1. 2023 ICD-10-CM Index
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2. 'H' Terms
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3. Index Terms Starting With 'H' (Hypoplasia, hypoplastic)

Index Terms Starting With 'H' (Hypoplasia, hypoplastic)

• Hypoplasia, hypoplastic

  • adrenal Q89.1
    (gland)
    ICD-10-CM Diagnosis Code Q89.1

    Congenital malformations of adrenal gland

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Type 1 Excludes

    • adrenogenital disorders (E25.-)
    • congenital adrenal hyperplasia (E25.0)
  • alimentary tract, congenital Q45.8
    ICD-10-CM Diagnosis Code Q45.8

    Other specified congenital malformations of digestive system

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Absence (complete) (partial) of alimentary tract NOS
    • Duplication of digestive system
    • Malposition, congenital of digestive system
    • upper Q40.8
      ICD-10-CM Diagnosis Code Q40.8

      Other specified congenital malformations of upper alimentary tract

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • anus, anal (canal) Q42.3
    ICD-10-CM Diagnosis Code Q42.3

    Congenital absence, atresia and stenosis of anus without fistula

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Imperforate anus
    • with fistula Q42.2
      ICD-10-CM Diagnosis Code Q42.2

      Congenital absence, atresia and stenosis of anus with fistula

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • aorta, aortic Q25.42
    ICD-10-CM Diagnosis Code Q25.42

    Hypoplasia of aorta

    2017 - New Code 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    • ascending, in hypoplastic left heart syndrome Q23.4
      ICD-10-CM Diagnosis Code Q23.4

      Hypoplastic left heart syndrome

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    • valve Q23.1
      ICD-10-CM Diagnosis Code Q23.1

      Congenital insufficiency of aortic valve

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Bicuspid aortic valve
      • Congenital aortic insufficiency
      • in hypoplastic left heart syndrome Q23.4
        ICD-10-CM Diagnosis Code Q23.4

        Hypoplastic left heart syndrome

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • areola, congenital Q83.8
    ICD-10-CM Diagnosis Code Q83.8

    Other congenital malformations of breast

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • arm (congenital) - see Defect, reduction, upper limb
  • artery (peripheral) Q27.8
    ICD-10-CM Diagnosis Code Q27.8

    Other specified congenital malformations of peripheral vascular system

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Absence of peripheral vascular system
    • Atresia of peripheral vascular system
    • Congenital aneurysm (peripheral)
    • Congenital stricture, artery
    • Congenital varix

    Type 1 Excludes

    • arteriovenous malformation (Q27.3-)
    • brain Q28.3
      (congenital)
      ICD-10-CM Diagnosis Code Q28.3

      Other malformations of cerebral vessels

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Congenital cerebral aneurysm (nonruptured)
      • Congenital malformation of cerebral vessels NOS
      • Developmental venous anomaly
    • coronary Q24.5
      ICD-10-CM Diagnosis Code Q24.5

      Malformation of coronary vessels

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Congenital coronary (artery) aneurysm
    • digestive system Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
    • lower limb Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
    • pulmonary Q25.79
      ICD-10-CM Diagnosis Code Q25.79

      Other congenital malformations of pulmonary artery

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Aberrant pulmonary artery
      • Agenesis of pulmonary artery
      • Congenital aneurysm of pulmonary artery
      • Congenital anomaly of pulmonary artery
      • Hypoplasia of pulmonary artery
      • functional, unilateral J43.0
        ICD-10-CM Diagnosis Code J43.0

        Unilateral pulmonary emphysema [MacLeod's syndrome]

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Swyer-James syndrome
        • Unilateral emphysema
        • Unilateral hyperlucent lung
        • Unilateral pulmonary artery functional hypoplasia
        • Unilateral transparency of lung
    • retinal Q14.1
      (congenital)
      ICD-10-CM Diagnosis Code Q14.1

      Congenital malformation of retina

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Congenital retinal aneurysm
    • specified site NEC Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
    • umbilical Q27.0
      ICD-10-CM Diagnosis Code Q27.0

      Congenital absence and hypoplasia of umbilical artery

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Single umbilical artery
    • upper limb Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
  • auditory canal Q17.8
    ICD-10-CM Diagnosis Code Q17.8

    Other specified congenital malformations of ear

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital absence of lobe of ear
    • causing impairment of hearing Q16.9
      ICD-10-CM Diagnosis Code Q16.9

      Congenital malformation of ear causing impairment of hearing, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Congenital absence of ear NOS
  • biliary duct or passage Q44.5
    ICD-10-CM Diagnosis Code Q44.5

    Other congenital malformations of bile ducts

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Accessory hepatic duct
    • Biliary duct duplication
    • Congenital malformation of bile duct NOS
    • Cystic duct duplication
  • bone NOS Q79.9
    ICD-10-CM Diagnosis Code Q79.9

    Congenital malformation of musculoskeletal system, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital anomaly of musculoskeletal system NOS
    • Congenital deformity of musculoskeletal system NOS
    • face Q75.8
      ICD-10-CM Diagnosis Code Q75.8

      Other specified congenital malformations of skull and face bones

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of skull bone, congenital
      • Congenital deformity of forehead
      • Platybasia
    • marrow D61.9
      ICD-10-CM Diagnosis Code D61.9

      Aplastic anemia, unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Hypoplastic anemia NOS
      • Medullary hypoplasia
      • megakaryocytic D69.49
        ICD-10-CM Diagnosis Code D69.49

        Other primary thrombocytopenia

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

        Applicable To

        • Megakaryocytic hypoplasia
        • Primary thrombocytopenia NOS
    • skull - see Hypoplasia, skull
  • brain Q02
    ICD-10-CM Diagnosis Code Q02

    Microcephaly

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Code First

    • , if applicable, congenital Zika virus disease

    Includes

    • hydromicrocephaly
    • micrencephalon

    Type 1 Excludes

    • Meckel-Gruber syndrome (Q61.9)
    • gyri Q04.3
      ICD-10-CM Diagnosis Code Q04.3

      Other reduction deformities of brain

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of part of brain
      • Agenesis of part of brain
      • Agyria
      • Aplasia of part of brain
      • Hydranencephaly
      • Hypoplasia of part of brain
      • Lissencephaly
      • Microgyria
      • Pachygyria

      Type 1 Excludes

      • congenital malformations of corpus callosum (Q04.0)
    • part of Q04.3
      ICD-10-CM Diagnosis Code Q04.3

      Other reduction deformities of brain

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of part of brain
      • Agenesis of part of brain
      • Agyria
      • Aplasia of part of brain
      • Hydranencephaly
      • Hypoplasia of part of brain
      • Lissencephaly
      • Microgyria
      • Pachygyria

      Type 1 Excludes

      • congenital malformations of corpus callosum (Q04.0)
  • breast N64.82
    (areola)
    ICD-10-CM Diagnosis Code N64.82

    Hypoplasia of breast

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Adult Dx (15-124 years)

    Applicable To

    • Micromastia

    Type 1 Excludes

    • congenital absence of breast (Q83.0)
    • hypoplasia of native breast in relation to reconstructed breast (N65.1)
  • bronchus Q32.4
    ICD-10-CM Diagnosis Code Q32.4

    Other congenital malformations of bronchus

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Absence of bronchus
    • Agenesis of bronchus
    • Atresia of bronchus
    • Congenital diverticulum of bronchus
    • Congenital malformation of bronchus NOS
  • cardiac Q24.8
    ICD-10-CM Diagnosis Code Q24.8

    Other specified congenital malformations of heart

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital diverticulum of left ventricle
    • Congenital malformation of myocardium
    • Congenital malformation of pericardium
    • Malposition of heart
    • Uhl's disease
  • carpus - see Defect, reduction, upper limb, specified type NEC
  • cartilage hair Q78.8
    ICD-10-CM Diagnosis Code Q78.8

    Other specified osteochondrodysplasias

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Osteopoikilosis
  • cecum Q42.8
    ICD-10-CM Diagnosis Code Q42.8

    Congenital absence, atresia and stenosis of other parts of large intestine

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • cementum K00.4
    ICD-10-CM Diagnosis Code K00.4

    Disturbances in tooth formation

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Aplasia and hypoplasia of cementum
    • Dilaceration of tooth
    • Enamel hypoplasia (neonatal) (postnatal) (prenatal)
    • Regional odontodysplasia
    • Turner's tooth

    Type 1 Excludes

    • Hutchinson's teeth and mulberry molars in congenital syphilis (A50.5)

    Type 2 Excludes

    • mottled teeth (K00.3)
  • cephalic Q02
    ICD-10-CM Diagnosis Code Q02

    Microcephaly

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Code First

    • , if applicable, congenital Zika virus disease

    Includes

    • hydromicrocephaly
    • micrencephalon

    Type 1 Excludes

    • Meckel-Gruber syndrome (Q61.9)
  • cerebellum Q04.3
    ICD-10-CM Diagnosis Code Q04.3

    Other reduction deformities of brain

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Absence of part of brain
    • Agenesis of part of brain
    • Agyria
    • Aplasia of part of brain
    • Hydranencephaly
    • Hypoplasia of part of brain
    • Lissencephaly
    • Microgyria
    • Pachygyria

    Type 1 Excludes

    • congenital malformations of corpus callosum (Q04.0)
  • cervix Q51.821
    (uteri)
    ICD-10-CM Diagnosis Code Q51.821

    Hypoplasia of cervix

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  • clavicle Q74.0
    (congenital)
    ICD-10-CM Diagnosis Code Q74.0

    Other congenital malformations of upper limb(s), including shoulder girdle

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Accessory carpal bones
    • Cleidocranial dysostosis
    • Congenital pseudarthrosis of clavicle
    • Macrodactylia (fingers)
    • Madelung's deformity
    • Radioulnar synostosis
    • Sprengel's deformity
    • Triphalangeal thumb
  • coccyx Q76.49
    ICD-10-CM Diagnosis Code Q76.49

    Other congenital malformations of spine, not associated with scoliosis

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital absence of vertebra NOS
    • Congenital fusion of spine NOS
    • Congenital malformation of lumbosacral (joint) (region) NOS
    • Congenital malformation of spine NOS
    • Hemivertebra NOS
    • Malformation of spine NOS
    • Platyspondylisis NOS
    • Supernumerary vertebra NOS
  • colon Q42.9
    ICD-10-CM Diagnosis Code Q42.9

    Congenital absence, atresia and stenosis of large intestine, part unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    • specified NEC Q42.8
      ICD-10-CM Diagnosis Code Q42.8

      Congenital absence, atresia and stenosis of other parts of large intestine

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • corpus callosum Q04.0
    ICD-10-CM Diagnosis Code Q04.0

    Congenital malformations of corpus callosum

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Agenesis of corpus callosum
  • cricoid cartilage Q31.2
    ICD-10-CM Diagnosis Code Q31.2

    Laryngeal hypoplasia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • digestive organ(s) Q45.8
    ICD-10-CM Diagnosis Code Q45.8

    Other specified congenital malformations of digestive system

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Absence (complete) (partial) of alimentary tract NOS
    • Duplication of digestive system
    • Malposition, congenital of digestive system
    • upper Q40.8
      (congenital)
      ICD-10-CM Diagnosis Code Q40.8

      Other specified congenital malformations of upper alimentary tract

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • ear (auricle) (lobe) Q17.2
    ICD-10-CM Diagnosis Code Q17.2

    Microtia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    • middle Q16.4
      ICD-10-CM Diagnosis Code Q16.4

      Other congenital malformations of middle ear

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Congenital malformation of middle ear NOS
  • enamel of teeth K00.4
    (neonatal) (postnatal) (prenatal)
    ICD-10-CM Diagnosis Code K00.4

    Disturbances in tooth formation

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Aplasia and hypoplasia of cementum
    • Dilaceration of tooth
    • Enamel hypoplasia (neonatal) (postnatal) (prenatal)
    • Regional odontodysplasia
    • Turner's tooth

    Type 1 Excludes

    • Hutchinson's teeth and mulberry molars in congenital syphilis (A50.5)

    Type 2 Excludes

    • mottled teeth (K00.3)
  • endocrine Q89.2
    (gland)
    ICD-10-CM Diagnosis Code Q89.2

    Congenital malformations of other endocrine glands

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital malformation of parathyroid or thyroid gland
    • Persistent thyroglossal duct
    • Thyroglossal cyst

    Type 1 Excludes

    • congenital goiter (E03.0)
    • congenital hypothyroidism (E03.1)
  • endometrium N85.8
    ICD-10-CM Diagnosis Code N85.8

    Other specified noninflammatory disorders of uterus

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx

    Applicable To

    • Atrophy of uterus, acquired
    • Fibrosis of uterus NOS
  • epididymis Q55.4
    (congenital)
    ICD-10-CM Diagnosis Code Q55.4

    Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt

    Applicable To

    • Absence or aplasia of prostate
    • Absence or aplasia of spermatic cord
    • Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
  • epiglottis Q31.2
    ICD-10-CM Diagnosis Code Q31.2

    Laryngeal hypoplasia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • erythroid, congenital D61.01
    ICD-10-CM Diagnosis Code D61.01

    Constitutional (pure) red blood cell aplasia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Blackfan-Diamond syndrome
    • Congenital (pure) red cell aplasia
    • Familial hypoplastic anemia
    • Primary (pure) red cell aplasia
    • Red cell (pure) aplasia of infants

    Type 1 Excludes

    • acquired red cell aplasia (D60.9)
  • esophagus Q39.8
    (congenital)
    ICD-10-CM Diagnosis Code Q39.8

    Other congenital malformations of esophagus

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital absence of esophagus
    • Congenital displacement of esophagus
    • Congenital duplication of esophagus
  • eustachian tube Q17.8
    ICD-10-CM Diagnosis Code Q17.8

    Other specified congenital malformations of ear

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital absence of lobe of ear
  • eye Q11.2
    ICD-10-CM Diagnosis Code Q11.2

    Microphthalmos

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Cryptophthalmos NOS
    • Dysplasia of eye
    • Hypoplasia of eye
    • Rudimentary eye

    Type 1 Excludes

    • cryptophthalmos syndrome (Q87.0)
  • eyelid Q10.3
    (congenital)
    ICD-10-CM Diagnosis Code Q10.3

    Other congenital malformations of eyelid

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Ablepharon
    • Blepharophimosis, congenital
    • Coloboma of eyelid
    • Congenital absence or agenesis of cilia
    • Congenital absence or agenesis of eyelid
    • Congenital accessory eyelid
    • Congenital accessory eye muscle
    • Congenital malformation of eyelid NOS
  • face Q18.8
    ICD-10-CM Diagnosis Code Q18.8

    Other specified congenital malformations of face and neck

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Medial cyst of face and neck
    • Medial fistula of face and neck
    • Medial sinus of face and neck
    • bone Q75.8
      (s)
      ICD-10-CM Diagnosis Code Q75.8

      Other specified congenital malformations of skull and face bones

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of skull bone, congenital
      • Congenital deformity of forehead
      • Platybasia
  • femur (congenital) - see Defect, reduction, lower limb, specified type NEC
  • fibula (congenital) - see Defect, reduction, lower limb, specified type NEC
  • finger (congenital) - see Defect, reduction, upper limb, specified type NEC
  • focal dermal Q82.8
    ICD-10-CM Diagnosis Code Q82.8

    Other specified congenital malformations of skin

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Abnormal palmar creases
    • Accessory skin tags
    • Benign familial pemphigus [Hailey-Hailey]
    • Congenital poikiloderma
    • Cutis laxa (hyperelastica)
    • Dermatoglyphic anomalies
    • Inherited keratosis palmaris et plantaris
    • Keratosis follicularis [Darier-White]

    Type 1 Excludes

    • Ehlers-Danlos syndromes (Q79.6-)
  • foot - see Defect, reduction, lower limb, specified type NEC
  • gallbladder Q44.0
    ICD-10-CM Diagnosis Code Q44.0

    Agenesis, aplasia and hypoplasia of gallbladder

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital absence of gallbladder
  • genitalia, genital organ(s)
    • female, congenital Q52.8
      ICD-10-CM Diagnosis Code Q52.8

      Other specified congenital malformations of female genitalia

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
      • external Q52.79
        ICD-10-CM Diagnosis Code Q52.79

        Other congenital malformations of vulva

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt

        Applicable To

        • Congenital cyst of vulva
      • internal NEC Q52.8
        ICD-10-CM Diagnosis Code Q52.8

        Other specified congenital malformations of female genitalia

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
    • in adiposogenital dystrophy E23.6
      ICD-10-CM Diagnosis Code E23.6

      Other disorders of pituitary gland

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Abscess of pituitary
      • Adiposogenital dystrophy
  • glottis Q31.2
    ICD-10-CM Diagnosis Code Q31.2

    Laryngeal hypoplasia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • hair Q84.2
    ICD-10-CM Diagnosis Code Q84.2

    Other congenital malformations of hair

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital hypertrichosis
    • Congenital malformation of hair NOS
    • Persistent lanugo
  • hand (congenital) - see Defect, reduction, upper limb, specified type NEC
  • heart Q24.8
    ICD-10-CM Diagnosis Code Q24.8

    Other specified congenital malformations of heart

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital diverticulum of left ventricle
    • Congenital malformation of myocardium
    • Congenital malformation of pericardium
    • Malposition of heart
    • Uhl's disease
  • humerus (congenital) - see Defect, reduction, upper limb, specified type NEC
  • intestine (small) Q41.9
    ICD-10-CM Diagnosis Code Q41.9

    Congenital absence, atresia and stenosis of small intestine, part unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital absence, atresia and stenosis of intestine NOS
    • large Q42.9
      ICD-10-CM Diagnosis Code Q42.9

      Congenital absence, atresia and stenosis of large intestine, part unspecified

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
      • specified NEC Q42.8
        ICD-10-CM Diagnosis Code Q42.8

        Congenital absence, atresia and stenosis of other parts of large intestine

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • jaw M26.09
    ICD-10-CM Diagnosis Code M26.09

    Other specified anomalies of jaw size

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • alveolar M26.79
      ICD-10-CM Diagnosis Code M26.79

      Other specified alveolar anomalies

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • lower M26.04
      ICD-10-CM Diagnosis Code M26.04

      Mandibular hypoplasia

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      • alveolar M26.74
        ICD-10-CM Diagnosis Code M26.74

        Alveolar mandibular hypoplasia

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • upper M26.02
      ICD-10-CM Diagnosis Code M26.02

      Maxillary hypoplasia

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      • alveolar M26.73
        ICD-10-CM Diagnosis Code M26.73

        Alveolar maxillary hypoplasia

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • kidney(s) Q60.5
    ICD-10-CM Diagnosis Code Q60.5

    Renal hypoplasia, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    • bilateral Q60.4
      ICD-10-CM Diagnosis Code Q60.4

      Renal hypoplasia, bilateral

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
    • unilateral Q60.3
      ICD-10-CM Diagnosis Code Q60.3

      Renal hypoplasia, unilateral

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • labium Q52.79
    (majus) (minus)
    ICD-10-CM Diagnosis Code Q52.79

    Other congenital malformations of vulva

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt

    Applicable To

    • Congenital cyst of vulva
  • larynx Q31.2
    ICD-10-CM Diagnosis Code Q31.2

    Laryngeal hypoplasia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • left heart syndrome Q23.4
    ICD-10-CM Diagnosis Code Q23.4

    Hypoplastic left heart syndrome

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • leg (congenital) - see Defect, reduction, lower limb
  • limb Q73.8
    ICD-10-CM Diagnosis Code Q73.8

    Other reduction defects of unspecified limb(s)

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Longitudinal reduction deformity of unspecified limb(s)
    • Ectromelia of limb NOS
    • Hemimelia of limb NOS
    • Reduction defect of limb NOS
    • lower (congenital) - see Defect, reduction, lower limb
    • upper (congenital) - see Defect, reduction, upper limb
  • liver Q44.7
    ICD-10-CM Diagnosis Code Q44.7

    Other congenital malformations of liver

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Accessory liver
    • Alagille's syndrome
    • Congenital absence of liver
    • Congenital hepatomegaly
    • Congenital malformation of liver NOS
  • lung (lobe) (not associated with short gestation) Q33.6
    ICD-10-CM Diagnosis Code Q33.6

    Congenital hypoplasia and dysplasia of lung

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Type 1 Excludes

    • pulmonary hypoplasia associated with short gestation (P28.0)
    • associated with immaturity, low birth weight, prematurity, or short gestation P28.0
      ICD-10-CM Diagnosis Code P28.0

      Primary atelectasis of newborn

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Code on Newborn Record

      Applicable To

      • Primary failure to expand terminal respiratory units
      • Pulmonary hypoplasia associated with short gestation
      • Pulmonary immaturity NOS
  • mammary Q83.8
    (areola)
    ICD-10-CM Diagnosis Code Q83.8

    Other congenital malformations of breast

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • mandible, mandibular M26.04
    ICD-10-CM Diagnosis Code M26.04

    Mandibular hypoplasia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • alveolar M26.74
      ICD-10-CM Diagnosis Code M26.74

      Alveolar mandibular hypoplasia

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • unilateral condylar M27.8
      ICD-10-CM Diagnosis Code M27.8

      Other specified diseases of jaws

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Cherubism
      • Exostosis
      • Fibrous dysplasia
      • Unilateral condylar hyperplasia
      • Unilateral condylar hypoplasia

      Type 1 Excludes

      • jaw pain (R68.84)
  • maxillary M26.02
    ICD-10-CM Diagnosis Code M26.02

    Maxillary hypoplasia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • alveolar M26.73
      ICD-10-CM Diagnosis Code M26.73

      Alveolar maxillary hypoplasia

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
  • medullary D61.9
    ICD-10-CM Diagnosis Code D61.9

    Aplastic anemia, unspecified

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Hypoplastic anemia NOS
    • Medullary hypoplasia
  • megakaryocytic D69.49
    ICD-10-CM Diagnosis Code D69.49

    Other primary thrombocytopenia

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Megakaryocytic hypoplasia
    • Primary thrombocytopenia NOS
  • metacarpus - see Defect, reduction, upper limb, specified type NEC
  • metatarsus - see Defect, reduction, lower limb, specified type NEC
  • muscle Q79.8
    ICD-10-CM Diagnosis Code Q79.8

    Other congenital malformations of musculoskeletal system

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Absence of muscle
    • Absence of tendon
    • Accessory muscle
    • Amyotrophia congenita
    • Congenital constricting bands
    • Congenital shortening of tendon
    • Poland syndrome
  • nail Q84.6
    (s)
    ICD-10-CM Diagnosis Code Q84.6

    Other congenital malformations of nails

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital clubnail
    • Congenital koilonychia
    • Congenital malformation of nail NOS
  • nose, nasal Q30.1
    ICD-10-CM Diagnosis Code Q30.1

    Agenesis and underdevelopment of nose

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital absent of nose
  • optic nerve H47.03-
    ICD-10-CM Diagnosis Code H47.03-

    Optic nerve hypoplasia

    2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
  • osseous meatus Q17.8
    (ear)
    ICD-10-CM Diagnosis Code Q17.8

    Other specified congenital malformations of ear

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital absence of lobe of ear
  • ovary, congenital Q50.39
    ICD-10-CM Diagnosis Code Q50.39

    Other congenital malformation of ovary

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt

    Applicable To

    • Congenital malformation of ovary NOS
  • pancreas Q45.0
    ICD-10-CM Diagnosis Code Q45.0

    Agenesis, aplasia and hypoplasia of pancreas

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital absence of pancreas
  • parathyroid Q89.2
    (gland)
    ICD-10-CM Diagnosis Code Q89.2

    Congenital malformations of other endocrine glands

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital malformation of parathyroid or thyroid gland
    • Persistent thyroglossal duct
    • Thyroglossal cyst

    Type 1 Excludes

    • congenital goiter (E03.0)
    • congenital hypothyroidism (E03.1)
  • parotid gland Q38.4
    ICD-10-CM Diagnosis Code Q38.4

    Congenital malformations of salivary glands and ducts

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Atresia of salivary glands and ducts
    • Congenital absence of salivary glands and ducts
    • Congenital accessory salivary glands and ducts
    • Congenital fistula of salivary gland
  • patella Q74.1
    ICD-10-CM Diagnosis Code Q74.1

    Congenital malformation of knee

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital absence of patella
    • Congenital dislocation of patella
    • Congenital genu valgum
    • Congenital genu varum
    • Rudimentary patella

    Type 1 Excludes

    • congenital dislocation of knee (Q68.2)
    • congenital genu recurvatum (Q68.2)
    • nail patella syndrome (Q87.2)
  • pelvis, pelvic girdle Q74.2
    ICD-10-CM Diagnosis Code Q74.2

    Other congenital malformations of lower limb(s), including pelvic girdle

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital fusion of sacroiliac joint
    • Congenital malformation of ankle joint
    • Congenital malformation of sacroiliac joint

    Type 1 Excludes

    • anteversion of femur (neck) (Q65.89)
  • penis Q55.62
    (congenital)
    ICD-10-CM Diagnosis Code Q55.62

    Hypoplasia of penis

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt

    Applicable To

    • Micropenis
  • peripheral vascular system Q27.8
    ICD-10-CM Diagnosis Code Q27.8

    Other specified congenital malformations of peripheral vascular system

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Absence of peripheral vascular system
    • Atresia of peripheral vascular system
    • Congenital aneurysm (peripheral)
    • Congenital stricture, artery
    • Congenital varix

    Type 1 Excludes

    • arteriovenous malformation (Q27.3-)
    • digestive system Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
    • lower limb Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
    • specified site NEC Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
    • upper limb Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
  • pituitary Q89.2
    (gland) (congenital)
    ICD-10-CM Diagnosis Code Q89.2

    Congenital malformations of other endocrine glands

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital malformation of parathyroid or thyroid gland
    • Persistent thyroglossal duct
    • Thyroglossal cyst

    Type 1 Excludes

    • congenital goiter (E03.0)
    • congenital hypothyroidism (E03.1)
  • pulmonary (not associated with short gestation) Q33.6
    ICD-10-CM Diagnosis Code Q33.6

    Congenital hypoplasia and dysplasia of lung

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Type 1 Excludes

    • pulmonary hypoplasia associated with short gestation (P28.0)
    • artery, functional J43.0
      ICD-10-CM Diagnosis Code J43.0

      Unilateral pulmonary emphysema [MacLeod's syndrome]

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Swyer-James syndrome
      • Unilateral emphysema
      • Unilateral hyperlucent lung
      • Unilateral pulmonary artery functional hypoplasia
      • Unilateral transparency of lung
    • associated with short gestation P28.0
      ICD-10-CM Diagnosis Code P28.0

      Primary atelectasis of newborn

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Code on Newborn Record

      Applicable To

      • Primary failure to expand terminal respiratory units
      • Pulmonary hypoplasia associated with short gestation
      • Pulmonary immaturity NOS
  • radioulnar - see Defect, reduction, upper limb, specified type NEC
  • radius - see Defect, reduction, upper limb
  • rectum Q42.1
    ICD-10-CM Diagnosis Code Q42.1

    Congenital absence, atresia and stenosis of rectum without fistula

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Imperforate rectum
    • with fistula Q42.0
      ICD-10-CM Diagnosis Code Q42.0

      Congenital absence, atresia and stenosis of rectum with fistula

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • respiratory system NEC Q34.8
    ICD-10-CM Diagnosis Code Q34.8

    Other specified congenital malformations of respiratory system

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Atresia of nasopharynx
  • rib Q76.6
    ICD-10-CM Diagnosis Code Q76.6

    Other congenital malformations of ribs

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Accessory rib
    • Congenital absence of rib
    • Congenital fusion of ribs
    • Congenital malformation of ribs NOS

    Type 1 Excludes

    • short rib syndrome (Q77.2)
  • right heart syndrome Q22.6
    ICD-10-CM Diagnosis Code Q22.6

    Hypoplastic right heart syndrome

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • sacrum Q76.49
    ICD-10-CM Diagnosis Code Q76.49

    Other congenital malformations of spine, not associated with scoliosis

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital absence of vertebra NOS
    • Congenital fusion of spine NOS
    • Congenital malformation of lumbosacral (joint) (region) NOS
    • Congenital malformation of spine NOS
    • Hemivertebra NOS
    • Malformation of spine NOS
    • Platyspondylisis NOS
    • Supernumerary vertebra NOS
  • scapula Q74.0
    ICD-10-CM Diagnosis Code Q74.0

    Other congenital malformations of upper limb(s), including shoulder girdle

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Accessory carpal bones
    • Cleidocranial dysostosis
    • Congenital pseudarthrosis of clavicle
    • Macrodactylia (fingers)
    • Madelung's deformity
    • Radioulnar synostosis
    • Sprengel's deformity
    • Triphalangeal thumb
  • scrotum Q55.1
    ICD-10-CM Diagnosis Code Q55.1

    Hypoplasia of testis and scrotum

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt

    Applicable To

    • Fusion of testes
  • shoulder girdle Q74.0
    ICD-10-CM Diagnosis Code Q74.0

    Other congenital malformations of upper limb(s), including shoulder girdle

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Accessory carpal bones
    • Cleidocranial dysostosis
    • Congenital pseudarthrosis of clavicle
    • Macrodactylia (fingers)
    • Madelung's deformity
    • Radioulnar synostosis
    • Sprengel's deformity
    • Triphalangeal thumb
  • skin Q82.8
    ICD-10-CM Diagnosis Code Q82.8

    Other specified congenital malformations of skin

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Abnormal palmar creases
    • Accessory skin tags
    • Benign familial pemphigus [Hailey-Hailey]
    • Congenital poikiloderma
    • Cutis laxa (hyperelastica)
    • Dermatoglyphic anomalies
    • Inherited keratosis palmaris et plantaris
    • Keratosis follicularis [Darier-White]

    Type 1 Excludes

    • Ehlers-Danlos syndromes (Q79.6-)
  • skull (bone) Q75.8
    ICD-10-CM Diagnosis Code Q75.8

    Other specified congenital malformations of skull and face bones

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Absence of skull bone, congenital
    • Congenital deformity of forehead
    • Platybasia
    • with
      • anencephaly Q00.0
        ICD-10-CM Diagnosis Code Q00.0

        Anencephaly

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

        Applicable To

        • Acephaly
        • Acrania
        • Amyelencephaly
        • Hemianencephaly
        • Hemicephaly
      • encephalocele - see Encephalocele
      • hydrocephalus Q03.9
        ICD-10-CM Diagnosis Code Q03.9

        Congenital hydrocephalus, unspecified

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
        • with spina bifida - see Spina bifida, by site, with hydrocephalus
      • microcephaly Q02
        ICD-10-CM Diagnosis Code Q02

        Microcephaly

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

        Code First

        • , if applicable, congenital Zika virus disease

        Includes

        • hydromicrocephaly
        • micrencephalon

        Type 1 Excludes

        • Meckel-Gruber syndrome (Q61.9)
  • spinal Q06.1
    (cord) (ventral horn cell)
    ICD-10-CM Diagnosis Code Q06.1

    Hypoplasia and dysplasia of spinal cord

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Atelomyelia
    • Myelatelia
    • Myelodysplasia of spinal cord
  • spine Q76.49
    ICD-10-CM Diagnosis Code Q76.49

    Other congenital malformations of spine, not associated with scoliosis

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital absence of vertebra NOS
    • Congenital fusion of spine NOS
    • Congenital malformation of lumbosacral (joint) (region) NOS
    • Congenital malformation of spine NOS
    • Hemivertebra NOS
    • Malformation of spine NOS
    • Platyspondylisis NOS
    • Supernumerary vertebra NOS
  • sternum Q76.7
    ICD-10-CM Diagnosis Code Q76.7

    Congenital malformation of sternum

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital absence of sternum
    • Sternum bifidum
  • tarsus - see Defect, reduction, lower limb, specified type NEC
  • testis Q55.1
    ICD-10-CM Diagnosis Code Q55.1

    Hypoplasia of testis and scrotum

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Male Dx POA Exempt

    Applicable To

    • Fusion of testes
  • thymic, with immunodeficiency D82.1
    ICD-10-CM Diagnosis Code D82.1

    Di George's syndrome

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Pharyngeal pouch syndrome
    • Thymic alymphoplasia
    • Thymic aplasia or hypoplasia with immunodeficiency
  • thymus (gland) Q89.2
    ICD-10-CM Diagnosis Code Q89.2

    Congenital malformations of other endocrine glands

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital malformation of parathyroid or thyroid gland
    • Persistent thyroglossal duct
    • Thyroglossal cyst

    Type 1 Excludes

    • congenital goiter (E03.0)
    • congenital hypothyroidism (E03.1)
    • with immunodeficiency D82.1
      ICD-10-CM Diagnosis Code D82.1

      Di George's syndrome

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

      Applicable To

      • Pharyngeal pouch syndrome
      • Thymic alymphoplasia
      • Thymic aplasia or hypoplasia with immunodeficiency
  • thyroid (gland) E03.1
    ICD-10-CM Diagnosis Code E03.1

    Congenital hypothyroidism without goiter

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Aplasia of thyroid (with myxedema)
    • Congenital atrophy of thyroid
    • Congenital hypothyroidism NOS
    • cartilage Q31.2
      ICD-10-CM Diagnosis Code Q31.2

      Laryngeal hypoplasia

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt
  • tibiofibular (congenital) - see Defect, reduction, lower limb, specified type NEC
  • toe - see Defect, reduction, lower limb, specified type NEC
  • tongue Q38.3
    ICD-10-CM Diagnosis Code Q38.3

    Other congenital malformations of tongue

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Aglossia
    • Bifid tongue
    • Congenital adhesion of tongue
    • Congenital fissure of tongue
    • Congenital malformation of tongue NOS
    • Double tongue
    • Hypoglossia
    • Hypoplasia of tongue
    • Microglossia
  • Turner's K00.4
    ICD-10-CM Diagnosis Code K00.4

    Disturbances in tooth formation

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Aplasia and hypoplasia of cementum
    • Dilaceration of tooth
    • Enamel hypoplasia (neonatal) (postnatal) (prenatal)
    • Regional odontodysplasia
    • Turner's tooth

    Type 1 Excludes

    • Hutchinson's teeth and mulberry molars in congenital syphilis (A50.5)

    Type 2 Excludes

    • mottled teeth (K00.3)
  • ulna (congenital) - see Defect, reduction, upper limb
  • umbilical artery Q27.0
    ICD-10-CM Diagnosis Code Q27.0

    Congenital absence and hypoplasia of umbilical artery

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Single umbilical artery
  • unilateral condylar M27.8
    ICD-10-CM Diagnosis Code M27.8

    Other specified diseases of jaws

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    Applicable To

    • Cherubism
    • Exostosis
    • Fibrous dysplasia
    • Unilateral condylar hyperplasia
    • Unilateral condylar hypoplasia

    Type 1 Excludes

    • jaw pain (R68.84)
  • ureter Q62.8
    ICD-10-CM Diagnosis Code Q62.8

    Other congenital malformations of ureter

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Anomaly of ureter NOS
  • uterus, congenital Q51.811
    ICD-10-CM Diagnosis Code Q51.811

    Hypoplasia of uterus

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt
  • vagina Q52.4
    ICD-10-CM Diagnosis Code Q52.4

    Other congenital malformations of vagina

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt

    Applicable To

    • Canal of Nuck cyst, congenital
    • Congenital malformation of vagina NOS
    • Embryonic vaginal cyst
    • Gartner's duct cyst
  • vascular NEC peripheral Q27.8
    ICD-10-CM Diagnosis Code Q27.8

    Other specified congenital malformations of peripheral vascular system

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Absence of peripheral vascular system
    • Atresia of peripheral vascular system
    • Congenital aneurysm (peripheral)
    • Congenital stricture, artery
    • Congenital varix

    Type 1 Excludes

    • arteriovenous malformation (Q27.3-)
    • brain Q28.3
      ICD-10-CM Diagnosis Code Q28.3

      Other malformations of cerebral vessels

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Congenital cerebral aneurysm (nonruptured)
      • Congenital malformation of cerebral vessels NOS
      • Developmental venous anomaly
    • digestive system Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
    • lower limb Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
    • specified site NEC Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
    • upper limb Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
  • vein(s) (peripheral) Q27.8
    ICD-10-CM Diagnosis Code Q27.8

    Other specified congenital malformations of peripheral vascular system

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Absence of peripheral vascular system
    • Atresia of peripheral vascular system
    • Congenital aneurysm (peripheral)
    • Congenital stricture, artery
    • Congenital varix

    Type 1 Excludes

    • arteriovenous malformation (Q27.3-)
    • brain Q28.3
      ICD-10-CM Diagnosis Code Q28.3

      Other malformations of cerebral vessels

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Congenital cerebral aneurysm (nonruptured)
      • Congenital malformation of cerebral vessels NOS
      • Developmental venous anomaly
    • digestive system Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
    • great Q26.8
      ICD-10-CM Diagnosis Code Q26.8

      Other congenital malformations of great veins

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of vena cava (inferior) (superior)
      • Azygos continuation of inferior vena cava
      • Persistent left posterior cardinal vein
      • Scimitar syndrome
    • lower limb Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
    • specified site NEC Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
    • upper limb Q27.8
      ICD-10-CM Diagnosis Code Q27.8

      Other specified congenital malformations of peripheral vascular system

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

      Applicable To

      • Absence of peripheral vascular system
      • Atresia of peripheral vascular system
      • Congenital aneurysm (peripheral)
      • Congenital stricture, artery
      • Congenital varix

      Type 1 Excludes

      • arteriovenous malformation (Q27.3-)
  • vena cava Q26.8
    (inferior) (superior)
    ICD-10-CM Diagnosis Code Q26.8

    Other congenital malformations of great veins

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Absence of vena cava (inferior) (superior)
    • Azygos continuation of inferior vena cava
    • Persistent left posterior cardinal vein
    • Scimitar syndrome
  • vertebra Q76.49
    ICD-10-CM Diagnosis Code Q76.49

    Other congenital malformations of spine, not associated with scoliosis

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Congenital absence of vertebra NOS
    • Congenital fusion of spine NOS
    • Congenital malformation of lumbosacral (joint) (region) NOS
    • Congenital malformation of spine NOS
    • Hemivertebra NOS
    • Malformation of spine NOS
    • Platyspondylisis NOS
    • Supernumerary vertebra NOS
  • vulva, congenital Q52.79
    ICD-10-CM Diagnosis Code Q52.79

    Other congenital malformations of vulva

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code Female Dx POA Exempt

    Applicable To

    • Congenital cyst of vulva
  • zonule Q12.8
    (ciliary)
    ICD-10-CM Diagnosis Code Q12.8

    Other congenital lens malformations

    2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code POA Exempt

    Applicable To

    • Microphakia