Code Q60.2

      Renal agenesis, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • bilateral Q60.1
        ICD-10-CM Diagnosis Code Q60.1

        Renal agenesis, bilateral

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • unilateral Q60.0
        ICD-10-CM Diagnosis Code Q60.0

        Renal agenesis, unilateral

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • labium Q52.71
      (majus) (minus)
      ICD-10-CM Diagnosis Code Q52.71

      Congenital absence of vulva

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • labyrinth, membranous Q16.5
      ICD-10-CM Diagnosis Code Q16.5

      Congenital malformation of inner ear

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of membranous labyrinth
      • Congenital anomaly of organ of Corti
    • lacrimal apparatus Q10.4
      ICD-10-CM Diagnosis Code Q10.4

      Absence and agenesis of lacrimal apparatus

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of punctum lacrimale
    • larynx Q31.8
      ICD-10-CM Diagnosis Code Q31.8

      Other congenital malformations of larynx

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of larynx
      • Agenesis of larynx
      • Atresia of larynx
      • Congenital cleft thyroid cartilage
      • Congenital fissure of epiglottis
      • Congenital stenosis of larynx NEC
      • Posterior cleft of cricoid cartilage
    • leg (complete) Q72.0-
      ICD-10-CM Diagnosis Code Q72.0-

      Congenital complete absence of lower limb

        2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
      • lower leg (with foot present) - see Agenesis, leg, with foot present
        • and foot Q72.2-
          ICD-10-CM Diagnosis Code Q72.2-

          Congenital absence of both lower leg and foot

            2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
      • with foot present Q72.1-
        ICD-10-CM Diagnosis Code Q72.1-

        Congenital absence of thigh and lower leg with foot present

          2016 2017 2018 2019 2020 Non-Billable/Non-Specific Code
    • lens Q12.3
      ICD-10-CM Diagnosis Code Q12.3

      Congenital aphakia

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • limb (complete) Q73.0
      ICD-10-CM Diagnosis Code Q73.0

      Congenital absence of unspecified limb(s)

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Amelia NOS
    • lip Q38.0
      ICD-10-CM Diagnosis Code Q38.0

      Congenital malformations of lips, not elsewhere classified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital fistula of lip
      • Congenital malformation of lip NOS
      • Van der Woude's syndrome
      Type 1 Excludes
    • liver Q44.7
      ICD-10-CM Diagnosis Code Q44.7

      Other congenital malformations of liver

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Accessory liver
      • Alagille's syndrome
      • Congenital absence of liver
      • Congenital hepatomegaly
      • Congenital malformation of liver NOS
    • lung Q33.3
      (fissure) (lobe) (bilateral) (unilateral)
      ICD-10-CM Diagnosis Code Q33.3

      Agenesis of lung

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of lung (lobe)
    • mandible, maxilla M26.09
      ICD-10-CM Diagnosis Code M26.09

      Other specified anomalies of jaw size

        2016 2017 2018 2019 2020 Billable/Specific Code
    • metacarpus - see Agenesis, hand
    • metatarsus - see Agenesis, foot
    • muscle Q79.8
      ICD-10-CM Diagnosis Code Q79.8

      Other congenital malformations of musculoskeletal system

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of muscle
      • Absence of tendon
      • Accessory muscle
      • Amyotrophia congenita
      • Congenital constricting bands
      • Congenital shortening of tendon
      • Poland syndrome
      • eyelid Q10.3
        ICD-10-CM Diagnosis Code Q10.3

        Other congenital malformations of eyelid

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Ablepharon
        • Blepharophimosis, congenital
        • Coloboma of eyelid
        • Congenital absence or agenesis of cilia
        • Congenital absence or agenesis of eyelid
        • Congenital accessory eyelid
        • Congenital accessory eye muscle
        • Congenital malformation of eyelid NOS
      • ocular Q15.8
        ICD-10-CM Diagnosis Code Q15.8

        Other specified congenital malformations of eye

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • musculoskeletal system NEC Q79.8
      ICD-10-CM Diagnosis Code Q79.8

      Other congenital malformations of musculoskeletal system

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of muscle
      • Absence of tendon
      • Accessory muscle
      • Amyotrophia congenita
      • Congenital constricting bands
      • Congenital shortening of tendon
      • Poland syndrome
    • nail Q84.3
      (s)
      ICD-10-CM Diagnosis Code Q84.3

      Anonychia

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Type 1 Excludes
      • nail patella syndrome (Q87.2)
    • neck, part Q18.8
      ICD-10-CM Diagnosis Code Q18.8

      Other specified congenital malformations of face and neck

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Medial cyst of face and neck
      • Medial fistula of face and neck
      • Medial sinus of face and neck
    • nerve Q07.8
      ICD-10-CM Diagnosis Code Q07.8

      Other specified congenital malformations of nervous system

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Agenesis of nerve
      • Displacement of brachial plexus
      • Jaw-winking syndrome
      • Marcus Gunn's syndrome
    • nervous system, part NEC Q07.8
      ICD-10-CM Diagnosis Code Q07.8

      Other specified congenital malformations of nervous system

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Agenesis of nerve
      • Displacement of brachial plexus
      • Jaw-winking syndrome
      • Marcus Gunn's syndrome
    • nipple Q83.2
      ICD-10-CM Diagnosis Code Q83.2

      Absent nipple

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • nose Q30.1
      ICD-10-CM Diagnosis Code Q30.1

      Agenesis and underdevelopment of nose

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absent of nose
    • nuclear Q07.8
      ICD-10-CM Diagnosis Code Q07.8

      Other specified congenital malformations of nervous system

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Agenesis of nerve
      • Displacement of brachial plexus
      • Jaw-winking syndrome
      • Marcus Gunn's syndrome
    • organ
      • of Corti Q16.5
        ICD-10-CM Diagnosis Code Q16.5

        Congenital malformation of inner ear

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital anomaly of membranous labyrinth
        • Congenital anomaly of organ of Corti
      • or site not listed - see Anomaly, by site
    • osseous meatus Q16.1
      (ear)
      ICD-10-CM Diagnosis Code Q16.1

      Congenital absence, atresia and stricture of auditory canal (external)

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital atresia or stricture of osseous meatus
    • ovary
      • bilateral Q50.02
        ICD-10-CM Diagnosis Code Q50.02

        Congenital absence of ovary, bilateral

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • unilateral Q50.01
        ICD-10-CM Diagnosis Code Q50.01

        Congenital absence of ovary, unilateral

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • oviduct Q50.6
      ICD-10-CM Diagnosis Code Q50.6

      Other congenital malformations of fallopian tube and broad ligament

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of fallopian tube and broad ligament
      • Accessory fallopian tube and broad ligament
      • Atresia of fallopian tube and broad ligament
      • Congenital malformation of fallopian tube or broad ligament NOS
    • pancreas Q45.0
      ICD-10-CM Diagnosis Code Q45.0

      Agenesis, aplasia and hypoplasia of pancreas

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of pancreas
    • parathyroid Q89.2
      (gland)
      ICD-10-CM Diagnosis Code Q89.2

      Congenital malformations of other endocrine glands

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of parathyroid or thyroid gland
      • Persistent thyroglossal duct
      • Thyroglossal cyst
      Type 1 Excludes
      • congenital goiter (E03.0)
      • congenital hypothyroidism (E03.1)
    • parotid gland Q38.4
      (s)
      ICD-10-CM Diagnosis Code Q38.4

      Congenital malformations of salivary glands and ducts

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Atresia of salivary glands and ducts
      • Congenital absence of salivary glands and ducts
      • Congenital accessory salivary glands and ducts
      • Congenital fistula of salivary gland
    • patella Q74.1
      ICD-10-CM Diagnosis Code Q74.1

      Congenital malformation of knee

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of patella
      • Congenital dislocation of patella
      • Congenital genu valgum
      • Congenital genu varum
      • Rudimentary patella
      Type 1 Excludes
      • congenital dislocation of knee (Q68.2)
      • congenital genu recurvatum (Q68.2)
      • nail patella syndrome (Q87.2)
    • pelvic girdle Q74.2
      (complete) (partial)
      ICD-10-CM Diagnosis Code Q74.2

      Other congenital malformations of lower limb(s), including pelvic girdle

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital fusion of sacroiliac joint
      • Congenital malformation of ankle joint
      • Congenital malformation of sacroiliac joint
      Type 1 Excludes
      • anteversion of femur (neck) (Q65.89)
    • penis Q55.5
      ICD-10-CM Diagnosis Code Q55.5

      Congenital absence and aplasia of penis

        2016 2017 2018 2019 2020 Billable/Specific Code Male Dx POA Exempt
    • pericardium Q24.8
      ICD-10-CM Diagnosis Code Q24.8

      Other specified congenital malformations of heart

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital diverticulum of left ventricle
      • Congenital malformation of myocardium
      • Congenital malformation of pericardium
      • Malposition of heart
      • Uhl's disease
    • pituitary Q89.2
      (gland)
      ICD-10-CM Diagnosis Code Q89.2

      Congenital malformations of other endocrine glands

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of parathyroid or thyroid gland
      • Persistent thyroglossal duct
      • Thyroglossal cyst
      Type 1 Excludes
      • congenital goiter (E03.0)
      • congenital hypothyroidism (E03.1)
    • prostate Q55.4
      ICD-10-CM Diagnosis Code Q55.4

      Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate

        2016 2017 2018 2019 2020 Billable/Specific Code Male Dx POA Exempt
      Applicable To
      • Absence or aplasia of prostate
      • Absence or aplasia of spermatic cord
      • Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
    • punctum lacrimale Q10.4
      ICD-10-CM Diagnosis Code Q10.4

      Absence and agenesis of lacrimal apparatus

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of punctum lacrimale
    • radioulnar - see Defect, reduction, upper limb
    • radius - see Defect, reduction, upper limb, longitudinal, radius
    • rectum Q42.1
      ICD-10-CM Diagnosis Code Q42.1

      Congenital absence, atresia and stenosis of rectum without fistula

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Imperforate rectum
      • with fistula Q42.0
        ICD-10-CM Diagnosis Code Q42.0

        Congenital absence, atresia and stenosis of rectum with fistula

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • renal Q60.2
      ICD-10-CM Diagnosis Code Q60.2

      Renal agenesis, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • bilateral Q60.1
        ICD-10-CM Diagnosis Code Q60.1

        Renal agenesis, bilateral

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • unilateral Q60.0
        ICD-10-CM Diagnosis Code Q60.0

        Renal agenesis, unilateral

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • respiratory organ NEC Q34.8
      ICD-10-CM Diagnosis Code Q34.8

      Other specified congenital malformations of respiratory system

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Atresia of nasopharynx
    • rib Q76.6
      ICD-10-CM Diagnosis Code Q76.6

      Other congenital malformations of ribs

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Accessory rib
      • Congenital absence of rib
      • Congenital fusion of ribs
      • Congenital malformation of ribs NOS
      Type 1 Excludes
      • short rib syndrome (Q77.2)
    • roof of orbit Q75.8
      ICD-10-CM Diagnosis Code Q75.8

      Other specified congenital malformations of skull and face bones

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of skull bone, congenital
      • Congenital deformity of forehead
      • Platybasia
    • round ligament Q52.8
      ICD-10-CM Diagnosis Code Q52.8

      Other specified congenital malformations of female genitalia

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • sacrum Q76.49
      ICD-10-CM Diagnosis Code Q76.49

      Other congenital malformations of spine, not associated with scoliosis

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of vertebra NOS
      • Congenital fusion of spine NOS
      • Congenital malformation of lumbosacral (joint) (region) NOS
      • Congenital malformation of spine NOS
      • Hemivertebra NOS
      • Malformation of spine NOS
      • Platyspondylisis NOS
      • Supernumerary vertebra NOS
    • salivary gland Q38.4
      ICD-10-CM Diagnosis Code Q38.4

      Congenital malformations of salivary glands and ducts

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Atresia of salivary glands and ducts
      • Congenital absence of salivary glands and ducts
      • Congenital accessory salivary glands and ducts
      • Congenital fistula of salivary gland
    • scapula Q74.0
      ICD-10-CM Diagnosis Code Q74.0

      Other congenital malformations of upper limb(s), including shoulder girdle

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Accessory carpal bones
      • Cleidocranial dysostosis
      • Congenital pseudarthrosis of clavicle
      • Macrodactylia (fingers)
      • Madelung's deformity
      • Radioulnar synostosis
      • Sprengel's deformity
      • Triphalangeal thumb
    • scrotum Q55.29
      ICD-10-CM Diagnosis Code Q55.29

      Other congenital malformations of testis and scrotum

        2016 2017 2018 2019 2020 Billable/Specific Code Male Dx POA Exempt
    • seminal vesicles Q55.4
      ICD-10-CM Diagnosis Code Q55.4

      Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate

        2016 2017 2018 2019 2020 Billable/Specific Code Male Dx POA Exempt
      Applicable To
      • Absence or aplasia of prostate
      • Absence or aplasia of spermatic cord
      • Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
    • septum
      • atrial Q21.1
        ICD-10-CM Diagnosis Code Q21.1

        Atrial septal defect

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Coronary sinus defect
        • Patent or persistent foramen ovale
        • Patent or persistent ostium secundum defect (type II)
        • Patent or persistent sinus venosus defect
      • between aorta and pulmonary artery Q21.4
        ICD-10-CM Diagnosis Code Q21.4

        Aortopulmonary septal defect

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Aortic septal defect
        • Aortopulmonary window
      • ventricular Q20.4
        ICD-10-CM Diagnosis Code Q20.4

        Double inlet ventricle

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Common ventricle
        • Cor triloculare biatriatum
        • Single ventricle
    • shoulder girdle Q74.0
      (complete) (partial)
      ICD-10-CM Diagnosis Code Q74.0

      Other congenital malformations of upper limb(s), including shoulder girdle

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Accessory carpal bones
      • Cleidocranial dysostosis
      • Congenital pseudarthrosis of clavicle
      • Macrodactylia (fingers)
      • Madelung's deformity
      • Radioulnar synostosis
      • Sprengel's deformity
      • Triphalangeal thumb
    • skull (bone) Q75.8
      ICD-10-CM Diagnosis Code Q75.8

      Other specified congenital malformations of skull and face bones

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of skull bone, congenital
      • Congenital deformity of forehead
      • Platybasia
      • with
        • anencephaly Q00.0
          ICD-10-CM Diagnosis Code Q00.0

          Anencephaly

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Acephaly
          • Acrania
          • Amyelencephaly
          • Hemianencephaly
          • Hemicephaly
        • encephalocele - see Encephalocele
        • hydrocephalus Q03.9
          ICD-10-CM Diagnosis Code Q03.9

          Congenital hydrocephalus, unspecified

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        • microcephaly Q02
          ICD-10-CM Diagnosis Code Q02

          Microcephaly

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Code First
          • , if applicable, congenital Zika virus disease
          Includes
          • hydromicrocephaly
          • micrencephalon
          Type 1 Excludes
          • Meckel-Gruber syndrome (Q61.9)
    • spermatic cord Q55.4
      ICD-10-CM Diagnosis Code Q55.4

      Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate

        2016 2017 2018 2019 2020 Billable/Specific Code Male Dx POA Exempt
      Applicable To
      • Absence or aplasia of prostate
      • Absence or aplasia of spermatic cord
      • Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
    • spinal cord Q06.0
      ICD-10-CM Diagnosis Code Q06.0

      Amyelia

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • spine Q76.49
      ICD-10-CM Diagnosis Code Q76.49

      Other congenital malformations of spine, not associated with scoliosis

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of vertebra NOS
      • Congenital fusion of spine NOS
      • Congenital malformation of lumbosacral (joint) (region) NOS
      • Congenital malformation of spine NOS
      • Hemivertebra NOS
      • Malformation of spine NOS
      • Platyspondylisis NOS
      • Supernumerary vertebra NOS
    • spleen Q89.01
      ICD-10-CM Diagnosis Code Q89.01

      Asplenia (congenital)

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • sternum Q76.7
      ICD-10-CM Diagnosis Code Q76.7

      Congenital malformation of sternum

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of sternum
      • Sternum bifidum
    • stomach Q40.2
      ICD-10-CM Diagnosis Code Q40.2

      Other specified congenital malformations of stomach

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital displacement of stomach
      • Congenital diverticulum of stomach
      • Congenital hourglass stomach
      • Congenital duplication of stomach
      • Megalogastria
      • Microgastria
    • submaxillary gland Q38.4
      (s) (congenital)
      ICD-10-CM Diagnosis Code Q38.4

      Congenital malformations of salivary glands and ducts

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Atresia of salivary glands and ducts
      • Congenital absence of salivary glands and ducts
      • Congenital accessory salivary glands and ducts
      • Congenital fistula of salivary gland
    • tarsus - see Agenesis, foot
    • tendon Q79.8
      ICD-10-CM Diagnosis Code Q79.8

      Other congenital malformations of musculoskeletal system

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of muscle
      • Absence of tendon
      • Accessory muscle
      • Amyotrophia congenita
      • Congenital constricting bands
      • Congenital shortening of tendon
      • Poland syndrome
    • testicle Q55.0
      ICD-10-CM Diagnosis Code Q55.0

      Absence and aplasia of testis

        2016 2017 2018 2019 2020 Billable/Specific Code Male Dx POA Exempt
      Applicable To
      • Monorchism
    • thymus Q89.2
      (gland)
      ICD-10-CM Diagnosis Code Q89.2

      Congenital malformations of other endocrine glands

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of parathyroid or thyroid gland
      • Persistent thyroglossal duct
      • Thyroglossal cyst
      Type 1 Excludes
      • congenital goiter (E03.0)
      • congenital hypothyroidism (E03.1)
    • thyroid (gland) E03.1
      ICD-10-CM Diagnosis Code E03.1

      Congenital hypothyroidism without goiter

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Aplasia of thyroid (with myxedema)
      • Congenital atrophy of thyroid
      • Congenital hypothyroidism NOS
      • cartilage Q31.8
        ICD-10-CM Diagnosis Code Q31.8

        Other congenital malformations of larynx

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Absence of larynx
        • Agenesis of larynx
        • Atresia of larynx
        • Congenital cleft thyroid cartilage
        • Congenital fissure of epiglottis
        • Congenital stenosis of larynx NEC
        • Posterior cleft of cricoid cartilage
    • tibia - see Defect, reduction, lower limb, longitudinal, tibia
    • tibiofibular - see Defect, reduction, lower limb, specified type NEC
    • toe (and foot) (complete) (partial) - see Agenesis, foot
    • tongue Q38.3
      ICD-10-CM Diagnosis Code Q38.3

      Other congenital malformations of tongue

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Aglossia
      • Bifid tongue
      • Congenital adhesion of tongue
      • Congenital fissure of tongue
      • Congenital malformation of tongue NOS
      • Double tongue
      • Hypoglossia
      • Hypoplasia of tongue
      • Microglossia
    • trachea Q32.1
      (cartilage)
      ICD-10-CM Diagnosis Code Q32.1

      Other congenital malformations of trachea

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Atresia of trachea
      • Congenital anomaly of tracheal cartilage
      • Congenital dilatation of trachea
      • Congenital malformation of trachea
      • Congenital stenosis of trachea
      • Congenital tracheocele
    • ulna - see Defect, reduction, upper limb, longitudinal, ulna
    • upper limb - see Agenesis, arm
    • ureter Q62.4
      ICD-10-CM Diagnosis Code Q62.4

      Agenesis of ureter

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence ureter
    • urethra Q64.5
      ICD-10-CM Diagnosis Code Q64.5

      Congenital absence of bladder and urethra

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • urinary tract NEC Q64.8
      ICD-10-CM Diagnosis Code Q64.8

      Other specified congenital malformations of urinary system

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • uterus Q51.0
      ICD-10-CM Diagnosis Code Q51.0

      Agenesis and aplasia of uterus

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of uterus
    • uvula Q38.5
      ICD-10-CM Diagnosis Code Q38.5

      Congenital malformations of palate, not elsewhere classified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of uvula
      • Congenital malformation of palate NOS
      • Congenital high arched palate
      Type 1 Excludes
      • cleft palate (Q35.-)
      • cleft palate with cleft lip (Q37.-)
    • vagina Q52.0
      ICD-10-CM Diagnosis Code Q52.0

      Congenital absence of vagina

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Vaginal agenesis, total or partial
    • vas deferens Q55.4
      ICD-10-CM Diagnosis Code Q55.4

      Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate

        2016 2017 2018 2019 2020 Billable/Specific Code Male Dx POA Exempt
      Applicable To
      • Absence or aplasia of prostate
      • Absence or aplasia of spermatic cord
      • Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
    • vein(s) (peripheral) Q27.9
      ICD-10-CM Diagnosis Code Q27.9

      Congenital malformation of peripheral vascular system, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Anomaly of artery or vein NOS
      • brain Q28.3
        ICD-10-CM Diagnosis Code Q28.3

        Other malformations of cerebral vessels

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital cerebral aneurysm (nonruptured)
        • Congenital malformation of cerebral vessels NOS
        • Developmental venous anomaly
      • great NEC Q26.8
        ICD-10-CM Diagnosis Code Q26.8

        Other congenital malformations of great veins

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Absence of vena cava (inferior) (superior)
        • Azygos continuation of inferior vena cava
        • Persistent left posterior cardinal vein
        • Scimitar syndrome
      • portal Q26.5
        ICD-10-CM Diagnosis Code Q26.5

        Anomalous portal venous connection

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
    • vena cava Q26.8
      (inferior) (superior)
      ICD-10-CM Diagnosis Code Q26.8

      Other congenital malformations of great veins

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of vena cava (inferior) (superior)
      • Azygos continuation of inferior vena cava
      • Persistent left posterior cardinal vein
      • Scimitar syndrome
    • vermis of cerebellum Q04.3
      ICD-10-CM Diagnosis Code Q04.3

      Other reduction deformities of brain

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of part of brain
      • Agenesis of part of brain
      • Agyria
      • Aplasia of part of brain
      • Hydranencephaly
      • Hypoplasia of part of brain
      • Lissencephaly
      • Microgyria
      • Pachygyria
      Type 1 Excludes
      • congenital malformations of corpus callosum (Q04.0)
    • vertebra Q76.49
      ICD-10-CM Diagnosis Code Q76.49

      Other congenital malformations of spine, not associated with scoliosis

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of vertebra NOS
      • Congenital fusion of spine NOS
      • Congenital malformation of lumbosacral (joint) (region) NOS
      • Congenital malformation of spine NOS
      • Hemivertebra NOS
      • Malformation of spine NOS
      • Platyspondylisis NOS
      • Supernumerary vertebra NOS
    • vulva Q52.71
      ICD-10-CM Diagnosis Code Q52.71

      Congenital absence of vulva

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt