• Cardiomyopathy (familial) (idiopathic) I42.9
    ICD-10-CM Diagnosis Code I42.9

    Cardiomyopathy, unspecified

      2016 2017 2018 2019 2020 Billable/Specific Code
    Applicable To
    • Cardiomyopathy (primary) (secondary) NOS

    • alcoholic I42.6
      ICD-10-CM Diagnosis Code I42.6

      Alcoholic cardiomyopathy

        2016 2017 2018 2019 2020 Billable/Specific Code
      Code Also
      • presence of alcoholism (F10.-)
    • amyloid E85.4
      ICD-10-CM Diagnosis Code E85.4

      Organ-limited amyloidosis

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Localized amyloidosis
      • Transthyretin-related (ATTR) familial amyloid cardiomyopathy
      • transthyretin-related E85.4
        (ATTR)
        ICD-10-CM Diagnosis Code E85.4

        Organ-limited amyloidosis

          2016 2017 2018 2019 2020 Billable/Specific Code
        Applicable To
        • Localized amyloidosis
        • Transthyretin-related (ATTR) familial amyloid cardiomyopathy
    • arteriosclerotic - see Disease, heart, ischemic, atherosclerotic
    • beriberi E51.12
      ICD-10-CM Diagnosis Code E51.12

      Wet beriberi

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Beriberi with cardiovascular manifestations
      • Cardiovascular beriberi
      • Shoshin disease
    • cobalt-beer I42.6
      ICD-10-CM Diagnosis Code I42.6

      Alcoholic cardiomyopathy

        2016 2017 2018 2019 2020 Billable/Specific Code
      Code Also
      • presence of alcoholism (F10.-)
    • congenital I42.4
      ICD-10-CM Diagnosis Code I42.4

      Endocardial fibroelastosis

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Congenital cardiomyopathy
      • Elastomyofibrosis
    • congestive I42.0
      ICD-10-CM Diagnosis Code I42.0

      Dilated cardiomyopathy

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Congestive cardiomyopathy
    • constrictive NOS I42.5
      ICD-10-CM Diagnosis Code I42.5

      Other restrictive cardiomyopathy

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Constrictive cardiomyopathy NOS
    • dilated I42.0
      ICD-10-CM Diagnosis Code I42.0

      Dilated cardiomyopathy

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Congestive cardiomyopathy
    • due to
      • alcohol I42.6
        ICD-10-CM Diagnosis Code I42.6

        Alcoholic cardiomyopathy

          2016 2017 2018 2019 2020 Billable/Specific Code
        Code Also
        • presence of alcoholism (F10.-)
      • beriberi E51.12
        ICD-10-CM Diagnosis Code E51.12

        Wet beriberi

          2016 2017 2018 2019 2020 Billable/Specific Code
        Applicable To
        • Beriberi with cardiovascular manifestations
        • Cardiovascular beriberi
        • Shoshin disease
      • cardiac glycogenosis E74.02
        ICD-10-CM Diagnosis Code E74.02

        Pompe disease

          2016 2017 2018 2019 2020 Billable/Specific Code
        Applicable To
        • Cardiac glycogenosis
        • Type II glycogen storage disease
      • drugs I42.7
        ICD-10-CM Diagnosis Code I42.7

        Cardiomyopathy due to drug and external agent

          2016 2017 2018 2019 2020 Billable/Specific Code
        Code First
        • poisoning due to drug or toxin, if applicable (T36-T65 with fifth or sixth character 1-4 or 6)
        Use Additional
        • code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
      • external agents NEC I42.7
        ICD-10-CM Diagnosis Code I42.7

        Cardiomyopathy due to drug and external agent

          2016 2017 2018 2019 2020 Billable/Specific Code
        Code First
        • poisoning due to drug or toxin, if applicable (T36-T65 with fifth or sixth character 1-4 or 6)
        Use Additional
        • code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
      • Friedreich's ataxia G11.1
        ICD-10-CM Diagnosis Code G11.1

        Early-onset cerebellar ataxia

          2016 2017 2018 2019 2020 Billable/Specific Code
        Applicable To
        • Early-onset cerebellar ataxia with essential tremor
        • Early-onset cerebellar ataxia with myoclonus [Hunt's ataxia]
        • Early-onset cerebellar ataxia with retained tendon reflexes
        • Friedreich's ataxia (autosomal recessive)
        • X-linked recessive spinocerebellar ataxia
      • myotonia atrophica G71.11
        ICD-10-CM Diagnosis Code G71.11

        Myotonic muscular dystrophy

          2016 2017 2018 2019 2020 Billable/Specific Code
        Applicable To
        • Dystrophia myotonica [Steinert]
        • Myotonia atrophica
        • Myotonic dystrophy
        • Proximal myotonic myopathy (PROMM)
        • Steinert disease
      • progressive muscular dystrophy G71.09
        ICD-10-CM Diagnosis Code G71.09

        Other specified muscular dystrophies

          2019 - New Code 2020 Billable/Specific Code
        Applicable To
        • Benign scapuloperoneal muscular dystrophy with early contractures [Emery-Dreifuss]
        • Congenital muscular dystrophy NOS
        • Congenital muscular dystrophy with specific morphological abnormalities of the muscle fiber
        • Distal muscular dystrophy
        • Limb-girdle muscular dystrophy
        • Ocular muscular dystrophy
        • Oculopharyngeal muscular dystrophy
        • Scapuloperoneal muscular dystrophy
    • glycogen storage E74.02
      ICD-10-CM Diagnosis Code E74.02

      Pompe disease

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Cardiac glycogenosis
      • Type II glycogen storage disease
    • hypertensive - see Hypertension, heart
    • hypertrophic (nonobstructive) I42.2
      ICD-10-CM Diagnosis Code I42.2

      Other hypertrophic cardiomyopathy

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Nonobstructive hypertrophic cardiomyopathy
      • obstructive I42.1
        ICD-10-CM Diagnosis Code I42.1

        Obstructive hypertrophic cardiomyopathy

          2016 2017 2018 2019 2020 Billable/Specific Code
        Applicable To
        • Hypertrophic subaortic stenosis (idiopathic)
        • congenital Q24.8
          ICD-10-CM Diagnosis Code Q24.8

          Other specified congenital malformations of heart

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Congenital diverticulum of left ventricle
          • Congenital malformation of myocardium
          • Congenital malformation of pericardium
          • Malposition of heart
          • Uhl's disease
    • in
      • Chagas' disease (chronic) B57.2
        ICD-10-CM Diagnosis Code B57.2

        Chagas' disease (chronic) with heart involvement

          2016 2017 2018 2019 2020 Billable/Specific Code
        Applicable To
        • American trypanosomiasis NOS
        • Chagas' disease (chronic) NOS
        • Chagas' disease (chronic) with myocarditis
        • Trypanosomiasis NOS
        • acute B57.0
          ICD-10-CM Diagnosis Code B57.0

          Acute Chagas' disease with heart involvement

            2016 2017 2018 2019 2020 Billable/Specific Code
          Applicable To
          • Acute Chagas' disease with myocarditis
      • sarcoidosis D86.85
        ICD-10-CM Diagnosis Code D86.85

        Sarcoid myocarditis

          2016 2017 2018 2019 2020 Billable/Specific Code
    • ischemic I25.5
      ICD-10-CM Diagnosis Code I25.5

      Ischemic cardiomyopathy

        2016 2017 2018 2019 2020 Billable/Specific Code
      Type 2 Excludes
    • metabolic E88.9
      ICD-10-CM Diagnosis Code E88.9

      Metabolic disorder, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code
      • thyrotoxic E05.90
        ICD-10-CM Diagnosis Code E05.90

        Thyrotoxicosis, unspecified without thyrotoxic crisis or storm

          2016 2017 2018 2019 2020 Billable/Specific Code
        • with thyroid storm E05.91
          ICD-10-CM Diagnosis Code E05.91

          Thyrotoxicosis, unspecified with thyrotoxic crisis or storm

            2016 2017 2018 2019 2020 Billable/Specific Code
    • newborn I42.8
      ICD-10-CM Diagnosis Code I42.8

      Other cardiomyopathies

        2016 2017 2018 2019 2020 Billable/Specific Code
      • congenital I42.4
        ICD-10-CM Diagnosis Code I42.4

        Endocardial fibroelastosis

          2016 2017 2018 2019 2020 Billable/Specific Code
        Applicable To
        • Congenital cardiomyopathy
        • Elastomyofibrosis
    • non-ischemic I42.8
      - see also by cause
      ICD-10-CM Diagnosis Code I42.8

      Other cardiomyopathies

        2016 2017 2018 2019 2020 Billable/Specific Code
    • nutritional E63.9
      ICD-10-CM Diagnosis Code E63.9

      Nutritional deficiency, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code
      • beriberi E51.12
        ICD-10-CM Diagnosis Code E51.12

        Wet beriberi

          2016 2017 2018 2019 2020 Billable/Specific Code
        Applicable To
        • Beriberi with cardiovascular manifestations
        • Cardiovascular beriberi
        • Shoshin disease
    • obscure of Africa I42.8
      ICD-10-CM Diagnosis Code I42.8

      Other cardiomyopathies

        2016 2017 2018 2019 2020 Billable/Specific Code
    • peripartum O90.3
      ICD-10-CM Diagnosis Code O90.3

      Peripartum cardiomyopathy

        2016 2017 2018 2019 2020 Billable/Specific Code Maternity Dx (12-55 years)
      Applicable To
      • Conditions in I42.- arising during pregnancy and the puerperium
      Type 1 Excludes
      • pre-existing heart disease complicating pregnancy and the puerperium (O99.4-)
    • postpartum O90.3
      ICD-10-CM Diagnosis Code O90.3

      Peripartum cardiomyopathy

        2016 2017 2018 2019 2020 Billable/Specific Code Maternity Dx (12-55 years)
      Applicable To
      • Conditions in I42.- arising during pregnancy and the puerperium
      Type 1 Excludes
      • pre-existing heart disease complicating pregnancy and the puerperium (O99.4-)
    • restrictive NEC I42.5
      ICD-10-CM Diagnosis Code I42.5

      Other restrictive cardiomyopathy

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Constrictive cardiomyopathy NOS
    • rheumatic I09.0
      ICD-10-CM Diagnosis Code I09.0

      Rheumatic myocarditis

        2016 2017 2018 2019 2020 Billable/Specific Code
      Type 1 Excludes
      • myocarditis not specified as rheumatic (I51.4)
    • secondary I42.9
      ICD-10-CM Diagnosis Code I42.9

      Cardiomyopathy, unspecified

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Cardiomyopathy (primary) (secondary) NOS
    • specified NEC I42.8
      ICD-10-CM Diagnosis Code I42.8

      Other cardiomyopathies

        2016 2017 2018 2019 2020 Billable/Specific Code
    • stress induced I51.81
      ICD-10-CM Diagnosis Code I51.81

      Takotsubo syndrome

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Reversible left ventricular dysfunction following sudden emotional stress
      • Stress induced cardiomyopathy
      • Takotsubo cardiomyopathy
      • Transient left ventricular apical ballooning syndrome
    • takotsubo I51.81
      ICD-10-CM Diagnosis Code I51.81

      Takotsubo syndrome

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Reversible left ventricular dysfunction following sudden emotional stress
      • Stress induced cardiomyopathy
      • Takotsubo cardiomyopathy
      • Transient left ventricular apical ballooning syndrome
    • thyrotoxic E05.90
      ICD-10-CM Diagnosis Code E05.90

      Thyrotoxicosis, unspecified without thyrotoxic crisis or storm

        2016 2017 2018 2019 2020 Billable/Specific Code
      • with thyroid storm E05.91
        ICD-10-CM Diagnosis Code E05.91

        Thyrotoxicosis, unspecified with thyrotoxic crisis or storm

          2016 2017 2018 2019 2020 Billable/Specific Code
    • toxic NEC I42.7
      ICD-10-CM Diagnosis Code I42.7

      Cardiomyopathy due to drug and external agent

        2016 2017 2018 2019 2020 Billable/Specific Code
      Code First
      • poisoning due to drug or toxin, if applicable (T36-T65 with fifth or sixth character 1-4 or 6)
      Use Additional
      • code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
    • transthyretin-related E85.4
      (ATTR)
      ICD-10-CM Diagnosis Code E85.4

      Organ-limited amyloidosis

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Localized amyloidosis
      • Transthyretin-related (ATTR) familial amyloid cardiomyopathy
    • tuberculous A18.84
      ICD-10-CM Diagnosis Code A18.84

      Tuberculosis of heart

        2016 2017 2018 2019 2020 Billable/Specific Code
      Applicable To
      • Tuberculous cardiomyopathy
      • Tuberculous endocarditis
      • Tuberculous myocarditis
      • Tuberculous pericarditis
    • viral B33.24
      ICD-10-CM Diagnosis Code B33.24

      Viral cardiomyopathy

        2016 2017 2018 2019 2020 Billable/Specific Code