1. 2023 ICD-10-CM Index
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2. 'D' Terms
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3. Index Terms Starting With 'D' (Deficiency, deficient)

Index Terms Starting With 'D' (Deficiency, deficient)

• Deficiency, deficient

  • 11-hydroxylase E25.0
    ICD-10-CM Diagnosis Code E25.0

    Congenital adrenogenital disorders associated with enzyme deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Congenital adrenal hyperplasia
    • 21-Hydroxylase deficiency
    • Salt-losing congenital adrenal hyperplasia
  • 21-hydroxylase E25.0
    ICD-10-CM Diagnosis Code E25.0

    Congenital adrenogenital disorders associated with enzyme deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Congenital adrenal hyperplasia
    • 21-Hydroxylase deficiency
    • Salt-losing congenital adrenal hyperplasia
  • 3-beta hydroxysteroid dehydrogenase E25.0
    ICD-10-CM Diagnosis Code E25.0

    Congenital adrenogenital disorders associated with enzyme deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Congenital adrenal hyperplasia
    • 21-Hydroxylase deficiency
    • Salt-losing congenital adrenal hyperplasia
  • 5-alpha reductase E29.1
    (with male pseudohermaphroditism)
    ICD-10-CM Diagnosis Code E29.1

    Testicular hypofunction

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx

    Applicable To

    • Defective biosynthesis of testicular androgen NOS
    • 5-delta-Reductase deficiency (with male pseudohermaphroditism)
    • Testicular hypogonadism NOS

    Type 1 Excludes

    • postprocedural testicular hypofunction (E89.5)

    Use Additional

    • code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
  • AADC E70.81
    (aromatic L-amino acid decarboxylase)
    ICD-10-CM Diagnosis Code E70.81

    Aromatic L-amino acid decarboxylase deficiency

    2021 - New Code 2022 2023 Billable/Specific Code

    Applicable To

    • AADC deficiency
  • abdominal muscle syndrome Q79.4
    ICD-10-CM Diagnosis Code Q79.4

    Prune belly syndrome

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital prolapse of bladder mucosa
    • Eagle-Barrett syndrome
  • AC globulin (congenital) (hereditary) D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
    • acquired D68.4
      ICD-10-CM Diagnosis Code D68.4

      Acquired coagulation factor deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Deficiency of coagulation factor due to liver disease
      • Deficiency of coagulation factor due to vitamin K deficiency

      Type 1 Excludes

      • vitamin K deficiency of newborn (P53)
  • accelerator globulin D68.2
    (Ac G) (blood)
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
  • acid phosphatase E83.39
    ICD-10-CM Diagnosis Code E83.39

    Other disorders of phosphorus metabolism

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Acid phosphatase deficiency
    • Hypophosphatasia
  • acid sphingomyelinase (ASMD) E75.249
    ICD-10-CM Diagnosis Code E75.249

    Niemann-Pick disease, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Acid sphingomyelinase deficiency (ASMD) NOS
    • type
      • A E75.240
        ICD-10-CM Diagnosis Code E75.240

        Niemann-Pick disease type A

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Acid sphingomyelinase deficiency type A (ASMD type A)
        • Infantile neurovisceral acid sphingomyelinase deficiency
      • A/B E75.244
        ICD-10-CM Diagnosis Code E75.244

        Niemann-Pick disease type A/B

        2022 - New Code 2023 Billable/Specific Code

        Applicable To

        • Acid sphingomyelinase deficiency type A/B (ASMD type A/B)
        • Chronic neurovisceral acid sphingomyelinase deficiency
      • B E75.241
        ICD-10-CM Diagnosis Code E75.241

        Niemann-Pick disease type B

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Acid sphingomyelinase deficiency type B (ASMD type B)
        • Chronic visceral acid sphingomyelinase deficiency
  • activating factor D68.2
    (blood)
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
  • ADA2 D81.32
    (adenosine deaminase 2)
    ICD-10-CM Diagnosis Code D81.32

    Adenosine deaminase 2 deficiency

    2020 - New Code 2021 2022 2023 Billable/Specific Code

    Applicable To

    • ADA2 deficiency
    • Adenosine deaminase deficiency type 2

    Code Also

    • , if applicable, any associated manifestations, such as:
    • polyarteritis nodosa (M30.0)
    • stroke (I63.-)
  • adenosine deaminase (ADA) D81.30
    ICD-10-CM Diagnosis Code D81.30

    Adenosine deaminase deficiency, unspecified

    2020 - New Code 2021 2022 2023 Billable/Specific Code

    Applicable To

    • ADA deficiency NOS
    • partial D81.39
      (type 1)
      ICD-10-CM Diagnosis Code D81.39

      Other adenosine deaminase deficiency

      2020 - New Code 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Adenosine deaminase [ADA] deficiency type 1, NOS
      • Adenosine deaminase [ADA] deficiency type 1, without SCID
      • Adenosine deaminase [ADA] deficiency type 1, without severe combined immunodeficiency
      • Partial ADA deficiency (type 1)
      • Partial adenosine deaminase deficiency (type 1)
    • specified NEC D81.39
      ICD-10-CM Diagnosis Code D81.39

      Other adenosine deaminase deficiency

      2020 - New Code 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Adenosine deaminase [ADA] deficiency type 1, NOS
      • Adenosine deaminase [ADA] deficiency type 1, without SCID
      • Adenosine deaminase [ADA] deficiency type 1, without severe combined immunodeficiency
      • Partial ADA deficiency (type 1)
      • Partial adenosine deaminase deficiency (type 1)
    • type 1 D81.39
      (without SCID) (without severe combined immunodeficiency)
      ICD-10-CM Diagnosis Code D81.39

      Other adenosine deaminase deficiency

      2020 - New Code 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Adenosine deaminase [ADA] deficiency type 1, NOS
      • Adenosine deaminase [ADA] deficiency type 1, without SCID
      • Adenosine deaminase [ADA] deficiency type 1, without severe combined immunodeficiency
      • Partial ADA deficiency (type 1)
      • Partial adenosine deaminase deficiency (type 1)
    • type 2 D81.32
      ICD-10-CM Diagnosis Code D81.32

      Adenosine deaminase 2 deficiency

      2020 - New Code 2021 2022 2023 Billable/Specific Code

      Applicable To

      • ADA2 deficiency
      • Adenosine deaminase deficiency type 2

      Code Also

      • , if applicable, any associated manifestations, such as:
      • polyarteritis nodosa (M30.0)
      • stroke (I63.-)
    • with severe combined immunodeficiency D81.31
      (SCID)
      ICD-10-CM Diagnosis Code D81.31

      Severe combined immunodeficiency due to adenosine deaminase deficiency

      2020 - New Code 2021 2022 2023 Billable/Specific Code

      Applicable To

      • ADA deficiency with SCID
      • Adenosine deaminase [ADA] deficiency with severe combined immunodeficiency
  • aldolase E74.19
    (hereditary)
    ICD-10-CM Diagnosis Code E74.19

    Other disorders of fructose metabolism

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Fructose-1, 6-diphosphatase deficiency
  • alpha-1-antitrypsin E88.01
    ICD-10-CM Diagnosis Code E88.01

    Alpha-1-antitrypsin deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AAT deficiency
  • amino-acids E72.9
    ICD-10-CM Diagnosis Code E72.9

    Disorder of amino-acid metabolism, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • anemia - see Anemia
  • aneurin E51.9
    ICD-10-CM Diagnosis Code E51.9

    Thiamine deficiency, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • anti-hemophilic
    • factor (A) D66
      ICD-10-CM Diagnosis Code D66

      Hereditary factor VIII deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Classical hemophilia
      • Deficiency factor VIII (with functional defect)
      • Hemophilia NOS
      • Hemophilia A

      Type 1 Excludes

      • factor VIII deficiency with vascular defect (D68.0-)
      • B D67
        ICD-10-CM Diagnosis Code D67

        Hereditary factor IX deficiency

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Christmas disease
        • Factor IX deficiency (with functional defect)
        • Hemophilia B
        • Plasma thromboplastin component [PTC] deficiency
      • C D68.1
        ICD-10-CM Diagnosis Code D68.1

        Hereditary factor XI deficiency

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Hemophilia C
        • Plasma thromboplastin antecedent [PTA] deficiency
        • Rosenthal's disease
    • globulin D66
      (AHG)
      ICD-10-CM Diagnosis Code D66

      Hereditary factor VIII deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Classical hemophilia
      • Deficiency factor VIII (with functional defect)
      • Hemophilia NOS
      • Hemophilia A

      Type 1 Excludes

      • factor VIII deficiency with vascular defect (D68.0-)
  • antibody with
    • hyperimmunoglobulinemia D80.6
      ICD-10-CM Diagnosis Code D80.6

      Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • near-normal immunoglobins D80.6
      ICD-10-CM Diagnosis Code D80.6

      Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • antidiuretic hormone E23.2
    ICD-10-CM Diagnosis Code E23.2

    Diabetes insipidus

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Type 1 Excludes

    • nephrogenic diabetes insipidus (N25.1)
  • antithrombin D68.59
    (antithrombin III)
    ICD-10-CM Diagnosis Code D68.59

    Other primary thrombophilia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Antithrombin III deficiency
    • Hypercoagulable state NOS
    • Primary hypercoagulable state NEC
    • Primary thrombophilia NEC
    • Protein C deficiency
    • Protein S deficiency
    • Thrombophilia NOS
  • aromatic L-amino acid decarboxylase E70.81
    (AADC)
    ICD-10-CM Diagnosis Code E70.81

    Aromatic L-amino acid decarboxylase deficiency

    2021 - New Code 2022 2023 Billable/Specific Code

    Applicable To

    • AADC deficiency
  • ascorbic acid E54
    ICD-10-CM Diagnosis Code E54

    Ascorbic acid deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Deficiency of vitamin C
    • Scurvy

    Type 1 Excludes

    • scorbutic anemia (D53.2)
    • sequelae of vitamin C deficiency (E64.2)
  • attention (disorder) (syndrome) F98.8
    ICD-10-CM Diagnosis Code F98.8

    Other specified behavioral and emotional disorders with onset usually occurring in childhood and adolescence

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Excessive masturbation
    • Nail-biting
    • Nose-picking
    • Thumb-sucking
    • with hyperactivity - see Disorder, attention-deficit hyperactivity
  • autoprothrombin
    • C D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • I D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • II D67
      ICD-10-CM Diagnosis Code D67

      Hereditary factor IX deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Christmas disease
      • Factor IX deficiency (with functional defect)
      • Hemophilia B
      • Plasma thromboplastin component [PTC] deficiency
  • beta-glucuronidase E76.29
    ICD-10-CM Diagnosis Code E76.29

    Other mucopolysaccharidoses

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • beta-Glucuronidase deficiency
    • Maroteaux-Lamy (mild) (severe) syndrome
    • Mucopolysaccharidosis, types VI, VII
  • biotin E53.8
    ICD-10-CM Diagnosis Code E53.8

    Deficiency of other specified B group vitamins

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Biotin deficiency
    • Cyanocobalamin deficiency
    • Folate deficiency
    • Folic acid deficiency
    • Pantothenic acid deficiency
    • Vitamin B12 deficiency

    Type 1 Excludes

    • folate deficiency anemia (D52.-)
    • vitamin B12 deficiency anemia (D51.-)
  • biotin-dependent carboxylase D81.819
    ICD-10-CM Diagnosis Code D81.819

    Biotin-dependent carboxylase deficiency, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Multiple carboxylase deficiency, unspecified
  • biotinidase D81.810
    ICD-10-CM Diagnosis Code D81.810

    Biotinidase deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • brancher enzyme E74.03
    (amylopectinosis)
    ICD-10-CM Diagnosis Code E74.03

    Cori disease

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Forbes disease
    • Type III glycogen storage disease
  • C1 esterase inhibitor D84.1
    (C1-INH)
    ICD-10-CM Diagnosis Code D84.1

    Defects in the complement system

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • C1 esterase inhibitor [C1-INH] deficiency
  • calciferol E55.9
    ICD-10-CM Diagnosis Code E55.9

    Vitamin D deficiency, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Avitaminosis D
    • with
      • adult osteomalacia M83.8
        ICD-10-CM Diagnosis Code M83.8

        Other adult osteomalacia

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Adult Dx (15-124 years)
      • rickets - see Rickets
  • calcium E58
    (dietary)
    ICD-10-CM Diagnosis Code E58

    Dietary calcium deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Type 1 Excludes

    • disorders of calcium metabolism (E83.5-)
    • sequelae of calcium deficiency (E64.8)
  • calorie, severe E43
    ICD-10-CM Diagnosis Code E43

    Unspecified severe protein-calorie malnutrition

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Starvation edema
    • with marasmus E41
      ICD-10-CM Diagnosis Code E41

      Nutritional marasmus

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Severe malnutrition with marasmus

      Type 1 Excludes

      • marasmic kwashiorkor (E42)
      • and kwashiorkor E42
        ICD-10-CM Diagnosis Code E42

        Marasmic kwashiorkor

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Intermediate form severe protein-calorie malnutrition
        • Severe protein-calorie malnutrition with signs of both kwashiorkor and marasmus
  • cardiac - see Insufficiency, myocardial
  • carnitine E71.40
    ICD-10-CM Diagnosis Code E71.40

    Disorder of carnitine metabolism, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • due to
      • hemodialysis E71.43
        ICD-10-CM Diagnosis Code E71.43

        Iatrogenic carnitine deficiency

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Carnitine deficiency due to hemodialysis
        • Carnitine deficiency due to Valproic acid therapy
      • inborn errors of metabolism E71.42
        ICD-10-CM Diagnosis Code E71.42

        Carnitine deficiency due to inborn errors of metabolism

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Code Also

        • associated inborn error or metabolism
      • Valproic acid therapy E71.43
        ICD-10-CM Diagnosis Code E71.43

        Iatrogenic carnitine deficiency

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Carnitine deficiency due to hemodialysis
        • Carnitine deficiency due to Valproic acid therapy
    • iatrogenic E71.43
      ICD-10-CM Diagnosis Code E71.43

      Iatrogenic carnitine deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Carnitine deficiency due to hemodialysis
      • Carnitine deficiency due to Valproic acid therapy
    • muscle palmityltransferase E71.314
      ICD-10-CM Diagnosis Code E71.314

      Muscle carnitine palmitoyltransferase deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • primary E71.41
      ICD-10-CM Diagnosis Code E71.41

      Primary carnitine deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • secondary E71.448
      ICD-10-CM Diagnosis Code E71.448

      Other secondary carnitine deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • carotene E50.9
    ICD-10-CM Diagnosis Code E50.9

    Vitamin A deficiency, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Hypovitaminosis A NOS
  • central nervous system G96.89
    ICD-10-CM Diagnosis Code G96.89

    Other specified disorders of central nervous system

    2021 - New Code 2022 2023 Billable/Specific Code
  • ceruloplasmin E83.01
    (Wilson)
    ICD-10-CM Diagnosis Code E83.01

    Wilson's disease

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Code Also

    • associated Kayser Fleischer ring (H18.04-)
  • choline E53.8
    ICD-10-CM Diagnosis Code E53.8

    Deficiency of other specified B group vitamins

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Biotin deficiency
    • Cyanocobalamin deficiency
    • Folate deficiency
    • Folic acid deficiency
    • Pantothenic acid deficiency
    • Vitamin B12 deficiency

    Type 1 Excludes

    • folate deficiency anemia (D52.-)
    • vitamin B12 deficiency anemia (D51.-)
  • Christmas factor D67
    ICD-10-CM Diagnosis Code D67

    Hereditary factor IX deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Christmas disease
    • Factor IX deficiency (with functional defect)
    • Hemophilia B
    • Plasma thromboplastin component [PTC] deficiency
  • chromium E61.4
    ICD-10-CM Diagnosis Code E61.4

    Chromium deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • chronic neurovisceral acid sphingomyelinase E75.244
    ICD-10-CM Diagnosis Code E75.244

    Niemann-Pick disease type A/B

    2022 - New Code 2023 Billable/Specific Code

    Applicable To

    • Acid sphingomyelinase deficiency type A/B (ASMD type A/B)
    • Chronic neurovisceral acid sphingomyelinase deficiency
  • chronic visceral acid sphingomyelinase E75.241
    ICD-10-CM Diagnosis Code E75.241

    Niemann-Pick disease type B

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Acid sphingomyelinase deficiency type B (ASMD type B)
    • Chronic visceral acid sphingomyelinase deficiency
  • clotting D68.9
    (blood) - see also Deficiency, coagulation factor
    ICD-10-CM Diagnosis Code D68.9

    Coagulation defect, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • clotting factor NEC D68.2
    (hereditary) - see also Deficiency, factor
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
  • coagulation NOS D68.9
    ICD-10-CM Diagnosis Code D68.9

    Coagulation defect, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • acquired D68.4
      (any)
      ICD-10-CM Diagnosis Code D68.4

      Acquired coagulation factor deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Deficiency of coagulation factor due to liver disease
      • Deficiency of coagulation factor due to vitamin K deficiency

      Type 1 Excludes

      • vitamin K deficiency of newborn (P53)
    • antepartum hemorrhage - see Hemorrhage, antepartum, with coagulation defect
    • clotting factor NEC D68.2
      - see also Deficiency, factor
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • due to
      • hyperprothrombinemia D68.4
        ICD-10-CM Diagnosis Code D68.4

        Acquired coagulation factor deficiency

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Deficiency of coagulation factor due to liver disease
        • Deficiency of coagulation factor due to vitamin K deficiency

        Type 1 Excludes

        • vitamin K deficiency of newborn (P53)
      • liver disease D68.4
        ICD-10-CM Diagnosis Code D68.4

        Acquired coagulation factor deficiency

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Deficiency of coagulation factor due to liver disease
        • Deficiency of coagulation factor due to vitamin K deficiency

        Type 1 Excludes

        • vitamin K deficiency of newborn (P53)
      • vitamin K deficiency D68.4
        ICD-10-CM Diagnosis Code D68.4

        Acquired coagulation factor deficiency

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Deficiency of coagulation factor due to liver disease
        • Deficiency of coagulation factor due to vitamin K deficiency

        Type 1 Excludes

        • vitamin K deficiency of newborn (P53)
    • newborn, transient P61.6
      ICD-10-CM Diagnosis Code P61.6

      Other transient neonatal disorders of coagulation

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Code on Newborn Record
    • postpartum O72.3
      ICD-10-CM Diagnosis Code O72.3

      Postpartum coagulation defects

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Maternity Dx (12-55 years) Female Dx

      Applicable To

      • Postpartum afibrinogenemia
      • Postpartum fibrinolysis
    • specified NEC D68.8
      ICD-10-CM Diagnosis Code D68.8

      Other specified coagulation defects

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Type 1 Excludes

      • hemorrhagic disease of newborn (P53)
    • with
      • ectopic pregnancy O08.1
        ICD-10-CM Diagnosis Code O08.1

        Delayed or excessive hemorrhage following ectopic and molar pregnancy

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Maternity Dx (12-55 years) Female Dx

        Applicable To

        • Afibrinogenemia following ectopic and molar pregnancy
        • Defibrination syndrome following ectopic and molar pregnancy
        • Hemolysis following ectopic and molar pregnancy
        • Intravascular coagulation following ectopic and molar pregnancy

        Type 1 Excludes

        • delayed or excessive hemorrhage due to incomplete abortion (O03.1)
      • molar pregnancy O08.1
        ICD-10-CM Diagnosis Code O08.1

        Delayed or excessive hemorrhage following ectopic and molar pregnancy

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Maternity Dx (12-55 years) Female Dx

        Applicable To

        • Afibrinogenemia following ectopic and molar pregnancy
        • Defibrination syndrome following ectopic and molar pregnancy
        • Hemolysis following ectopic and molar pregnancy
        • Intravascular coagulation following ectopic and molar pregnancy

        Type 1 Excludes

        • delayed or excessive hemorrhage due to incomplete abortion (O03.1)
  • cognitive F09
    ICD-10-CM Diagnosis Code F09

    Unspecified mental disorder due to known physiological condition

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Mental disorder NOS due to known physiological condition
    • Organic brain syndrome NOS
    • Organic mental disorder NOS
    • Organic psychosis NOS
    • Symptomatic psychosis NOS

    Code First

    • the underlying physiological condition

    Type 1 Excludes

    • mild neurocognitive disorder due to known physiological condition (F06.7-)
    • psychosis NOS (F29)
  • color vision H53.50
    ICD-10-CM Diagnosis Code H53.50

    Unspecified color vision deficiencies

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Color blindness NOS
    • achromatopsia H53.51
      ICD-10-CM Diagnosis Code H53.51

      Achromatopsia

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • acquired H53.52
      ICD-10-CM Diagnosis Code H53.52

      Acquired color vision deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • deuteranomaly H53.53
      ICD-10-CM Diagnosis Code H53.53

      Deuteranomaly

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Deuteranopia
    • protanomaly H53.54
      ICD-10-CM Diagnosis Code H53.54

      Protanomaly

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Protanopia
    • specified type NEC H53.59
      ICD-10-CM Diagnosis Code H53.59

      Other color vision deficiencies

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • tritanomaly H53.55
      ICD-10-CM Diagnosis Code H53.55

      Tritanomaly

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Tritanopia
  • combined glucocorticoid and mineralocorticoid E27.49
    ICD-10-CM Diagnosis Code E27.49

    Other adrenocortical insufficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Adrenal hemorrhage
    • Adrenal infarction
  • contact factor D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
  • copper E61.0
    (nutritional)
    ICD-10-CM Diagnosis Code E61.0

    Copper deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • corticoadrenal E27.40
    ICD-10-CM Diagnosis Code E27.40

    Unspecified adrenocortical insufficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Adrenocortical insufficiency NOS
    • Hypoaldosteronism
    • primary E27.1
      ICD-10-CM Diagnosis Code E27.1

      Primary adrenocortical insufficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Addison's disease
      • Autoimmune adrenalitis

      Type 1 Excludes

      • Addison only phenotype adrenoleukodystrophy (E71.528)
      • amyloidosis (E85.-)
      • tuberculous Addison's disease (A18.7)
      • Waterhouse-Friderichsen syndrome (A39.1)
  • craniofacial axis Q75.0
    ICD-10-CM Diagnosis Code Q75.0

    Craniosynostosis

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Acrocephaly
    • Imperfect fusion of skull
    • Oxycephaly
    • Trigonocephaly
  • cyanocobalamin E53.8
    ICD-10-CM Diagnosis Code E53.8

    Deficiency of other specified B group vitamins

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Biotin deficiency
    • Cyanocobalamin deficiency
    • Folate deficiency
    • Folic acid deficiency
    • Pantothenic acid deficiency
    • Vitamin B12 deficiency

    Type 1 Excludes

    • folate deficiency anemia (D52.-)
    • vitamin B12 deficiency anemia (D51.-)
  • debrancher enzyme E74.03
    (limit dextrinosis)
    ICD-10-CM Diagnosis Code E74.03

    Cori disease

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Forbes disease
    • Type III glycogen storage disease
  • dehydrogenase
    • long chain/very long chain acyl CoA E71.310
      ICD-10-CM Diagnosis Code E71.310

      Long chain/very long chain acyl CoA dehydrogenase deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • LCAD
      • VLCAD
    • medium chain acyl CoA E71.311
      ICD-10-CM Diagnosis Code E71.311

      Medium chain acyl CoA dehydrogenase deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • MCAD
    • short chain acyl CoA E71.312
      ICD-10-CM Diagnosis Code E71.312

      Short chain acyl CoA dehydrogenase deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • SCAD
  • diet E63.9
    ICD-10-CM Diagnosis Code E63.9

    Nutritional deficiency, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • dihydropyrimidine dehydrogenase E88.89
    (DPD)
    ICD-10-CM Diagnosis Code E88.89

    Other specified metabolic disorders

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Launois-Bensaude adenolipomatosis

    Type 1 Excludes

    • adult pulmonary Langerhans cell histiocytosis (J84.82)
  • disaccharidase E73.9
    ICD-10-CM Diagnosis Code E73.9

    Lactose intolerance, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • edema - see Malnutrition, severe
  • endocrine E34.9
    ICD-10-CM Diagnosis Code E34.9

    Endocrine disorder, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Endocrine disturbance NOS
    • Hormone disturbance NOS
  • energy-supply - see Malnutrition
  • enzymes, circulating NEC E88.09
    ICD-10-CM Diagnosis Code E88.09

    Other disorders of plasma-protein metabolism, not elsewhere classified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Bisalbuminemia
  • ergosterol E55.9
    ICD-10-CM Diagnosis Code E55.9

    Vitamin D deficiency, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Avitaminosis D
    • with
      • adult osteomalacia M83.8
        ICD-10-CM Diagnosis Code M83.8

        Other adult osteomalacia

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Adult Dx (15-124 years)
      • rickets - see Rickets
  • essential fatty acid E63.0
    (EFA)
    ICD-10-CM Diagnosis Code E63.0

    Essential fatty acid [EFA] deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • eye movements
    • saccadic H55.81
      ICD-10-CM Diagnosis Code H55.81

      Deficient saccadic eye movements

      2016 2017 2018 2019 2020 2021 - Revised Code 2022 2023 Billable/Specific Code
    • smooth pursuit H55.82
      ICD-10-CM Diagnosis Code H55.82

      Deficient smooth pursuit eye movements

      2021 - New Code 2022 2023 Billable/Specific Code
  • factor - see also Deficiency, coagulation
    • Hageman D68.2
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • I D68.2
      (congenital) (hereditary)
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • II D68.2
      (congenital) (hereditary)
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • IX D67
      (congenital) (functional) (hereditary) (with functional defect)
      ICD-10-CM Diagnosis Code D67

      Hereditary factor IX deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Christmas disease
      • Factor IX deficiency (with functional defect)
      • Hemophilia B
      • Plasma thromboplastin component [PTC] deficiency
    • multiple (congenital) D68.8
      ICD-10-CM Diagnosis Code D68.8

      Other specified coagulation defects

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Type 1 Excludes

      • hemorrhagic disease of newborn (P53)
      • acquired D68.4
        ICD-10-CM Diagnosis Code D68.4

        Acquired coagulation factor deficiency

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Deficiency of coagulation factor due to liver disease
        • Deficiency of coagulation factor due to vitamin K deficiency

        Type 1 Excludes

        • vitamin K deficiency of newborn (P53)
    • V D68.2
      (congenital) (hereditary)
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • VII D68.2
      (congenital) (hereditary)
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • VIII (congenital) (functional) (hereditary) (with functional defect) D66
      ICD-10-CM Diagnosis Code D66

      Hereditary factor VIII deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Classical hemophilia
      • Deficiency factor VIII (with functional defect)
      • Hemophilia NOS
      • Hemophilia A

      Type 1 Excludes

      • factor VIII deficiency with vascular defect (D68.0-)
      • with vascular defect - see Disease, von Willebrand
    • X D68.2
      (congenital) (hereditary)
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • XI D68.1
      (congenital) (hereditary)
      ICD-10-CM Diagnosis Code D68.1

      Hereditary factor XI deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Hemophilia C
      • Plasma thromboplastin antecedent [PTA] deficiency
      • Rosenthal's disease
    • XII D68.2
      (congenital) (hereditary)
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
    • XIII D68.2
      (congenital) (hereditary)
      ICD-10-CM Diagnosis Code D68.2

      Hereditary deficiency of other clotting factors

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • AC globulin deficiency
      • Congenital afibrinogenemia
      • Deficiency of factor I [fibrinogen]
      • Deficiency of factor II [prothrombin]
      • Deficiency of factor V [labile]
      • Deficiency of factor VII [stable]
      • Deficiency of factor X [Stuart-Prower]
      • Deficiency of factor XII [Hageman]
      • Deficiency of factor XIII [fibrin stabilizing]
      • Dysfibrinogenemia (congenital)
      • Hypoproconvertinemia
      • Owren's disease
      • Proaccelerin deficiency
  • femoral, proximal focal (congenital) - see Defect, reduction, lower limb, longitudinal, femur
  • fibrin-stabilizing factor (congenital) (hereditary) D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
    • acquired D68.4
      ICD-10-CM Diagnosis Code D68.4

      Acquired coagulation factor deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Deficiency of coagulation factor due to liver disease
      • Deficiency of coagulation factor due to vitamin K deficiency

      Type 1 Excludes

      • vitamin K deficiency of newborn (P53)
  • fibrinase D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
  • fibrinogen (congenital) (hereditary) D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
    • acquired D65
      ICD-10-CM Diagnosis Code D65

      Disseminated intravascular coagulation [defibrination syndrome]

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Afibrinogenemia, acquired
      • Consumption coagulopathy
      • Diffuse or disseminated intravascular coagulation [DIC]
      • Fibrinolytic hemorrhage, acquired
      • Fibrinolytic purpura
      • Purpura fulminans

      Type 1 Excludes

      • disseminated intravascular coagulation (complicating):
      • abortion or ectopic or molar pregnancy (O00-O07, O08.1)
      • in newborn (P60)
      • pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
  • folate E53.8
    ICD-10-CM Diagnosis Code E53.8

    Deficiency of other specified B group vitamins

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Biotin deficiency
    • Cyanocobalamin deficiency
    • Folate deficiency
    • Folic acid deficiency
    • Pantothenic acid deficiency
    • Vitamin B12 deficiency

    Type 1 Excludes

    • folate deficiency anemia (D52.-)
    • vitamin B12 deficiency anemia (D51.-)
  • folic acid E53.8
    ICD-10-CM Diagnosis Code E53.8

    Deficiency of other specified B group vitamins

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Biotin deficiency
    • Cyanocobalamin deficiency
    • Folate deficiency
    • Folic acid deficiency
    • Pantothenic acid deficiency
    • Vitamin B12 deficiency

    Type 1 Excludes

    • folate deficiency anemia (D52.-)
    • vitamin B12 deficiency anemia (D51.-)
  • foreskin N47.3
    ICD-10-CM Diagnosis Code N47.3

    Deficient foreskin

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx
  • fructokinase E74.11
    ICD-10-CM Diagnosis Code E74.11

    Essential fructosuria

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Fructokinase deficiency
  • fructose 1,6-diphosphatase E74.19
    ICD-10-CM Diagnosis Code E74.19

    Other disorders of fructose metabolism

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Fructose-1, 6-diphosphatase deficiency
  • fructose-1-phosphate aldolase E74.19
    ICD-10-CM Diagnosis Code E74.19

    Other disorders of fructose metabolism

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Fructose-1, 6-diphosphatase deficiency
  • GABA E72.81
    (gamma aminobutyric acid)
    ICD-10-CM Diagnosis Code E72.81

    Disorders of gamma aminobutyric acid metabolism

    2019 - New Code 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • 4-hydroxybutyric aciduria
    • Disorders of GABA metabolism
    • GABA metabolic defect
    • GABA transaminase deficiency
    • GABA-T deficiency
    • Gamma-hydroxybutyric aciduria
    • SSADHD
    • Succinic semialdehyde dehydrogenase deficiency
  • GABA-T E72.81
    (gamma aminobutyric acid transaminase)
    ICD-10-CM Diagnosis Code E72.81

    Disorders of gamma aminobutyric acid metabolism

    2019 - New Code 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • 4-hydroxybutyric aciduria
    • Disorders of GABA metabolism
    • GABA metabolic defect
    • GABA transaminase deficiency
    • GABA-T deficiency
    • Gamma-hydroxybutyric aciduria
    • SSADHD
    • Succinic semialdehyde dehydrogenase deficiency
  • galactokinase E74.29
    ICD-10-CM Diagnosis Code E74.29

    Other disorders of galactose metabolism

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Galactokinase deficiency
  • galactose-1-phosphate uridyl transferase E74.29
    ICD-10-CM Diagnosis Code E74.29

    Other disorders of galactose metabolism

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Galactokinase deficiency
  • gammaglobulin in blood D80.1
    ICD-10-CM Diagnosis Code D80.1

    Nonfamilial hypogammaglobulinemia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Agammaglobulinemia with immunoglobulin-bearing B-lymphocytes
    • Common variable agammaglobulinemia [CVAgamma]
    • Hypogammaglobulinemia NOS
    • hereditary D80.0
      ICD-10-CM Diagnosis Code D80.0

      Hereditary hypogammaglobulinemia

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Autosomal recessive agammaglobulinemia (Swiss type)
      • X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency)
  • glass factor D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
  • glucocorticoid E27.49
    ICD-10-CM Diagnosis Code E27.49

    Other adrenocortical insufficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Adrenal hemorrhage
    • Adrenal infarction
    • mineralocorticoid E27.49
      ICD-10-CM Diagnosis Code E27.49

      Other adrenocortical insufficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Adrenal hemorrhage
      • Adrenal infarction
  • glucose transporter protein type 1 E74.810
    ICD-10-CM Diagnosis Code E74.810

    Glucose transporter protein type 1 deficiency

    2021 - New Code 2022 2023 Billable/Specific Code

    Applicable To

    • De Vivo syndrome
    • Glucose transport defect, blood-brain barrier
    • Glut1 deficiency
    • GLUT1 deficiency syndrome 1, infantile onset
    • GLUT1 deficiency syndrome 2, childhood onset
  • glucose-6-phosphatase E74.01
    ICD-10-CM Diagnosis Code E74.01

    von Gierke disease

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Type I glycogen storage disease
  • glucose-6-phosphate dehydrogenase
    • anemia D55.0
      ICD-10-CM Diagnosis Code D55.0

      Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Favism
      • G6PD deficiency anemia

      Type 1 Excludes

      • glucose-6-phosphate dehydrogenase (G6PD) deficiency without anemia (D75.A)
    • without anemia D75.A
      ICD-10-CM Diagnosis Code D75.A

      Glucose-6-phosphate dehydrogenase (G6PD) deficiency without anemia

      2020 - New Code 2021 2022 2023 Billable/Specific Code

      Type 1 Excludes

      • glucose-6-phosphate dehydrogenase (G6PD) deficiency with anemia (D55.0)
  • glucuronyl transferase E80.5
    ICD-10-CM Diagnosis Code E80.5

    Crigler-Najjar syndrome

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • Glut1 E74.810
    ICD-10-CM Diagnosis Code E74.810

    Glucose transporter protein type 1 deficiency

    2021 - New Code 2022 2023 Billable/Specific Code

    Applicable To

    • De Vivo syndrome
    • Glucose transport defect, blood-brain barrier
    • Glut1 deficiency
    • GLUT1 deficiency syndrome 1, infantile onset
    • GLUT1 deficiency syndrome 2, childhood onset
  • glycogen synthetase E74.09
    ICD-10-CM Diagnosis Code E74.09

    Other glycogen storage disease

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Andersen disease
    • Hers disease
    • Tauri disease
    • Glycogen storage disease, types 0, IV, VI-XI
    • Liver phosphorylase deficiency
    • Muscle phosphofructokinase deficiency
  • gonadotropin E23.0
    (isolated)
    ICD-10-CM Diagnosis Code E23.0

    Hypopituitarism

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Fertile eunuch syndrome
    • Hypogonadotropic hypogonadism
    • Idiopathic growth hormone deficiency
    • Isolated deficiency of gonadotropin
    • Isolated deficiency of growth hormone
    • Isolated deficiency of pituitary hormone
    • Kallmann's syndrome
    • Lorain-Levi short stature
    • Necrosis of pituitary gland (postpartum)
    • Panhypopituitarism
    • Pituitary cachexia
    • Pituitary insufficiency NOS
    • Pituitary short stature
    • Sheehan's syndrome
    • Simmonds' disease
  • growth hormone E23.0
    (idiopathic) (isolated)
    ICD-10-CM Diagnosis Code E23.0

    Hypopituitarism

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Fertile eunuch syndrome
    • Hypogonadotropic hypogonadism
    • Idiopathic growth hormone deficiency
    • Isolated deficiency of gonadotropin
    • Isolated deficiency of growth hormone
    • Isolated deficiency of pituitary hormone
    • Kallmann's syndrome
    • Lorain-Levi short stature
    • Necrosis of pituitary gland (postpartum)
    • Panhypopituitarism
    • Pituitary cachexia
    • Pituitary insufficiency NOS
    • Pituitary short stature
    • Sheehan's syndrome
    • Simmonds' disease
  • Hageman factor D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
  • hemoglobin D64.9
    ICD-10-CM Diagnosis Code D64.9

    Anemia, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • hepatophosphorylase E74.09
    ICD-10-CM Diagnosis Code E74.09

    Other glycogen storage disease

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Andersen disease
    • Hers disease
    • Tauri disease
    • Glycogen storage disease, types 0, IV, VI-XI
    • Liver phosphorylase deficiency
    • Muscle phosphofructokinase deficiency
  • homogentisate 1,2-dioxygenase E70.29
    ICD-10-CM Diagnosis Code E70.29

    Other disorders of tyrosine metabolism

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Alkaptonuria
    • Ochronosis
  • hormone
    • anterior pituitary (partial) E23.0
      ICD-10-CM Diagnosis Code E23.0

      Hypopituitarism

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Fertile eunuch syndrome
      • Hypogonadotropic hypogonadism
      • Idiopathic growth hormone deficiency
      • Isolated deficiency of gonadotropin
      • Isolated deficiency of growth hormone
      • Isolated deficiency of pituitary hormone
      • Kallmann's syndrome
      • Lorain-Levi short stature
      • Necrosis of pituitary gland (postpartum)
      • Panhypopituitarism
      • Pituitary cachexia
      • Pituitary insufficiency NOS
      • Pituitary short stature
      • Sheehan's syndrome
      • Simmonds' disease
      • growth E23.0
        ICD-10-CM Diagnosis Code E23.0

        Hypopituitarism

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Fertile eunuch syndrome
        • Hypogonadotropic hypogonadism
        • Idiopathic growth hormone deficiency
        • Isolated deficiency of gonadotropin
        • Isolated deficiency of growth hormone
        • Isolated deficiency of pituitary hormone
        • Kallmann's syndrome
        • Lorain-Levi short stature
        • Necrosis of pituitary gland (postpartum)
        • Panhypopituitarism
        • Pituitary cachexia
        • Pituitary insufficiency NOS
        • Pituitary short stature
        • Sheehan's syndrome
        • Simmonds' disease
    • growth E23.0
      (isolated)
      ICD-10-CM Diagnosis Code E23.0

      Hypopituitarism

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Fertile eunuch syndrome
      • Hypogonadotropic hypogonadism
      • Idiopathic growth hormone deficiency
      • Isolated deficiency of gonadotropin
      • Isolated deficiency of growth hormone
      • Isolated deficiency of pituitary hormone
      • Kallmann's syndrome
      • Lorain-Levi short stature
      • Necrosis of pituitary gland (postpartum)
      • Panhypopituitarism
      • Pituitary cachexia
      • Pituitary insufficiency NOS
      • Pituitary short stature
      • Sheehan's syndrome
      • Simmonds' disease
    • pituitary E23.0
      ICD-10-CM Diagnosis Code E23.0

      Hypopituitarism

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Fertile eunuch syndrome
      • Hypogonadotropic hypogonadism
      • Idiopathic growth hormone deficiency
      • Isolated deficiency of gonadotropin
      • Isolated deficiency of growth hormone
      • Isolated deficiency of pituitary hormone
      • Kallmann's syndrome
      • Lorain-Levi short stature
      • Necrosis of pituitary gland (postpartum)
      • Panhypopituitarism
      • Pituitary cachexia
      • Pituitary insufficiency NOS
      • Pituitary short stature
      • Sheehan's syndrome
      • Simmonds' disease
    • testicular E29.1
      ICD-10-CM Diagnosis Code E29.1

      Testicular hypofunction

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx

      Applicable To

      • Defective biosynthesis of testicular androgen NOS
      • 5-delta-Reductase deficiency (with male pseudohermaphroditism)
      • Testicular hypogonadism NOS

      Type 1 Excludes

      • postprocedural testicular hypofunction (E89.5)

      Use Additional

      • code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
  • hypoxanthine- E79.1
    (guanine)-phosphoribosyltransferase (HG- PRT) (total H-PRT)
    ICD-10-CM Diagnosis Code E79.1

    Lesch-Nyhan syndrome

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • HGPRT deficiency
  • immunity D84.9
    ICD-10-CM Diagnosis Code D84.9

    Immunodeficiency, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Immunocompromised NOS
    • Immunodeficient NOS
    • Immunosuppressed NOS
    • cell-mediated D84.89
      ICD-10-CM Diagnosis Code D84.89

      Other immunodeficiencies

      2021 - New Code 2022 2023 Billable/Specific Code
      • with thrombocytopenia and eczema D82.0
        ICD-10-CM Diagnosis Code D82.0

        Wiskott-Aldrich syndrome

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Immunodeficiency with thrombocytopenia and eczema
    • combined D81.9
      ICD-10-CM Diagnosis Code D81.9

      Combined immunodeficiency, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Severe combined immunodeficiency disorder [SCID] NOS
    • humoral D80.9
      ICD-10-CM Diagnosis Code D80.9

      Immunodeficiency with predominantly antibody defects, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • IgA D80.2
      (secretory)
      ICD-10-CM Diagnosis Code D80.2

      Selective deficiency of immunoglobulin A [IgA]

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • IgG D80.3
      ICD-10-CM Diagnosis Code D80.3

      Selective deficiency of immunoglobulin G [IgG] subclasses

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • IgM D80.4
      ICD-10-CM Diagnosis Code D80.4

      Selective deficiency of immunoglobulin M [IgM]

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • immuno - see Immunodeficiency
  • immunoglobulin, selective
    • A D80.2
      (IgA)
      ICD-10-CM Diagnosis Code D80.2

      Selective deficiency of immunoglobulin A [IgA]

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • G D80.3
      (IgG) (subclasses)
      ICD-10-CM Diagnosis Code D80.3

      Selective deficiency of immunoglobulin G [IgG] subclasses

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • M D80.4
      (IgM)
      ICD-10-CM Diagnosis Code D80.4

      Selective deficiency of immunoglobulin M [IgM]

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • infantile neurovisceral acid sphingomyelinase E75.240
    ICD-10-CM Diagnosis Code E75.240

    Niemann-Pick disease type A

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Acid sphingomyelinase deficiency type A (ASMD type A)
    • Infantile neurovisceral acid sphingomyelinase deficiency
  • inositol E53.8
    (B complex)
    ICD-10-CM Diagnosis Code E53.8

    Deficiency of other specified B group vitamins

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Biotin deficiency
    • Cyanocobalamin deficiency
    • Folate deficiency
    • Folic acid deficiency
    • Pantothenic acid deficiency
    • Vitamin B12 deficiency

    Type 1 Excludes

    • folate deficiency anemia (D52.-)
    • vitamin B12 deficiency anemia (D51.-)
  • intrinsic
    • factor D51.0
      (congenital)
      ICD-10-CM Diagnosis Code D51.0

      Vitamin B12 deficiency anemia due to intrinsic factor deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Addison anemia
      • Biermer anemia
      • Pernicious (congenital) anemia
      • Congenital intrinsic factor deficiency
    • sphincter N36.42
      ICD-10-CM Diagnosis Code N36.42

      Intrinsic sphincter deficiency (ISD)

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      • with urethral hypermobility N36.43
        ICD-10-CM Diagnosis Code N36.43

        Combined hypermobility of urethra and intrinsic sphincter deficiency

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • iodine E61.8
    ICD-10-CM Diagnosis Code E61.8

    Deficiency of other specified nutrient elements

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • congenital syndrome - see Syndrome, iodine-deficiency, congenital
  • iron E61.1
    ICD-10-CM Diagnosis Code E61.1

    Iron deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Type 1 Excludes

    • iron deficiency anemia (D50.-)
    • anemia D50.9
      ICD-10-CM Diagnosis Code D50.9

      Iron deficiency anemia, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • kalium E87.6
    ICD-10-CM Diagnosis Code E87.6

    Hypokalemia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Potassium [K] deficiency
  • kappa-light chain D80.8
    ICD-10-CM Diagnosis Code D80.8

    Other immunodeficiencies with predominantly antibody defects

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Kappa light chain deficiency
  • labile factor (congenital) (hereditary) D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
    • acquired D68.4
      ICD-10-CM Diagnosis Code D68.4

      Acquired coagulation factor deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Deficiency of coagulation factor due to liver disease
      • Deficiency of coagulation factor due to vitamin K deficiency

      Type 1 Excludes

      • vitamin K deficiency of newborn (P53)
  • lacrimal fluid (acquired) - see also Syndrome, dry eye
    • congenital Q10.6
      ICD-10-CM Diagnosis Code Q10.6

      Other congenital malformations of lacrimal apparatus

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Congenital malformation of lacrimal apparatus NOS
  • lactase
    • congenital E73.0
      ICD-10-CM Diagnosis Code E73.0

      Congenital lactase deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • secondary E73.1
      ICD-10-CM Diagnosis Code E73.1

      Secondary lactase deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • Laki-Lorand factor D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
  • lecithin cholesterol acyltransferase E78.6
    ICD-10-CM Diagnosis Code E78.6

    Lipoprotein deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Abetalipoproteinemia
    • Depressed HDL cholesterol
    • High-density lipoprotein deficiency
    • Hypoalphalipoproteinemia
    • Hypobetalipoproteinemia (familial)
    • Lecithin cholesterol acyltransferase deficiency
    • Tangier disease
  • lipocaic K86.89
    ICD-10-CM Diagnosis Code K86.89

    Other specified diseases of pancreas

    2017 - New Code 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Aseptic pancreatic necrosis, unrelated to acute pancreatitis
    • Atrophy of pancreas
    • Calculus of pancreas
    • Cirrhosis of pancreas
    • Fibrosis of pancreas
    • Pancreatic fat necrosis, unrelated to acute pancreatitis
    • Pancreatic infantilism
    • Pancreatic necrosis NOS, unrelated to acute pancreatitis
  • lipoprotein E78.6
    (familial) (high density)
    ICD-10-CM Diagnosis Code E78.6

    Lipoprotein deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Abetalipoproteinemia
    • Depressed HDL cholesterol
    • High-density lipoprotein deficiency
    • Hypoalphalipoproteinemia
    • Hypobetalipoproteinemia (familial)
    • Lecithin cholesterol acyltransferase deficiency
    • Tangier disease
  • liver phosphorylase E74.09
    ICD-10-CM Diagnosis Code E74.09

    Other glycogen storage disease

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Andersen disease
    • Hers disease
    • Tauri disease
    • Glycogen storage disease, types 0, IV, VI-XI
    • Liver phosphorylase deficiency
    • Muscle phosphofructokinase deficiency
  • lysosomal alpha-1, 4 glucosidase E74.02
    ICD-10-CM Diagnosis Code E74.02

    Pompe disease

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Cardiac glycogenosis
    • Type II glycogen storage disease
  • magnesium E61.2
    ICD-10-CM Diagnosis Code E61.2

    Magnesium deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • major histocompatibility complex
    • class I D81.6
      ICD-10-CM Diagnosis Code D81.6

      Major histocompatibility complex class I deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Bare lymphocyte syndrome
    • class II D81.7
      ICD-10-CM Diagnosis Code D81.7

      Major histocompatibility complex class II deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • manganese E61.3
    ICD-10-CM Diagnosis Code E61.3

    Manganese deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • menadione (vitamin K) E56.1
    ICD-10-CM Diagnosis Code E56.1

    Deficiency of vitamin K

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Type 1 Excludes

    • deficiency of coagulation factor due to vitamin K deficiency (D68.4)
    • vitamin K deficiency of newborn (P53)
    • newborn P53
      ICD-10-CM Diagnosis Code P53

      Hemorrhagic disease of newborn

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Code on Newborn Record

      Applicable To

      • Vitamin K deficiency of newborn
  • mental (familial) (hereditary) - see Disability, intellectual
  • methylenetetrahydrofolate reductase E72.12
    (MTHFR)
    ICD-10-CM Diagnosis Code E72.12

    Methylenetetrahydrofolate reductase deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • mevalonate kinase M04.1
    ICD-10-CM Diagnosis Code M04.1

    Periodic fever syndromes

    2017 - New Code 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Familial Mediterranean fever
    • Hyperimmunoglobin D syndrome
    • Mevalonate kinase deficiency
    • Tumor necrosis factor receptor associated periodic syndrome [TRAPS]
  • mineral NEC E61.8
    ICD-10-CM Diagnosis Code E61.8

    Deficiency of other specified nutrient elements

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • mineralocorticoid E27.49
    ICD-10-CM Diagnosis Code E27.49

    Other adrenocortical insufficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Adrenal hemorrhage
    • Adrenal infarction
    • with glucocorticoid E27.49
      ICD-10-CM Diagnosis Code E27.49

      Other adrenocortical insufficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Adrenal hemorrhage
      • Adrenal infarction
  • molybdenum E61.5
    (nutritional)
    ICD-10-CM Diagnosis Code E61.5

    Molybdenum deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • moral F60.2
    ICD-10-CM Diagnosis Code F60.2

    Antisocial personality disorder

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Amoral personality (disorder)
    • Asocial personality (disorder)
    • Dissocial personality disorder
    • Psychopathic personality (disorder)
    • Sociopathic personality (disorder)

    Type 1 Excludes

    • conduct disorders (F91.-)

    Type 2 Excludes

    • borderline personality disorder (F60.3)
  • multiple nutrient elements E61.7
    ICD-10-CM Diagnosis Code E61.7

    Deficiency of multiple nutrient elements

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • multiple sulfatase E75.26
    (MSD)
    ICD-10-CM Diagnosis Code E75.26

    Sulfatase deficiency

    2019 - New Code 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Multiple sulfatase deficiency (MSD)
  • muscle
    • carnitine E71.314
      (palmityltransferase)
      ICD-10-CM Diagnosis Code E71.314

      Muscle carnitine palmitoyltransferase deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • phosphofructokinase E74.09
      ICD-10-CM Diagnosis Code E74.09

      Other glycogen storage disease

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Andersen disease
      • Hers disease
      • Tauri disease
      • Glycogen storage disease, types 0, IV, VI-XI
      • Liver phosphorylase deficiency
      • Muscle phosphofructokinase deficiency
  • myoadenylate deaminase E79.2
    ICD-10-CM Diagnosis Code E79.2

    Myoadenylate deaminase deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • myocardial - see Insufficiency, myocardial
  • myophosphorylase E74.04
    ICD-10-CM Diagnosis Code E74.04

    McArdle disease

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Type V glycogen storage disease
  • NADH diaphorase or reductase D74.0
    (congenital)
    ICD-10-CM Diagnosis Code D74.0

    Congenital methemoglobinemia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Congenital NADH-methemoglobin reductase deficiency
    • Hemoglobin-M [Hb-M] disease
    • Methemoglobinemia, hereditary
  • NADH-methemoglobin reductase D74.0
    (congenital)
    ICD-10-CM Diagnosis Code D74.0

    Congenital methemoglobinemia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Congenital NADH-methemoglobin reductase deficiency
    • Hemoglobin-M [Hb-M] disease
    • Methemoglobinemia, hereditary
  • natrium E87.1
    ICD-10-CM Diagnosis Code E87.1

    Hypo-osmolality and hyponatremia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Sodium [Na] deficiency

    Type 1 Excludes

    • syndrome of inappropriate secretion of antidiuretic hormone (E22.2)
  • niacin E52
    (amide) (-tryptophan)
    ICD-10-CM Diagnosis Code E52

    Niacin deficiency [pellagra]

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Niacin (-tryptophan) deficiency
    • Nicotinamide deficiency
    • Pellagra (alcoholic)

    Type 1 Excludes

    • sequelae of niacin deficiency (E64.8)
  • nicotinamide E52
    ICD-10-CM Diagnosis Code E52

    Niacin deficiency [pellagra]

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Niacin (-tryptophan) deficiency
    • Nicotinamide deficiency
    • Pellagra (alcoholic)

    Type 1 Excludes

    • sequelae of niacin deficiency (E64.8)
  • nicotinic acid E52
    ICD-10-CM Diagnosis Code E52

    Niacin deficiency [pellagra]

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Niacin (-tryptophan) deficiency
    • Nicotinamide deficiency
    • Pellagra (alcoholic)

    Type 1 Excludes

    • sequelae of niacin deficiency (E64.8)
  • number of teeth - see Anodontia
  • nutrient element E61.9
    ICD-10-CM Diagnosis Code E61.9

    Deficiency of nutrient element, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • multiple E61.7
      ICD-10-CM Diagnosis Code E61.7

      Deficiency of multiple nutrient elements

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • specified NEC E61.8
      ICD-10-CM Diagnosis Code E61.8

      Deficiency of other specified nutrient elements

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • nutrition, nutritional E63.9
    - see also Nutrition deficient
    ICD-10-CM Diagnosis Code E63.9

    Nutritional deficiency, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • sequelae - see Sequelae, nutritional deficiency
    • specified NEC E63.8
      ICD-10-CM Diagnosis Code E63.8

      Other specified nutritional deficiencies

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • of interleukin 1 receptor antagonist [DIRA] M04.8
    ICD-10-CM Diagnosis Code M04.8

    Other autoinflammatory syndromes

    2017 - New Code 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Blau syndrome
    • Deficiency of interleukin 1 receptor antagonist [DIRA]
    • Majeed syndrome
    • Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome [PFAPA]
    • Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome [PAPA]
  • ornithine transcarbamylase E72.4
    ICD-10-CM Diagnosis Code E72.4

    Disorders of ornithine metabolism

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Hyperammonemia-Hyperornithinemia-Homocitrullinemia syndrome
    • Ornithinemia (types I, II)
    • Ornithine transcarbamylase deficiency

    Type 1 Excludes

    • hereditary choroidal dystrophy (H31.2-)
  • ovarian E28.39
    ICD-10-CM Diagnosis Code E28.39

    Other primary ovarian failure

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx

    Applicable To

    • Decreased estrogen
    • Resistant ovary syndrome
  • oxygen - see Anoxia
  • pantothenic acid E53.8
    ICD-10-CM Diagnosis Code E53.8

    Deficiency of other specified B group vitamins

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Biotin deficiency
    • Cyanocobalamin deficiency
    • Folate deficiency
    • Folic acid deficiency
    • Pantothenic acid deficiency
    • Vitamin B12 deficiency

    Type 1 Excludes

    • folate deficiency anemia (D52.-)
    • vitamin B12 deficiency anemia (D51.-)
  • parathyroid E20.9
    (gland)
    ICD-10-CM Diagnosis Code E20.9

    Hypoparathyroidism, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Parathyroid tetany
  • perineum N81.89
    (female)
    ICD-10-CM Diagnosis Code N81.89

    Other female genital prolapse

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx

    Applicable To

    • Deficient perineum
    • Old laceration of muscles of pelvic floor
  • phenylalanine hydroxylase E70.1
    ICD-10-CM Diagnosis Code E70.1

    Other hyperphenylalaninemias

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • phosphoenolpyruvate carboxykinase E74.4
    ICD-10-CM Diagnosis Code E74.4

    Disorders of pyruvate metabolism and gluconeogenesis

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Deficiency of phosphoenolpyruvate carboxykinase
    • Deficiency of pyruvate carboxylase
    • Deficiency of pyruvate dehydrogenase

    Type 1 Excludes

    • disorders of pyruvate metabolism and gluconeogenesis with anemia (D55.-)
    • Leigh's syndrome (G31.82)
  • phosphofructokinase E74.19
    ICD-10-CM Diagnosis Code E74.19

    Other disorders of fructose metabolism

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Fructose-1, 6-diphosphatase deficiency
  • phosphomannomutuse E74.818
    ICD-10-CM Diagnosis Code E74.818

    Other disorders of glucose transport

    2021 - New Code 2022 2023 Billable/Specific Code

    Applicable To

    • (Familial) renal glycosuria
  • phosphomannose isomerase E74.818
    ICD-10-CM Diagnosis Code E74.818

    Other disorders of glucose transport

    2021 - New Code 2022 2023 Billable/Specific Code

    Applicable To

    • (Familial) renal glycosuria
  • phosphomannosyl mutase E74.818
    ICD-10-CM Diagnosis Code E74.818

    Other disorders of glucose transport

    2021 - New Code 2022 2023 Billable/Specific Code

    Applicable To

    • (Familial) renal glycosuria
  • phosphorylase kinase, liver E74.09
    ICD-10-CM Diagnosis Code E74.09

    Other glycogen storage disease

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Andersen disease
    • Hers disease
    • Tauri disease
    • Glycogen storage disease, types 0, IV, VI-XI
    • Liver phosphorylase deficiency
    • Muscle phosphofructokinase deficiency
  • pituitary hormone E23.0
    (isolated)
    ICD-10-CM Diagnosis Code E23.0

    Hypopituitarism

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Fertile eunuch syndrome
    • Hypogonadotropic hypogonadism
    • Idiopathic growth hormone deficiency
    • Isolated deficiency of gonadotropin
    • Isolated deficiency of growth hormone
    • Isolated deficiency of pituitary hormone
    • Kallmann's syndrome
    • Lorain-Levi short stature
    • Necrosis of pituitary gland (postpartum)
    • Panhypopituitarism
    • Pituitary cachexia
    • Pituitary insufficiency NOS
    • Pituitary short stature
    • Sheehan's syndrome
    • Simmonds' disease
  • plasma thromboplastin
    • antecedent D68.1
      (PTA)
      ICD-10-CM Diagnosis Code D68.1

      Hereditary factor XI deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Hemophilia C
      • Plasma thromboplastin antecedent [PTA] deficiency
      • Rosenthal's disease
    • component D67
      (PTC)
      ICD-10-CM Diagnosis Code D67

      Hereditary factor IX deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Christmas disease
      • Factor IX deficiency (with functional defect)
      • Hemophilia B
      • Plasma thromboplastin component [PTC] deficiency
  • plasminogen E88.02
    (type 1) (type 2)
    ICD-10-CM Diagnosis Code E88.02

    Plasminogen deficiency

    2019 - New Code 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Dysplasminogenemia
    • Hypoplasminogenemia
    • Type 1 plasminogen deficiency
    • Type 2 plasminogen deficiency

    Code Also

    • , if applicable, ligneous conjunctivitis (H10.51)

    Use Additional

    • code for associated findings, such as:
    • hydrocephalus (G91.4)
    • otitis media (H67.-)
    • respiratory disorder related to plasminogen deficiency (J99)
  • platelet NEC D69.1
    ICD-10-CM Diagnosis Code D69.1

    Qualitative platelet defects

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Bernard-Soulier [giant platelet] syndrome
    • Glanzmann's disease
    • Grey platelet syndrome
    • Thromboasthenia (hemorrhagic) (hereditary)
    • Thrombocytopathy

    Type 1 Excludes

    • hemolytic-uremic syndrome (D59.3-)

    Type 2 Excludes

    • von Willebrand disease (D68.0-)
    • constitutional - see Disease, von Willebrand
  • polyglandular E31.8
    ICD-10-CM Diagnosis Code E31.8

    Other polyglandular dysfunction

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • autoimmune E31.0
      ICD-10-CM Diagnosis Code E31.0

      Autoimmune polyglandular failure

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Schmidt's syndrome
  • potassium E87.6
    (K)
    ICD-10-CM Diagnosis Code E87.6

    Hypokalemia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Potassium [K] deficiency
  • prepuce N47.3
    ICD-10-CM Diagnosis Code N47.3

    Deficient foreskin

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx
  • proaccelerin (congenital) (hereditary) D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
    • acquired D68.4
      ICD-10-CM Diagnosis Code D68.4

      Acquired coagulation factor deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Deficiency of coagulation factor due to liver disease
      • Deficiency of coagulation factor due to vitamin K deficiency

      Type 1 Excludes

      • vitamin K deficiency of newborn (P53)
  • proconvertin factor (congenital) (hereditary) D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
    • acquired D68.4
      ICD-10-CM Diagnosis Code D68.4

      Acquired coagulation factor deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Deficiency of coagulation factor due to liver disease
      • Deficiency of coagulation factor due to vitamin K deficiency

      Type 1 Excludes

      • vitamin K deficiency of newborn (P53)
  • protein E46
    - see also Malnutrition
    ICD-10-CM Diagnosis Code E46

    Unspecified protein-calorie malnutrition

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Malnutrition NOS
    • Protein-calorie imbalance NOS

    Type 1 Excludes

    • nutritional deficiency NOS (E63.9)
    • anemia D53.0
      ICD-10-CM Diagnosis Code D53.0

      Protein deficiency anemia

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Amino-acid deficiency anemia
      • Orotaciduric anemia

      Type 1 Excludes

      • Lesch-Nyhan syndrome (E79.1)
    • C D68.59
      ICD-10-CM Diagnosis Code D68.59

      Other primary thrombophilia

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Antithrombin III deficiency
      • Hypercoagulable state NOS
      • Primary hypercoagulable state NEC
      • Primary thrombophilia NEC
      • Protein C deficiency
      • Protein S deficiency
      • Thrombophilia NOS
    • S D68.59
      ICD-10-CM Diagnosis Code D68.59

      Other primary thrombophilia

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Antithrombin III deficiency
      • Hypercoagulable state NOS
      • Primary hypercoagulable state NEC
      • Primary thrombophilia NEC
      • Protein C deficiency
      • Protein S deficiency
      • Thrombophilia NOS
  • prothrombin (congenital) (heredItary) D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
    • acquired D68.4
      ICD-10-CM Diagnosis Code D68.4

      Acquired coagulation factor deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Deficiency of coagulation factor due to liver disease
      • Deficiency of coagulation factor due to vitamin K deficiency

      Type 1 Excludes

      • vitamin K deficiency of newborn (P53)
  • Prower factor D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
  • pseudocholinesterase E88.09
    ICD-10-CM Diagnosis Code E88.09

    Other disorders of plasma-protein metabolism, not elsewhere classified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Bisalbuminemia
  • PTA D68.1
    (plasma thromboplastin antecedent)
    ICD-10-CM Diagnosis Code D68.1

    Hereditary factor XI deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Hemophilia C
    • Plasma thromboplastin antecedent [PTA] deficiency
    • Rosenthal's disease
  • PTC D67
    (plasma thromboplastin component)
    ICD-10-CM Diagnosis Code D67

    Hereditary factor IX deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Christmas disease
    • Factor IX deficiency (with functional defect)
    • Hemophilia B
    • Plasma thromboplastin component [PTC] deficiency
  • purine nucleoside phosphorylase D81.5
    (PNP)
    ICD-10-CM Diagnosis Code D81.5

    Purine nucleoside phosphorylase [PNP] deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • pyracin E53.1
    (alpha) (beta)
    ICD-10-CM Diagnosis Code E53.1

    Pyridoxine deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Vitamin B6 deficiency

    Type 1 Excludes

    • pyridoxine-responsive sideroblastic anemia (D64.3)
  • pyridoxal E53.1
    ICD-10-CM Diagnosis Code E53.1

    Pyridoxine deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Vitamin B6 deficiency

    Type 1 Excludes

    • pyridoxine-responsive sideroblastic anemia (D64.3)
  • pyridoxamine E53.1
    ICD-10-CM Diagnosis Code E53.1

    Pyridoxine deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Vitamin B6 deficiency

    Type 1 Excludes

    • pyridoxine-responsive sideroblastic anemia (D64.3)
  • pyridoxine E53.1
    (derivatives)
    ICD-10-CM Diagnosis Code E53.1

    Pyridoxine deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Vitamin B6 deficiency

    Type 1 Excludes

    • pyridoxine-responsive sideroblastic anemia (D64.3)
  • pyruvate
    • carboxylase E74.4
      ICD-10-CM Diagnosis Code E74.4

      Disorders of pyruvate metabolism and gluconeogenesis

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Deficiency of phosphoenolpyruvate carboxykinase
      • Deficiency of pyruvate carboxylase
      • Deficiency of pyruvate dehydrogenase

      Type 1 Excludes

      • disorders of pyruvate metabolism and gluconeogenesis with anemia (D55.-)
      • Leigh's syndrome (G31.82)
    • dehydrogenase E74.4
      ICD-10-CM Diagnosis Code E74.4

      Disorders of pyruvate metabolism and gluconeogenesis

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Deficiency of phosphoenolpyruvate carboxykinase
      • Deficiency of pyruvate carboxylase
      • Deficiency of pyruvate dehydrogenase

      Type 1 Excludes

      • disorders of pyruvate metabolism and gluconeogenesis with anemia (D55.-)
      • Leigh's syndrome (G31.82)
  • riboflavin E53.0
    (vitamin B2)
    ICD-10-CM Diagnosis Code E53.0

    Riboflavin deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Ariboflavinosis
    • Vitamin B2 deficiency
  • salt E87.1
    ICD-10-CM Diagnosis Code E87.1

    Hypo-osmolality and hyponatremia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Sodium [Na] deficiency

    Type 1 Excludes

    • syndrome of inappropriate secretion of antidiuretic hormone (E22.2)
  • secretion
    • ovary E28.39
      ICD-10-CM Diagnosis Code E28.39

      Other primary ovarian failure

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx

      Applicable To

      • Decreased estrogen
      • Resistant ovary syndrome
    • salivary gland K11.7
      (any)
      ICD-10-CM Diagnosis Code K11.7

      Disturbances of salivary secretion

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Hypoptyalism
      • Ptyalism
      • Xerostomia

      Type 2 Excludes

      • dry mouth NOS (R68.2)
    • urine R34
      ICD-10-CM Diagnosis Code R34

      Anuria and oliguria

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Type 1 Excludes

      • anuria and oliguria complicating abortion or ectopic or molar pregnancy (O00-O07, O08.4)
      • anuria and oliguria complicating pregnancy (O26.83-)
      • anuria and oliguria complicating the puerperium (O90.4)
  • selenium E59
    (dietary)
    ICD-10-CM Diagnosis Code E59

    Dietary selenium deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Keshan disease

    Type 1 Excludes

    • sequelae of selenium deficiency (E64.8)
  • serum antitrypsin, familial E88.01
    ICD-10-CM Diagnosis Code E88.01

    Alpha-1-antitrypsin deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AAT deficiency
  • short stature homeobox gene (SHOX)
    • with
      • dyschondrosteosis Q78.8
        ICD-10-CM Diagnosis Code Q78.8

        Other specified osteochondrodysplasias

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

        Applicable To

        • Osteopoikilosis
      • short stature E34.328
        (idiopathic)
        ICD-10-CM Diagnosis Code E34.328

        Other genetic causes of short stature

        2023 - New Code Billable/Specific Code

        Applicable To

        • Short stature due to ACAN gene variant
        • Short stature due to aggrecan deficiency
        • Short stature due to NPR-2 gene variant
      • Turner's syndrome Q96.9
        ICD-10-CM Diagnosis Code Q96.9

        Turner's syndrome, unspecified

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  • sodium E87.1
    (Na)
    ICD-10-CM Diagnosis Code E87.1

    Hypo-osmolality and hyponatremia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Sodium [Na] deficiency

    Type 1 Excludes

    • syndrome of inappropriate secretion of antidiuretic hormone (E22.2)
  • SPCA D68.2
    (factor VII)
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
  • sphincter, intrinsic N36.42
    ICD-10-CM Diagnosis Code N36.42

    Intrinsic sphincter deficiency (ISD)

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • with urethral hypermobility N36.43
      ICD-10-CM Diagnosis Code N36.43

      Combined hypermobility of urethra and intrinsic sphincter deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • stable factor (congenital) (hereditary) D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
    • acquired D68.4
      ICD-10-CM Diagnosis Code D68.4

      Acquired coagulation factor deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Deficiency of coagulation factor due to liver disease
      • Deficiency of coagulation factor due to vitamin K deficiency

      Type 1 Excludes

      • vitamin K deficiency of newborn (P53)
  • Stuart-Prower D68.2
    (factor X)
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
  • succinic semialdehyde dehydrogenase E72.81
    ICD-10-CM Diagnosis Code E72.81

    Disorders of gamma aminobutyric acid metabolism

    2019 - New Code 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • 4-hydroxybutyric aciduria
    • Disorders of GABA metabolism
    • GABA metabolic defect
    • GABA transaminase deficiency
    • GABA-T deficiency
    • Gamma-hydroxybutyric aciduria
    • SSADHD
    • Succinic semialdehyde dehydrogenase deficiency
  • sucrase E74.39
    ICD-10-CM Diagnosis Code E74.39

    Other disorders of intestinal carbohydrate absorption

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Disorder of intestinal carbohydrate absorption NOS
    • Glucose-galactose malabsorption
    • Sucrase deficiency
  • sulfatase E75.26
    ICD-10-CM Diagnosis Code E75.26

    Sulfatase deficiency

    2019 - New Code 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Multiple sulfatase deficiency (MSD)
  • sulfite oxidase E72.19
    ICD-10-CM Diagnosis Code E72.19

    Other disorders of sulfur-bearing amino-acid metabolism

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Cystathioninuria
    • Methioninemia
    • Sulfite oxidase deficiency
  • thiamin, thiaminic (chloride) E51.9
    ICD-10-CM Diagnosis Code E51.9

    Thiamine deficiency, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • beriberi (dry) E51.11
      ICD-10-CM Diagnosis Code E51.11

      Dry beriberi

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Beriberi NOS
      • Beriberi with polyneuropathy
      • wet E51.12
        ICD-10-CM Diagnosis Code E51.12

        Wet beriberi

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Beriberi with cardiovascular manifestations
        • Cardiovascular beriberi
        • Shoshin disease
  • thrombokinase D68.2
    ICD-10-CM Diagnosis Code D68.2

    Hereditary deficiency of other clotting factors

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency
    • newborn P53
      ICD-10-CM Diagnosis Code P53

      Hemorrhagic disease of newborn

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Code on Newborn Record

      Applicable To

      • Vitamin K deficiency of newborn
  • thyroid (gland) - see Hypothyroidism
  • tocopherol E56.0
    ICD-10-CM Diagnosis Code E56.0

    Deficiency of vitamin E

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • tooth bud K00.0
    ICD-10-CM Diagnosis Code K00.0

    Anodontia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Hypodontia
    • Oligodontia

    Type 1 Excludes

    • acquired absence of teeth (K08.1-)
  • transcobalamine II D51.2
    (anemia)
    ICD-10-CM Diagnosis Code D51.2

    Transcobalamin II deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • vanadium E61.6
    ICD-10-CM Diagnosis Code E61.6

    Vanadium deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • vascular I99.9
    ICD-10-CM Diagnosis Code I99.9

    Unspecified disorder of circulatory system

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • vasopressin E23.2
    ICD-10-CM Diagnosis Code E23.2

    Diabetes insipidus

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Type 1 Excludes

    • nephrogenic diabetes insipidus (N25.1)
  • vertical ridge K06.8
    ICD-10-CM Diagnosis Code K06.8

    Other specified disorders of gingiva and edentulous alveolar ridge

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Fibrous epulis
    • Flabby alveolar ridge
    • Giant cell epulis
    • Peripheral giant cell granuloma of gingiva
    • Pyogenic granuloma of gingiva
    • Vertical ridge deficiency

    Type 2 Excludes

    • gingival cyst (K09.0)
  • viosterol - see Deficiency, calciferol
  • vitamin (multiple) E56.9
    ICD-10-CM Diagnosis Code E56.9

    Vitamin deficiency, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • A E50.9
      ICD-10-CM Diagnosis Code E50.9

      Vitamin A deficiency, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Hypovitaminosis A NOS
      • sequelae E64.1
        ICD-10-CM Diagnosis Code E64.1

        Sequelae of vitamin A deficiency

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      • with
        • Bitot's spot E50.1
          (corneal)
          ICD-10-CM Diagnosis Code E50.1

          Vitamin A deficiency with Bitot's spot and conjunctival xerosis

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

          Applicable To

          • Bitot's spot in the young child
        • follicular keratosis E50.8
          ICD-10-CM Diagnosis Code E50.8

          Other manifestations of vitamin A deficiency

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

          Applicable To

          • Follicular keratosis
          • Xeroderma
        • keratomalacia E50.4
          ICD-10-CM Diagnosis Code E50.4

          Vitamin A deficiency with keratomalacia

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
        • manifestations NEC E50.8
          ICD-10-CM Diagnosis Code E50.8

          Other manifestations of vitamin A deficiency

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

          Applicable To

          • Follicular keratosis
          • Xeroderma
        • night blindness E50.5
          ICD-10-CM Diagnosis Code E50.5

          Vitamin A deficiency with night blindness

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
        • scar of cornea, xerophthalmic E50.6
          ICD-10-CM Diagnosis Code E50.6

          Vitamin A deficiency with xerophthalmic scars of cornea

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
        • xeroderma E50.8
          ICD-10-CM Diagnosis Code E50.8

          Other manifestations of vitamin A deficiency

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

          Applicable To

          • Follicular keratosis
          • Xeroderma
        • xerophthalmia E50.7
          ICD-10-CM Diagnosis Code E50.7

          Other ocular manifestations of vitamin A deficiency

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

          Applicable To

          • Xerophthalmia NOS
        • xerosis
          • conjunctival E50.0
            ICD-10-CM Diagnosis Code E50.0

            Vitamin A deficiency with conjunctival xerosis

            2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
            • and Bitot's spot E50.1
              ICD-10-CM Diagnosis Code E50.1

              Vitamin A deficiency with Bitot's spot and conjunctival xerosis

              2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

              Applicable To

              • Bitot's spot in the young child
          • cornea E50.2
            ICD-10-CM Diagnosis Code E50.2

            Vitamin A deficiency with corneal xerosis

            2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
            • and ulceration E50.3
              ICD-10-CM Diagnosis Code E50.3

              Vitamin A deficiency with corneal ulceration and xerosis

              2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • B (complex) E53.9
      ICD-10-CM Diagnosis Code E53.9

      Vitamin B deficiency, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      • with
        • beriberi (dry) E51.11
          ICD-10-CM Diagnosis Code E51.11

          Dry beriberi

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

          Applicable To

          • Beriberi NOS
          • Beriberi with polyneuropathy
          • wet E51.12
            ICD-10-CM Diagnosis Code E51.12

            Wet beriberi

            2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

            Applicable To

            • Beriberi with cardiovascular manifestations
            • Cardiovascular beriberi
            • Shoshin disease
        • pellagra E52
          ICD-10-CM Diagnosis Code E52

          Niacin deficiency [pellagra]

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

          Applicable To

          • Niacin (-tryptophan) deficiency
          • Nicotinamide deficiency
          • Pellagra (alcoholic)

          Type 1 Excludes

          • sequelae of niacin deficiency (E64.8)
    • B1 NOS E51.9
      ICD-10-CM Diagnosis Code E51.9

      Thiamine deficiency, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      • beriberi (dry) E51.11
        ICD-10-CM Diagnosis Code E51.11

        Dry beriberi

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Beriberi NOS
        • Beriberi with polyneuropathy
        • wet E51.12
          ICD-10-CM Diagnosis Code E51.12

          Wet beriberi

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

          Applicable To

          • Beriberi with cardiovascular manifestations
          • Cardiovascular beriberi
          • Shoshin disease
        • with circulatory system manifestations E51.11
          ICD-10-CM Diagnosis Code E51.11

          Dry beriberi

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

          Applicable To

          • Beriberi NOS
          • Beriberi with polyneuropathy
    • B12 E53.8
      ICD-10-CM Diagnosis Code E53.8

      Deficiency of other specified B group vitamins

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Biotin deficiency
      • Cyanocobalamin deficiency
      • Folate deficiency
      • Folic acid deficiency
      • Pantothenic acid deficiency
      • Vitamin B12 deficiency

      Type 1 Excludes

      • folate deficiency anemia (D52.-)
      • vitamin B12 deficiency anemia (D51.-)
    • B2 E53.0
      (riboflavin)
      ICD-10-CM Diagnosis Code E53.0

      Riboflavin deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Ariboflavinosis
      • Vitamin B2 deficiency
    • B6 E53.1
      ICD-10-CM Diagnosis Code E53.1

      Pyridoxine deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Vitamin B6 deficiency

      Type 1 Excludes

      • pyridoxine-responsive sideroblastic anemia (D64.3)
    • C E54
      ICD-10-CM Diagnosis Code E54

      Ascorbic acid deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Deficiency of vitamin C
      • Scurvy

      Type 1 Excludes

      • scorbutic anemia (D53.2)
      • sequelae of vitamin C deficiency (E64.2)
      • sequelae E64.2
        ICD-10-CM Diagnosis Code E64.2

        Sequelae of vitamin C deficiency

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    • D E55.9
      ICD-10-CM Diagnosis Code E55.9

      Vitamin D deficiency, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Avitaminosis D
      • 25-hydroxylase E83.32
        ICD-10-CM Diagnosis Code E83.32

        Hereditary vitamin D-dependent rickets (type 1) (type 2)

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • 25-hydroxyvitamin D 1-alpha-hydroxylase deficiency
        • Pseudovitamin D deficiency
        • Vitamin D receptor defect
      • with
        • adult osteomalacia M83.8
          ICD-10-CM Diagnosis Code M83.8

          Other adult osteomalacia

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Adult Dx (15-124 years)
        • rickets - see Rickets
    • E E56.0
      ICD-10-CM Diagnosis Code E56.0

      Deficiency of vitamin E

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • folic acid E53.8
      ICD-10-CM Diagnosis Code E53.8

      Deficiency of other specified B group vitamins

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Biotin deficiency
      • Cyanocobalamin deficiency
      • Folate deficiency
      • Folic acid deficiency
      • Pantothenic acid deficiency
      • Vitamin B12 deficiency

      Type 1 Excludes

      • folate deficiency anemia (D52.-)
      • vitamin B12 deficiency anemia (D51.-)
    • G E53.0
      ICD-10-CM Diagnosis Code E53.0

      Riboflavin deficiency

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Ariboflavinosis
      • Vitamin B2 deficiency
    • group B E53.9
      ICD-10-CM Diagnosis Code E53.9

      Vitamin B deficiency, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      • specified NEC E53.8
        ICD-10-CM Diagnosis Code E53.8

        Deficiency of other specified B group vitamins

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Biotin deficiency
        • Cyanocobalamin deficiency
        • Folate deficiency
        • Folic acid deficiency
        • Pantothenic acid deficiency
        • Vitamin B12 deficiency

        Type 1 Excludes

        • folate deficiency anemia (D52.-)
        • vitamin B12 deficiency anemia (D51.-)
    • H E53.8
      (biotin)
      ICD-10-CM Diagnosis Code E53.8

      Deficiency of other specified B group vitamins

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Biotin deficiency
      • Cyanocobalamin deficiency
      • Folate deficiency
      • Folic acid deficiency
      • Pantothenic acid deficiency
      • Vitamin B12 deficiency

      Type 1 Excludes

      • folate deficiency anemia (D52.-)
      • vitamin B12 deficiency anemia (D51.-)
    • K E56.1
      ICD-10-CM Diagnosis Code E56.1

      Deficiency of vitamin K

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Type 1 Excludes

      • deficiency of coagulation factor due to vitamin K deficiency (D68.4)
      • vitamin K deficiency of newborn (P53)
      • of newborn P53
        ICD-10-CM Diagnosis Code P53

        Hemorrhagic disease of newborn

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Code on Newborn Record

        Applicable To

        • Vitamin K deficiency of newborn
    • nicotinic E52
      ICD-10-CM Diagnosis Code E52

      Niacin deficiency [pellagra]

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Niacin (-tryptophan) deficiency
      • Nicotinamide deficiency
      • Pellagra (alcoholic)

      Type 1 Excludes

      • sequelae of niacin deficiency (E64.8)
    • P E56.8
      ICD-10-CM Diagnosis Code E56.8

      Deficiency of other vitamins

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • PP E52
      (pellagra-preventing)
      ICD-10-CM Diagnosis Code E52

      Niacin deficiency [pellagra]

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Niacin (-tryptophan) deficiency
      • Nicotinamide deficiency
      • Pellagra (alcoholic)

      Type 1 Excludes

      • sequelae of niacin deficiency (E64.8)
    • specified NEC E56.8
      ICD-10-CM Diagnosis Code E56.8

      Deficiency of other vitamins

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • thiamin E51.9
      ICD-10-CM Diagnosis Code E51.9

      Thiamine deficiency, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      • beriberi - see Beriberi
  • von Willebrand factor
    • partial quantitative D68.01
      - see also Disease, von Willebrand
      ICD-10-CM Diagnosis Code D68.01

      Von Willebrand disease, type 1

      2023 - New Code Billable/Specific Code

      Applicable To

      • Partial quantitative deficiency of von Willebrand factor
      • Type 1C von Willebrand disease
    • total quantitative D68.03
      - see also Disease, von Willebrand
      ICD-10-CM Diagnosis Code D68.03

      Von Willebrand disease, type 3

      2023 - New Code Billable/Specific Code

      Applicable To

      • (Near) complete absence of von Willebrand factor
      • Total quantitative deficiency of von Willebrand factor
  • zinc, dietary E60
    ICD-10-CM Diagnosis Code E60

    Dietary zinc deficiency

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code