2023 ICD-10-CM Index
'A' Terms
Index Terms Starting With 'A' (Anomaly, anomalous)

Index Terms Starting With 'A' (Anomaly, anomalous)

Anomaly, anomalous (congenital) (unspecified type) Q89.9
ICD-10-CM Diagnosis Code Q89.9
Congenital malformation, unspecified
Applicable To
Congenital anomaly NOS
Congenital deformity NOS
- abdominal wall NEC Q79.59
  ICD-10-CM Diagnosis Code Q79.59
  Other congenital malformations of abdominal wall
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- acoustic nerve Q07.8
  ICD-10-CM Diagnosis Code Q07.8
  Other specified congenital malformations of nervous system
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Agenesis of nerve
  Displacement of brachial plexus
  Jaw-winking syndrome
  Marcus Gunn's syndrome
- adrenal Q89.1
  (gland)
  ICD-10-CM Diagnosis Code Q89.1
  Congenital malformations of adrenal gland
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Type 1 Excludes
  adrenogenital disorders (E25.-)
  congenital adrenal hyperplasia (E25.0)
- Alder D72.0
  (-Reilly) (leukocyte granulation)
  ICD-10-CM Diagnosis Code D72.0
  Genetic anomalies of leukocytes
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Alder (granulation) (granulocyte) anomaly
  Alder syndrome
  Hereditary leukocytic hypersegmentation
  Hereditary leukocytic hyposegmentation
  Hereditary leukomelanopathy
  May-Hegglin (granulation) (granulocyte) anomaly
  May-Hegglin syndrome
  Pelger-Huët (granulation) (granulocyte) anomaly
  Pelger-Huët syndrome
  Type 1 Excludes
  Chédiak (-Steinbrinck)-Higashi syndrome (E70.330)
- alimentary tract Q45.9
  ICD-10-CM Diagnosis Code Q45.9
  Congenital malformation of digestive system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of digestive system
  Congenital deformity of digestive system
  - upper Q40.9
    ICD-10-CM Diagnosis Code Q40.9
    Congenital malformation of upper alimentary tract, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital anomaly of upper alimentary tract
    Congenital deformity of upper alimentary tract
- alveolar M26.70
  ICD-10-CM Diagnosis Code M26.70
  Unspecified alveolar anomaly
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - hyperplasia M26.79
    ICD-10-CM Diagnosis Code M26.79
    Other specified alveolar anomalies
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - mandibular M26.72
      ICD-10-CM Diagnosis Code M26.72
      Alveolar mandibular hyperplasia
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - maxillary M26.71
      ICD-10-CM Diagnosis Code M26.71
      Alveolar maxillary hyperplasia
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - hypoplasia M26.79
    ICD-10-CM Diagnosis Code M26.79
    Other specified alveolar anomalies
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - mandibular M26.74
      ICD-10-CM Diagnosis Code M26.74
      Alveolar mandibular hypoplasia
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - maxillary M26.73
      ICD-10-CM Diagnosis Code M26.73
      Alveolar maxillary hypoplasia
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - ridge M26.79
    (process)
    ICD-10-CM Diagnosis Code M26.79
    Other specified alveolar anomalies
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - specified NEC M26.79
    ICD-10-CM Diagnosis Code M26.79
    Other specified alveolar anomalies
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
- ankle Q74.2
  (joint)
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- anus Q43.9
  ICD-10-CM Diagnosis Code Q43.9
  Congenital malformation of intestine, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- aorta (arch) Q25.40
  ICD-10-CM Diagnosis Code Q25.40
  Congenital malformation of aorta unspecified
  2017 - New Code 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - coarctation Q25.1
    (preductal) (postductal)
    ICD-10-CM Diagnosis Code Q25.1
    Coarctation of aorta
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Coarctation of aorta (preductal) (postductal)
    Stenosis of aorta
- aortic cusp or valve Q23.9
  ICD-10-CM Diagnosis Code Q23.9
  Congenital malformation of aortic and mitral valves, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- appendix Q43.8
  ICD-10-CM Diagnosis Code Q43.8
  Other specified congenital malformations of intestine
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital blind loop syndrome
  Congenital diverticulitis, colon
  Congenital diverticulum, intestine
  Dolichocolon
  Megaloappendix
  Megaloduodenum
  Microcolon
  Transposition of appendix
  Transposition of colon
  Transposition of intestine
- apple peel syndrome Q41.1
  ICD-10-CM Diagnosis Code Q41.1
  Congenital absence, atresia and stenosis of jejunum
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Apple peel syndrome
  Imperforate jejunum
- aqueduct of Sylvius Q03.0
  ICD-10-CM Diagnosis Code Q03.0
  Malformations of aqueduct of Sylvius
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Anomaly of aqueduct of Sylvius
  Obstruction of aqueduct of Sylvius, congenital
  Stenosis of aqueduct of Sylvius
  - with spina bifida - see Spina bifida, with hydrocephalus
- arm Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- arteriovenous NEC
  - coronary Q24.5
    ICD-10-CM Diagnosis Code Q24.5
    Malformation of coronary vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital coronary (artery) aneurysm
  - gastrointestinal Q27.33
    ICD-10-CM Diagnosis Code Q27.33
    Arteriovenous malformation of digestive system vessel
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    - acquired - see Angiodysplasia
- artery (peripheral) Q27.9
  ICD-10-CM Diagnosis Code Q27.9
  Congenital malformation of peripheral vascular system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Anomaly of artery or vein NOS
  - basilar NEC Q28.1
    ICD-10-CM Diagnosis Code Q28.1
    Other malformations of precerebral vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital malformation of precerebral vessels NOS
    Congenital precerebral aneurysm (nonruptured)
  - cerebral Q28.3
    ICD-10-CM Diagnosis Code Q28.3
    Other malformations of cerebral vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital cerebral aneurysm (nonruptured)
    Congenital malformation of cerebral vessels NOS
    Developmental venous anomaly
  - coronary Q24.5
    ICD-10-CM Diagnosis Code Q24.5
    Malformation of coronary vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital coronary (artery) aneurysm
  - digestive system Q27.8
    ICD-10-CM Diagnosis Code Q27.8
    Other specified congenital malformations of peripheral vascular system
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Absence of peripheral vascular system
    Atresia of peripheral vascular system
    Congenital aneurysm (peripheral)
    Congenital stricture, artery
    Congenital varix
    Type 1 Excludes
    arteriovenous malformation (Q27.3-)
  - eye Q15.8
    ICD-10-CM Diagnosis Code Q15.8
    Other specified congenital malformations of eye
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - great Q25.9
    ICD-10-CM Diagnosis Code Q25.9
    Congenital malformation of great arteries, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    - specified NEC Q25.8
      ICD-10-CM Diagnosis Code Q25.8
      Other congenital malformations of other great arteries
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - lower limb Q27.8
    ICD-10-CM Diagnosis Code Q27.8
    Other specified congenital malformations of peripheral vascular system
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Absence of peripheral vascular system
    Atresia of peripheral vascular system
    Congenital aneurysm (peripheral)
    Congenital stricture, artery
    Congenital varix
    Type 1 Excludes
    arteriovenous malformation (Q27.3-)
  - peripheral Q27.9
    ICD-10-CM Diagnosis Code Q27.9
    Congenital malformation of peripheral vascular system, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Anomaly of artery or vein NOS
    - specified NEC Q27.8
      ICD-10-CM Diagnosis Code Q27.8
      Other specified congenital malformations of peripheral vascular system
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Absence of peripheral vascular system
      Atresia of peripheral vascular system
      Congenital aneurysm (peripheral)
      Congenital stricture, artery
      Congenital varix
      Type 1 Excludes
      arteriovenous malformation (Q27.3-)
  - pulmonary NEC Q25.79
    ICD-10-CM Diagnosis Code Q25.79
    Other congenital malformations of pulmonary artery
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Aberrant pulmonary artery
    Agenesis of pulmonary artery
    Congenital aneurysm of pulmonary artery
    Congenital anomaly of pulmonary artery
    Hypoplasia of pulmonary artery
  - renal Q27.2
    ICD-10-CM Diagnosis Code Q27.2
    Other congenital malformations of renal artery
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital malformation of renal artery NOS
    Multiple renal arteries
  - retina Q14.1
    ICD-10-CM Diagnosis Code Q14.1
    Congenital malformation of retina
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital retinal aneurysm
  - specified site NEC Q27.8
    ICD-10-CM Diagnosis Code Q27.8
    Other specified congenital malformations of peripheral vascular system
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Absence of peripheral vascular system
    Atresia of peripheral vascular system
    Congenital aneurysm (peripheral)
    Congenital stricture, artery
    Congenital varix
    Type 1 Excludes
    arteriovenous malformation (Q27.3-)
  - subclavian Q27.8
    ICD-10-CM Diagnosis Code Q27.8
    Other specified congenital malformations of peripheral vascular system
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Absence of peripheral vascular system
    Atresia of peripheral vascular system
    Congenital aneurysm (peripheral)
    Congenital stricture, artery
    Congenital varix
    Type 1 Excludes
    arteriovenous malformation (Q27.3-)
    - origin Q25.48
      ICD-10-CM Diagnosis Code Q25.48
      Anomalous origin of subclavian artery
      2017 - New Code 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - umbilical Q27.0
    ICD-10-CM Diagnosis Code Q27.0
    Congenital absence and hypoplasia of umbilical artery
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Single umbilical artery
  - upper limb Q27.8
    ICD-10-CM Diagnosis Code Q27.8
    Other specified congenital malformations of peripheral vascular system
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Absence of peripheral vascular system
    Atresia of peripheral vascular system
    Congenital aneurysm (peripheral)
    Congenital stricture, artery
    Congenital varix
    Type 1 Excludes
    arteriovenous malformation (Q27.3-)
  - vertebral NEC Q28.1
    ICD-10-CM Diagnosis Code Q28.1
    Other malformations of precerebral vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital malformation of precerebral vessels NOS
    Congenital precerebral aneurysm (nonruptured)
- aryteno-epiglottic folds Q31.8
  ICD-10-CM Diagnosis Code Q31.8
  Other congenital malformations of larynx
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of larynx
  Agenesis of larynx
  Atresia of larynx
  Congenital cleft thyroid cartilage
  Congenital fissure of epiglottis
  Congenital stenosis of larynx NEC
  Posterior cleft of cricoid cartilage
- atrial
  - bands or folds Q20.8
    ICD-10-CM Diagnosis Code Q20.8
    Other congenital malformations of cardiac chambers and connections
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Cor binoculare
  - septa Q21.10
    ICD-10-CM Diagnosis Code Q21.10
    Atrial septal defect, unspecified
    2023 - New Code Billable/Specific Code POA Exempt
- atrioventricular
  - excitation I45.6
    ICD-10-CM Diagnosis Code I45.6
    Pre-excitation syndrome
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    Accelerated atrioventricular conduction
    Accessory atrioventricular conduction
    Anomalous atrioventricular excitation
    Lown-Ganong-Levine syndrome
    Pre-excitation atrioventricular conduction
    Wolff-Parkinson-White syndrome
  - septum Q21.0
    ICD-10-CM Diagnosis Code Q21.0
    Ventricular septal defect
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Roger's disease
- auditory canal Q17.8
  ICD-10-CM Diagnosis Code Q17.8
  Other specified congenital malformations of ear
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of lobe of ear
- auricle
  - ear Q17.8
    ICD-10-CM Diagnosis Code Q17.8
    Other specified congenital malformations of ear
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital absence of lobe of ear
    - causing impairment of hearing Q16.9
      ICD-10-CM Diagnosis Code Q16.9
      Congenital malformation of ear causing impairment of hearing, unspecified
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Congenital absence of ear NOS
  - heart Q20.8
    ICD-10-CM Diagnosis Code Q20.8
    Other congenital malformations of cardiac chambers and connections
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Cor binoculare
- Axenfeld's Q15.0
  ICD-10-CM Diagnosis Code Q15.0
  Congenital glaucoma
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Axenfeld's anomaly
  Buphthalmos
  Glaucoma of childhood
  Glaucoma of newborn
  Hydrophthalmos
  Keratoglobus, congenital, with glaucoma
  Macrocornea with glaucoma
  Macrophthalmos in congenital glaucoma
  Megalocornea with glaucoma
- back Q89.9
  ICD-10-CM Diagnosis Code Q89.9
  Congenital malformation, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS
  Congenital deformity NOS
- band
  - atrial Q20.8
    ICD-10-CM Diagnosis Code Q20.8
    Other congenital malformations of cardiac chambers and connections
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Cor binoculare
  - heart Q24.8
    ICD-10-CM Diagnosis Code Q24.8
    Other specified congenital malformations of heart
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital diverticulum of left ventricle
    Congenital malformation of myocardium
    Congenital malformation of pericardium
    Malposition of heart
    Uhl's disease
  - ventricular Q24.8
    ICD-10-CM Diagnosis Code Q24.8
    Other specified congenital malformations of heart
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital diverticulum of left ventricle
    Congenital malformation of myocardium
    Congenital malformation of pericardium
    Malposition of heart
    Uhl's disease
- Bartholin's duct Q38.4
  ICD-10-CM Diagnosis Code Q38.4
  Congenital malformations of salivary glands and ducts
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Atresia of salivary glands and ducts
  Congenital absence of salivary glands and ducts
  Congenital accessory salivary glands and ducts
  Congenital fistula of salivary gland
- biliary duct or passage Q44.5
  ICD-10-CM Diagnosis Code Q44.5
  Other congenital malformations of bile ducts
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory hepatic duct
  Biliary duct duplication
  Congenital malformation of bile duct NOS
  Cystic duct duplication
- bladder Q64.70
  ICD-10-CM Diagnosis Code Q64.70
  Unspecified congenital malformation of bladder and urethra
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Malformation of bladder or urethra NOS
  - absence Q64.5
    ICD-10-CM Diagnosis Code Q64.5
    Congenital absence of bladder and urethra
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - diverticulum Q64.6
    ICD-10-CM Diagnosis Code Q64.6
    Congenital diverticulum of bladder
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - exstrophy Q64.10
    ICD-10-CM Diagnosis Code Q64.10
    Exstrophy of urinary bladder, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Ectopia vesicae
    - cloacal Q64.12
      ICD-10-CM Diagnosis Code Q64.12
      Cloacal exstrophy of urinary bladder
      2016 2017 2018 - Revised Code 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    - extroversion Q64.19
      ICD-10-CM Diagnosis Code Q64.19
      Other exstrophy of urinary bladder
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Extroversion of bladder
    - specified type NEC Q64.19
      ICD-10-CM Diagnosis Code Q64.19
      Other exstrophy of urinary bladder
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Extroversion of bladder
    - supravesical fissure Q64.11
      ICD-10-CM Diagnosis Code Q64.11
      Supravesical fissure of urinary bladder
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - neck obstruction Q64.31
    ICD-10-CM Diagnosis Code Q64.31
    Congenital bladder neck obstruction
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital obstruction of vesicourethral orifice
  - specified type NEC Q64.79
    ICD-10-CM Diagnosis Code Q64.79
    Other congenital malformations of bladder and urethra
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- bone Q79.9
  ICD-10-CM Diagnosis Code Q79.9
  Congenital malformation of musculoskeletal system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of musculoskeletal system NOS
  Congenital deformity of musculoskeletal system NOS
  - arm Q74.0
    ICD-10-CM Diagnosis Code Q74.0
    Other congenital malformations of upper limb(s), including shoulder girdle
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Accessory carpal bones
    Cleidocranial dysostosis
    Congenital pseudarthrosis of clavicle
    Macrodactylia (fingers)
    Madelung's deformity
    Radioulnar synostosis
    Sprengel's deformity
    Triphalangeal thumb
  - face Q75.9
    ICD-10-CM Diagnosis Code Q75.9
    Congenital malformation of skull and face bones, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital anomaly of face bones NOS
    Congenital anomaly of skull NOS
  - leg Q74.2
    ICD-10-CM Diagnosis Code Q74.2
    Other congenital malformations of lower limb(s), including pelvic girdle
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital fusion of sacroiliac joint
    Congenital malformation of ankle joint
    Congenital malformation of sacroiliac joint
    Type 1 Excludes
    anteversion of femur (neck) (Q65.89)
  - pelvic girdle Q74.2
    ICD-10-CM Diagnosis Code Q74.2
    Other congenital malformations of lower limb(s), including pelvic girdle
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital fusion of sacroiliac joint
    Congenital malformation of ankle joint
    Congenital malformation of sacroiliac joint
    Type 1 Excludes
    anteversion of femur (neck) (Q65.89)
  - shoulder girdle Q74.0
    ICD-10-CM Diagnosis Code Q74.0
    Other congenital malformations of upper limb(s), including shoulder girdle
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Accessory carpal bones
    Cleidocranial dysostosis
    Congenital pseudarthrosis of clavicle
    Macrodactylia (fingers)
    Madelung's deformity
    Radioulnar synostosis
    Sprengel's deformity
    Triphalangeal thumb
  - skull Q75.9
    ICD-10-CM Diagnosis Code Q75.9
    Congenital malformation of skull and face bones, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital anomaly of face bones NOS
    Congenital anomaly of skull NOS
    - with
      - anencephaly Q00.0
        ICD-10-CM Diagnosis Code Q00.0
        Anencephaly
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        Acephaly
        Acrania
        Amyelencephaly
        Hemianencephaly
        Hemicephaly
      - encephalocele - see Encephalocele
      - hydrocephalus Q03.9
        ICD-10-CM Diagnosis Code Q03.9
        Congenital hydrocephalus, unspecified
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        with spina bifida - see Spina bifida, by site, with hydrocephalus
      - microcephaly Q02
        ICD-10-CM Diagnosis Code Q02
        Microcephaly
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Code First
        , if applicable, congenital Zika virus disease
        Includes
        hydromicrocephaly
        micrencephalon
        Type 1 Excludes
        Meckel-Gruber syndrome (Q61.9)
- brain (multiple) Q04.9
  ICD-10-CM Diagnosis Code Q04.9
  Congenital malformation of brain, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS of brain
  Congenital deformity NOS of brain
  Congenital disease or lesion NOS of brain
  Multiple anomalies NOS of brain, congenital
  - vessel Q28.3
    ICD-10-CM Diagnosis Code Q28.3
    Other malformations of cerebral vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital cerebral aneurysm (nonruptured)
    Congenital malformation of cerebral vessels NOS
    Developmental venous anomaly
- breast Q83.9
  ICD-10-CM Diagnosis Code Q83.9
  Congenital malformation of breast, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- broad ligament Q50.6
  ICD-10-CM Diagnosis Code Q50.6
  Other congenital malformations of fallopian tube and broad ligament
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Absence of fallopian tube and broad ligament
  Accessory fallopian tube and broad ligament
  Atresia of fallopian tube and broad ligament
  Congenital malformation of fallopian tube or broad ligament NOS
- bronchus Q32.4
  ICD-10-CM Diagnosis Code Q32.4
  Other congenital malformations of bronchus
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of bronchus
  Agenesis of bronchus
  Atresia of bronchus
  Congenital diverticulum of bronchus
  Congenital malformation of bronchus NOS
- bulbus cordis Q21.9
  ICD-10-CM Diagnosis Code Q21.9
  Congenital malformation of cardiac septum, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Septal (heart) defect NOS
- bursa Q79.9
  ICD-10-CM Diagnosis Code Q79.9
  Congenital malformation of musculoskeletal system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of musculoskeletal system NOS
  Congenital deformity of musculoskeletal system NOS
- canal of Nuck Q52.4
  ICD-10-CM Diagnosis Code Q52.4
  Other congenital malformations of vagina
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Canal of Nuck cyst, congenital
  Congenital malformation of vagina NOS
  Embryonic vaginal cyst
  Gartner's duct cyst
- canthus Q10.3
  ICD-10-CM Diagnosis Code Q10.3
  Other congenital malformations of eyelid
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Ablepharon
  Blepharophimosis, congenital
  Coloboma of eyelid
  Congenital absence or agenesis of cilia
  Congenital absence or agenesis of eyelid
  Congenital accessory eyelid
  Congenital accessory eye muscle
  Congenital malformation of eyelid NOS
- capillary Q27.9
  ICD-10-CM Diagnosis Code Q27.9
  Congenital malformation of peripheral vascular system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Anomaly of artery or vein NOS
- cardiac Q24.9
  ICD-10-CM Diagnosis Code Q24.9
  Congenital malformation of heart, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of heart
  Congenital disease of heart
  - chambers Q20.9
    ICD-10-CM Diagnosis Code Q20.9
    Congenital malformation of cardiac chambers and connections, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    - specified NEC Q20.8
      ICD-10-CM Diagnosis Code Q20.8
      Other congenital malformations of cardiac chambers and connections
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Cor binoculare
  - septal closure Q21.9
    ICD-10-CM Diagnosis Code Q21.9
    Congenital malformation of cardiac septum, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Septal (heart) defect NOS
    - specified NEC Q21.8
      ICD-10-CM Diagnosis Code Q21.8
      Other congenital malformations of cardiac septa
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Eisenmenger's defect
      Pentalogy of Fallot
      Code Also
      , if applicable:
      Eisenmenger's complex (I27.83)
      Eisenmenger's syndrome (I27.83)
  - valve NEC Q24.8
    ICD-10-CM Diagnosis Code Q24.8
    Other specified congenital malformations of heart
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital diverticulum of left ventricle
    Congenital malformation of myocardium
    Congenital malformation of pericardium
    Malposition of heart
    Uhl's disease
    - pulmonary Q22.3
      ICD-10-CM Diagnosis Code Q22.3
      Other congenital malformations of pulmonary valve
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Congenital malformation of pulmonary valve NOS
      Supernumerary cusps of pulmonary valve
- cardiovascular system Q28.8
  ICD-10-CM Diagnosis Code Q28.8
  Other specified congenital malformations of circulatory system
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital aneurysm, specified site NEC
  Spinal vessel anomaly
- carpus Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- caruncle, lacrimal Q10.6
  ICD-10-CM Diagnosis Code Q10.6
  Other congenital malformations of lacrimal apparatus
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of lacrimal apparatus NOS
- cascade stomach Q40.2
  ICD-10-CM Diagnosis Code Q40.2
  Other specified congenital malformations of stomach
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital displacement of stomach
  Congenital diverticulum of stomach
  Congenital hourglass stomach
  Congenital duplication of stomach
  Megalogastria
  Microgastria
- cauda equina Q06.3
  ICD-10-CM Diagnosis Code Q06.3
  Other congenital cauda equina malformations
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- cecum Q43.9
  ICD-10-CM Diagnosis Code Q43.9
  Congenital malformation of intestine, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- cerebral Q04.9
  ICD-10-CM Diagnosis Code Q04.9
  Congenital malformation of brain, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS of brain
  Congenital deformity NOS of brain
  Congenital disease or lesion NOS of brain
  Multiple anomalies NOS of brain, congenital
  - vessels Q28.3
    ICD-10-CM Diagnosis Code Q28.3
    Other malformations of cerebral vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital cerebral aneurysm (nonruptured)
    Congenital malformation of cerebral vessels NOS
    Developmental venous anomaly
- cervix Q51.9
  ICD-10-CM Diagnosis Code Q51.9
  Congenital malformation of uterus and cervix, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
- Chédiak-Higashi E70.330
  (-Steinbrinck) (congenital gigantism of peroxidase granules)
  ICD-10-CM Diagnosis Code E70.330
  Chediak-Higashi syndrome
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
- cheek Q18.9
  ICD-10-CM Diagnosis Code Q18.9
  Congenital malformation of face and neck, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS of face and neck
- chest wall Q67.8
  ICD-10-CM Diagnosis Code Q67.8
  Other congenital deformities of chest
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital deformity of chest wall NOS
  - bones Q76.9
    ICD-10-CM Diagnosis Code Q76.9
    Congenital malformation of bony thorax, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- chin Q18.9
  ICD-10-CM Diagnosis Code Q18.9
  Congenital malformation of face and neck, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS of face and neck
- chordae tendineae Q24.8
  ICD-10-CM Diagnosis Code Q24.8
  Other specified congenital malformations of heart
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital diverticulum of left ventricle
  Congenital malformation of myocardium
  Congenital malformation of pericardium
  Malposition of heart
  Uhl's disease
- choroid Q14.3
  ICD-10-CM Diagnosis Code Q14.3
  Congenital malformation of choroid
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - plexus Q07.8
    ICD-10-CM Diagnosis Code Q07.8
    Other specified congenital malformations of nervous system
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Agenesis of nerve
    Displacement of brachial plexus
    Jaw-winking syndrome
    Marcus Gunn's syndrome
- chromosomes, chromosomal Q99.9
  ICD-10-CM Diagnosis Code Q99.9
  Chromosomal abnormality, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - D (1) - see condition, chromosome 13
  - E (3) - see condition, chromosome 18
  - G - see condition, chromosome 21
  - sex
    - female phenotype Q97.8
      ICD-10-CM Diagnosis Code Q97.8
      Other specified sex chromosome abnormalities, female phenotype
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
    - gonadal dysgenesis Q99.1
      (pure)
      ICD-10-CM Diagnosis Code Q99.1
      46, XX true hermaphrodite
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      46, XX with streak gonads
      46, XY with streak gonads
      Pure gonadal dysgenesis
    - Klinefelter's Q98.4
      ICD-10-CM Diagnosis Code Q98.4
      Klinefelter syndrome, unspecified
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
    - male phenotype Q98.9
      ICD-10-CM Diagnosis Code Q98.9
      Sex chromosome abnormality, male phenotype, unspecified
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
    - Turner's Q96.9
      ICD-10-CM Diagnosis Code Q96.9
      Turner's syndrome, unspecified
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  - specified NEC Q99.8
    ICD-10-CM Diagnosis Code Q99.8
    Other specified chromosome abnormalities
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- cilia Q10.3
  ICD-10-CM Diagnosis Code Q10.3
  Other congenital malformations of eyelid
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Ablepharon
  Blepharophimosis, congenital
  Coloboma of eyelid
  Congenital absence or agenesis of cilia
  Congenital absence or agenesis of eyelid
  Congenital accessory eyelid
  Congenital accessory eye muscle
  Congenital malformation of eyelid NOS
- circulatory system Q28.9
  ICD-10-CM Diagnosis Code Q28.9
  Congenital malformation of circulatory system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- clavicle Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- clitoris Q52.6
  ICD-10-CM Diagnosis Code Q52.6
  Congenital malformation of clitoris
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
- coccyx Q76.49
  ICD-10-CM Diagnosis Code Q76.49
  Other congenital malformations of spine, not associated with scoliosis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of vertebra NOS
  Congenital fusion of spine NOS
  Congenital malformation of lumbosacral (joint) (region) NOS
  Congenital malformation of spine NOS
  Hemivertebra NOS
  Malformation of spine NOS
  Platyspondylisis NOS
  Supernumerary vertebra NOS
- colon Q43.9
  ICD-10-CM Diagnosis Code Q43.9
  Congenital malformation of intestine, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- common duct Q44.5
  ICD-10-CM Diagnosis Code Q44.5
  Other congenital malformations of bile ducts
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory hepatic duct
  Biliary duct duplication
  Congenital malformation of bile duct NOS
  Cystic duct duplication
- communication
  - coronary artery Q24.5
    ICD-10-CM Diagnosis Code Q24.5
    Malformation of coronary vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital coronary (artery) aneurysm
  - left ventricle with right atrium Q21.0
    ICD-10-CM Diagnosis Code Q21.0
    Ventricular septal defect
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Roger's disease
- concha Q17.3
  (ear)
  ICD-10-CM Diagnosis Code Q17.3
  Other misshapen ear
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Pointed ear
- connection
  - portal vein Q26.5
    ICD-10-CM Diagnosis Code Q26.5
    Anomalous portal venous connection
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - pulmonary venous Q26.4
    ICD-10-CM Diagnosis Code Q26.4
    Anomalous pulmonary venous connection, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    - partial Q26.3
      ICD-10-CM Diagnosis Code Q26.3
      Partial anomalous pulmonary venous connection
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Partial anomalous pulmonary venous return
    - total Q26.2
      ICD-10-CM Diagnosis Code Q26.2
      Total anomalous pulmonary venous connection
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Total anomalous pulmonary venous return [TAPVR], subdiaphragmatic
      Total anomalous pulmonary venous return [TAPVR], supradiaphragmatic
  - renal artery with kidney Q27.2
    ICD-10-CM Diagnosis Code Q27.2
    Other congenital malformations of renal artery
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital malformation of renal artery NOS
    Multiple renal arteries
- cornea Q13.4
  (shape)
  ICD-10-CM Diagnosis Code Q13.4
  Other congenital corneal malformations
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of cornea NOS
  Microcornea
  Peter's anomaly
- coronary artery or vein Q24.5
  ICD-10-CM Diagnosis Code Q24.5
  Malformation of coronary vessels
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital coronary (artery) aneurysm
- cranium - see Anomaly, skull
- cricoid cartilage Q31.8
  ICD-10-CM Diagnosis Code Q31.8
  Other congenital malformations of larynx
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of larynx
  Agenesis of larynx
  Atresia of larynx
  Congenital cleft thyroid cartilage
  Congenital fissure of epiglottis
  Congenital stenosis of larynx NEC
  Posterior cleft of cricoid cartilage
- cystic duct Q44.5
  ICD-10-CM Diagnosis Code Q44.5
  Other congenital malformations of bile ducts
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory hepatic duct
  Biliary duct duplication
  Congenital malformation of bile duct NOS
  Cystic duct duplication
- dental
  - alveolar - see Anomaly, alveolar
  - arch relationship M26.20
    ICD-10-CM Diagnosis Code M26.20
    Unspecified anomaly of dental arch relationship
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - specified NEC M26.29
      ICD-10-CM Diagnosis Code M26.29
      Other anomalies of dental arch relationship
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      Midline deviation of dental arch
      Overbite (excessive) deep
      Overbite (excessive) horizontal
      Overbite (excessive) vertical
      Posterior lingual occlusion of mandibular teeth
- dentofacial M26.9
  ICD-10-CM Diagnosis Code M26.9
  Dentofacial anomaly, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - alveolar - see Anomaly, alveolar
  - dental arch relationship M26.20
    ICD-10-CM Diagnosis Code M26.20
    Unspecified anomaly of dental arch relationship
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - specified NEC M26.29
      ICD-10-CM Diagnosis Code M26.29
      Other anomalies of dental arch relationship
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      Midline deviation of dental arch
      Overbite (excessive) deep
      Overbite (excessive) horizontal
      Overbite (excessive) vertical
      Posterior lingual occlusion of mandibular teeth
  - functional M26.50
    ICD-10-CM Diagnosis Code M26.50
    Dentofacial functional abnormalities, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - specified NEC M26.59
      ICD-10-CM Diagnosis Code M26.59
      Other dentofacial functional abnormalities
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      Centric occlusion (of teeth) NOS
      Malocclusion due to abnormal swallowing
      Malocclusion due to mouth breathing
      Malocclusion due to tongue, lip or finger habits
  - jaw size M26.00
    ICD-10-CM Diagnosis Code M26.00
    Unspecified anomaly of jaw size
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - macrogenia M26.05
      ICD-10-CM Diagnosis Code M26.05
      Macrogenia
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - mandibular
      - hyperplasia M26.03
        ICD-10-CM Diagnosis Code M26.03
        Mandibular hyperplasia
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      - hypoplasia M26.04
        ICD-10-CM Diagnosis Code M26.04
        Mandibular hypoplasia
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - maxillary
      - hyperplasia M26.01
        ICD-10-CM Diagnosis Code M26.01
        Maxillary hyperplasia
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      - hypoplasia M26.02
        ICD-10-CM Diagnosis Code M26.02
        Maxillary hypoplasia
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - microgenia M26.06
      ICD-10-CM Diagnosis Code M26.06
      Microgenia
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - specified type NEC M26.09
      ICD-10-CM Diagnosis Code M26.09
      Other specified anomalies of jaw size
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - jaw-cranial base relationship M26.10
    ICD-10-CM Diagnosis Code M26.10
    Unspecified anomaly of jaw-cranial base relationship
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - asymmetry M26.12
      ICD-10-CM Diagnosis Code M26.12
      Other jaw asymmetry
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      - maxillary M26.11
        ICD-10-CM Diagnosis Code M26.11
        Maxillary asymmetry
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - specified type NEC M26.19
      ICD-10-CM Diagnosis Code M26.19
      Other specified anomalies of jaw-cranial base relationship
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - malocclusion M26.4
    ICD-10-CM Diagnosis Code M26.4
    Malocclusion, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - dental arch relationship NEC M26.29
      ICD-10-CM Diagnosis Code M26.29
      Other anomalies of dental arch relationship
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      Midline deviation of dental arch
      Overbite (excessive) deep
      Overbite (excessive) horizontal
      Overbite (excessive) vertical
      Posterior lingual occlusion of mandibular teeth
    - jaw size - see Anomaly, dentofacial, jaw size
    - jaw-cranial base relationship - see Anomaly, dentofacial, jaw-cranial base relationship
  - specified type NEC M26.89
    ICD-10-CM Diagnosis Code M26.89
    Other dentofacial anomalies
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - temporomandibular joint M26.60-
    ICD-10-CM Diagnosis Code M26.60-
    Temporomandibular joint disorder, unspecified
    2016 2017 - Converted to Parent Code 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    - adhesions M26.61-
      ICD-10-CM Diagnosis Code M26.61-
      Adhesions and ankylosis of temporomandibular joint
      2016 2017 - Converted to Parent Code 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    - ankylosis M26.61-
      ICD-10-CM Diagnosis Code M26.61-
      Adhesions and ankylosis of temporomandibular joint
      2016 2017 - Converted to Parent Code 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    - arthralgia M26.62-
      ICD-10-CM Diagnosis Code M26.62-
      Arthralgia of temporomandibular joint
      2016 2017 - Converted to Parent Code 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    - articular disc M26.63-
      ICD-10-CM Diagnosis Code M26.63-
      Articular disc disorder of temporomandibular joint
      2016 2017 - Converted to Parent Code 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    - specified type NEC M26.69
      ICD-10-CM Diagnosis Code M26.69
      Other specified disorders of temporomandibular joint
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - tooth position, fully erupted M26.30
    ICD-10-CM Diagnosis Code M26.30
    Unspecified anomaly of tooth position of fully erupted tooth or teeth
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    Abnormal spacing of fully erupted tooth or teeth NOS
    Displacement of fully erupted tooth or teeth NOS
    Transposition of fully erupted tooth or teeth NOS
    - specified NEC M26.39
      ICD-10-CM Diagnosis Code M26.39
      Other anomalies of tooth position of fully erupted tooth or teeth
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
- dermatoglyphic Q82.8
  ICD-10-CM Diagnosis Code Q82.8
  Other specified congenital malformations of skin
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Abnormal palmar creases
  Accessory skin tags
  Benign familial pemphigus [Hailey-Hailey]
  Congenital poikiloderma
  Cutis laxa (hyperelastica)
  Dermatoglyphic anomalies
  Inherited keratosis palmaris et plantaris
  Keratosis follicularis [Darier-White]
  Type 1 Excludes
  Ehlers-Danlos syndromes (Q79.6-)
- diaphragm Q79.1
  (apertures)
  ICD-10-CM Diagnosis Code Q79.1
  Other congenital malformations of diaphragm
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of diaphragm
  Congenital malformation of diaphragm NOS
  Eventration of diaphragm
- digestive organ(s) Q45.9
  ICD-10-CM Diagnosis Code Q45.9
  Congenital malformation of digestive system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of digestive system
  Congenital deformity of digestive system
  - lower Q43.9
    ICD-10-CM Diagnosis Code Q43.9
    Congenital malformation of intestine, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - upper Q40.9
    ICD-10-CM Diagnosis Code Q40.9
    Congenital malformation of upper alimentary tract, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital anomaly of upper alimentary tract
    Congenital deformity of upper alimentary tract
- distance, interarch M26.25
  (excessive) (inadequate)
  ICD-10-CM Diagnosis Code M26.25
  Anomalies of interarch distance
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
- distribution, coronary artery Q24.5
  ICD-10-CM Diagnosis Code Q24.5
  Malformation of coronary vessels
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital coronary (artery) aneurysm
- ductus
  - arteriosus Q25.0
    ICD-10-CM Diagnosis Code Q25.0
    Patent ductus arteriosus
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Patent ductus Botallo
    Persistent ductus arteriosus
  - botalli Q25.0
    ICD-10-CM Diagnosis Code Q25.0
    Patent ductus arteriosus
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Patent ductus Botallo
    Persistent ductus arteriosus
- duodenum Q43.9
  ICD-10-CM Diagnosis Code Q43.9
  Congenital malformation of intestine, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- dura (brain) Q04.9
  ICD-10-CM Diagnosis Code Q04.9
  Congenital malformation of brain, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS of brain
  Congenital deformity NOS of brain
  Congenital disease or lesion NOS of brain
  Multiple anomalies NOS of brain, congenital
  - spinal cord Q06.9
    ICD-10-CM Diagnosis Code Q06.9
    Congenital malformation of spinal cord, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital anomaly NOS of spinal cord
    Congenital deformity NOS of spinal cord
    Congenital disease or lesion NOS of spinal cord
- ear (external) Q17.9
  ICD-10-CM Diagnosis Code Q17.9
  Congenital malformation of ear, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of ear NOS
  - causing impairment of hearing Q16.9
    ICD-10-CM Diagnosis Code Q16.9
    Congenital malformation of ear causing impairment of hearing, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital absence of ear NOS
  - inner Q16.5
    ICD-10-CM Diagnosis Code Q16.5
    Congenital malformation of inner ear
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital anomaly of membranous labyrinth
    Congenital anomaly of organ of Corti
  - middle Q16.4
    (causing impairment of hearing)
    ICD-10-CM Diagnosis Code Q16.4
    Other congenital malformations of middle ear
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital malformation of middle ear NOS
  - ossicles Q16.3
    ICD-10-CM Diagnosis Code Q16.3
    Congenital malformation of ear ossicles
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital fusion of ear ossicles
- Ebstein's Q22.5
  (heart) (tricuspid valve)
  ICD-10-CM Diagnosis Code Q22.5
  Ebstein's anomaly
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- ectodermal Q82.9
  ICD-10-CM Diagnosis Code Q82.9
  Congenital malformation of skin, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- Eisenmenger's Q21.8
  (ventricular septal defect)
  ICD-10-CM Diagnosis Code Q21.8
  Other congenital malformations of cardiac septa
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Eisenmenger's defect
  Pentalogy of Fallot
  Code Also
  , if applicable:
  Eisenmenger's complex (I27.83)
  Eisenmenger's syndrome (I27.83)
- ejaculatory duct Q55.4
  ICD-10-CM Diagnosis Code Q55.4
  Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
  Applicable To
  Absence or aplasia of prostate
  Absence or aplasia of spermatic cord
  Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
- elbow Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- endocrine gland NEC Q89.2
  ICD-10-CM Diagnosis Code Q89.2
  Congenital malformations of other endocrine glands
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of parathyroid or thyroid gland
  Persistent thyroglossal duct
  Thyroglossal cyst
  Type 1 Excludes
  congenital goiter (E03.0)
  congenital hypothyroidism (E03.1)
- epididymis Q55.4
  ICD-10-CM Diagnosis Code Q55.4
  Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
  Applicable To
  Absence or aplasia of prostate
  Absence or aplasia of spermatic cord
  Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
- epiglottis Q31.8
  ICD-10-CM Diagnosis Code Q31.8
  Other congenital malformations of larynx
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of larynx
  Agenesis of larynx
  Atresia of larynx
  Congenital cleft thyroid cartilage
  Congenital fissure of epiglottis
  Congenital stenosis of larynx NEC
  Posterior cleft of cricoid cartilage
- esophagus Q39.9
  ICD-10-CM Diagnosis Code Q39.9
  Congenital malformation of esophagus, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- eustachian tube Q17.8
  ICD-10-CM Diagnosis Code Q17.8
  Other specified congenital malformations of ear
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of lobe of ear
- eye Q15.9
  ICD-10-CM Diagnosis Code Q15.9
  Congenital malformation of eye, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of eye
  Congenital deformity of eye
  - anterior segment Q13.9
    ICD-10-CM Diagnosis Code Q13.9
    Congenital malformation of anterior segment of eye, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    - specified NEC Q13.89
      ICD-10-CM Diagnosis Code Q13.89
      Other congenital malformations of anterior segment of eye
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - posterior segment Q14.9
    ICD-10-CM Diagnosis Code Q14.9
    Congenital malformation of posterior segment of eye, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    - specified NEC Q14.8
      ICD-10-CM Diagnosis Code Q14.8
      Other congenital malformations of posterior segment of eye
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Coloboma of the fundus
  - ptosis Q10.0
    (eyelid)
    ICD-10-CM Diagnosis Code Q10.0
    Congenital ptosis
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - specified NEC Q15.8
    ICD-10-CM Diagnosis Code Q15.8
    Other specified congenital malformations of eye
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- eyebrow Q18.8
  ICD-10-CM Diagnosis Code Q18.8
  Other specified congenital malformations of face and neck
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Medial cyst of face and neck
  Medial fistula of face and neck
  Medial sinus of face and neck
- eyelid Q10.3
  ICD-10-CM Diagnosis Code Q10.3
  Other congenital malformations of eyelid
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Ablepharon
  Blepharophimosis, congenital
  Coloboma of eyelid
  Congenital absence or agenesis of cilia
  Congenital absence or agenesis of eyelid
  Congenital accessory eyelid
  Congenital accessory eye muscle
  Congenital malformation of eyelid NOS
  - ptosis Q10.0
    ICD-10-CM Diagnosis Code Q10.0
    Congenital ptosis
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- face Q18.9
  ICD-10-CM Diagnosis Code Q18.9
  Congenital malformation of face and neck, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS of face and neck
  - bone Q75.9
    (s)
    ICD-10-CM Diagnosis Code Q75.9
    Congenital malformation of skull and face bones, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital anomaly of face bones NOS
    Congenital anomaly of skull NOS
- fallopian tube Q50.6
  ICD-10-CM Diagnosis Code Q50.6
  Other congenital malformations of fallopian tube and broad ligament
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Absence of fallopian tube and broad ligament
  Accessory fallopian tube and broad ligament
  Atresia of fallopian tube and broad ligament
  Congenital malformation of fallopian tube or broad ligament NOS
- fascia Q79.9
  ICD-10-CM Diagnosis Code Q79.9
  Congenital malformation of musculoskeletal system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of musculoskeletal system NOS
  Congenital deformity of musculoskeletal system NOS
- femur NEC Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- fibula NEC Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- finger Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- fixation, intestine Q43.3
  ICD-10-CM Diagnosis Code Q43.3
  Congenital malformations of intestinal fixation
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital omental, anomalous adhesions [bands]
  Congenital peritoneal adhesions [bands]
  Incomplete rotation of cecum and colon
  Insufficient rotation of cecum and colon
  Jackson's membrane
  Malrotation of colon
  Rotation failure of cecum and colon
  Universal mesentery
- flexion (joint) Q74.9
  ICD-10-CM Diagnosis Code Q74.9
  Unspecified congenital malformation of limb(s)
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of limb(s) NOS
  - hip or thigh Q65.89
    ICD-10-CM Diagnosis Code Q65.89
    Other specified congenital deformities of hip
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Anteversion of femoral neck
    Congenital acetabular dysplasia
- foot NEC Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
  - varus Q66.3-
    (congenital)
    ICD-10-CM Diagnosis Code Q66.3-
    Other congenital varus deformities of feet
    2016 2017 2018 2019 2020 - Converted to Parent Code 2021 2022 2023 Non-Billable/Non-Specific Code
    Applicable To
    Hallux varus, congenital
- foramen
  - Botalli Q21.12
    ICD-10-CM Diagnosis Code Q21.12
    Patent foramen ovale
    2023 - New Code Billable/Specific Code POA Exempt
    Applicable To
    Persistent foramen ovale
  - ovale Q21.12
    ICD-10-CM Diagnosis Code Q21.12
    Patent foramen ovale
    2023 - New Code Billable/Specific Code POA Exempt
    Applicable To
    Persistent foramen ovale
- forearm Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- forehead Q75.8
  ICD-10-CM Diagnosis Code Q75.8
  Other specified congenital malformations of skull and face bones
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of skull bone, congenital
  Congenital deformity of forehead
  Platybasia
- form, teeth K00.2
  ICD-10-CM Diagnosis Code K00.2
  Abnormalities of size and form of teeth
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Concrescence of teeth
  Fusion of teeth
  Gemination of teeth
  Dens evaginatus
  Dens in dente
  Dens invaginatus
  Enamel pearls
  Macrodontia
  Microdontia
  Peg-shaped [conical] teeth
  Supernumerary roots
  Taurodontism
  Tuberculum paramolare
  Type 1 Excludes
  abnormalities of teeth due to congenital syphilis (A50.5)
  tuberculum Carabelli, which is regarded as a normal variation and should not be coded
- fovea centralis Q14.1
  ICD-10-CM Diagnosis Code Q14.1
  Congenital malformation of retina
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital retinal aneurysm
- frontal bone - see Anomaly, skull
- gallbladder Q44.1
  (position) (shape) (size)
  ICD-10-CM Diagnosis Code Q44.1
  Other congenital malformations of gallbladder
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of gallbladder NOS
  Intrahepatic gallbladder
- Gartner's duct Q52.4
  ICD-10-CM Diagnosis Code Q52.4
  Other congenital malformations of vagina
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Canal of Nuck cyst, congenital
  Congenital malformation of vagina NOS
  Embryonic vaginal cyst
  Gartner's duct cyst
- gastrointestinal tract Q45.9
  ICD-10-CM Diagnosis Code Q45.9
  Congenital malformation of digestive system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of digestive system
  Congenital deformity of digestive system
- genitalia, genital organ(s)
  - female Q52.9
    ICD-10-CM Diagnosis Code Q52.9
    Congenital malformation of female genitalia, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
    - external Q52.70
      ICD-10-CM Diagnosis Code Q52.70
      Unspecified congenital malformations of vulva
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
      Applicable To
      Congenital malformation of vulva NOS
    - internal NOS Q52.9
      ICD-10-CM Diagnosis Code Q52.9
      Congenital malformation of female genitalia, unspecified
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  - male Q55.9
    ICD-10-CM Diagnosis Code Q55.9
    Congenital malformation of male genital organ, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
    Applicable To
    Congenital anomaly of male genital organ
    Congenital deformity of male genital organ
    - hydrocele P83.5
      ICD-10-CM Diagnosis Code P83.5
      Congenital hydrocele
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx Code on Newborn Record
    - specified NEC Q55.8
      ICD-10-CM Diagnosis Code Q55.8
      Other specified congenital malformations of male genital organs
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
- genitourinary NEC
  - female Q52.9
    ICD-10-CM Diagnosis Code Q52.9
    Congenital malformation of female genitalia, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  - male Q55.9
    ICD-10-CM Diagnosis Code Q55.9
    Congenital malformation of male genital organ, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
    Applicable To
    Congenital anomaly of male genital organ
    Congenital deformity of male genital organ
- Gerbode Q21.0
  ICD-10-CM Diagnosis Code Q21.0
  Ventricular septal defect
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Roger's disease
- glottis Q31.8
  ICD-10-CM Diagnosis Code Q31.8
  Other congenital malformations of larynx
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of larynx
  Agenesis of larynx
  Atresia of larynx
  Congenital cleft thyroid cartilage
  Congenital fissure of epiglottis
  Congenital stenosis of larynx NEC
  Posterior cleft of cricoid cartilage
- granulation or granulocyte, genetic D72.0
  (constitutional) (leukocyte)
  ICD-10-CM Diagnosis Code D72.0
  Genetic anomalies of leukocytes
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Alder (granulation) (granulocyte) anomaly
  Alder syndrome
  Hereditary leukocytic hypersegmentation
  Hereditary leukocytic hyposegmentation
  Hereditary leukomelanopathy
  May-Hegglin (granulation) (granulocyte) anomaly
  May-Hegglin syndrome
  Pelger-Huët (granulation) (granulocyte) anomaly
  Pelger-Huët syndrome
  Type 1 Excludes
  Chédiak (-Steinbrinck)-Higashi syndrome (E70.330)
- gum Q38.6
  ICD-10-CM Diagnosis Code Q38.6
  Other congenital malformations of mouth
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of mouth NOS
- gyri Q07.9
  ICD-10-CM Diagnosis Code Q07.9
  Congenital malformation of nervous system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS of nervous system
  Congenital deformity NOS of nervous system
  Congenital disease or lesion NOS of nervous system
- hair Q84.2
  ICD-10-CM Diagnosis Code Q84.2
  Other congenital malformations of hair
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital hypertrichosis
  Congenital malformation of hair NOS
  Persistent lanugo
- hand Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- hard tissue formation in pulp K04.3
  ICD-10-CM Diagnosis Code K04.3
  Abnormal hard tissue formation in pulp
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Secondary or irregular dentine
- head - see Anomaly, skull
- heart Q24.9
  ICD-10-CM Diagnosis Code Q24.9
  Congenital malformation of heart, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of heart
  Congenital disease of heart
  - auricle Q20.8
    ICD-10-CM Diagnosis Code Q20.8
    Other congenital malformations of cardiac chambers and connections
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Cor binoculare
  - bands or folds Q24.8
    ICD-10-CM Diagnosis Code Q24.8
    Other specified congenital malformations of heart
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital diverticulum of left ventricle
    Congenital malformation of myocardium
    Congenital malformation of pericardium
    Malposition of heart
    Uhl's disease
  - fibroelastosis cordis I42.4
    ICD-10-CM Diagnosis Code I42.4
    Endocardial fibroelastosis
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    Congenital cardiomyopathy
    Elastomyofibrosis
  - obstructive NEC Q22.6
    ICD-10-CM Diagnosis Code Q22.6
    Hypoplastic right heart syndrome
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - patent ductus arteriosus Q25.0
    (Botalli)
    ICD-10-CM Diagnosis Code Q25.0
    Patent ductus arteriosus
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Patent ductus Botallo
    Persistent ductus arteriosus
  - septum Q21.9
    ICD-10-CM Diagnosis Code Q21.9
    Congenital malformation of cardiac septum, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Septal (heart) defect NOS
    - auricular Q21.19
      ICD-10-CM Diagnosis Code Q21.19
      Other specified atrial septal defect
      2023 - New Code Billable/Specific Code POA Exempt
      Applicable To
      Common atrium
      Other specified atrial septal abnormality
    - interatrial Q21.19
      ICD-10-CM Diagnosis Code Q21.19
      Other specified atrial septal defect
      2023 - New Code Billable/Specific Code POA Exempt
      Applicable To
      Common atrium
      Other specified atrial septal abnormality
    - interventricular Q21.0
      ICD-10-CM Diagnosis Code Q21.0
      Ventricular septal defect
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Roger's disease
      - with pulmonary stenosis or atresia, dextraposition of aorta and hypertrophy of right ventricle Q21.3
        ICD-10-CM Diagnosis Code Q21.3
        Tetralogy of Fallot
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        Ventricular septal defect with pulmonary stenosis or atresia, dextroposition of aorta and hypertrophy of right ventricle.
    - specified NEC Q21.8
      ICD-10-CM Diagnosis Code Q21.8
      Other congenital malformations of cardiac septa
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Eisenmenger's defect
      Pentalogy of Fallot
      Code Also
      , if applicable:
      Eisenmenger's complex (I27.83)
      Eisenmenger's syndrome (I27.83)
    - ventricular Q21.0
      ICD-10-CM Diagnosis Code Q21.0
      Ventricular septal defect
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Roger's disease
      - with pulmonary stenosis or atresia, dextraposition of aorta and hypertrophy of right ventricle Q21.3
        ICD-10-CM Diagnosis Code Q21.3
        Tetralogy of Fallot
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        Ventricular septal defect with pulmonary stenosis or atresia, dextroposition of aorta and hypertrophy of right ventricle.
  - tetralogy of Fallot Q21.3
    ICD-10-CM Diagnosis Code Q21.3
    Tetralogy of Fallot
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Ventricular septal defect with pulmonary stenosis or atresia, dextroposition of aorta and hypertrophy of right ventricle.
  - valve NEC Q24.8
    ICD-10-CM Diagnosis Code Q24.8
    Other specified congenital malformations of heart
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital diverticulum of left ventricle
    Congenital malformation of myocardium
    Congenital malformation of pericardium
    Malposition of heart
    Uhl's disease
    - aortic
      - bicuspid valve Q23.1
        ICD-10-CM Diagnosis Code Q23.1
        Congenital insufficiency of aortic valve
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        Bicuspid aortic valve
        Congenital aortic insufficiency
      - insufficiency Q23.1
        ICD-10-CM Diagnosis Code Q23.1
        Congenital insufficiency of aortic valve
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        Bicuspid aortic valve
        Congenital aortic insufficiency
      - stenosis Q23.0
        ICD-10-CM Diagnosis Code Q23.0
        Congenital stenosis of aortic valve
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        Congenital aortic atresia
        Congenital aortic stenosis NOS
        Type 1 Excludes
        congenital stenosis of aortic valve in hypoplastic left heart syndrome (Q23.4)
        congenital subaortic stenosis (Q24.4)
        supravalvular aortic stenosis (congenital) (Q25.3)
        subaortic Q24.4
        ICD-10-CM Diagnosis Code Q24.4
        Congenital subaortic stenosis
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    - mitral
      - insufficiency Q23.3
        ICD-10-CM Diagnosis Code Q23.3
        Congenital mitral insufficiency
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      - stenosis Q23.2
        ICD-10-CM Diagnosis Code Q23.2
        Congenital mitral stenosis
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        Congenital mitral atresia
    - pulmonary Q22.3
      ICD-10-CM Diagnosis Code Q22.3
      Other congenital malformations of pulmonary valve
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Congenital malformation of pulmonary valve NOS
      Supernumerary cusps of pulmonary valve
      - atresia Q22.0
        ICD-10-CM Diagnosis Code Q22.0
        Pulmonary valve atresia
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      - insufficiency Q22.2
        ICD-10-CM Diagnosis Code Q22.2
        Congenital pulmonary valve insufficiency
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        Congenital pulmonary valve regurgitation
      - stenosis Q22.1
        ICD-10-CM Diagnosis Code Q22.1
        Congenital pulmonary valve stenosis
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        infundibular Q24.3
        ICD-10-CM Diagnosis Code Q24.3
        Pulmonary infundibular stenosis
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        Subvalvular pulmonic stenosis
        subvalvular Q24.3
        ICD-10-CM Diagnosis Code Q24.3
        Pulmonary infundibular stenosis
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        Subvalvular pulmonic stenosis
    - tricuspid
      - atresia Q22.4
        ICD-10-CM Diagnosis Code Q22.4
        Congenital tricuspid stenosis
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        Congenital tricuspid atresia
      - stenosis Q22.4
        ICD-10-CM Diagnosis Code Q22.4
        Congenital tricuspid stenosis
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        Congenital tricuspid atresia
  - ventricle Q20.8
    ICD-10-CM Diagnosis Code Q20.8
    Other congenital malformations of cardiac chambers and connections
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Cor binoculare
- heel NEC Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- Hegglin's D72.0
  ICD-10-CM Diagnosis Code D72.0
  Genetic anomalies of leukocytes
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Alder (granulation) (granulocyte) anomaly
  Alder syndrome
  Hereditary leukocytic hypersegmentation
  Hereditary leukocytic hyposegmentation
  Hereditary leukomelanopathy
  May-Hegglin (granulation) (granulocyte) anomaly
  May-Hegglin syndrome
  Pelger-Huët (granulation) (granulocyte) anomaly
  Pelger-Huët syndrome
  Type 1 Excludes
  Chédiak (-Steinbrinck)-Higashi syndrome (E70.330)
- hemianencephaly Q00.0
  ICD-10-CM Diagnosis Code Q00.0
  Anencephaly
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Acephaly
  Acrania
  Amyelencephaly
  Hemianencephaly
  Hemicephaly
- hemicephaly Q00.0
  ICD-10-CM Diagnosis Code Q00.0
  Anencephaly
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Acephaly
  Acrania
  Amyelencephaly
  Hemianencephaly
  Hemicephaly
- hemicrania Q00.0
  ICD-10-CM Diagnosis Code Q00.0
  Anencephaly
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Acephaly
  Acrania
  Amyelencephaly
  Hemianencephaly
  Hemicephaly
- hepatic duct Q44.5
  ICD-10-CM Diagnosis Code Q44.5
  Other congenital malformations of bile ducts
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory hepatic duct
  Biliary duct duplication
  Congenital malformation of bile duct NOS
  Cystic duct duplication
- hip NEC Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- hourglass stomach Q40.2
  ICD-10-CM Diagnosis Code Q40.2
  Other specified congenital malformations of stomach
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital displacement of stomach
  Congenital diverticulum of stomach
  Congenital hourglass stomach
  Congenital duplication of stomach
  Megalogastria
  Microgastria
- humerus Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- hydatid of Morgagni
  - female Q50.5
    ICD-10-CM Diagnosis Code Q50.5
    Embryonic cyst of broad ligament
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
    Applicable To
    Epoophoron cyst
    Parovarian cyst
  - male (epididymal) Q55.4
    ICD-10-CM Diagnosis Code Q55.4
    Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
    Applicable To
    Absence or aplasia of prostate
    Absence or aplasia of spermatic cord
    Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
    - testicular Q55.29
      ICD-10-CM Diagnosis Code Q55.29
      Other congenital malformations of testis and scrotum
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
- hymen Q52.4
  ICD-10-CM Diagnosis Code Q52.4
  Other congenital malformations of vagina
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Canal of Nuck cyst, congenital
  Congenital malformation of vagina NOS
  Embryonic vaginal cyst
  Gartner's duct cyst
- hypersegmentation of neutrophils, hereditary D72.0
  ICD-10-CM Diagnosis Code D72.0
  Genetic anomalies of leukocytes
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Alder (granulation) (granulocyte) anomaly
  Alder syndrome
  Hereditary leukocytic hypersegmentation
  Hereditary leukocytic hyposegmentation
  Hereditary leukomelanopathy
  May-Hegglin (granulation) (granulocyte) anomaly
  May-Hegglin syndrome
  Pelger-Huët (granulation) (granulocyte) anomaly
  Pelger-Huët syndrome
  Type 1 Excludes
  Chédiak (-Steinbrinck)-Higashi syndrome (E70.330)
- hypophyseal Q89.2
  ICD-10-CM Diagnosis Code Q89.2
  Congenital malformations of other endocrine glands
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of parathyroid or thyroid gland
  Persistent thyroglossal duct
  Thyroglossal cyst
  Type 1 Excludes
  congenital goiter (E03.0)
  congenital hypothyroidism (E03.1)
- ileocecal Q43.9
  (coil) (valve)
  ICD-10-CM Diagnosis Code Q43.9
  Congenital malformation of intestine, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- ileum Q43.9
  ICD-10-CM Diagnosis Code Q43.9
  Congenital malformation of intestine, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- ilium NEC Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- integument Q84.9
  ICD-10-CM Diagnosis Code Q84.9
  Congenital malformation of integument, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of integument NOS
  Congenital deformity of integument NOS
  - specified NEC Q84.8
    ICD-10-CM Diagnosis Code Q84.8
    Other specified congenital malformations of integument
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Aplasia cutis congenita
- interarch distance M26.25
  (excessive) (inadequate)
  ICD-10-CM Diagnosis Code M26.25
  Anomalies of interarch distance
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
- intervertebral cartilage or disc Q76.49
  ICD-10-CM Diagnosis Code Q76.49
  Other congenital malformations of spine, not associated with scoliosis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of vertebra NOS
  Congenital fusion of spine NOS
  Congenital malformation of lumbosacral (joint) (region) NOS
  Congenital malformation of spine NOS
  Hemivertebra NOS
  Malformation of spine NOS
  Platyspondylisis NOS
  Supernumerary vertebra NOS
- intestine (large) (small) Q43.9
  ICD-10-CM Diagnosis Code Q43.9
  Congenital malformation of intestine, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - with anomalous adhesions, fixation or malrotation Q43.3
    ICD-10-CM Diagnosis Code Q43.3
    Congenital malformations of intestinal fixation
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital omental, anomalous adhesions [bands]
    Congenital peritoneal adhesions [bands]
    Incomplete rotation of cecum and colon
    Insufficient rotation of cecum and colon
    Jackson's membrane
    Malrotation of colon
    Rotation failure of cecum and colon
    Universal mesentery
- iris Q13.2
  ICD-10-CM Diagnosis Code Q13.2
  Other congenital malformations of iris
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Anisocoria, congenital
  Atresia of pupil
  Congenital malformation of iris NOS
  Corectopia
- ischium NEC Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- jaw - see Anomaly, dentofacial
  - alveolar - see Anomaly, alveolar
- jaw-cranial base relationship - see Anomaly, dentofacial, jaw-cranial base relationship
- jejunum Q43.8
  ICD-10-CM Diagnosis Code Q43.8
  Other specified congenital malformations of intestine
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital blind loop syndrome
  Congenital diverticulitis, colon
  Congenital diverticulum, intestine
  Dolichocolon
  Megaloappendix
  Megaloduodenum
  Microcolon
  Transposition of appendix
  Transposition of colon
  Transposition of intestine
- joint Q74.9
  ICD-10-CM Diagnosis Code Q74.9
  Unspecified congenital malformation of limb(s)
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of limb(s) NOS
  - specified NEC Q74.8
    ICD-10-CM Diagnosis Code Q74.8
    Other specified congenital malformations of limb(s)
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- Jordan's D72.0
  ICD-10-CM Diagnosis Code D72.0
  Genetic anomalies of leukocytes
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Alder (granulation) (granulocyte) anomaly
  Alder syndrome
  Hereditary leukocytic hypersegmentation
  Hereditary leukocytic hyposegmentation
  Hereditary leukomelanopathy
  May-Hegglin (granulation) (granulocyte) anomaly
  May-Hegglin syndrome
  Pelger-Huët (granulation) (granulocyte) anomaly
  Pelger-Huët syndrome
  Type 1 Excludes
  Chédiak (-Steinbrinck)-Higashi syndrome (E70.330)
- kidney(s) (calyx) (pelvis) Q63.9
  ICD-10-CM Diagnosis Code Q63.9
  Congenital malformation of kidney, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - artery Q27.2
    ICD-10-CM Diagnosis Code Q27.2
    Other congenital malformations of renal artery
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital malformation of renal artery NOS
    Multiple renal arteries
  - specified NEC Q63.8
    ICD-10-CM Diagnosis Code Q63.8
    Other specified congenital malformations of kidney
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital renal calculi
- Klippel-Feil Q76.1
  (brevicollis)
  ICD-10-CM Diagnosis Code Q76.1
  Klippel-Feil syndrome
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Cervical fusion syndrome
- knee Q74.1
  ICD-10-CM Diagnosis Code Q74.1
  Congenital malformation of knee
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of patella
  Congenital dislocation of patella
  Congenital genu valgum
  Congenital genu varum
  Rudimentary patella
  Type 1 Excludes
  congenital dislocation of knee (Q68.2)
  congenital genu recurvatum (Q68.2)
  nail patella syndrome (Q87.2)
- labium Q52.70
  (majus) (minus)
  ICD-10-CM Diagnosis Code Q52.70
  Unspecified congenital malformations of vulva
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Congenital malformation of vulva NOS
- labyrinth, membranous Q16.5
  ICD-10-CM Diagnosis Code Q16.5
  Congenital malformation of inner ear
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of membranous labyrinth
  Congenital anomaly of organ of Corti
- lacrimal apparatus or duct Q10.6
  ICD-10-CM Diagnosis Code Q10.6
  Other congenital malformations of lacrimal apparatus
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of lacrimal apparatus NOS
- larynx, laryngeal (muscle) Q31.9
  ICD-10-CM Diagnosis Code Q31.9
  Congenital malformation of larynx, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - web Q31.0
    (bed)
    ICD-10-CM Diagnosis Code Q31.0
    Web of larynx
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Glottic web of larynx
    Subglottic web of larynx
    Web of larynx NOS
- lens Q12.9
  ICD-10-CM Diagnosis Code Q12.9
  Congenital lens malformation, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- leukocytes, genetic D72.0
  ICD-10-CM Diagnosis Code D72.0
  Genetic anomalies of leukocytes
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Alder (granulation) (granulocyte) anomaly
  Alder syndrome
  Hereditary leukocytic hypersegmentation
  Hereditary leukocytic hyposegmentation
  Hereditary leukomelanopathy
  May-Hegglin (granulation) (granulocyte) anomaly
  May-Hegglin syndrome
  Pelger-Huët (granulation) (granulocyte) anomaly
  Pelger-Huët syndrome
  Type 1 Excludes
  Chédiak (-Steinbrinck)-Higashi syndrome (E70.330)
  - granulation D72.0
    (constitutional)
    ICD-10-CM Diagnosis Code D72.0
    Genetic anomalies of leukocytes
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    Alder (granulation) (granulocyte) anomaly
    Alder syndrome
    Hereditary leukocytic hypersegmentation
    Hereditary leukocytic hyposegmentation
    Hereditary leukomelanopathy
    May-Hegglin (granulation) (granulocyte) anomaly
    May-Hegglin syndrome
    Pelger-Huët (granulation) (granulocyte) anomaly
    Pelger-Huët syndrome
    Type 1 Excludes
    Chédiak (-Steinbrinck)-Higashi syndrome (E70.330)
- lid Q10.3
  (fold)
  ICD-10-CM Diagnosis Code Q10.3
  Other congenital malformations of eyelid
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Ablepharon
  Blepharophimosis, congenital
  Coloboma of eyelid
  Congenital absence or agenesis of cilia
  Congenital absence or agenesis of eyelid
  Congenital accessory eyelid
  Congenital accessory eye muscle
  Congenital malformation of eyelid NOS
- ligament Q79.9
  ICD-10-CM Diagnosis Code Q79.9
  Congenital malformation of musculoskeletal system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of musculoskeletal system NOS
  Congenital deformity of musculoskeletal system NOS
  - broad Q50.6
    ICD-10-CM Diagnosis Code Q50.6
    Other congenital malformations of fallopian tube and broad ligament
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
    Applicable To
    Absence of fallopian tube and broad ligament
    Accessory fallopian tube and broad ligament
    Atresia of fallopian tube and broad ligament
    Congenital malformation of fallopian tube or broad ligament NOS
  - round Q52.8
    ICD-10-CM Diagnosis Code Q52.8
    Other specified congenital malformations of female genitalia
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
- limb Q74.9
  ICD-10-CM Diagnosis Code Q74.9
  Unspecified congenital malformation of limb(s)
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of limb(s) NOS
  - lower NEC Q74.2
    ICD-10-CM Diagnosis Code Q74.2
    Other congenital malformations of lower limb(s), including pelvic girdle
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital fusion of sacroiliac joint
    Congenital malformation of ankle joint
    Congenital malformation of sacroiliac joint
    Type 1 Excludes
    anteversion of femur (neck) (Q65.89)
    - reduction deformity - see Defect, reduction, lower limb
  - upper Q74.0
    ICD-10-CM Diagnosis Code Q74.0
    Other congenital malformations of upper limb(s), including shoulder girdle
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Accessory carpal bones
    Cleidocranial dysostosis
    Congenital pseudarthrosis of clavicle
    Macrodactylia (fingers)
    Madelung's deformity
    Radioulnar synostosis
    Sprengel's deformity
    Triphalangeal thumb
- lip Q38.0
  ICD-10-CM Diagnosis Code Q38.0
  Congenital malformations of lips, not elsewhere classified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fistula of lip
  Congenital malformation of lip NOS
  Van der Woude's syndrome
  Type 1 Excludes
  cleft lip (Q36.-)
  cleft lip with cleft palate (Q37.-)
  macrocheilia (Q18.6)
  microcheilia (Q18.7)
- liver Q44.7
  ICD-10-CM Diagnosis Code Q44.7
  Other congenital malformations of liver
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory liver
  Alagille's syndrome
  Congenital absence of liver
  Congenital hepatomegaly
  Congenital malformation of liver NOS
  - duct Q44.5
    ICD-10-CM Diagnosis Code Q44.5
    Other congenital malformations of bile ducts
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Accessory hepatic duct
    Biliary duct duplication
    Congenital malformation of bile duct NOS
    Cystic duct duplication
- lower limb NEC Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- lumbosacral (joint) (region) Q76.49
  ICD-10-CM Diagnosis Code Q76.49
  Other congenital malformations of spine, not associated with scoliosis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of vertebra NOS
  Congenital fusion of spine NOS
  Congenital malformation of lumbosacral (joint) (region) NOS
  Congenital malformation of spine NOS
  Hemivertebra NOS
  Malformation of spine NOS
  Platyspondylisis NOS
  Supernumerary vertebra NOS
  - kyphosis - see Kyphosis, congenital
  - lordosis - see Lordosis, congenital
- lung Q33.9
  (fissure) (lobe)
  ICD-10-CM Diagnosis Code Q33.9
  Congenital malformation of lung, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- mandible - see Anomaly, dentofacial
- maxilla - see Anomaly, dentofacial
- May D72.0
  (-Hegglin)
  ICD-10-CM Diagnosis Code D72.0
  Genetic anomalies of leukocytes
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Alder (granulation) (granulocyte) anomaly
  Alder syndrome
  Hereditary leukocytic hypersegmentation
  Hereditary leukocytic hyposegmentation
  Hereditary leukomelanopathy
  May-Hegglin (granulation) (granulocyte) anomaly
  May-Hegglin syndrome
  Pelger-Huët (granulation) (granulocyte) anomaly
  Pelger-Huët syndrome
  Type 1 Excludes
  Chédiak (-Steinbrinck)-Higashi syndrome (E70.330)
- meatus urinarius NEC Q64.79
  ICD-10-CM Diagnosis Code Q64.79
  Other congenital malformations of bladder and urethra
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- meningeal bands or folds Q07.9
  ICD-10-CM Diagnosis Code Q07.9
  Congenital malformation of nervous system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS of nervous system
  Congenital deformity NOS of nervous system
  Congenital disease or lesion NOS of nervous system
  - constriction of Q07.8
    ICD-10-CM Diagnosis Code Q07.8
    Other specified congenital malformations of nervous system
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Agenesis of nerve
    Displacement of brachial plexus
    Jaw-winking syndrome
    Marcus Gunn's syndrome
  - spinal Q06.9
    ICD-10-CM Diagnosis Code Q06.9
    Congenital malformation of spinal cord, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital anomaly NOS of spinal cord
    Congenital deformity NOS of spinal cord
    Congenital disease or lesion NOS of spinal cord
- meninges Q07.9
  ICD-10-CM Diagnosis Code Q07.9
  Congenital malformation of nervous system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS of nervous system
  Congenital deformity NOS of nervous system
  Congenital disease or lesion NOS of nervous system
  - cerebral Q04.8
    ICD-10-CM Diagnosis Code Q04.8
    Other specified congenital malformations of brain
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Arnold-Chiari syndrome, type IV
    Macrogyria
  - spinal Q06.9
    ICD-10-CM Diagnosis Code Q06.9
    Congenital malformation of spinal cord, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital anomaly NOS of spinal cord
    Congenital deformity NOS of spinal cord
    Congenital disease or lesion NOS of spinal cord
- meningocele Q05.9
  ICD-10-CM Diagnosis Code Q05.9
  Spina bifida, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- mesentery Q45.9
  ICD-10-CM Diagnosis Code Q45.9
  Congenital malformation of digestive system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of digestive system
  Congenital deformity of digestive system
- metacarpus Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- metatarsus NEC Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- middle ear Q16.4
  ICD-10-CM Diagnosis Code Q16.4
  Other congenital malformations of middle ear
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of middle ear NOS
  - ossicles Q16.3
    ICD-10-CM Diagnosis Code Q16.3
    Congenital malformation of ear ossicles
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital fusion of ear ossicles
- mitral (leaflets) (valve) Q23.9
  ICD-10-CM Diagnosis Code Q23.9
  Congenital malformation of aortic and mitral valves, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - insufficiency Q23.3
    ICD-10-CM Diagnosis Code Q23.3
    Congenital mitral insufficiency
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - specified NEC Q23.8
    ICD-10-CM Diagnosis Code Q23.8
    Other congenital malformations of aortic and mitral valves
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - stenosis Q23.2
    ICD-10-CM Diagnosis Code Q23.2
    Congenital mitral stenosis
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital mitral atresia
- mouth Q38.6
  ICD-10-CM Diagnosis Code Q38.6
  Other congenital malformations of mouth
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of mouth NOS
- Müllerian - see also Anomaly, by site
  - uterus NEC Q51.818
    ICD-10-CM Diagnosis Code Q51.818
    Other congenital malformations of uterus
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
    Applicable To
    Müllerian anomaly of uterus NEC
- multiple NEC Q89.7
  ICD-10-CM Diagnosis Code Q89.7
  Multiple congenital malformations, not elsewhere classified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Multiple congenital anomalies NOS
  Multiple congenital deformities NOS
  Type 1 Excludes
  congenital malformation syndromes affecting multiple systems (Q87.-)
- muscle Q79.9
  ICD-10-CM Diagnosis Code Q79.9
  Congenital malformation of musculoskeletal system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of musculoskeletal system NOS
  Congenital deformity of musculoskeletal system NOS
  - eyelid Q10.3
    ICD-10-CM Diagnosis Code Q10.3
    Other congenital malformations of eyelid
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Ablepharon
    Blepharophimosis, congenital
    Coloboma of eyelid
    Congenital absence or agenesis of cilia
    Congenital absence or agenesis of eyelid
    Congenital accessory eyelid
    Congenital accessory eye muscle
    Congenital malformation of eyelid NOS
- musculoskeletal system, except limbs Q79.9
  ICD-10-CM Diagnosis Code Q79.9
  Congenital malformation of musculoskeletal system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of musculoskeletal system NOS
  Congenital deformity of musculoskeletal system NOS
- myocardium Q24.8
  ICD-10-CM Diagnosis Code Q24.8
  Other specified congenital malformations of heart
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital diverticulum of left ventricle
  Congenital malformation of myocardium
  Congenital malformation of pericardium
  Malposition of heart
  Uhl's disease
- nail Q84.6
  ICD-10-CM Diagnosis Code Q84.6
  Other congenital malformations of nails
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital clubnail
  Congenital koilonychia
  Congenital malformation of nail NOS
- narrowness, eyelid Q10.3
  ICD-10-CM Diagnosis Code Q10.3
  Other congenital malformations of eyelid
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Ablepharon
  Blepharophimosis, congenital
  Coloboma of eyelid
  Congenital absence or agenesis of cilia
  Congenital absence or agenesis of eyelid
  Congenital accessory eyelid
  Congenital accessory eye muscle
  Congenital malformation of eyelid NOS
- nasal sinus Q30.8
  (wall)
  ICD-10-CM Diagnosis Code Q30.8
  Other congenital malformations of nose
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory nose
  Congenital anomaly of nasal sinus wall
- neck Q18.9
  (any part)
  ICD-10-CM Diagnosis Code Q18.9
  Congenital malformation of face and neck, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS of face and neck
- nerve Q07.9
  ICD-10-CM Diagnosis Code Q07.9
  Congenital malformation of nervous system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS of nervous system
  Congenital deformity NOS of nervous system
  Congenital disease or lesion NOS of nervous system
  - acoustic Q07.8
    ICD-10-CM Diagnosis Code Q07.8
    Other specified congenital malformations of nervous system
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Agenesis of nerve
    Displacement of brachial plexus
    Jaw-winking syndrome
    Marcus Gunn's syndrome
  - optic Q07.8
    ICD-10-CM Diagnosis Code Q07.8
    Other specified congenital malformations of nervous system
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Agenesis of nerve
    Displacement of brachial plexus
    Jaw-winking syndrome
    Marcus Gunn's syndrome
- nervous system Q07.9
  (central)
  ICD-10-CM Diagnosis Code Q07.9
  Congenital malformation of nervous system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS of nervous system
  Congenital deformity NOS of nervous system
  Congenital disease or lesion NOS of nervous system
- nipple Q83.9
  ICD-10-CM Diagnosis Code Q83.9
  Congenital malformation of breast, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- nose, nasal (bones) (cartilage) (septum) (sinus) Q30.9
  ICD-10-CM Diagnosis Code Q30.9
  Congenital malformation of nose, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - specified NEC Q30.8
    ICD-10-CM Diagnosis Code Q30.8
    Other congenital malformations of nose
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Accessory nose
    Congenital anomaly of nasal sinus wall
- ocular muscle Q15.8
  ICD-10-CM Diagnosis Code Q15.8
  Other specified congenital malformations of eye
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- omphalomesenteric duct Q43.0
  ICD-10-CM Diagnosis Code Q43.0
  Meckel's diverticulum (displaced) (hypertrophic)
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Persistent omphalomesenteric duct
  Persistent vitelline duct
- opening, pulmonary veins Q26.4
  ICD-10-CM Diagnosis Code Q26.4
  Anomalous pulmonary venous connection, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- optic
  - disc Q14.2
    ICD-10-CM Diagnosis Code Q14.2
    Congenital malformation of optic disc
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Coloboma of optic disc
  - nerve Q07.8
    ICD-10-CM Diagnosis Code Q07.8
    Other specified congenital malformations of nervous system
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Agenesis of nerve
    Displacement of brachial plexus
    Jaw-winking syndrome
    Marcus Gunn's syndrome
- opticociliary vessels Q13.2
  ICD-10-CM Diagnosis Code Q13.2
  Other congenital malformations of iris
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Anisocoria, congenital
  Atresia of pupil
  Congenital malformation of iris NOS
  Corectopia
- orbit Q10.7
  (eye)
  ICD-10-CM Diagnosis Code Q10.7
  Congenital malformation of orbit
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- organ Q89.9
  ICD-10-CM Diagnosis Code Q89.9
  Congenital malformation, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS
  Congenital deformity NOS
  - of Corti Q16.5
    ICD-10-CM Diagnosis Code Q16.5
    Congenital malformation of inner ear
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital anomaly of membranous labyrinth
    Congenital anomaly of organ of Corti
- origin
  - artery
    - innominate Q25.8
      ICD-10-CM Diagnosis Code Q25.8
      Other congenital malformations of other great arteries
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    - pulmonary Q25.79
      ICD-10-CM Diagnosis Code Q25.79
      Other congenital malformations of pulmonary artery
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Aberrant pulmonary artery
      Agenesis of pulmonary artery
      Congenital aneurysm of pulmonary artery
      Congenital anomaly of pulmonary artery
      Hypoplasia of pulmonary artery
    - renal Q27.2
      ICD-10-CM Diagnosis Code Q27.2
      Other congenital malformations of renal artery
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Congenital malformation of renal artery NOS
      Multiple renal arteries
    - subclavian Q25.48
      ICD-10-CM Diagnosis Code Q25.48
      Anomalous origin of subclavian artery
      2017 - New Code 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- osseous meatus Q16.1
  (ear)
  ICD-10-CM Diagnosis Code Q16.1
  Congenital absence, atresia and stricture of auditory canal (external)
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital atresia or stricture of osseous meatus
- ovary Q50.39
  ICD-10-CM Diagnosis Code Q50.39
  Other congenital malformation of ovary
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Congenital malformation of ovary NOS
- oviduct Q50.6
  ICD-10-CM Diagnosis Code Q50.6
  Other congenital malformations of fallopian tube and broad ligament
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Absence of fallopian tube and broad ligament
  Accessory fallopian tube and broad ligament
  Atresia of fallopian tube and broad ligament
  Congenital malformation of fallopian tube or broad ligament NOS
- palate Q38.5
  (hard) (soft)
  ICD-10-CM Diagnosis Code Q38.5
  Congenital malformations of palate, not elsewhere classified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of uvula
  Congenital malformation of palate NOS
  Congenital high arched palate
  Type 1 Excludes
  cleft palate (Q35.-)
  cleft palate with cleft lip (Q37.-)
- pancreas or pancreatic duct Q45.3
  ICD-10-CM Diagnosis Code Q45.3
  Other congenital malformations of pancreas and pancreatic duct
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory pancreas
  Congenital malformation of pancreas or pancreatic duct NOS
  Type 1 Excludes
  congenital diabetes mellitus (E10.-)
  cystic fibrosis (E84.0-E84.9)
  fibrocystic disease of pancreas (E84.-)
  neonatal diabetes mellitus (P70.2)
- papillary muscles Q24.8
  ICD-10-CM Diagnosis Code Q24.8
  Other specified congenital malformations of heart
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital diverticulum of left ventricle
  Congenital malformation of myocardium
  Congenital malformation of pericardium
  Malposition of heart
  Uhl's disease
- parathyroid gland Q89.2
  ICD-10-CM Diagnosis Code Q89.2
  Congenital malformations of other endocrine glands
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of parathyroid or thyroid gland
  Persistent thyroglossal duct
  Thyroglossal cyst
  Type 1 Excludes
  congenital goiter (E03.0)
  congenital hypothyroidism (E03.1)
- paraurethral ducts Q64.79
  ICD-10-CM Diagnosis Code Q64.79
  Other congenital malformations of bladder and urethra
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- parotid Q38.4
  (gland)
  ICD-10-CM Diagnosis Code Q38.4
  Congenital malformations of salivary glands and ducts
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Atresia of salivary glands and ducts
  Congenital absence of salivary glands and ducts
  Congenital accessory salivary glands and ducts
  Congenital fistula of salivary gland
- patella Q74.1
  ICD-10-CM Diagnosis Code Q74.1
  Congenital malformation of knee
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of patella
  Congenital dislocation of patella
  Congenital genu valgum
  Congenital genu varum
  Rudimentary patella
  Type 1 Excludes
  congenital dislocation of knee (Q68.2)
  congenital genu recurvatum (Q68.2)
  nail patella syndrome (Q87.2)
- Pelger-Huët D72.0
  (hereditary hyposegmentation)
  ICD-10-CM Diagnosis Code D72.0
  Genetic anomalies of leukocytes
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Alder (granulation) (granulocyte) anomaly
  Alder syndrome
  Hereditary leukocytic hypersegmentation
  Hereditary leukocytic hyposegmentation
  Hereditary leukomelanopathy
  May-Hegglin (granulation) (granulocyte) anomaly
  May-Hegglin syndrome
  Pelger-Huët (granulation) (granulocyte) anomaly
  Pelger-Huët syndrome
  Type 1 Excludes
  Chédiak (-Steinbrinck)-Higashi syndrome (E70.330)
- pelvic girdle NEC Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- pelvis (bony) Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
  - rachitic E64.3
    ICD-10-CM Diagnosis Code E64.3
    Sequelae of rickets
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- penis Q55.69
  (glans)
  ICD-10-CM Diagnosis Code Q55.69
  Other congenital malformation of penis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
  Applicable To
  Congenital malformation of penis NOS
- pericardium Q24.8
  ICD-10-CM Diagnosis Code Q24.8
  Other specified congenital malformations of heart
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital diverticulum of left ventricle
  Congenital malformation of myocardium
  Congenital malformation of pericardium
  Malposition of heart
  Uhl's disease
- peripheral vascular system Q27.9
  ICD-10-CM Diagnosis Code Q27.9
  Congenital malformation of peripheral vascular system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Anomaly of artery or vein NOS
- Peter's Q13.4
  ICD-10-CM Diagnosis Code Q13.4
  Other congenital corneal malformations
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of cornea NOS
  Microcornea
  Peter's anomaly
- pharynx Q38.8
  ICD-10-CM Diagnosis Code Q38.8
  Other congenital malformations of pharynx
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of pharynx NOS
  Imperforate pharynx
- pigmentation L81.9
  ICD-10-CM Diagnosis Code L81.9
  Disorder of pigmentation, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  - congenital Q82.8
    ICD-10-CM Diagnosis Code Q82.8
    Other specified congenital malformations of skin
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Abnormal palmar creases
    Accessory skin tags
    Benign familial pemphigus [Hailey-Hailey]
    Congenital poikiloderma
    Cutis laxa (hyperelastica)
    Dermatoglyphic anomalies
    Inherited keratosis palmaris et plantaris
    Keratosis follicularis [Darier-White]
    Type 1 Excludes
    Ehlers-Danlos syndromes (Q79.6-)
- pituitary Q89.2
  (gland)
  ICD-10-CM Diagnosis Code Q89.2
  Congenital malformations of other endocrine glands
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of parathyroid or thyroid gland
  Persistent thyroglossal duct
  Thyroglossal cyst
  Type 1 Excludes
  congenital goiter (E03.0)
  congenital hypothyroidism (E03.1)
- pleural Q34.0
  (folds)
  ICD-10-CM Diagnosis Code Q34.0
  Anomaly of pleura
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- portal vein Q26.5
  ICD-10-CM Diagnosis Code Q26.5
  Anomalous portal venous connection
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - connection Q26.5
    ICD-10-CM Diagnosis Code Q26.5
    Anomalous portal venous connection
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- position, tooth, teeth, fully erupted M26.30
  ICD-10-CM Diagnosis Code M26.30
  Unspecified anomaly of tooth position of fully erupted tooth or teeth
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Abnormal spacing of fully erupted tooth or teeth NOS
  Displacement of fully erupted tooth or teeth NOS
  Transposition of fully erupted tooth or teeth NOS
  - specified NEC M26.39
    ICD-10-CM Diagnosis Code M26.39
    Other anomalies of tooth position of fully erupted tooth or teeth
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
- precerebral vessel Q28.1
  ICD-10-CM Diagnosis Code Q28.1
  Other malformations of precerebral vessels
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of precerebral vessels NOS
  Congenital precerebral aneurysm (nonruptured)
- prepuce Q55.69
  ICD-10-CM Diagnosis Code Q55.69
  Other congenital malformation of penis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
  Applicable To
  Congenital malformation of penis NOS
- prostate Q55.4
  ICD-10-CM Diagnosis Code Q55.4
  Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
  Applicable To
  Absence or aplasia of prostate
  Absence or aplasia of spermatic cord
  Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
- pulmonary Q33.9
  ICD-10-CM Diagnosis Code Q33.9
  Congenital malformation of lung, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - artery NEC Q25.79
    ICD-10-CM Diagnosis Code Q25.79
    Other congenital malformations of pulmonary artery
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Aberrant pulmonary artery
    Agenesis of pulmonary artery
    Congenital aneurysm of pulmonary artery
    Congenital anomaly of pulmonary artery
    Hypoplasia of pulmonary artery
  - valve Q22.3
    ICD-10-CM Diagnosis Code Q22.3
    Other congenital malformations of pulmonary valve
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital malformation of pulmonary valve NOS
    Supernumerary cusps of pulmonary valve
    - atresia Q22.0
      ICD-10-CM Diagnosis Code Q22.0
      Pulmonary valve atresia
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    - insufficiency Q22.2
      ICD-10-CM Diagnosis Code Q22.2
      Congenital pulmonary valve insufficiency
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Congenital pulmonary valve regurgitation
    - specified type NEC Q22.3
      ICD-10-CM Diagnosis Code Q22.3
      Other congenital malformations of pulmonary valve
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Congenital malformation of pulmonary valve NOS
      Supernumerary cusps of pulmonary valve
    - stenosis Q22.1
      ICD-10-CM Diagnosis Code Q22.1
      Congenital pulmonary valve stenosis
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      - infundibular Q24.3
        ICD-10-CM Diagnosis Code Q24.3
        Pulmonary infundibular stenosis
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        Subvalvular pulmonic stenosis
      - subvalvular Q24.3
        ICD-10-CM Diagnosis Code Q24.3
        Pulmonary infundibular stenosis
        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        Applicable To
        Subvalvular pulmonic stenosis
  - venous connection Q26.4
    ICD-10-CM Diagnosis Code Q26.4
    Anomalous pulmonary venous connection, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    - partial Q26.3
      ICD-10-CM Diagnosis Code Q26.3
      Partial anomalous pulmonary venous connection
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Partial anomalous pulmonary venous return
    - total Q26.2
      ICD-10-CM Diagnosis Code Q26.2
      Total anomalous pulmonary venous connection
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Total anomalous pulmonary venous return [TAPVR], subdiaphragmatic
      Total anomalous pulmonary venous return [TAPVR], supradiaphragmatic
- pupil Q13.2
  ICD-10-CM Diagnosis Code Q13.2
  Other congenital malformations of iris
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Anisocoria, congenital
  Atresia of pupil
  Congenital malformation of iris NOS
  Corectopia
  - function H57.00
    ICD-10-CM Diagnosis Code H57.00
    Unspecified anomaly of pupillary function
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - anisocoria H57.02
      ICD-10-CM Diagnosis Code H57.02
      Anisocoria
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - Argyll Robertson pupil H57.01
      ICD-10-CM Diagnosis Code H57.01
      Argyll Robertson pupil, atypical
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Type 1 Excludes
      syphilitic Argyll Robertson pupil (A52.19)
    - miosis H57.03
      ICD-10-CM Diagnosis Code H57.03
      Miosis
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - mydriasis H57.04
      ICD-10-CM Diagnosis Code H57.04
      Mydriasis
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - specified type NEC H57.09
      ICD-10-CM Diagnosis Code H57.09
      Other anomalies of pupillary function
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    - tonic pupil H57.05-
      ICD-10-CM Diagnosis Code H57.05-
      Tonic pupil
      2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
- pylorus Q40.3
  ICD-10-CM Diagnosis Code Q40.3
  Congenital malformation of stomach, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- radius Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- rectum Q43.9
  ICD-10-CM Diagnosis Code Q43.9
  Congenital malformation of intestine, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- reduction (extremity) (limb)
  - femur (longitudinal) - see Defect, reduction, lower limb, longitudinal, femur
  - fibula (longitudinal) - see Defect, reduction, lower limb, longitudinal, fibula
  - lower limb - see Defect, reduction, lower limb
  - radius (longitudinal) - see Defect, reduction, upper limb, longitudinal, radius
  - tibia (longitudinal) - see Defect, reduction, lower limb, longitudinal, tibia
  - ulna (longitudinal) - see Defect, reduction, upper limb, longitudinal, ulna
  - upper limb - see Defect, reduction, upper limb
- refraction - see Disorder, refraction
- renal Q63.9
  ICD-10-CM Diagnosis Code Q63.9
  Congenital malformation of kidney, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - artery Q27.2
    ICD-10-CM Diagnosis Code Q27.2
    Other congenital malformations of renal artery
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital malformation of renal artery NOS
    Multiple renal arteries
  - pelvis Q63.9
    ICD-10-CM Diagnosis Code Q63.9
    Congenital malformation of kidney, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    - specified NEC Q63.8
      ICD-10-CM Diagnosis Code Q63.8
      Other specified congenital malformations of kidney
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Congenital renal calculi
- respiratory system Q34.9
  ICD-10-CM Diagnosis Code Q34.9
  Congenital malformation of respiratory system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of respiratory system
  Congenital anomaly of respiratory system NOS
  - specified NEC Q34.8
    ICD-10-CM Diagnosis Code Q34.8
    Other specified congenital malformations of respiratory system
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Atresia of nasopharynx
- retina Q14.1
  ICD-10-CM Diagnosis Code Q14.1
  Congenital malformation of retina
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital retinal aneurysm
- rib Q76.6
  ICD-10-CM Diagnosis Code Q76.6
  Other congenital malformations of ribs
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory rib
  Congenital absence of rib
  Congenital fusion of ribs
  Congenital malformation of ribs NOS
  Type 1 Excludes
  short rib syndrome (Q77.2)
  - cervical Q76.5
    ICD-10-CM Diagnosis Code Q76.5
    Cervical rib
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Supernumerary rib in cervical region
- Rieger's Q13.81
  ICD-10-CM Diagnosis Code Q13.81
  Rieger's anomaly
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Use Additional
  code for associated glaucoma (H42)
- rotation - see Malrotation
  - hip or thigh Q65.89
    ICD-10-CM Diagnosis Code Q65.89
    Other specified congenital deformities of hip
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Anteversion of femoral neck
    Congenital acetabular dysplasia
- round ligament Q52.8
  ICD-10-CM Diagnosis Code Q52.8
  Other specified congenital malformations of female genitalia
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
- sacroiliac Q74.2
  (joint)
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- sacrum NEC Q76.49
  ICD-10-CM Diagnosis Code Q76.49
  Other congenital malformations of spine, not associated with scoliosis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of vertebra NOS
  Congenital fusion of spine NOS
  Congenital malformation of lumbosacral (joint) (region) NOS
  Congenital malformation of spine NOS
  Hemivertebra NOS
  Malformation of spine NOS
  Platyspondylisis NOS
  Supernumerary vertebra NOS
  - kyphosis - see Kyphosis, congenital
  - lordosis - see Lordosis, congenital
- saddle nose, syphilitic A50.57
  ICD-10-CM Diagnosis Code A50.57
  Syphilitic saddle nose
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
- salivary duct or gland Q38.4
  ICD-10-CM Diagnosis Code Q38.4
  Congenital malformations of salivary glands and ducts
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Atresia of salivary glands and ducts
  Congenital absence of salivary glands and ducts
  Congenital accessory salivary glands and ducts
  Congenital fistula of salivary gland
- scapula Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- scrotum - see Malformation, testis and scrotum
- sebaceous gland Q82.9
  ICD-10-CM Diagnosis Code Q82.9
  Congenital malformation of skin, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- seminal vesicles Q55.4
  ICD-10-CM Diagnosis Code Q55.4
  Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
  Applicable To
  Absence or aplasia of prostate
  Absence or aplasia of spermatic cord
  Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
- sense organs NEC Q07.8
  ICD-10-CM Diagnosis Code Q07.8
  Other specified congenital malformations of nervous system
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Agenesis of nerve
  Displacement of brachial plexus
  Jaw-winking syndrome
  Marcus Gunn's syndrome
- sex chromosomes NEC - see also Anomaly, chromosomes
  - female phenotype Q97.8
    ICD-10-CM Diagnosis Code Q97.8
    Other specified sex chromosome abnormalities, female phenotype
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  - male phenotype Q98.9
    ICD-10-CM Diagnosis Code Q98.9
    Sex chromosome abnormality, male phenotype, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
- shoulder Q74.0
  (girdle) (joint)
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- sigmoid Q43.9
  (flexure)
  ICD-10-CM Diagnosis Code Q43.9
  Congenital malformation of intestine, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- simian crease Q82.8
  ICD-10-CM Diagnosis Code Q82.8
  Other specified congenital malformations of skin
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Abnormal palmar creases
  Accessory skin tags
  Benign familial pemphigus [Hailey-Hailey]
  Congenital poikiloderma
  Cutis laxa (hyperelastica)
  Dermatoglyphic anomalies
  Inherited keratosis palmaris et plantaris
  Keratosis follicularis [Darier-White]
  Type 1 Excludes
  Ehlers-Danlos syndromes (Q79.6-)
- sinus of Valsalva Q25.49
  ICD-10-CM Diagnosis Code Q25.49
  Other congenital malformations of aorta
  2017 - New Code 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Aortic arch
  Bovine arch
- skeleton generalized Q78.9
  ICD-10-CM Diagnosis Code Q78.9
  Osteochondrodysplasia, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Chondrodystrophy NOS
  Osteodystrophy NOS
- skin Q82.9
  (appendage)
  ICD-10-CM Diagnosis Code Q82.9
  Congenital malformation of skin, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- skull Q75.9
  ICD-10-CM Diagnosis Code Q75.9
  Congenital malformation of skull and face bones, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of face bones NOS
  Congenital anomaly of skull NOS
  - with
    - anencephaly Q00.0
      ICD-10-CM Diagnosis Code Q00.0
      Anencephaly
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Acephaly
      Acrania
      Amyelencephaly
      Hemianencephaly
      Hemicephaly
    - encephalocele - see Encephalocele
    - hydrocephalus Q03.9
      ICD-10-CM Diagnosis Code Q03.9
      Congenital hydrocephalus, unspecified
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      - with spina bifida - see Spina bifida, by site, with hydrocephalus
    - microcephaly Q02
      ICD-10-CM Diagnosis Code Q02
      Microcephaly
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Code First
      , if applicable, congenital Zika virus disease
      Includes
      hydromicrocephaly
      micrencephalon
      Type 1 Excludes
      Meckel-Gruber syndrome (Q61.9)
- specified organ or site NEC Q89.8
  ICD-10-CM Diagnosis Code Q89.8
  Other specified congenital malformations
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Use Additional
  code(s) to identify all associated manifestations
- spermatic cord Q55.4
  ICD-10-CM Diagnosis Code Q55.4
  Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
  Applicable To
  Absence or aplasia of prostate
  Absence or aplasia of spermatic cord
  Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
- spine, spinal NEC Q76.49
  ICD-10-CM Diagnosis Code Q76.49
  Other congenital malformations of spine, not associated with scoliosis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of vertebra NOS
  Congenital fusion of spine NOS
  Congenital malformation of lumbosacral (joint) (region) NOS
  Congenital malformation of spine NOS
  Hemivertebra NOS
  Malformation of spine NOS
  Platyspondylisis NOS
  Supernumerary vertebra NOS
  - column NEC Q76.49
    ICD-10-CM Diagnosis Code Q76.49
    Other congenital malformations of spine, not associated with scoliosis
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital absence of vertebra NOS
    Congenital fusion of spine NOS
    Congenital malformation of lumbosacral (joint) (region) NOS
    Congenital malformation of spine NOS
    Hemivertebra NOS
    Malformation of spine NOS
    Platyspondylisis NOS
    Supernumerary vertebra NOS
    - kyphosis - see Kyphosis, congenital
    - lordosis - see Lordosis, congenital
  - cord Q06.9
    ICD-10-CM Diagnosis Code Q06.9
    Congenital malformation of spinal cord, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital anomaly NOS of spinal cord
    Congenital deformity NOS of spinal cord
    Congenital disease or lesion NOS of spinal cord
  - nerve root Q07.8
    ICD-10-CM Diagnosis Code Q07.8
    Other specified congenital malformations of nervous system
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Agenesis of nerve
    Displacement of brachial plexus
    Jaw-winking syndrome
    Marcus Gunn's syndrome
- spleen Q89.09
  ICD-10-CM Diagnosis Code Q89.09
  Congenital malformations of spleen
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital splenomegaly
  - agenesis Q89.01
    ICD-10-CM Diagnosis Code Q89.01
    Asplenia (congenital)
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- stenonian duct Q38.4
  ICD-10-CM Diagnosis Code Q38.4
  Congenital malformations of salivary glands and ducts
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Atresia of salivary glands and ducts
  Congenital absence of salivary glands and ducts
  Congenital accessory salivary glands and ducts
  Congenital fistula of salivary gland
- sternum NEC Q76.7
  ICD-10-CM Diagnosis Code Q76.7
  Congenital malformation of sternum
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of sternum
  Sternum bifidum
- stomach Q40.3
  ICD-10-CM Diagnosis Code Q40.3
  Congenital malformation of stomach, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- submaxillary gland Q38.4
  ICD-10-CM Diagnosis Code Q38.4
  Congenital malformations of salivary glands and ducts
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Atresia of salivary glands and ducts
  Congenital absence of salivary glands and ducts
  Congenital accessory salivary glands and ducts
  Congenital fistula of salivary gland
- tarsus NEC Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- tendon Q79.9
  ICD-10-CM Diagnosis Code Q79.9
  Congenital malformation of musculoskeletal system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of musculoskeletal system NOS
  Congenital deformity of musculoskeletal system NOS
- testis - see Malformation, testis and scrotum
- thigh NEC Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- thorax (wall) Q67.8
  ICD-10-CM Diagnosis Code Q67.8
  Other congenital deformities of chest
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital deformity of chest wall NOS
  - bony Q76.9
    ICD-10-CM Diagnosis Code Q76.9
    Congenital malformation of bony thorax, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- throat Q38.8
  ICD-10-CM Diagnosis Code Q38.8
  Other congenital malformations of pharynx
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of pharynx NOS
  Imperforate pharynx
- thumb Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- thymus gland Q89.2
  ICD-10-CM Diagnosis Code Q89.2
  Congenital malformations of other endocrine glands
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of parathyroid or thyroid gland
  Persistent thyroglossal duct
  Thyroglossal cyst
  Type 1 Excludes
  congenital goiter (E03.0)
  congenital hypothyroidism (E03.1)
- thyroid (gland) Q89.2
  ICD-10-CM Diagnosis Code Q89.2
  Congenital malformations of other endocrine glands
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital malformation of parathyroid or thyroid gland
  Persistent thyroglossal duct
  Thyroglossal cyst
  Type 1 Excludes
  congenital goiter (E03.0)
  congenital hypothyroidism (E03.1)
  - cartilage Q31.8
    ICD-10-CM Diagnosis Code Q31.8
    Other congenital malformations of larynx
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Absence of larynx
    Agenesis of larynx
    Atresia of larynx
    Congenital cleft thyroid cartilage
    Congenital fissure of epiglottis
    Congenital stenosis of larynx NEC
    Posterior cleft of cricoid cartilage
- tibia NEC Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
  - saber A50.56
    ICD-10-CM Diagnosis Code A50.56
    Late congenital syphilitic osteochondropathy
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
- toe Q74.2
  ICD-10-CM Diagnosis Code Q74.2
  Other congenital malformations of lower limb(s), including pelvic girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital fusion of sacroiliac joint
  Congenital malformation of ankle joint
  Congenital malformation of sacroiliac joint
  Type 1 Excludes
  anteversion of femur (neck) (Q65.89)
- tongue Q38.3
  ICD-10-CM Diagnosis Code Q38.3
  Other congenital malformations of tongue
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Aglossia
  Bifid tongue
  Congenital adhesion of tongue
  Congenital fissure of tongue
  Congenital malformation of tongue NOS
  Double tongue
  Hypoglossia
  Hypoplasia of tongue
  Microglossia
- tooth, teeth K00.9
  ICD-10-CM Diagnosis Code K00.9
  Disorder of tooth development, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  Applicable To
  Disorder of odontogenesis NOS
  - eruption K00.6
    ICD-10-CM Diagnosis Code K00.6
    Disturbances in tooth eruption
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    Dentia praecox
    Natal tooth
    Neonatal tooth
    Premature eruption of tooth
    Premature shedding of primary [deciduous] tooth
    Prenatal teeth
    Retained [persistent] primary tooth
    Type 2 Excludes
    embedded and impacted teeth (K01.-)
  - position, fully erupted M26.30
    ICD-10-CM Diagnosis Code M26.30
    Unspecified anomaly of tooth position of fully erupted tooth or teeth
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    Abnormal spacing of fully erupted tooth or teeth NOS
    Displacement of fully erupted tooth or teeth NOS
    Transposition of fully erupted tooth or teeth NOS
  - spacing, fully erupted M26.30
    ICD-10-CM Diagnosis Code M26.30
    Unspecified anomaly of tooth position of fully erupted tooth or teeth
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    Applicable To
    Abnormal spacing of fully erupted tooth or teeth NOS
    Displacement of fully erupted tooth or teeth NOS
    Transposition of fully erupted tooth or teeth NOS
- trachea Q32.1
  (cartilage)
  ICD-10-CM Diagnosis Code Q32.1
  Other congenital malformations of trachea
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Atresia of trachea
  Congenital anomaly of tracheal cartilage
  Congenital dilatation of trachea
  Congenital malformation of trachea
  Congenital stenosis of trachea
  Congenital tracheocele
- tragus Q17.9
  ICD-10-CM Diagnosis Code Q17.9
  Congenital malformation of ear, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of ear NOS
- tricuspid (leaflet) (valve) Q22.9
  ICD-10-CM Diagnosis Code Q22.9
  Congenital malformation of tricuspid valve, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - atresia or stenosis Q22.4
    ICD-10-CM Diagnosis Code Q22.4
    Congenital tricuspid stenosis
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital tricuspid atresia
  - Ebstein's Q22.5
    ICD-10-CM Diagnosis Code Q22.5
    Ebstein's anomaly
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- Uhl's Q24.8
  (hypoplasia of myocardium, right ventricle)
  ICD-10-CM Diagnosis Code Q24.8
  Other specified congenital malformations of heart
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital diverticulum of left ventricle
  Congenital malformation of myocardium
  Congenital malformation of pericardium
  Malposition of heart
  Uhl's disease
- ulna Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- umbilical artery Q27.0
  ICD-10-CM Diagnosis Code Q27.0
  Congenital absence and hypoplasia of umbilical artery
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Single umbilical artery
- union
  - cricoid cartilage and thyroid cartilage Q31.8
    ICD-10-CM Diagnosis Code Q31.8
    Other congenital malformations of larynx
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Absence of larynx
    Agenesis of larynx
    Atresia of larynx
    Congenital cleft thyroid cartilage
    Congenital fissure of epiglottis
    Congenital stenosis of larynx NEC
    Posterior cleft of cricoid cartilage
  - thyroid cartilage and hyoid bone Q31.8
    ICD-10-CM Diagnosis Code Q31.8
    Other congenital malformations of larynx
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Absence of larynx
    Agenesis of larynx
    Atresia of larynx
    Congenital cleft thyroid cartilage
    Congenital fissure of epiglottis
    Congenital stenosis of larynx NEC
    Posterior cleft of cricoid cartilage
  - trachea with larynx Q31.8
    ICD-10-CM Diagnosis Code Q31.8
    Other congenital malformations of larynx
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Absence of larynx
    Agenesis of larynx
    Atresia of larynx
    Congenital cleft thyroid cartilage
    Congenital fissure of epiglottis
    Congenital stenosis of larynx NEC
    Posterior cleft of cricoid cartilage
- upper limb Q74.0
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb
- urachus Q64.4
  ICD-10-CM Diagnosis Code Q64.4
  Malformation of urachus
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Cyst of urachus
  Patent urachus
  Prolapse of urachus
- ureter Q62.8
  ICD-10-CM Diagnosis Code Q62.8
  Other congenital malformations of ureter
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Anomaly of ureter NOS
  - obstructive NEC Q62.39
    ICD-10-CM Diagnosis Code Q62.39
    Other obstructive defects of renal pelvis and ureter
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Ureteropelvic junction obstruction NOS
    - cecoureterocele Q62.32
      ICD-10-CM Diagnosis Code Q62.32
      Cecoureterocele
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Ectopic ureterocele
    - orthotopic ureterocele Q62.31
      ICD-10-CM Diagnosis Code Q62.31
      Congenital ureterocele, orthotopic
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- urethra Q64.70
  ICD-10-CM Diagnosis Code Q64.70
  Unspecified congenital malformation of bladder and urethra
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Malformation of bladder or urethra NOS
  - absence Q64.5
    ICD-10-CM Diagnosis Code Q64.5
    Congenital absence of bladder and urethra
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - double Q64.74
    ICD-10-CM Diagnosis Code Q64.74
    Double urethra
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - fistula to rectum Q64.73
    ICD-10-CM Diagnosis Code Q64.73
    Congenital urethrorectal fistula
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - obstructive Q64.39
    ICD-10-CM Diagnosis Code Q64.39
    Other atresia and stenosis of urethra and bladder neck
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Atresia and stenosis of urethra and bladder neck NOS
    - stricture Q64.32
      ICD-10-CM Diagnosis Code Q64.32
      Congenital stricture of urethra
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - prolapse Q64.71
    ICD-10-CM Diagnosis Code Q64.71
    Congenital prolapse of urethra
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  - specified type NEC Q64.79
    ICD-10-CM Diagnosis Code Q64.79
    Other congenital malformations of bladder and urethra
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- urinary tract Q64.9
  ICD-10-CM Diagnosis Code Q64.9
  Congenital malformation of urinary system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly NOS of urinary system
  Congenital deformity NOS of urinary system
- uterus Q51.9
  ICD-10-CM Diagnosis Code Q51.9
  Congenital malformation of uterus and cervix, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  - with only one functioning horn Q51.4
    ICD-10-CM Diagnosis Code Q51.4
    Unicornate uterus
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
    Applicable To
    Unicornate uterus with or without a separate uterine horn
    Uterus with only one functioning horn
- uvula Q38.5
  ICD-10-CM Diagnosis Code Q38.5
  Congenital malformations of palate, not elsewhere classified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of uvula
  Congenital malformation of palate NOS
  Congenital high arched palate
  Type 1 Excludes
  cleft palate (Q35.-)
  cleft palate with cleft lip (Q37.-)
- vagina Q52.4
  ICD-10-CM Diagnosis Code Q52.4
  Other congenital malformations of vagina
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Canal of Nuck cyst, congenital
  Congenital malformation of vagina NOS
  Embryonic vaginal cyst
  Gartner's duct cyst
- valleculae Q31.8
  ICD-10-CM Diagnosis Code Q31.8
  Other congenital malformations of larynx
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of larynx
  Agenesis of larynx
  Atresia of larynx
  Congenital cleft thyroid cartilage
  Congenital fissure of epiglottis
  Congenital stenosis of larynx NEC
  Posterior cleft of cricoid cartilage
- valve (heart) Q24.8
  ICD-10-CM Diagnosis Code Q24.8
  Other specified congenital malformations of heart
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital diverticulum of left ventricle
  Congenital malformation of myocardium
  Congenital malformation of pericardium
  Malposition of heart
  Uhl's disease
  - coronary sinus Q24.5
    ICD-10-CM Diagnosis Code Q24.5
    Malformation of coronary vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital coronary (artery) aneurysm
  - inferior vena cava Q24.8
    ICD-10-CM Diagnosis Code Q24.8
    Other specified congenital malformations of heart
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital diverticulum of left ventricle
    Congenital malformation of myocardium
    Congenital malformation of pericardium
    Malposition of heart
    Uhl's disease
  - pulmonary Q22.3
    ICD-10-CM Diagnosis Code Q22.3
    Other congenital malformations of pulmonary valve
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital malformation of pulmonary valve NOS
    Supernumerary cusps of pulmonary valve
  - sinus coronario Q24.5
    ICD-10-CM Diagnosis Code Q24.5
    Malformation of coronary vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital coronary (artery) aneurysm
  - venae cavae inferioris Q24.8
    ICD-10-CM Diagnosis Code Q24.8
    Other specified congenital malformations of heart
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital diverticulum of left ventricle
    Congenital malformation of myocardium
    Congenital malformation of pericardium
    Malposition of heart
    Uhl's disease
- vas deferens Q55.4
  ICD-10-CM Diagnosis Code Q55.4
  Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt
  Applicable To
  Absence or aplasia of prostate
  Absence or aplasia of spermatic cord
  Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
- vascular Q27.9
  ICD-10-CM Diagnosis Code Q27.9
  Congenital malformation of peripheral vascular system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Anomaly of artery or vein NOS
  - brain Q28.3
    ICD-10-CM Diagnosis Code Q28.3
    Other malformations of cerebral vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital cerebral aneurysm (nonruptured)
    Congenital malformation of cerebral vessels NOS
    Developmental venous anomaly
  - ring Q25.45
    ICD-10-CM Diagnosis Code Q25.45
    Double aortic arch
    2017 - New Code 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Vascular ring of aorta
- vein(s) (peripheral) Q27.9
  ICD-10-CM Diagnosis Code Q27.9
  Congenital malformation of peripheral vascular system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Anomaly of artery or vein NOS
  - brain Q28.3
    ICD-10-CM Diagnosis Code Q28.3
    Other malformations of cerebral vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital cerebral aneurysm (nonruptured)
    Congenital malformation of cerebral vessels NOS
    Developmental venous anomaly
  - cerebral Q28.3
    ICD-10-CM Diagnosis Code Q28.3
    Other malformations of cerebral vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital cerebral aneurysm (nonruptured)
    Congenital malformation of cerebral vessels NOS
    Developmental venous anomaly
  - coronary Q24.5
    ICD-10-CM Diagnosis Code Q24.5
    Malformation of coronary vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital coronary (artery) aneurysm
  - developmental Q28.3
    ICD-10-CM Diagnosis Code Q28.3
    Other malformations of cerebral vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital cerebral aneurysm (nonruptured)
    Congenital malformation of cerebral vessels NOS
    Developmental venous anomaly
  - great Q26.9
    ICD-10-CM Diagnosis Code Q26.9
    Congenital malformation of great vein, unspecified
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital anomaly of vena cava (inferior) (superior) NOS
    - specified NEC Q26.8
      ICD-10-CM Diagnosis Code Q26.8
      Other congenital malformations of great veins
      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      Applicable To
      Absence of vena cava (inferior) (superior)
      Azygos continuation of inferior vena cava
      Persistent left posterior cardinal vein
      Scimitar syndrome
- vena cava Q26.9
  (inferior) (superior)
  ICD-10-CM Diagnosis Code Q26.9
  Congenital malformation of great vein, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital anomaly of vena cava (inferior) (superior) NOS
- venous - see Anomaly, vein(s)
- venous return Q26.8
  ICD-10-CM Diagnosis Code Q26.8
  Other congenital malformations of great veins
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Absence of vena cava (inferior) (superior)
  Azygos continuation of inferior vena cava
  Persistent left posterior cardinal vein
  Scimitar syndrome
- ventricular
  - bands or folds Q24.8
    ICD-10-CM Diagnosis Code Q24.8
    Other specified congenital malformations of heart
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital diverticulum of left ventricle
    Congenital malformation of myocardium
    Congenital malformation of pericardium
    Malposition of heart
    Uhl's disease
  - septa Q21.0
    ICD-10-CM Diagnosis Code Q21.0
    Ventricular septal defect
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Roger's disease
- vertebra Q76.49
  ICD-10-CM Diagnosis Code Q76.49
  Other congenital malformations of spine, not associated with scoliosis
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital absence of vertebra NOS
  Congenital fusion of spine NOS
  Congenital malformation of lumbosacral (joint) (region) NOS
  Congenital malformation of spine NOS
  Hemivertebra NOS
  Malformation of spine NOS
  Platyspondylisis NOS
  Supernumerary vertebra NOS
  - kyphosis - see Kyphosis, congenital
  - lordosis - see Lordosis, congenital
- vesicourethral orifice Q64.79
  ICD-10-CM Diagnosis Code Q64.79
  Other congenital malformations of bladder and urethra
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
- vessel(s) Q27.9
  ICD-10-CM Diagnosis Code Q27.9
  Congenital malformation of peripheral vascular system, unspecified
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Anomaly of artery or vein NOS
  - optic papilla Q14.2
    ICD-10-CM Diagnosis Code Q14.2
    Congenital malformation of optic disc
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Coloboma of optic disc
  - precerebral Q28.1
    ICD-10-CM Diagnosis Code Q28.1
    Other malformations of precerebral vessels
    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    Applicable To
    Congenital malformation of precerebral vessels NOS
    Congenital precerebral aneurysm (nonruptured)
- vitelline duct Q43.0
  ICD-10-CM Diagnosis Code Q43.0
  Meckel's diverticulum (displaced) (hypertrophic)
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Persistent omphalomesenteric duct
  Persistent vitelline duct
- vitreous body or humor Q14.0
  ICD-10-CM Diagnosis Code Q14.0
  Congenital malformation of vitreous humor
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Congenital vitreous opacity
- vulva Q52.70
  ICD-10-CM Diagnosis Code Q52.70
  Unspecified congenital malformations of vulva
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  Applicable To
  Congenital malformation of vulva NOS
- wrist Q74.0
  (joint)
  ICD-10-CM Diagnosis Code Q74.0
  Other congenital malformations of upper limb(s), including shoulder girdle
  2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  Applicable To
  Accessory carpal bones
  Cleidocranial dysostosis
  Congenital pseudarthrosis of clavicle
  Macrodactylia (fingers)
  Madelung's deformity
  Radioulnar synostosis
  Sprengel's deformity
  Triphalangeal thumb

Index Terms Starting With 'A' (Anomaly, anomalous)

Anomaly, anomalous (congenital) (unspecified type) Q89.9ICD-10-CM Diagnosis Code Q89.9Congenital malformation, unspecified2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt Applicable ToCongenital anomaly NOSCongenital deformity NOS

Congenital malformation, unspecified

Other congenital malformations of abdominal wall

Other specified congenital malformations of nervous system

Congenital malformations of adrenal gland

Genetic anomalies of leukocytes

Congenital malformation of digestive system, unspecified

Congenital malformation of upper alimentary tract, unspecified

Unspecified alveolar anomaly

Other specified alveolar anomalies

Alveolar mandibular hyperplasia

Alveolar maxillary hyperplasia

Other specified alveolar anomalies

Alveolar mandibular hypoplasia

Alveolar maxillary hypoplasia

Other specified alveolar anomalies

Other specified alveolar anomalies

Other congenital malformations of lower limb(s), including pelvic girdle

Congenital malformation of intestine, unspecified

Congenital malformation of aorta unspecified

Coarctation of aorta

Congenital malformation of aortic and mitral valves, unspecified

Other specified congenital malformations of intestine

Congenital absence, atresia and stenosis of jejunum

Malformations of aqueduct of Sylvius

Other congenital malformations of upper limb(s), including shoulder girdle

Malformation of coronary vessels

Arteriovenous malformation of digestive system vessel

Congenital malformation of peripheral vascular system, unspecified

Other malformations of precerebral vessels

Other malformations of cerebral vessels

Malformation of coronary vessels

Other specified congenital malformations of peripheral vascular system

Other specified congenital malformations of eye

Congenital malformation of great arteries, unspecified

Other congenital malformations of other great arteries

Other specified congenital malformations of peripheral vascular system

Congenital malformation of peripheral vascular system, unspecified

Other specified congenital malformations of peripheral vascular system

Other congenital malformations of pulmonary artery

Other congenital malformations of renal artery

Congenital malformation of retina

Other specified congenital malformations of peripheral vascular system

Other specified congenital malformations of peripheral vascular system

Anomalous origin of subclavian artery

Congenital absence and hypoplasia of umbilical artery

Other specified congenital malformations of peripheral vascular system

Other malformations of precerebral vessels

Other congenital malformations of larynx

Other congenital malformations of cardiac chambers and connections

Atrial septal defect, unspecified

Pre-excitation syndrome

Ventricular septal defect

Other specified congenital malformations of ear

Other specified congenital malformations of ear

Congenital malformation of ear causing impairment of hearing, unspecified

Other congenital malformations of cardiac chambers and connections

Congenital glaucoma

Congenital malformation, unspecified

Other congenital malformations of cardiac chambers and connections

Other specified congenital malformations of heart

Other specified congenital malformations of heart

Congenital malformations of salivary glands and ducts

Other congenital malformations of bile ducts

Unspecified congenital malformation of bladder and urethra

Congenital absence of bladder and urethra

Congenital diverticulum of bladder

Exstrophy of urinary bladder, unspecified

Cloacal exstrophy of urinary bladder

Other exstrophy of urinary bladder

Other exstrophy of urinary bladder

Supravesical fissure of urinary bladder

Congenital bladder neck obstruction

Other congenital malformations of bladder and urethra

Congenital malformation of musculoskeletal system, unspecified

Other congenital malformations of upper limb(s), including shoulder girdle

Congenital malformation of skull and face bones, unspecified

Other congenital malformations of lower limb(s), including pelvic girdle

Other congenital malformations of lower limb(s), including pelvic girdle

Anomaly, anomalous (congenital) (unspecified type) Q89.9
ICD-10-CM Diagnosis Code Q89.9
Congenital malformation, unspecified
2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
Applicable To
Congenital anomaly NOS
Congenital deformity NOS