• Deficiency, deficient

    • 11-hydroxylase E25.0
      ICD-10-CM Diagnosis Code E25.0

      Congenital adrenogenital disorders associated with enzyme deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Congenital adrenal hyperplasia
      • 21-Hydroxylase deficiency
      • Salt-losing congenital adrenal hyperplasia
    • 21-hydroxylase E25.0
      ICD-10-CM Diagnosis Code E25.0

      Congenital adrenogenital disorders associated with enzyme deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Congenital adrenal hyperplasia
      • 21-Hydroxylase deficiency
      • Salt-losing congenital adrenal hyperplasia
    • 3-beta hydroxysteroid dehydrogenase E25.0
      ICD-10-CM Diagnosis Code E25.0

      Congenital adrenogenital disorders associated with enzyme deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Congenital adrenal hyperplasia
      • 21-Hydroxylase deficiency
      • Salt-losing congenital adrenal hyperplasia
    • 5-alpha reductase E29.1
      (with male pseudohermaphroditism)
      ICD-10-CM Diagnosis Code E29.1

      Testicular hypofunction

        2016 2017 2018 2019 Billable/Specific Code Male Dx
      Applicable To
      • Defective biosynthesis of testicular androgen NOS
      • 5-delta-Reductase deficiency (with male pseudohermaphroditism)
      • Testicular hypogonadism NOS
      Type 1 Excludes
      • postprocedural testicular hypofunction (E89.5)
      Use Additional
      • code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
    • abdominal muscle syndrome Q79.4
      ICD-10-CM Diagnosis Code Q79.4

      Prune belly syndrome

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital prolapse of bladder mucosa
      • Eagle-Barrett syndrome
    • AC globulin (congenital) (hereditary) D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
      • acquired D68.4
        ICD-10-CM Diagnosis Code D68.4

        Acquired coagulation factor deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Deficiency of coagulation factor due to liver disease
        • Deficiency of coagulation factor due to vitamin K deficiency
        Type 1 Excludes
        • vitamin K deficiency of newborn (P53)
    • accelerator globulin D68.2
      (Ac G) (blood)
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • acid phosphatase E83.39
      ICD-10-CM Diagnosis Code E83.39

      Other disorders of phosphorus metabolism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Acid phosphatase deficiency
      • Hypophosphatasia
    • activating factor D68.2
      (blood)
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • adenosine deaminase D81.3
      (ADA)
      ICD-10-CM Diagnosis Code D81.3

      Adenosine deaminase [ADA] deficiency

        2016 2017 2018 2019 Billable/Specific Code
    • aldolase E74.19
      (hereditary)
      ICD-10-CM Diagnosis Code E74.19

      Other disorders of fructose metabolism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Fructose-1, 6-diphosphatase deficiency
    • alpha-1-antitrypsin E88.01
      ICD-10-CM Diagnosis Code E88.01

      Alpha-1-antitrypsin deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AAT deficiency
    • amino-acids E72.9
      ICD-10-CM Diagnosis Code E72.9

      Disorder of amino-acid metabolism, unspecified

        2016 2017 2018 2019 Billable/Specific Code
    • anemia - see Anemia
    • aneurin E51.9
      ICD-10-CM Diagnosis Code E51.9

      Thiamine deficiency, unspecified

        2016 2017 2018 2019 Billable/Specific Code
    • anti-hemophilic
      • factor (A) D66
        ICD-10-CM Diagnosis Code D66

        Hereditary factor VIII deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Classical hemophilia
        • Deficiency factor VIII (with functional defect)
        • Hemophilia NOS
        • Hemophilia A
        Type 1 Excludes
        • factor VIII deficiency with vascular defect (D68.0)
        • B D67
          ICD-10-CM Diagnosis Code D67

          Hereditary factor IX deficiency

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Christmas disease
          • Factor IX deficiency (with functional defect)
          • Hemophilia B
          • Plasma thromboplastin component [PTC] deficiency
        • C D68.1
          ICD-10-CM Diagnosis Code D68.1

          Hereditary factor XI deficiency

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Hemophilia C
          • Plasma thromboplastin antecedent [PTA] deficiency
          • Rosenthal's disease
      • globulin D66
        (AHG)
        ICD-10-CM Diagnosis Code D66

        Hereditary factor VIII deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Classical hemophilia
        • Deficiency factor VIII (with functional defect)
        • Hemophilia NOS
        • Hemophilia A
        Type 1 Excludes
        • factor VIII deficiency with vascular defect (D68.0)
    • antibody with
      • hyperimmunoglobulinemia D80.6
        ICD-10-CM Diagnosis Code D80.6

        Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia

          2016 2017 2018 2019 Billable/Specific Code
      • near-normal immunoglobins D80.6
        ICD-10-CM Diagnosis Code D80.6

        Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia

          2016 2017 2018 2019 Billable/Specific Code
    • antidiuretic hormone E23.2
      ICD-10-CM Diagnosis Code E23.2

      Diabetes insipidus

        2016 2017 2018 2019 Billable/Specific Code
      Type 1 Excludes
      • nephrogenic diabetes insipidus (N25.1)
    • antithrombin D68.59
      (antithrombin III)
      ICD-10-CM Diagnosis Code D68.59

      Other primary thrombophilia

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Antithrombin III deficiency
      • Hypercoagulable state NOS
      • Primary hypercoagulable state NEC
      • Primary thrombophilia NEC
      • Protein C deficiency
      • Protein S deficiency
      • Thrombophilia NOS
    • ascorbic acid E54
      ICD-10-CM Diagnosis Code E54

      Ascorbic acid deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Deficiency of vitamin C
      • Scurvy
      Type 1 Excludes
      • scorbutic anemia (D53.2)
      • sequelae of vitamin C deficiency (E64.2)
    • attention (disorder) (syndrome) F98.8
      ICD-10-CM Diagnosis Code F98.8

      Other specified behavioral and emotional disorders with onset usually occurring in childhood and adolescence

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Excessive masturbation
      • Nail-biting
      • Nose-picking
      • Thumb-sucking
    • autoprothrombin
      • C D68.2
        ICD-10-CM Diagnosis Code D68.2

        Hereditary deficiency of other clotting factors

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • AC globulin deficiency
        • Congenital afibrinogenemia
        • Deficiency of factor I [fibrinogen]
        • Deficiency of factor II [prothrombin]
        • Deficiency of factor V [labile]
        • Deficiency of factor VII [stable]
        • Deficiency of factor X [Stuart-Prower]
        • Deficiency of factor XII [Hageman]
        • Deficiency of factor XIII [fibrin stabilizing]
        • Dysfibrinogenemia (congenital)
        • Hypoproconvertinemia
        • Owren's disease
        • Proaccelerin deficiency
      • I D68.2
        ICD-10-CM Diagnosis Code D68.2

        Hereditary deficiency of other clotting factors

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • AC globulin deficiency
        • Congenital afibrinogenemia
        • Deficiency of factor I [fibrinogen]
        • Deficiency of factor II [prothrombin]
        • Deficiency of factor V [labile]
        • Deficiency of factor VII [stable]
        • Deficiency of factor X [Stuart-Prower]
        • Deficiency of factor XII [Hageman]
        • Deficiency of factor XIII [fibrin stabilizing]
        • Dysfibrinogenemia (congenital)
        • Hypoproconvertinemia
        • Owren's disease
        • Proaccelerin deficiency
      • II D67
        ICD-10-CM Diagnosis Code D67

        Hereditary factor IX deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Christmas disease
        • Factor IX deficiency (with functional defect)
        • Hemophilia B
        • Plasma thromboplastin component [PTC] deficiency
    • beta-glucuronidase E76.29
      ICD-10-CM Diagnosis Code E76.29

      Other mucopolysaccharidoses

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • beta-Glucuronidase deficiency
      • Maroteaux-Lamy (mild) (severe) syndrome
      • Mucopolysaccharidosis, types VI, VII
    • biotin E53.8
      ICD-10-CM Diagnosis Code E53.8

      Deficiency of other specified B group vitamins

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Biotin deficiency
      • Cyanocobalamin deficiency
      • Folate deficiency
      • Folic acid deficiency
      • Pantothenic acid deficiency
      • Vitamin B12 deficiency
      Type 1 Excludes
      • folate deficiency anemia (D52.-)
      • vitamin B12 deficiency anemia (D51.-)
    • biotin-dependent carboxylase D81.819
      ICD-10-CM Diagnosis Code D81.819

      Biotin-dependent carboxylase deficiency, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Multiple carboxylase deficiency, unspecified
    • biotinidase D81.810
      ICD-10-CM Diagnosis Code D81.810

      Biotinidase deficiency

        2016 2017 2018 2019 Billable/Specific Code
    • brancher enzyme E74.03
      (amylopectinosis)
      ICD-10-CM Diagnosis Code E74.03

      Cori disease

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Forbes disease
      • Type III glycogen storage disease
    • C1 esterase inhibitor D84.1
      (C1-INH)
      ICD-10-CM Diagnosis Code D84.1

      Defects in the complement system

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • C1 esterase inhibitor [C1-INH] deficiency
    • calciferol E55.9
      ICD-10-CM Diagnosis Code E55.9

      Vitamin D deficiency, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Avitaminosis D
      • with
        • adult osteomalacia M83.8
          ICD-10-CM Diagnosis Code M83.8

          Other adult osteomalacia

            2016 2017 2018 2019 Billable/Specific Code Adult Dx (15-124 years)
        • rickets - see Rickets
    • calcium E58
      (dietary)
      ICD-10-CM Diagnosis Code E58

      Dietary calcium deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Type 1 Excludes
      • disorders of calcium metabolism (E83.5-)
      • sequelae of calcium deficiency (E64.8)
    • calorie, severe E43
      ICD-10-CM Diagnosis Code E43

      Unspecified severe protein-calorie malnutrition

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Starvation edema
      • with marasmus E41
        ICD-10-CM Diagnosis Code E41

        Nutritional marasmus

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Severe malnutrition with marasmus
        Type 1 Excludes
        • marasmic kwashiorkor (E42)
        • and kwashiorkor E42
          ICD-10-CM Diagnosis Code E42

          Marasmic kwashiorkor

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Intermediate form severe protein-calorie malnutrition
          • Severe protein-calorie malnutrition with signs of both kwashiorkor and marasmus
    • cardiac - see Insufficiency, myocardial
    • carnitine E71.40
      ICD-10-CM Diagnosis Code E71.40

      Disorder of carnitine metabolism, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      • due to
        • hemodialysis E71.43
          ICD-10-CM Diagnosis Code E71.43

          Iatrogenic carnitine deficiency

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Carnitine deficiency due to hemodialysis
          • Carnitine deficiency due to Valproic acid therapy
        • inborn errors of metabolism E71.42
          ICD-10-CM Diagnosis Code E71.42

          Carnitine deficiency due to inborn errors of metabolism

            2016 2017 2018 2019 Billable/Specific Code
          Code Also
          • associated inborn error or metabolism
        • Valproic acid therapy E71.43
          ICD-10-CM Diagnosis Code E71.43

          Iatrogenic carnitine deficiency

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Carnitine deficiency due to hemodialysis
          • Carnitine deficiency due to Valproic acid therapy
      • iatrogenic E71.43
        ICD-10-CM Diagnosis Code E71.43

        Iatrogenic carnitine deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Carnitine deficiency due to hemodialysis
        • Carnitine deficiency due to Valproic acid therapy
      • muscle palmityltransferase E71.314
        ICD-10-CM Diagnosis Code E71.314

        Muscle carnitine palmitoyltransferase deficiency

          2016 2017 2018 2019 Billable/Specific Code
      • primary E71.41
        ICD-10-CM Diagnosis Code E71.41

        Primary carnitine deficiency

          2016 2017 2018 2019 Billable/Specific Code
      • secondary E71.448
        ICD-10-CM Diagnosis Code E71.448

        Other secondary carnitine deficiency

          2016 2017 2018 2019 Billable/Specific Code
    • carotene E50.9
      ICD-10-CM Diagnosis Code E50.9

      Vitamin A deficiency, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Hypovitaminosis A NOS
    • central nervous system G96.8
      ICD-10-CM Diagnosis Code G96.8

      Other specified disorders of central nervous system

        2016 2017 2018 2019 Billable/Specific Code
    • ceruloplasmin E83.01
      (Wilson)
      ICD-10-CM Diagnosis Code E83.01

      Wilson's disease

        2016 2017 2018 2019 Billable/Specific Code
      Code Also
      • associated Kayser Fleischer ring (H18.04-)
    • choline E53.8
      ICD-10-CM Diagnosis Code E53.8

      Deficiency of other specified B group vitamins

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Biotin deficiency
      • Cyanocobalamin deficiency
      • Folate deficiency
      • Folic acid deficiency
      • Pantothenic acid deficiency
      • Vitamin B12 deficiency
      Type 1 Excludes
      • folate deficiency anemia (D52.-)
      • vitamin B12 deficiency anemia (D51.-)
    • Christmas factor D67
      ICD-10-CM Diagnosis Code D67

      Hereditary factor IX deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Christmas disease
      • Factor IX deficiency (with functional defect)
      • Hemophilia B
      • Plasma thromboplastin component [PTC] deficiency
    • chromium E61.4
      ICD-10-CM Diagnosis Code E61.4

      Chromium deficiency

        2016 2017 2018 2019 Billable/Specific Code
    • clotting D68.9
      (blood) - see also Deficiency, coagulation factor
      ICD-10-CM Diagnosis Code D68.9

      Coagulation defect, unspecified

        2016 2017 2018 2019 Billable/Specific Code
    • clotting factor NEC D68.2
      (hereditary) - see also Deficiency, factor
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • coagulation NOS D68.9
      ICD-10-CM Diagnosis Code D68.9

      Coagulation defect, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      • acquired D68.4
        (any)
        ICD-10-CM Diagnosis Code D68.4

        Acquired coagulation factor deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Deficiency of coagulation factor due to liver disease
        • Deficiency of coagulation factor due to vitamin K deficiency
        Type 1 Excludes
        • vitamin K deficiency of newborn (P53)
      • antepartum hemorrhage - see Hemorrhage, antepartum, with coagulation defect
      • clotting factor NEC D68.2
        - see also Deficiency, factor
        ICD-10-CM Diagnosis Code D68.2

        Hereditary deficiency of other clotting factors

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • AC globulin deficiency
        • Congenital afibrinogenemia
        • Deficiency of factor I [fibrinogen]
        • Deficiency of factor II [prothrombin]
        • Deficiency of factor V [labile]
        • Deficiency of factor VII [stable]
        • Deficiency of factor X [Stuart-Prower]
        • Deficiency of factor XII [Hageman]
        • Deficiency of factor XIII [fibrin stabilizing]
        • Dysfibrinogenemia (congenital)
        • Hypoproconvertinemia
        • Owren's disease
        • Proaccelerin deficiency
      • due to
        • hyperprothrombinemia D68.4
          ICD-10-CM Diagnosis Code D68.4

          Acquired coagulation factor deficiency

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Deficiency of coagulation factor due to liver disease
          • Deficiency of coagulation factor due to vitamin K deficiency
          Type 1 Excludes
          • vitamin K deficiency of newborn (P53)
        • liver disease D68.4
          ICD-10-CM Diagnosis Code D68.4

          Acquired coagulation factor deficiency

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Deficiency of coagulation factor due to liver disease
          • Deficiency of coagulation factor due to vitamin K deficiency
          Type 1 Excludes
          • vitamin K deficiency of newborn (P53)
        • vitamin K deficiency D68.4
          ICD-10-CM Diagnosis Code D68.4

          Acquired coagulation factor deficiency

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Deficiency of coagulation factor due to liver disease
          • Deficiency of coagulation factor due to vitamin K deficiency
          Type 1 Excludes
          • vitamin K deficiency of newborn (P53)
      • newborn, transient P61.6
        ICD-10-CM Diagnosis Code P61.6

        Other transient neonatal disorders of coagulation

          2016 2017 2018 2019 Billable/Specific Code Code on Newborn Record
      • postpartum O72.3
        ICD-10-CM Diagnosis Code O72.3

        Postpartum coagulation defects

          2016 2017 2018 2019 Billable/Specific Code Maternity Dx (12-55 years) Female Dx
        Applicable To
        • Postpartum afibrinogenemia
        • Postpartum fibrinolysis
      • specified NEC D68.8
        ICD-10-CM Diagnosis Code D68.8

        Other specified coagulation defects

          2016 2017 2018 2019 Billable/Specific Code
        Type 1 Excludes
        • hemorrhagic disease of newborn (P53)
      • with
        • ectopic pregnancy O08.1
          ICD-10-CM Diagnosis Code O08.1

          Delayed or excessive hemorrhage following ectopic and molar pregnancy

            2016 2017 2018 2019 Billable/Specific Code Maternity Dx (12-55 years) Female Dx
          Applicable To
          • Afibrinogenemia following ectopic and molar pregnancy
          • Defibrination syndrome following ectopic and molar pregnancy
          • Hemolysis following ectopic and molar pregnancy
          • Intravascular coagulation following ectopic and molar pregnancy
          Type 1 Excludes
          • delayed or excessive hemorrhage due to incomplete abortion (O03.1)
        • molar pregnancy O08.1
          ICD-10-CM Diagnosis Code O08.1

          Delayed or excessive hemorrhage following ectopic and molar pregnancy

            2016 2017 2018 2019 Billable/Specific Code Maternity Dx (12-55 years) Female Dx
          Applicable To
          • Afibrinogenemia following ectopic and molar pregnancy
          • Defibrination syndrome following ectopic and molar pregnancy
          • Hemolysis following ectopic and molar pregnancy
          • Intravascular coagulation following ectopic and molar pregnancy
          Type 1 Excludes
          • delayed or excessive hemorrhage due to incomplete abortion (O03.1)
    • cognitive F09
      ICD-10-CM Diagnosis Code F09

      Unspecified mental disorder due to known physiological condition

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Mental disorder NOS due to known physiological condition
      • Organic brain syndrome NOS
      • Organic mental disorder NOS
      • Organic psychosis NOS
      • Symptomatic psychosis NOS
      Code First
      • the underlying physiological condition
      Type 1 Excludes
      • psychosis NOS (F29)
    • color vision H53.50
      ICD-10-CM Diagnosis Code H53.50

      Unspecified color vision deficiencies

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Color blindness NOS
      • achromatopsia H53.51
        ICD-10-CM Diagnosis Code H53.51

        Achromatopsia

          2016 2017 2018 2019 Billable/Specific Code
      • acquired H53.52
        ICD-10-CM Diagnosis Code H53.52

        Acquired color vision deficiency

          2016 2017 2018 2019 Billable/Specific Code
      • deuteranomaly H53.53
        ICD-10-CM Diagnosis Code H53.53

        Deuteranomaly

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Deuteranopia
      • protanomaly H53.54
        ICD-10-CM Diagnosis Code H53.54

        Protanomaly

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Protanopia
      • specified type NEC H53.59
        ICD-10-CM Diagnosis Code H53.59

        Other color vision deficiencies

          2016 2017 2018 2019 Billable/Specific Code
      • tritanomaly H53.55
        ICD-10-CM Diagnosis Code H53.55

        Tritanomaly

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Tritanopia
    • combined glucocorticoid and mineralocorticoid E27.49
      ICD-10-CM Diagnosis Code E27.49

      Other adrenocortical insufficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Adrenal hemorrhage
      • Adrenal infarction
    • contact factor D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • copper E61.0
      (nutritional)
      ICD-10-CM Diagnosis Code E61.0

      Copper deficiency

        2016 2017 2018 2019 Billable/Specific Code
    • corticoadrenal E27.40
      ICD-10-CM Diagnosis Code E27.40

      Unspecified adrenocortical insufficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Adrenocortical insufficiency NOS
      • Hypoaldosteronism
      • primary E27.1
        ICD-10-CM Diagnosis Code E27.1

        Primary adrenocortical insufficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Addison's disease
        • Autoimmune adrenalitis
        Type 1 Excludes
        • Addison only phenotype adrenoleukodystrophy (E71.528)
        • amyloidosis (E85.-)
        • tuberculous Addison's disease (A18.7)
        • Waterhouse-Friderichsen syndrome (A39.1)
    • craniofacial axis Q75.0
      ICD-10-CM Diagnosis Code Q75.0

      Craniosynostosis

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Acrocephaly
      • Imperfect fusion of skull
      • Oxycephaly
      • Trigonocephaly
    • cyanocobalamin E53.8
      ICD-10-CM Diagnosis Code E53.8

      Deficiency of other specified B group vitamins

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Biotin deficiency
      • Cyanocobalamin deficiency
      • Folate deficiency
      • Folic acid deficiency
      • Pantothenic acid deficiency
      • Vitamin B12 deficiency
      Type 1 Excludes
      • folate deficiency anemia (D52.-)
      • vitamin B12 deficiency anemia (D51.-)
    • debrancher enzyme E74.03
      (limit dextrinosis)
      ICD-10-CM Diagnosis Code E74.03

      Cori disease

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Forbes disease
      • Type III glycogen storage disease
    • dehydrogenase
      • long chain/very long chain acyl CoA E71.310
        ICD-10-CM Diagnosis Code E71.310

        Long chain/very long chain acyl CoA dehydrogenase deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • LCAD
        • VLCAD
      • medium chain acyl CoA E71.311
        ICD-10-CM Diagnosis Code E71.311

        Medium chain acyl CoA dehydrogenase deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • MCAD
      • short chain acyl CoA E71.312
        ICD-10-CM Diagnosis Code E71.312

        Short chain acyl CoA dehydrogenase deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • SCAD
    • diet E63.9
      ICD-10-CM Diagnosis Code E63.9

      Nutritional deficiency, unspecified

        2016 2017 2018 2019 Billable/Specific Code
    • dihydropyrimidine dehydrogenase E88.89
      (DPD)
      ICD-10-CM Diagnosis Code E88.89

      Other specified metabolic disorders

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Launois-Bensaude adenolipomatosis
      Type 1 Excludes
      • adult pulmonary Langerhans cell histiocytosis (J84.82)
    • disaccharidase E73.9
      ICD-10-CM Diagnosis Code E73.9

      Lactose intolerance, unspecified

        2016 2017 2018 2019 Billable/Specific Code
    • edema - see Malnutrition, severe
    • endocrine E34.9
      ICD-10-CM Diagnosis Code E34.9

      Endocrine disorder, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Endocrine disturbance NOS
      • Hormone disturbance NOS
    • energy-supply - see Malnutrition
    • enzymes, circulating NEC E88.09
      ICD-10-CM Diagnosis Code E88.09

      Other disorders of plasma-protein metabolism, not elsewhere classified

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Bisalbuminemia
    • ergosterol E55.9
      ICD-10-CM Diagnosis Code E55.9

      Vitamin D deficiency, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Avitaminosis D
      • with
        • adult osteomalacia M83.8
          ICD-10-CM Diagnosis Code M83.8

          Other adult osteomalacia

            2016 2017 2018 2019 Billable/Specific Code Adult Dx (15-124 years)
        • rickets - see Rickets
    • essential fatty acid E63.0
      (EFA)
      ICD-10-CM Diagnosis Code E63.0

      Essential fatty acid [EFA] deficiency

        2016 2017 2018 2019 Billable/Specific Code
    • factor - see also Deficiency, coagulation
      • Hageman D68.2
        ICD-10-CM Diagnosis Code D68.2

        Hereditary deficiency of other clotting factors

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • AC globulin deficiency
        • Congenital afibrinogenemia
        • Deficiency of factor I [fibrinogen]
        • Deficiency of factor II [prothrombin]
        • Deficiency of factor V [labile]
        • Deficiency of factor VII [stable]
        • Deficiency of factor X [Stuart-Prower]
        • Deficiency of factor XII [Hageman]
        • Deficiency of factor XIII [fibrin stabilizing]
        • Dysfibrinogenemia (congenital)
        • Hypoproconvertinemia
        • Owren's disease
        • Proaccelerin deficiency
      • I D68.2
        (congenital) (hereditary)
        ICD-10-CM Diagnosis Code D68.2

        Hereditary deficiency of other clotting factors

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • AC globulin deficiency
        • Congenital afibrinogenemia
        • Deficiency of factor I [fibrinogen]
        • Deficiency of factor II [prothrombin]
        • Deficiency of factor V [labile]
        • Deficiency of factor VII [stable]
        • Deficiency of factor X [Stuart-Prower]
        • Deficiency of factor XII [Hageman]
        • Deficiency of factor XIII [fibrin stabilizing]
        • Dysfibrinogenemia (congenital)
        • Hypoproconvertinemia
        • Owren's disease
        • Proaccelerin deficiency
      • II D68.2
        (congenital) (hereditary)
        ICD-10-CM Diagnosis Code D68.2

        Hereditary deficiency of other clotting factors

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • AC globulin deficiency
        • Congenital afibrinogenemia
        • Deficiency of factor I [fibrinogen]
        • Deficiency of factor II [prothrombin]
        • Deficiency of factor V [labile]
        • Deficiency of factor VII [stable]
        • Deficiency of factor X [Stuart-Prower]
        • Deficiency of factor XII [Hageman]
        • Deficiency of factor XIII [fibrin stabilizing]
        • Dysfibrinogenemia (congenital)
        • Hypoproconvertinemia
        • Owren's disease
        • Proaccelerin deficiency
      • IX D67
        (congenital) (functional) (hereditary) (with functional defect)
        ICD-10-CM Diagnosis Code D67

        Hereditary factor IX deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Christmas disease
        • Factor IX deficiency (with functional defect)
        • Hemophilia B
        • Plasma thromboplastin component [PTC] deficiency
      • multiple (congenital) D68.8
        ICD-10-CM Diagnosis Code D68.8

        Other specified coagulation defects

          2016 2017 2018 2019 Billable/Specific Code
        Type 1 Excludes
        • hemorrhagic disease of newborn (P53)
        • acquired D68.4
          ICD-10-CM Diagnosis Code D68.4

          Acquired coagulation factor deficiency

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Deficiency of coagulation factor due to liver disease
          • Deficiency of coagulation factor due to vitamin K deficiency
          Type 1 Excludes
          • vitamin K deficiency of newborn (P53)
      • V D68.2
        (congenital) (hereditary)
        ICD-10-CM Diagnosis Code D68.2

        Hereditary deficiency of other clotting factors

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • AC globulin deficiency
        • Congenital afibrinogenemia
        • Deficiency of factor I [fibrinogen]
        • Deficiency of factor II [prothrombin]
        • Deficiency of factor V [labile]
        • Deficiency of factor VII [stable]
        • Deficiency of factor X [Stuart-Prower]
        • Deficiency of factor XII [Hageman]
        • Deficiency of factor XIII [fibrin stabilizing]
        • Dysfibrinogenemia (congenital)
        • Hypoproconvertinemia
        • Owren's disease
        • Proaccelerin deficiency
      • VII D68.2
        (congenital) (hereditary)
        ICD-10-CM Diagnosis Code D68.2

        Hereditary deficiency of other clotting factors

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • AC globulin deficiency
        • Congenital afibrinogenemia
        • Deficiency of factor I [fibrinogen]
        • Deficiency of factor II [prothrombin]
        • Deficiency of factor V [labile]
        • Deficiency of factor VII [stable]
        • Deficiency of factor X [Stuart-Prower]
        • Deficiency of factor XII [Hageman]
        • Deficiency of factor XIII [fibrin stabilizing]
        • Dysfibrinogenemia (congenital)
        • Hypoproconvertinemia
        • Owren's disease
        • Proaccelerin deficiency
      • VIII (congenital) (functional) (hereditary) (with functional defect) D66
        ICD-10-CM Diagnosis Code D66

        Hereditary factor VIII deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Classical hemophilia
        • Deficiency factor VIII (with functional defect)
        • Hemophilia NOS
        • Hemophilia A
        Type 1 Excludes
        • factor VIII deficiency with vascular defect (D68.0)
        • with vascular defect D68.0
          ICD-10-CM Diagnosis Code D68.0

          Von Willebrand's disease

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Angiohemophilia
          • Factor VIII deficiency with vascular defect
          • Vascular hemophilia
          Type 1 Excludes
          • capillary fragility (hereditary) (D69.8)
          • factor VIII deficiency NOS (D66)
          • factor VIII deficiency with functional defect (D66)
      • X D68.2
        (congenital) (hereditary)
        ICD-10-CM Diagnosis Code D68.2

        Hereditary deficiency of other clotting factors

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • AC globulin deficiency
        • Congenital afibrinogenemia
        • Deficiency of factor I [fibrinogen]
        • Deficiency of factor II [prothrombin]
        • Deficiency of factor V [labile]
        • Deficiency of factor VII [stable]
        • Deficiency of factor X [Stuart-Prower]
        • Deficiency of factor XII [Hageman]
        • Deficiency of factor XIII [fibrin stabilizing]
        • Dysfibrinogenemia (congenital)
        • Hypoproconvertinemia
        • Owren's disease
        • Proaccelerin deficiency
      • XI D68.1
        (congenital) (hereditary)
        ICD-10-CM Diagnosis Code D68.1

        Hereditary factor XI deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Hemophilia C
        • Plasma thromboplastin antecedent [PTA] deficiency
        • Rosenthal's disease
      • XII D68.2
        (congenital) (hereditary)
        ICD-10-CM Diagnosis Code D68.2

        Hereditary deficiency of other clotting factors

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • AC globulin deficiency
        • Congenital afibrinogenemia
        • Deficiency of factor I [fibrinogen]
        • Deficiency of factor II [prothrombin]
        • Deficiency of factor V [labile]
        • Deficiency of factor VII [stable]
        • Deficiency of factor X [Stuart-Prower]
        • Deficiency of factor XII [Hageman]
        • Deficiency of factor XIII [fibrin stabilizing]
        • Dysfibrinogenemia (congenital)
        • Hypoproconvertinemia
        • Owren's disease
        • Proaccelerin deficiency
      • XIII D68.2
        (congenital) (hereditary)
        ICD-10-CM Diagnosis Code D68.2

        Hereditary deficiency of other clotting factors

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • AC globulin deficiency
        • Congenital afibrinogenemia
        • Deficiency of factor I [fibrinogen]
        • Deficiency of factor II [prothrombin]
        • Deficiency of factor V [labile]
        • Deficiency of factor VII [stable]
        • Deficiency of factor X [Stuart-Prower]
        • Deficiency of factor XII [Hageman]
        • Deficiency of factor XIII [fibrin stabilizing]
        • Dysfibrinogenemia (congenital)
        • Hypoproconvertinemia
        • Owren's disease
        • Proaccelerin deficiency
    • femoral, proximal focal (congenital) - see Defect, reduction, lower limb, longitudinal, femur
    • fibrin-stabilizing factor (congenital) (hereditary) D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
      • acquired D68.4
        ICD-10-CM Diagnosis Code D68.4

        Acquired coagulation factor deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Deficiency of coagulation factor due to liver disease
        • Deficiency of coagulation factor due to vitamin K deficiency
        Type 1 Excludes
        • vitamin K deficiency of newborn (P53)
    • fibrinase D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • fibrinogen (congenital) (hereditary) D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
      • acquired D65
        ICD-10-CM Diagnosis Code D65

        Disseminated intravascular coagulation [defibrination syndrome]

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Afibrinogenemia, acquired
        • Consumption coagulopathy
        • Diffuse or disseminated intravascular coagulation [DIC]
        • Fibrinolytic hemorrhage, acquired
        • Fibrinolytic purpura
        • Purpura fulminans
        Type 1 Excludes
        • disseminated intravascular coagulation (complicating):
        • abortion or ectopic or molar pregnancy (O00-O07, O08.1)
        • in newborn (P60)
        • pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
    • folate E53.8
      ICD-10-CM Diagnosis Code E53.8

      Deficiency of other specified B group vitamins

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Biotin deficiency
      • Cyanocobalamin deficiency
      • Folate deficiency
      • Folic acid deficiency
      • Pantothenic acid deficiency
      • Vitamin B12 deficiency
      Type 1 Excludes
      • folate deficiency anemia (D52.-)
      • vitamin B12 deficiency anemia (D51.-)
    • folic acid E53.8
      ICD-10-CM Diagnosis Code E53.8

      Deficiency of other specified B group vitamins

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Biotin deficiency
      • Cyanocobalamin deficiency
      • Folate deficiency
      • Folic acid deficiency
      • Pantothenic acid deficiency
      • Vitamin B12 deficiency
      Type 1 Excludes
      • folate deficiency anemia (D52.-)
      • vitamin B12 deficiency anemia (D51.-)
    • foreskin N47.3
      ICD-10-CM Diagnosis Code N47.3

      Deficient foreskin

        2016 2017 2018 2019 Billable/Specific Code Male Dx
    • fructokinase E74.11
      ICD-10-CM Diagnosis Code E74.11

      Essential fructosuria

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Fructokinase deficiency
    • fructose 1,6-diphosphatase E74.19
      ICD-10-CM Diagnosis Code E74.19

      Other disorders of fructose metabolism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Fructose-1, 6-diphosphatase deficiency
    • fructose-1-phosphate aldolase E74.19
      ICD-10-CM Diagnosis Code E74.19

      Other disorders of fructose metabolism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Fructose-1, 6-diphosphatase deficiency
    • GABA E72.81
      (gamma aminobutyric acid)
      ICD-10-CM Diagnosis Code E72.81

      Disorders of gamma aminobutyric acid metabolism

        2019 - New Code Billable/Specific Code
      Applicable To
      • 4-hydroxybutyric aciduria
      • Disorders of GABA metabolism
      • GABA metabolic defect
      • GABA transaminase deficiency
      • GABA-T deficiency
      • Gamma-hydroxybutyric aciduria
      • SSADHD
      • Succinic semialdehyde dehydrogenase deficiency
    • GABA-T E72.81
      (gamma aminobutyric acid transaminase)
      ICD-10-CM Diagnosis Code E72.81

      Disorders of gamma aminobutyric acid metabolism

        2019 - New Code Billable/Specific Code
      Applicable To
      • 4-hydroxybutyric aciduria
      • Disorders of GABA metabolism
      • GABA metabolic defect
      • GABA transaminase deficiency
      • GABA-T deficiency
      • Gamma-hydroxybutyric aciduria
      • SSADHD
      • Succinic semialdehyde dehydrogenase deficiency
    • galactokinase E74.29
      ICD-10-CM Diagnosis Code E74.29

      Other disorders of galactose metabolism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Galactokinase deficiency
    • galactose-1-phosphate uridyl transferase E74.29
      ICD-10-CM Diagnosis Code E74.29

      Other disorders of galactose metabolism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Galactokinase deficiency
    • gammaglobulin in blood D80.1
      ICD-10-CM Diagnosis Code D80.1

      Nonfamilial hypogammaglobulinemia

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Agammaglobulinemia with immunoglobulin-bearing B-lymphocytes
      • Common variable agammaglobulinemia [CVAgamma]
      • Hypogammaglobulinemia NOS
      • hereditary D80.0
        ICD-10-CM Diagnosis Code D80.0

        Hereditary hypogammaglobulinemia

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Autosomal recessive agammaglobulinemia (Swiss type)
        • X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency)
    • glass factor D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • glucocorticoid E27.49
      ICD-10-CM Diagnosis Code E27.49

      Other adrenocortical insufficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Adrenal hemorrhage
      • Adrenal infarction
      • mineralocorticoid E27.49
        ICD-10-CM Diagnosis Code E27.49

        Other adrenocortical insufficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Adrenal hemorrhage
        • Adrenal infarction
    • glucose-6-phosphatase E74.01
      ICD-10-CM Diagnosis Code E74.01

      von Gierke disease

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Type I glycogen storage disease
    • glucose-6-phosphate dehydrogenase anemia D55.0
      ICD-10-CM Diagnosis Code D55.0

      Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Favism
      • G6PD deficiency anemia
    • glucuronyl transferase E80.5
      ICD-10-CM Diagnosis Code E80.5

      Crigler-Najjar syndrome

        2016 2017 2018 2019 Billable/Specific Code
    • glycogen synthetase E74.09
      ICD-10-CM Diagnosis Code E74.09

      Other glycogen storage disease

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Andersen disease
      • Hers disease
      • Tauri disease
      • Glycogen storage disease, types 0, IV, VI-XI
      • Liver phosphorylase deficiency
      • Muscle phosphofructokinase deficiency
    • gonadotropin E23.0
      (isolated)
      ICD-10-CM Diagnosis Code E23.0

      Hypopituitarism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Fertile eunuch syndrome
      • Hypogonadotropic hypogonadism
      • Idiopathic growth hormone deficiency
      • Isolated deficiency of gonadotropin
      • Isolated deficiency of growth hormone
      • Isolated deficiency of pituitary hormone
      • Kallmann's syndrome
      • Lorain-Levi short stature
      • Necrosis of pituitary gland (postpartum)
      • Panhypopituitarism
      • Pituitary cachexia
      • Pituitary insufficiency NOS
      • Pituitary short stature
      • Sheehan's syndrome
      • Simmonds' disease
    • growth hormone E23.0
      (idiopathic) (isolated)
      ICD-10-CM Diagnosis Code E23.0

      Hypopituitarism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Fertile eunuch syndrome
      • Hypogonadotropic hypogonadism
      • Idiopathic growth hormone deficiency
      • Isolated deficiency of gonadotropin
      • Isolated deficiency of growth hormone
      • Isolated deficiency of pituitary hormone
      • Kallmann's syndrome
      • Lorain-Levi short stature
      • Necrosis of pituitary gland (postpartum)
      • Panhypopituitarism
      • Pituitary cachexia
      • Pituitary insufficiency NOS
      • Pituitary short stature
      • Sheehan's syndrome
      • Simmonds' disease
    • Hageman factor D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • hemoglobin D64.9
      ICD-10-CM Diagnosis Code D64.9

      Anemia, unspecified

        2016 2017 2018 2019 Billable/Specific Code
    • hepatophosphorylase E74.09
      ICD-10-CM Diagnosis Code E74.09

      Other glycogen storage disease

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Andersen disease
      • Hers disease
      • Tauri disease
      • Glycogen storage disease, types 0, IV, VI-XI
      • Liver phosphorylase deficiency
      • Muscle phosphofructokinase deficiency
    • homogentisate 1,2-dioxygenase E70.29
      ICD-10-CM Diagnosis Code E70.29

      Other disorders of tyrosine metabolism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Alkaptonuria
      • Ochronosis
    • hormone
      • anterior pituitary (partial) E23.0
        ICD-10-CM Diagnosis Code E23.0

        Hypopituitarism

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Fertile eunuch syndrome
        • Hypogonadotropic hypogonadism
        • Idiopathic growth hormone deficiency
        • Isolated deficiency of gonadotropin
        • Isolated deficiency of growth hormone
        • Isolated deficiency of pituitary hormone
        • Kallmann's syndrome
        • Lorain-Levi short stature
        • Necrosis of pituitary gland (postpartum)
        • Panhypopituitarism
        • Pituitary cachexia
        • Pituitary insufficiency NOS
        • Pituitary short stature
        • Sheehan's syndrome
        • Simmonds' disease
        • growth E23.0
          ICD-10-CM Diagnosis Code E23.0

          Hypopituitarism

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Fertile eunuch syndrome
          • Hypogonadotropic hypogonadism
          • Idiopathic growth hormone deficiency
          • Isolated deficiency of gonadotropin
          • Isolated deficiency of growth hormone
          • Isolated deficiency of pituitary hormone
          • Kallmann's syndrome
          • Lorain-Levi short stature
          • Necrosis of pituitary gland (postpartum)
          • Panhypopituitarism
          • Pituitary cachexia
          • Pituitary insufficiency NOS
          • Pituitary short stature
          • Sheehan's syndrome
          • Simmonds' disease
      • growth E23.0
        (isolated)
        ICD-10-CM Diagnosis Code E23.0

        Hypopituitarism

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Fertile eunuch syndrome
        • Hypogonadotropic hypogonadism
        • Idiopathic growth hormone deficiency
        • Isolated deficiency of gonadotropin
        • Isolated deficiency of growth hormone
        • Isolated deficiency of pituitary hormone
        • Kallmann's syndrome
        • Lorain-Levi short stature
        • Necrosis of pituitary gland (postpartum)
        • Panhypopituitarism
        • Pituitary cachexia
        • Pituitary insufficiency NOS
        • Pituitary short stature
        • Sheehan's syndrome
        • Simmonds' disease
      • pituitary E23.0
        ICD-10-CM Diagnosis Code E23.0

        Hypopituitarism

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Fertile eunuch syndrome
        • Hypogonadotropic hypogonadism
        • Idiopathic growth hormone deficiency
        • Isolated deficiency of gonadotropin
        • Isolated deficiency of growth hormone
        • Isolated deficiency of pituitary hormone
        • Kallmann's syndrome
        • Lorain-Levi short stature
        • Necrosis of pituitary gland (postpartum)
        • Panhypopituitarism
        • Pituitary cachexia
        • Pituitary insufficiency NOS
        • Pituitary short stature
        • Sheehan's syndrome
        • Simmonds' disease
      • testicular E29.1
        ICD-10-CM Diagnosis Code E29.1

        Testicular hypofunction

          2016 2017 2018 2019 Billable/Specific Code Male Dx
        Applicable To
        • Defective biosynthesis of testicular androgen NOS
        • 5-delta-Reductase deficiency (with male pseudohermaphroditism)
        • Testicular hypogonadism NOS
        Type 1 Excludes
        • postprocedural testicular hypofunction (E89.5)
        Use Additional
        • code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
    • hypoxanthine- E79.1
      (guanine)-phosphoribosyltransferase (HG- PRT) (total H-PRT)
      ICD-10-CM Diagnosis Code E79.1

      Lesch-Nyhan syndrome

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • HGPRT deficiency
    • immunity D84.9
      ICD-10-CM Diagnosis Code D84.9

      Immunodeficiency, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      • cell-mediated D84.8
        ICD-10-CM Diagnosis Code D84.8

        Other specified immunodeficiencies

          2016 2017 2018 2019 Billable/Specific Code
        • with thrombocytopenia and eczema D82.0
          ICD-10-CM Diagnosis Code D82.0

          Wiskott-Aldrich syndrome

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Immunodeficiency with thrombocytopenia and eczema
      • combined D81.9
        ICD-10-CM Diagnosis Code D81.9

        Combined immunodeficiency, unspecified

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Severe combined immunodeficiency disorder [SCID] NOS
      • humoral D80.9
        ICD-10-CM Diagnosis Code D80.9

        Immunodeficiency with predominantly antibody defects, unspecified

          2016 2017 2018 2019 Billable/Specific Code
      • IgA D80.2
        (secretory)
        ICD-10-CM Diagnosis Code D80.2

        Selective deficiency of immunoglobulin A [IgA]

          2016 2017 2018 2019 Billable/Specific Code
      • IgG D80.3
        ICD-10-CM Diagnosis Code D80.3

        Selective deficiency of immunoglobulin G [IgG] subclasses

          2016 2017 2018 2019 Billable/Specific Code
      • IgM D80.4
        ICD-10-CM Diagnosis Code D80.4

        Selective deficiency of immunoglobulin M [IgM]

          2016 2017 2018 2019 Billable/Specific Code
    • immuno - see Immunodeficiency
    • immunoglobulin, selective
      • A D80.2
        (IgA)
        ICD-10-CM Diagnosis Code D80.2

        Selective deficiency of immunoglobulin A [IgA]

          2016 2017 2018 2019 Billable/Specific Code
      • G D80.3
        (IgG) (subclasses)
        ICD-10-CM Diagnosis Code D80.3

        Selective deficiency of immunoglobulin G [IgG] subclasses

          2016 2017 2018 2019 Billable/Specific Code
      • M D80.4
        (IgM)
        ICD-10-CM Diagnosis Code D80.4

        Selective deficiency of immunoglobulin M [IgM]

          2016 2017 2018 2019 Billable/Specific Code
    • inositol E53.8
      (B complex)
      ICD-10-CM Diagnosis Code E53.8

      Deficiency of other specified B group vitamins

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Biotin deficiency
      • Cyanocobalamin deficiency
      • Folate deficiency
      • Folic acid deficiency
      • Pantothenic acid deficiency
      • Vitamin B12 deficiency
      Type 1 Excludes
      • folate deficiency anemia (D52.-)
      • vitamin B12 deficiency anemia (D51.-)
    • intrinsic
      • factor D51.0
        (congenital)
        ICD-10-CM Diagnosis Code D51.0

        Vitamin B12 deficiency anemia due to intrinsic factor deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Addison anemia
        • Biermer anemia
        • Pernicious (congenital) anemia
        • Congenital intrinsic factor deficiency
      • sphincter N36.42
        ICD-10-CM Diagnosis Code N36.42

        Intrinsic sphincter deficiency (ISD)

          2016 2017 2018 2019 Billable/Specific Code
        • with urethral hypermobility N36.43
          ICD-10-CM Diagnosis Code N36.43

          Combined hypermobility of urethra and intrinsic sphincter deficiency

            2016 2017 2018 2019 Billable/Specific Code
    • iodine E61.8
      ICD-10-CM Diagnosis Code E61.8

      Deficiency of other specified nutrient elements

        2016 2017 2018 2019 Billable/Specific Code
    • iron E61.1
      ICD-10-CM Diagnosis Code E61.1

      Iron deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Type 1 Excludes
      • iron deficiency anemia (D50.-)
      • anemia D50.9
        ICD-10-CM Diagnosis Code D50.9

        Iron deficiency anemia, unspecified

          2016 2017 2018 2019 Billable/Specific Code
    • kalium E87.6
      ICD-10-CM Diagnosis Code E87.6

      Hypokalemia

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Potassium [K] deficiency
    • kappa-light chain D80.8
      ICD-10-CM Diagnosis Code D80.8

      Other immunodeficiencies with predominantly antibody defects

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Kappa light chain deficiency
    • labile factor (congenital) (hereditary) D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
      • acquired D68.4
        ICD-10-CM Diagnosis Code D68.4

        Acquired coagulation factor deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Deficiency of coagulation factor due to liver disease
        • Deficiency of coagulation factor due to vitamin K deficiency
        Type 1 Excludes
        • vitamin K deficiency of newborn (P53)
    • lacrimal fluid (acquired) - see also Syndrome, dry eye
      • congenital Q10.6
        ICD-10-CM Diagnosis Code Q10.6

        Other congenital malformations of lacrimal apparatus

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital malformation of lacrimal apparatus NOS
    • lactase
      • congenital E73.0
        ICD-10-CM Diagnosis Code E73.0

        Congenital lactase deficiency

          2016 2017 2018 2019 Billable/Specific Code
      • secondary E73.1
        ICD-10-CM Diagnosis Code E73.1

        Secondary lactase deficiency

          2016 2017 2018 2019 Billable/Specific Code
    • Laki-Lorand factor D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • lecithin cholesterol acyltransferase E78.6
      ICD-10-CM Diagnosis Code E78.6

      Lipoprotein deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Abetalipoproteinemia
      • Depressed HDL cholesterol
      • High-density lipoprotein deficiency
      • Hypoalphalipoproteinemia
      • Hypobetalipoproteinemia (familial)
      • Lecithin cholesterol acyltransferase deficiency
      • Tangier disease
    • lipocaic K86.89
      ICD-10-CM Diagnosis Code K86.89

      Other specified diseases of pancreas

        2017 - New Code 2018 2019 Billable/Specific Code
      Applicable To
      • Aseptic pancreatic necrosis, unrelated to acute pancreatitis
      • Atrophy of pancreas
      • Calculus of pancreas
      • Cirrhosis of pancreas
      • Fibrosis of pancreas
      • Pancreatic fat necrosis, unrelated to acute pancreatitis
      • Pancreatic infantilism
      • Pancreatic necrosis NOS, unrelated to acute pancreatitis
    • lipoprotein E78.6
      (familial) (high density)
      ICD-10-CM Diagnosis Code E78.6

      Lipoprotein deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Abetalipoproteinemia
      • Depressed HDL cholesterol
      • High-density lipoprotein deficiency
      • Hypoalphalipoproteinemia
      • Hypobetalipoproteinemia (familial)
      • Lecithin cholesterol acyltransferase deficiency
      • Tangier disease
    • liver phosphorylase E74.09
      ICD-10-CM Diagnosis Code E74.09

      Other glycogen storage disease

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Andersen disease
      • Hers disease
      • Tauri disease
      • Glycogen storage disease, types 0, IV, VI-XI
      • Liver phosphorylase deficiency
      • Muscle phosphofructokinase deficiency
    • lysosomal alpha-1, 4 glucosidase E74.02
      ICD-10-CM Diagnosis Code E74.02

      Pompe disease

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Cardiac glycogenosis
      • Type II glycogen storage disease
    • magnesium E61.2
      ICD-10-CM Diagnosis Code E61.2

      Magnesium deficiency

        2016 2017 2018 2019 Billable/Specific Code
    • major histocompatibility complex
      • class I D81.6
        ICD-10-CM Diagnosis Code D81.6

        Major histocompatibility complex class I deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Bare lymphocyte syndrome
      • class II D81.7
        ICD-10-CM Diagnosis Code D81.7

        Major histocompatibility complex class II deficiency

          2016 2017 2018 2019 Billable/Specific Code
    • manganese E61.3
      ICD-10-CM Diagnosis Code E61.3

      Manganese deficiency

        2016 2017 2018 2019 Billable/Specific Code
    • menadione (vitamin K) E56.1
      ICD-10-CM Diagnosis Code E56.1

      Deficiency of vitamin K

        2016 2017 2018 2019 Billable/Specific Code
      Type 1 Excludes
      • deficiency of coagulation factor due to vitamin K deficiency (D68.4)
      • vitamin K deficiency of newborn (P53)
      • newborn P53
        ICD-10-CM Diagnosis Code P53

        Hemorrhagic disease of newborn

          2016 2017 2018 2019 Billable/Specific Code Code on Newborn Record
        Applicable To
        • Vitamin K deficiency of newborn
    • mental (familial) (hereditary) - see Disability, intellectual
    • methylenetetrahydrofolate reductase E72.12
      (MTHFR)
      ICD-10-CM Diagnosis Code E72.12

      Methylenetetrahydrofolate reductase deficiency

        2016 2017 2018 2019 Billable/Specific Code
    • mevalonate kinase M04.1
      ICD-10-CM Diagnosis Code M04.1

      Periodic fever syndromes

        2017 - New Code 2018 2019 Billable/Specific Code
      Applicable To
      • Familial Mediterranean fever
      • Hyperimmunoglobin D syndrome
      • Mevalonate kinase deficiency
      • Tumor necrosis factor receptor associated periodic syndrome [TRAPS]
    • mineral NEC E61.8
      ICD-10-CM Diagnosis Code E61.8

      Deficiency of other specified nutrient elements

        2016 2017 2018 2019 Billable/Specific Code
    • mineralocorticoid E27.49
      ICD-10-CM Diagnosis Code E27.49

      Other adrenocortical insufficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Adrenal hemorrhage
      • Adrenal infarction
      • with glucocorticoid E27.49
        ICD-10-CM Diagnosis Code E27.49

        Other adrenocortical insufficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Adrenal hemorrhage
        • Adrenal infarction
    • molybdenum E61.5
      (nutritional)
      ICD-10-CM Diagnosis Code E61.5

      Molybdenum deficiency

        2016 2017 2018 2019 Billable/Specific Code
    • moral F60.2
      ICD-10-CM Diagnosis Code F60.2

      Antisocial personality disorder

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Amoral personality (disorder)
      • Asocial personality (disorder)
      • Dissocial personality disorder
      • Psychopathic personality (disorder)
      • Sociopathic personality (disorder)
      Type 1 Excludes
      • conduct disorders (F91.-)
      Type 2 Excludes
      • borderline personality disorder (F60.3)
    • multiple nutrient elements E61.7
      ICD-10-CM Diagnosis Code E61.7

      Deficiency of multiple nutrient elements

        2016 2017 2018 2019 Billable/Specific Code
    • multiple sulfatase E75.26
      (MSD)
      ICD-10-CM Diagnosis Code E75.26

      Sulfatase deficiency

        2019 - New Code Billable/Specific Code
      Applicable To
      • Multiple sulfatase deficiency (MSD)
    • muscle
      • carnitine E71.314
        (palmityltransferase)
        ICD-10-CM Diagnosis Code E71.314

        Muscle carnitine palmitoyltransferase deficiency

          2016 2017 2018 2019 Billable/Specific Code
      • phosphofructokinase E74.09
        ICD-10-CM Diagnosis Code E74.09

        Other glycogen storage disease

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Andersen disease
        • Hers disease
        • Tauri disease
        • Glycogen storage disease, types 0, IV, VI-XI
        • Liver phosphorylase deficiency
        • Muscle phosphofructokinase deficiency
    • myoadenylate deaminase E79.2
      ICD-10-CM Diagnosis Code E79.2

      Myoadenylate deaminase deficiency

        2016 2017 2018 2019 Billable/Specific Code
    • myocardial - see Insufficiency, myocardial
    • myophosphorylase E74.04
      ICD-10-CM Diagnosis Code E74.04

      McArdle disease

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Type V glycogen storage disease
    • NADH diaphorase or reductase D74.0
      (congenital)
      ICD-10-CM Diagnosis Code D74.0

      Congenital methemoglobinemia

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Congenital NADH-methemoglobin reductase deficiency
      • Hemoglobin-M [Hb-M] disease
      • Methemoglobinemia, hereditary
    • NADH-methemoglobin reductase D74.0
      (congenital)
      ICD-10-CM Diagnosis Code D74.0

      Congenital methemoglobinemia

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Congenital NADH-methemoglobin reductase deficiency
      • Hemoglobin-M [Hb-M] disease
      • Methemoglobinemia, hereditary
    • natrium E87.1
      ICD-10-CM Diagnosis Code E87.1

      Hypo-osmolality and hyponatremia

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Sodium [Na] deficiency
      Type 1 Excludes
      • syndrome of inappropriate secretion of antidiuretic hormone (E22.2)
    • niacin E52
      (amide) (-tryptophan)
      ICD-10-CM Diagnosis Code E52

      Niacin deficiency [pellagra]

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Niacin (-tryptophan) deficiency
      • Nicotinamide deficiency
      • Pellagra (alcoholic)
      Type 1 Excludes
      • sequelae of niacin deficiency (E64.8)
    • nicotinamide E52
      ICD-10-CM Diagnosis Code E52

      Niacin deficiency [pellagra]

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Niacin (-tryptophan) deficiency
      • Nicotinamide deficiency
      • Pellagra (alcoholic)
      Type 1 Excludes
      • sequelae of niacin deficiency (E64.8)
    • nicotinic acid E52
      ICD-10-CM Diagnosis Code E52

      Niacin deficiency [pellagra]

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Niacin (-tryptophan) deficiency
      • Nicotinamide deficiency
      • Pellagra (alcoholic)
      Type 1 Excludes
      • sequelae of niacin deficiency (E64.8)
    • number of teeth - see Anodontia
    • nutrient element E61.9
      ICD-10-CM Diagnosis Code E61.9

      Deficiency of nutrient element, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      • multiple E61.7
        ICD-10-CM Diagnosis Code E61.7

        Deficiency of multiple nutrient elements

          2016 2017 2018 2019 Billable/Specific Code
      • specified NEC E61.8
        ICD-10-CM Diagnosis Code E61.8

        Deficiency of other specified nutrient elements

          2016 2017 2018 2019 Billable/Specific Code
    • nutrition, nutritional E63.9
      ICD-10-CM Diagnosis Code E63.9

      Nutritional deficiency, unspecified

        2016 2017 2018 2019 Billable/Specific Code
    • of interleukin 1 receptor antagonist [DIRA] M04.8
      ICD-10-CM Diagnosis Code M04.8

      Other autoinflammatory syndromes

        2017 - New Code 2018 2019 Billable/Specific Code
      Applicable To
      • Blau syndrome
      • Deficiency of interleukin 1 receptor antagonist [DIRA]
      • Majeed syndrome
      • Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome [PFAPA]
      • Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome [PAPA]
    • ornithine transcarbamylase E72.4
      ICD-10-CM Diagnosis Code E72.4

      Disorders of ornithine metabolism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Hyperammonemia-Hyperornithinemia-Homocitrullinemia syndrome
      • Ornithinemia (types I, II)
      • Ornithine transcarbamylase deficiency
      Type 1 Excludes
      • hereditary choroidal dystrophy (H31.2-)
    • ovarian E28.39
      ICD-10-CM Diagnosis Code E28.39

      Other primary ovarian failure

        2016 2017 2018 2019 Billable/Specific Code Female Dx
      Applicable To
      • Decreased estrogen
      • Resistant ovary syndrome
    • oxygen - see Anoxia
    • pantothenic acid E53.8
      ICD-10-CM Diagnosis Code E53.8

      Deficiency of other specified B group vitamins

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Biotin deficiency
      • Cyanocobalamin deficiency
      • Folate deficiency
      • Folic acid deficiency
      • Pantothenic acid deficiency
      • Vitamin B12 deficiency
      Type 1 Excludes
      • folate deficiency anemia (D52.-)
      • vitamin B12 deficiency anemia (D51.-)
    • parathyroid E20.9
      (gland)
      ICD-10-CM Diagnosis Code E20.9

      Hypoparathyroidism, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Parathyroid tetany
    • perineum N81.89
      (female)
      ICD-10-CM Diagnosis Code N81.89

      Other female genital prolapse

        2016 2017 2018 2019 Billable/Specific Code Female Dx
      Applicable To
      • Deficient perineum
      • Old laceration of muscles of pelvic floor
    • phenylalanine hydroxylase E70.1
      ICD-10-CM Diagnosis Code E70.1

      Other hyperphenylalaninemias

        2016 2017 2018 2019 Billable/Specific Code
    • phosphoenolpyruvate carboxykinase E74.4
      ICD-10-CM Diagnosis Code E74.4

      Disorders of pyruvate metabolism and gluconeogenesis

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Deficiency of phosphoenolpyruvate carboxykinase
      • Deficiency of pyruvate carboxylase
      • Deficiency of pyruvate dehydrogenase
      Type 1 Excludes
      • disorders of pyruvate metabolism and gluconeogenesis with anemia (D55.-)
      • Leigh's syndrome (G31.82)
    • phosphofructokinase E74.19
      ICD-10-CM Diagnosis Code E74.19

      Other disorders of fructose metabolism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Fructose-1, 6-diphosphatase deficiency
    • phosphomannomutuse E74.8
      ICD-10-CM Diagnosis Code E74.8

      Other specified disorders of carbohydrate metabolism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Essential pentosuria
      • Renal glycosuria
    • phosphomannose isomerase E74.8
      ICD-10-CM Diagnosis Code E74.8

      Other specified disorders of carbohydrate metabolism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Essential pentosuria
      • Renal glycosuria
    • phosphomannosyl mutase E74.8
      ICD-10-CM Diagnosis Code E74.8

      Other specified disorders of carbohydrate metabolism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Essential pentosuria
      • Renal glycosuria
    • phosphorylase kinase, liver E74.09
      ICD-10-CM Diagnosis Code E74.09

      Other glycogen storage disease

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Andersen disease
      • Hers disease
      • Tauri disease
      • Glycogen storage disease, types 0, IV, VI-XI
      • Liver phosphorylase deficiency
      • Muscle phosphofructokinase deficiency
    • pituitary hormone E23.0
      (isolated)
      ICD-10-CM Diagnosis Code E23.0

      Hypopituitarism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Fertile eunuch syndrome
      • Hypogonadotropic hypogonadism
      • Idiopathic growth hormone deficiency
      • Isolated deficiency of gonadotropin
      • Isolated deficiency of growth hormone
      • Isolated deficiency of pituitary hormone
      • Kallmann's syndrome
      • Lorain-Levi short stature
      • Necrosis of pituitary gland (postpartum)
      • Panhypopituitarism
      • Pituitary cachexia
      • Pituitary insufficiency NOS
      • Pituitary short stature
      • Sheehan's syndrome
      • Simmonds' disease
    • plasma thromboplastin
      • antecedent D68.1
        (PTA)
        ICD-10-CM Diagnosis Code D68.1

        Hereditary factor XI deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Hemophilia C
        • Plasma thromboplastin antecedent [PTA] deficiency
        • Rosenthal's disease
      • component D67
        (PTC)
        ICD-10-CM Diagnosis Code D67

        Hereditary factor IX deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Christmas disease
        • Factor IX deficiency (with functional defect)
        • Hemophilia B
        • Plasma thromboplastin component [PTC] deficiency
    • plasminogen E88.02
      (type 1) (type 2)
      ICD-10-CM Diagnosis Code E88.02

      Plasminogen deficiency

        2019 - New Code Billable/Specific Code
      Applicable To
      • Dysplasminogenemia
      • Hypoplasminogenemia
      • Type 1 plasminogen deficiency
      • Type 2 plasminogen deficiency
      Code Also
      • , if applicable, ligneous conjunctivitis (H10.51)
      Use Additional
      • code for associated findings, such as:
      • hydrocephalus (G91.4)
      • ligneous conjunctivitis (H10.51)
      • otitis media (H67.-)
      • respiratory disorder related to plasminogen deficiency (J99)
    • platelet NEC D69.1
      ICD-10-CM Diagnosis Code D69.1

      Qualitative platelet defects

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Bernard-Soulier [giant platelet] syndrome
      • Glanzmann's disease
      • Grey platelet syndrome
      • Thromboasthenia (hemorrhagic) (hereditary)
      • Thrombocytopathy
      Type 1 Excludes
      • von Willebrand's disease (D68.0)
      • constitutional D68.0
        ICD-10-CM Diagnosis Code D68.0

        Von Willebrand's disease

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Angiohemophilia
        • Factor VIII deficiency with vascular defect
        • Vascular hemophilia
        Type 1 Excludes
        • capillary fragility (hereditary) (D69.8)
        • factor VIII deficiency NOS (D66)
        • factor VIII deficiency with functional defect (D66)
    • polyglandular E31.8
      ICD-10-CM Diagnosis Code E31.8

      Other polyglandular dysfunction

        2016 2017 2018 2019 Billable/Specific Code
      • autoimmune E31.0
        ICD-10-CM Diagnosis Code E31.0

        Autoimmune polyglandular failure

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Schmidt's syndrome
    • potassium E87.6
      (K)
      ICD-10-CM Diagnosis Code E87.6

      Hypokalemia

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Potassium [K] deficiency
    • prepuce N47.3
      ICD-10-CM Diagnosis Code N47.3

      Deficient foreskin

        2016 2017 2018 2019 Billable/Specific Code Male Dx
    • proaccelerin (congenital) (hereditary) D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
      • acquired D68.4
        ICD-10-CM Diagnosis Code D68.4

        Acquired coagulation factor deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Deficiency of coagulation factor due to liver disease
        • Deficiency of coagulation factor due to vitamin K deficiency
        Type 1 Excludes
        • vitamin K deficiency of newborn (P53)
    • proconvertin factor (congenital) (hereditary) D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
      • acquired D68.4
        ICD-10-CM Diagnosis Code D68.4

        Acquired coagulation factor deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Deficiency of coagulation factor due to liver disease
        • Deficiency of coagulation factor due to vitamin K deficiency
        Type 1 Excludes
        • vitamin K deficiency of newborn (P53)
    • protein E46
      - see also Malnutrition
      ICD-10-CM Diagnosis Code E46

      Unspecified protein-calorie malnutrition

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Malnutrition NOS
      • Protein-calorie imbalance NOS
      Type 1 Excludes
      • nutritional deficiency NOS (E63.9)
      • anemia D53.0
        ICD-10-CM Diagnosis Code D53.0

        Protein deficiency anemia

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Amino-acid deficiency anemia
        • Orotaciduric anemia
        Type 1 Excludes
        • Lesch-Nyhan syndrome (E79.1)
      • C D68.59
        ICD-10-CM Diagnosis Code D68.59

        Other primary thrombophilia

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Antithrombin III deficiency
        • Hypercoagulable state NOS
        • Primary hypercoagulable state NEC
        • Primary thrombophilia NEC
        • Protein C deficiency
        • Protein S deficiency
        • Thrombophilia NOS
      • S D68.59
        ICD-10-CM Diagnosis Code D68.59

        Other primary thrombophilia

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Antithrombin III deficiency
        • Hypercoagulable state NOS
        • Primary hypercoagulable state NEC
        • Primary thrombophilia NEC
        • Protein C deficiency
        • Protein S deficiency
        • Thrombophilia NOS
    • prothrombin (congenital) (heredItary) D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
      • acquired D68.4
        ICD-10-CM Diagnosis Code D68.4

        Acquired coagulation factor deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Deficiency of coagulation factor due to liver disease
        • Deficiency of coagulation factor due to vitamin K deficiency
        Type 1 Excludes
        • vitamin K deficiency of newborn (P53)
    • Prower factor D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • pseudocholinesterase E88.09
      ICD-10-CM Diagnosis Code E88.09

      Other disorders of plasma-protein metabolism, not elsewhere classified

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Bisalbuminemia
    • PTA D68.1
      (plasma thromboplastin antecedent)
      ICD-10-CM Diagnosis Code D68.1

      Hereditary factor XI deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Hemophilia C
      • Plasma thromboplastin antecedent [PTA] deficiency
      • Rosenthal's disease
    • PTC D67
      (plasma thromboplastin component)
      ICD-10-CM Diagnosis Code D67

      Hereditary factor IX deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Christmas disease
      • Factor IX deficiency (with functional defect)
      • Hemophilia B
      • Plasma thromboplastin component [PTC] deficiency
    • purine nucleoside phosphorylase D81.5
      (PNP)
      ICD-10-CM Diagnosis Code D81.5

      Purine nucleoside phosphorylase [PNP] deficiency

        2016 2017 2018 2019 Billable/Specific Code
    • pyracin E53.1
      (alpha) (beta)
      ICD-10-CM Diagnosis Code E53.1

      Pyridoxine deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Vitamin B6 deficiency
      Type 1 Excludes
      • pyridoxine-responsive sideroblastic anemia (D64.3)
    • pyridoxal E53.1
      ICD-10-CM Diagnosis Code E53.1

      Pyridoxine deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Vitamin B6 deficiency
      Type 1 Excludes
      • pyridoxine-responsive sideroblastic anemia (D64.3)
    • pyridoxamine E53.1
      ICD-10-CM Diagnosis Code E53.1

      Pyridoxine deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Vitamin B6 deficiency
      Type 1 Excludes
      • pyridoxine-responsive sideroblastic anemia (D64.3)
    • pyridoxine E53.1
      (derivatives)
      ICD-10-CM Diagnosis Code E53.1

      Pyridoxine deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Vitamin B6 deficiency
      Type 1 Excludes
      • pyridoxine-responsive sideroblastic anemia (D64.3)
    • pyruvate
      • carboxylase E74.4
        ICD-10-CM Diagnosis Code E74.4

        Disorders of pyruvate metabolism and gluconeogenesis

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Deficiency of phosphoenolpyruvate carboxykinase
        • Deficiency of pyruvate carboxylase
        • Deficiency of pyruvate dehydrogenase
        Type 1 Excludes
        • disorders of pyruvate metabolism and gluconeogenesis with anemia (D55.-)
        • Leigh's syndrome (G31.82)
      • dehydrogenase E74.4
        ICD-10-CM Diagnosis Code E74.4

        Disorders of pyruvate metabolism and gluconeogenesis

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Deficiency of phosphoenolpyruvate carboxykinase
        • Deficiency of pyruvate carboxylase
        • Deficiency of pyruvate dehydrogenase
        Type 1 Excludes
        • disorders of pyruvate metabolism and gluconeogenesis with anemia (D55.-)
        • Leigh's syndrome (G31.82)
    • riboflavin E53.0
      (vitamin B2)
      ICD-10-CM Diagnosis Code E53.0

      Riboflavin deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Ariboflavinosis
      • Vitamin B2 deficiency
    • salt E87.1
      ICD-10-CM Diagnosis Code E87.1

      Hypo-osmolality and hyponatremia

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Sodium [Na] deficiency
      Type 1 Excludes
      • syndrome of inappropriate secretion of antidiuretic hormone (E22.2)
    • secretion
      • ovary E28.39
        ICD-10-CM Diagnosis Code E28.39

        Other primary ovarian failure

          2016 2017 2018 2019 Billable/Specific Code Female Dx
        Applicable To
        • Decreased estrogen
        • Resistant ovary syndrome
      • salivary gland K11.7
        (any)
        ICD-10-CM Diagnosis Code K11.7

        Disturbances of salivary secretion

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Hypoptyalism
        • Ptyalism
        • Xerostomia
        Type 2 Excludes
      • urine R34
        ICD-10-CM Diagnosis Code R34

        Anuria and oliguria

          2016 2017 2018 2019 Billable/Specific Code
        Type 1 Excludes
        • anuria and oliguria complicating abortion or ectopic or molar pregnancy (O00-O07, O08.4)
        • anuria and oliguria complicating pregnancy (O26.83-)
        • anuria and oliguria complicating the puerperium (O90.4)
    • selenium E59
      (dietary)
      ICD-10-CM Diagnosis Code E59

      Dietary selenium deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Keshan disease
      Type 1 Excludes
      • sequelae of selenium deficiency (E64.8)
    • serum antitrypsin, familial E88.01
      ICD-10-CM Diagnosis Code E88.01

      Alpha-1-antitrypsin deficiency

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AAT deficiency
    • short stature homeobox gene (SHOX)
      • with
        • dyschondrosteosis Q78.8
          ICD-10-CM Diagnosis Code Q78.8

          Other specified osteochondrodysplasias

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Osteopoikilosis
        • short stature E34.3
          (idiopathic)
          ICD-10-CM Diagnosis Code E34.3

          Short stature due to endocrine disorder

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Constitutional short stature
          • Laron-type short stature
          Type 1 Excludes
          • achondroplastic short stature (Q77.4)
          • hypochondroplastic short stature (Q77.4)
          • nutritional short stature (E45)
          • pituitary short stature (E23.0)
          • progeria (E34.8)
          • renal short stature (N25.0)
          • Russell-Silver syndrome (Q87.1)
          • short-limbed stature with immunodeficiency (D82.2)
          • short stature in specific dysmorphic syndromes - code to syndrome - see Alphabetical Index
          • short stature NOS (R62.52)
        • Turner's syndrome Q96.9
          ICD-10-CM Diagnosis Code Q96.9

          Turner's syndrome, unspecified

            2016 2017 2018 2019 Billable/Specific Code Female Dx POA Exempt
    • sodium E87.1
      (Na)
      ICD-10-CM Diagnosis Code E87.1

      Hypo-osmolality and hyponatremia

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Sodium [Na] deficiency
      Type 1 Excludes
      • syndrome of inappropriate secretion of antidiuretic hormone (E22.2)
    • SPCA D68.2
      (factor VII)
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • sphincter, intrinsic N36.42
      ICD-10-CM Diagnosis Code N36.42

      Intrinsic sphincter deficiency (ISD)

        2016 2017 2018 2019 Billable/Specific Code
      • with urethral hypermobility N36.43
        ICD-10-CM Diagnosis Code N36.43

        Combined hypermobility of urethra and intrinsic sphincter deficiency

          2016 2017 2018 2019 Billable/Specific Code
    • stable factor (congenital) (hereditary) D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
      • acquired D68.4
        ICD-10-CM Diagnosis Code D68.4

        Acquired coagulation factor deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Deficiency of coagulation factor due to liver disease
        • Deficiency of coagulation factor due to vitamin K deficiency
        Type 1 Excludes
        • vitamin K deficiency of newborn (P53)
    • Stuart-Prower D68.2
      (factor X)
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • succinic semialdehyde dehydrogenase E72.81
      ICD-10-CM Diagnosis Code E72.81

      Disorders of gamma aminobutyric acid metabolism

        2019 - New Code Billable/Specific Code
      Applicable To
      • 4-hydroxybutyric aciduria
      • Disorders of GABA metabolism
      • GABA metabolic defect
      • GABA transaminase deficiency
      • GABA-T deficiency
      • Gamma-hydroxybutyric aciduria
      • SSADHD
      • Succinic semialdehyde dehydrogenase deficiency
    • sucrase E74.39
      ICD-10-CM Diagnosis Code E74.39

      Other disorders of intestinal carbohydrate absorption

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Disorder of intestinal carbohydrate absorption NOS
      • Glucose-galactose malabsorption
      • Sucrase deficiency
    • sulfatase E75.26
      ICD-10-CM Diagnosis Code E75.26

      Sulfatase deficiency

        2019 - New Code Billable/Specific Code
      Applicable To
      • Multiple sulfatase deficiency (MSD)
    • sulfite oxidase E72.19
      ICD-10-CM Diagnosis Code E72.19

      Other disorders of sulfur-bearing amino-acid metabolism

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Cystathioninuria
      • Methioninemia
      • Sulfite oxidase deficiency
    • thiamin, thiaminic (chloride) E51.9
      ICD-10-CM Diagnosis Code E51.9

      Thiamine deficiency, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      • beriberi (dry) E51.11
        ICD-10-CM Diagnosis Code E51.11

        Dry beriberi

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Beriberi NOS
        • Beriberi with polyneuropathy
        • wet E51.12
          ICD-10-CM Diagnosis Code E51.12

          Wet beriberi

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Beriberi with cardiovascular manifestations
          • Cardiovascular beriberi
          • Shoshin disease
    • thrombokinase D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
      • newborn P53
        ICD-10-CM Diagnosis Code P53

        Hemorrhagic disease of newborn

          2016 2017 2018 2019 Billable/Specific Code Code on Newborn Record
        Applicable To
        • Vitamin K deficiency of newborn
    • thyroid (gland) - see Hypothyroidism
    • tocopherol E56.0
      ICD-10-CM Diagnosis Code E56.0

      Deficiency of vitamin E

        2016 2017 2018 2019 Billable/Specific Code
    • tooth bud K00.0
      ICD-10-CM Diagnosis Code K00.0

      Anodontia

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Hypodontia
      • Oligodontia
      Type 1 Excludes
      • acquired absence of teeth (K08.1-)
    • transcobalamine II D51.2
      (anemia)
      ICD-10-CM Diagnosis Code D51.2

      Transcobalamin II deficiency

        2016 2017 2018 2019 Billable/Specific Code
    • vanadium E61.6
      ICD-10-CM Diagnosis Code E61.6

      Vanadium deficiency

        2016 2017 2018 2019 Billable/Specific Code
    • vascular I99.9
      ICD-10-CM Diagnosis Code I99.9

      Unspecified disorder of circulatory system

        2016 2017 2018 2019 Billable/Specific Code
    • vasopressin E23.2
      ICD-10-CM Diagnosis Code E23.2

      Diabetes insipidus

        2016 2017 2018 2019 Billable/Specific Code
      Type 1 Excludes
      • nephrogenic diabetes insipidus (N25.1)
    • vertical ridge K06.8
      ICD-10-CM Diagnosis Code K06.8

      Other specified disorders of gingiva and edentulous alveolar ridge

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Fibrous epulis
      • Flabby alveolar ridge
      • Giant cell epulis
      • Peripheral giant cell granuloma of gingiva
      • Pyogenic granuloma of gingiva
      • Vertical ridge deficiency
      Type 2 Excludes
    • viosterol - see Deficiency, calciferol
    • vitamin (multiple) E56.9
      ICD-10-CM Diagnosis Code E56.9

      Vitamin deficiency, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      • A E50.9
        ICD-10-CM Diagnosis Code E50.9

        Vitamin A deficiency, unspecified

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Hypovitaminosis A NOS
        • sequelae E64.1
          ICD-10-CM Diagnosis Code E64.1

          Sequelae of vitamin A deficiency

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • with
          • Bitot's spot E50.1
            (corneal)
            ICD-10-CM Diagnosis Code E50.1

            Vitamin A deficiency with Bitot's spot and conjunctival xerosis

              2016 2017 2018 2019 Billable/Specific Code
            Applicable To
            • Bitot's spot in the young child
          • follicular keratosis E50.8
            ICD-10-CM Diagnosis Code E50.8

            Other manifestations of vitamin A deficiency

              2016 2017 2018 2019 Billable/Specific Code
            Applicable To
            • Follicular keratosis
            • Xeroderma
          • keratomalacia E50.4
            ICD-10-CM Diagnosis Code E50.4

            Vitamin A deficiency with keratomalacia

              2016 2017 2018 2019 Billable/Specific Code
          • manifestations NEC E50.8
            ICD-10-CM Diagnosis Code E50.8

            Other manifestations of vitamin A deficiency

              2016 2017 2018 2019 Billable/Specific Code
            Applicable To
            • Follicular keratosis
            • Xeroderma
          • night blindness E50.5
            ICD-10-CM Diagnosis Code E50.5

            Vitamin A deficiency with night blindness

              2016 2017 2018 2019 Billable/Specific Code
          • scar of cornea, xerophthalmic E50.6
            ICD-10-CM Diagnosis Code E50.6

            Vitamin A deficiency with xerophthalmic scars of cornea

              2016 2017 2018 2019 Billable/Specific Code
          • xeroderma E50.8
            ICD-10-CM Diagnosis Code E50.8

            Other manifestations of vitamin A deficiency

              2016 2017 2018 2019 Billable/Specific Code
            Applicable To
            • Follicular keratosis
            • Xeroderma
          • xerophthalmia E50.7
            ICD-10-CM Diagnosis Code E50.7

            Other ocular manifestations of vitamin A deficiency

              2016 2017 2018 2019 Billable/Specific Code
            Applicable To
            • Xerophthalmia NOS
          • xerosis
            • conjunctival E50.0
              ICD-10-CM Diagnosis Code E50.0

              Vitamin A deficiency with conjunctival xerosis

                2016 2017 2018 2019 Billable/Specific Code
              • and Bitot's spot E50.1
                ICD-10-CM Diagnosis Code E50.1

                Vitamin A deficiency with Bitot's spot and conjunctival xerosis

                  2016 2017 2018 2019 Billable/Specific Code
                Applicable To
                • Bitot's spot in the young child
            • cornea E50.2
              ICD-10-CM Diagnosis Code E50.2

              Vitamin A deficiency with corneal xerosis

                2016 2017 2018 2019 Billable/Specific Code
              • and ulceration E50.3
                ICD-10-CM Diagnosis Code E50.3

                Vitamin A deficiency with corneal ulceration and xerosis

                  2016 2017 2018 2019 Billable/Specific Code
      • B (complex) E53.9
        ICD-10-CM Diagnosis Code E53.9

        Vitamin B deficiency, unspecified

          2016 2017 2018 2019 Billable/Specific Code
        • with
          • beriberi (dry) E51.11
            ICD-10-CM Diagnosis Code E51.11

            Dry beriberi

              2016 2017 2018 2019 Billable/Specific Code
            Applicable To
            • Beriberi NOS
            • Beriberi with polyneuropathy
            • wet E51.12
              ICD-10-CM Diagnosis Code E51.12

              Wet beriberi

                2016 2017 2018 2019 Billable/Specific Code
              Applicable To
              • Beriberi with cardiovascular manifestations
              • Cardiovascular beriberi
              • Shoshin disease
          • pellagra E52
            ICD-10-CM Diagnosis Code E52

            Niacin deficiency [pellagra]

              2016 2017 2018 2019 Billable/Specific Code
            Applicable To
            • Niacin (-tryptophan) deficiency
            • Nicotinamide deficiency
            • Pellagra (alcoholic)
            Type 1 Excludes
            • sequelae of niacin deficiency (E64.8)
      • B1 NOS E51.9
        ICD-10-CM Diagnosis Code E51.9

        Thiamine deficiency, unspecified

          2016 2017 2018 2019 Billable/Specific Code
        • beriberi (dry) E51.11
          ICD-10-CM Diagnosis Code E51.11

          Dry beriberi

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Beriberi NOS
          • Beriberi with polyneuropathy
          • wet E51.12
            ICD-10-CM Diagnosis Code E51.12

            Wet beriberi

              2016 2017 2018 2019 Billable/Specific Code
            Applicable To
            • Beriberi with cardiovascular manifestations
            • Cardiovascular beriberi
            • Shoshin disease
          • with circulatory system manifestations E51.11
            ICD-10-CM Diagnosis Code E51.11

            Dry beriberi

              2016 2017 2018 2019 Billable/Specific Code
            Applicable To
            • Beriberi NOS
            • Beriberi with polyneuropathy
      • B12 E53.8
        ICD-10-CM Diagnosis Code E53.8

        Deficiency of other specified B group vitamins

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Biotin deficiency
        • Cyanocobalamin deficiency
        • Folate deficiency
        • Folic acid deficiency
        • Pantothenic acid deficiency
        • Vitamin B12 deficiency
        Type 1 Excludes
        • folate deficiency anemia (D52.-)
        • vitamin B12 deficiency anemia (D51.-)
      • B2 E53.0
        (riboflavin)
        ICD-10-CM Diagnosis Code E53.0

        Riboflavin deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Ariboflavinosis
        • Vitamin B2 deficiency
      • B6 E53.1
        ICD-10-CM Diagnosis Code E53.1

        Pyridoxine deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Vitamin B6 deficiency
        Type 1 Excludes
        • pyridoxine-responsive sideroblastic anemia (D64.3)
      • C E54
        ICD-10-CM Diagnosis Code E54

        Ascorbic acid deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Deficiency of vitamin C
        • Scurvy
        Type 1 Excludes
        • scorbutic anemia (D53.2)
        • sequelae of vitamin C deficiency (E64.2)
        • sequelae E64.2
          ICD-10-CM Diagnosis Code E64.2

          Sequelae of vitamin C deficiency

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • D E55.9
        ICD-10-CM Diagnosis Code E55.9

        Vitamin D deficiency, unspecified

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Avitaminosis D
        • 25-hydroxylase E83.32
          ICD-10-CM Diagnosis Code E83.32

          Hereditary vitamin D-dependent rickets (type 1) (type 2)

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • 25-hydroxyvitamin D 1-alpha-hydroxylase deficiency
          • Pseudovitamin D deficiency
          • Vitamin D receptor defect
        • with
          • adult osteomalacia M83.8
            ICD-10-CM Diagnosis Code M83.8

            Other adult osteomalacia

              2016 2017 2018 2019 Billable/Specific Code Adult Dx (15-124 years)
          • rickets - see Rickets
      • E E56.0
        ICD-10-CM Diagnosis Code E56.0

        Deficiency of vitamin E

          2016 2017 2018 2019 Billable/Specific Code
      • folic acid E53.8
        ICD-10-CM Diagnosis Code E53.8

        Deficiency of other specified B group vitamins

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Biotin deficiency
        • Cyanocobalamin deficiency
        • Folate deficiency
        • Folic acid deficiency
        • Pantothenic acid deficiency
        • Vitamin B12 deficiency
        Type 1 Excludes
        • folate deficiency anemia (D52.-)
        • vitamin B12 deficiency anemia (D51.-)
      • G E53.0
        ICD-10-CM Diagnosis Code E53.0

        Riboflavin deficiency

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Ariboflavinosis
        • Vitamin B2 deficiency
      • group B E53.9
        ICD-10-CM Diagnosis Code E53.9

        Vitamin B deficiency, unspecified

          2016 2017 2018 2019 Billable/Specific Code
        • specified NEC E53.8
          ICD-10-CM Diagnosis Code E53.8

          Deficiency of other specified B group vitamins

            2016 2017 2018 2019 Billable/Specific Code
          Applicable To
          • Biotin deficiency
          • Cyanocobalamin deficiency
          • Folate deficiency
          • Folic acid deficiency
          • Pantothenic acid deficiency
          • Vitamin B12 deficiency
          Type 1 Excludes
          • folate deficiency anemia (D52.-)
          • vitamin B12 deficiency anemia (D51.-)
      • H E53.8
        (biotin)
        ICD-10-CM Diagnosis Code E53.8

        Deficiency of other specified B group vitamins

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Biotin deficiency
        • Cyanocobalamin deficiency
        • Folate deficiency
        • Folic acid deficiency
        • Pantothenic acid deficiency
        • Vitamin B12 deficiency
        Type 1 Excludes
        • folate deficiency anemia (D52.-)
        • vitamin B12 deficiency anemia (D51.-)
      • K E56.1
        ICD-10-CM Diagnosis Code E56.1

        Deficiency of vitamin K

          2016 2017 2018 2019 Billable/Specific Code
        Type 1 Excludes
        • deficiency of coagulation factor due to vitamin K deficiency (D68.4)
        • vitamin K deficiency of newborn (P53)
        • of newborn P53
          ICD-10-CM Diagnosis Code P53

          Hemorrhagic disease of newborn

            2016 2017 2018 2019 Billable/Specific Code Code on Newborn Record
          Applicable To
          • Vitamin K deficiency of newborn
      • nicotinic E52
        ICD-10-CM Diagnosis Code E52

        Niacin deficiency [pellagra]

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Niacin (-tryptophan) deficiency
        • Nicotinamide deficiency
        • Pellagra (alcoholic)
        Type 1 Excludes
        • sequelae of niacin deficiency (E64.8)
      • P E56.8
        ICD-10-CM Diagnosis Code E56.8

        Deficiency of other vitamins

          2016 2017 2018 2019 Billable/Specific Code
      • PP E52
        (pellagra-preventing)
        ICD-10-CM Diagnosis Code E52

        Niacin deficiency [pellagra]

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Niacin (-tryptophan) deficiency
        • Nicotinamide deficiency
        • Pellagra (alcoholic)
        Type 1 Excludes
        • sequelae of niacin deficiency (E64.8)
      • specified NEC E56.8
        ICD-10-CM Diagnosis Code E56.8

        Deficiency of other vitamins

          2016 2017 2018 2019 Billable/Specific Code
      • thiamin E51.9
        ICD-10-CM Diagnosis Code E51.9

        Thiamine deficiency, unspecified

          2016 2017 2018 2019 Billable/Specific Code
    • zinc, dietary E60
      ICD-10-CM Diagnosis Code E60

      Dietary zinc deficiency

        2016 2017 2018 2019 Billable/Specific Code