• Imperfect

    • aeration, lung (newborn) - see Atelectasis
    • closure (congenital)
      • alimentary tract NEC Q45.8
        ICD-10-CM Diagnosis Code Q45.8

        Other specified congenital malformations of digestive system

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Absence (complete) (partial) of alimentary tract NOS
        • Duplication of digestive system
        • Malposition, congenital of digestive system
        • lower Q43.8
          ICD-10-CM Diagnosis Code Q43.8

          Other specified congenital malformations of intestine

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Congenital blind loop syndrome
          • Congenital diverticulitis, colon
          • Congenital diverticulum, intestine
          • Dolichocolon
          • Megaloappendix
          • Megaloduodenum
          • Microcolon
          • Transposition of appendix
          • Transposition of colon
          • Transposition of intestine
        • upper Q40.8
          ICD-10-CM Diagnosis Code Q40.8

          Other specified congenital malformations of upper alimentary tract

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • atrioventricular ostium Q21.2
        ICD-10-CM Diagnosis Code Q21.2

        Atrioventricular septal defect

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Common atrioventricular canal
        • Endocardial cushion defect
        • Ostium primum atrial septal defect (type I)
      • atrium Q21.1
        (secundum)
        ICD-10-CM Diagnosis Code Q21.1

        Atrial septal defect

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Coronary sinus defect
        • Patent or persistent foramen ovale
        • Patent or persistent ostium secundum defect (type II)
        • Patent or persistent sinus venosus defect
      • branchial cleft NOS Q18.2
        ICD-10-CM Diagnosis Code Q18.2

        Other branchial cleft malformations

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Branchial cleft malformation NOS
        • Cervical auricle
        • Otocephaly
        • cyst Q18.0
          ICD-10-CM Diagnosis Code Q18.0

          Sinus, fistula and cyst of branchial cleft

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Branchial vestige
        • fistula Q18.0
          ICD-10-CM Diagnosis Code Q18.0

          Sinus, fistula and cyst of branchial cleft

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Branchial vestige
        • sinus Q18.0
          ICD-10-CM Diagnosis Code Q18.0

          Sinus, fistula and cyst of branchial cleft

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Branchial vestige
      • choroid Q14.3
        ICD-10-CM Diagnosis Code Q14.3

        Congenital malformation of choroid

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • cricoid cartilage Q31.8
        ICD-10-CM Diagnosis Code Q31.8

        Other congenital malformations of larynx

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Absence of larynx
        • Agenesis of larynx
        • Atresia of larynx
        • Congenital cleft thyroid cartilage
        • Congenital fissure of epiglottis
        • Congenital stenosis of larynx NEC
        • Posterior cleft of cricoid cartilage
      • cusps, heart valve NEC Q24.8
        ICD-10-CM Diagnosis Code Q24.8

        Other specified congenital malformations of heart

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital diverticulum of left ventricle
        • Congenital malformation of myocardium
        • Congenital malformation of pericardium
        • Malposition of heart
        • Uhl's disease
        • pulmonary Q22.3
          ICD-10-CM Diagnosis Code Q22.3

          Other congenital malformations of pulmonary valve

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Congenital malformation of pulmonary valve NOS
          • Supernumerary cusps of pulmonary valve
      • ductus
        • arteriosus Q25.0
          ICD-10-CM Diagnosis Code Q25.0

          Patent ductus arteriosus

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Patent ductus Botallo
          • Persistent ductus arteriosus
        • Botalli Q25.0
          ICD-10-CM Diagnosis Code Q25.0

          Patent ductus arteriosus

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Patent ductus Botallo
          • Persistent ductus arteriosus
      • ear drum Q16.4
        (causing impairment of hearing)
        ICD-10-CM Diagnosis Code Q16.4

        Other congenital malformations of middle ear

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital malformation of middle ear NOS
      • esophagus with communication to bronchus or trachea Q39.1
        ICD-10-CM Diagnosis Code Q39.1

        Atresia of esophagus with tracheo-esophageal fistula

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Atresia of esophagus with broncho-esophageal fistula
      • eyelid Q10.3
        ICD-10-CM Diagnosis Code Q10.3

        Other congenital malformations of eyelid

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Ablepharon
        • Blepharophimosis, congenital
        • Coloboma of eyelid
        • Congenital absence or agenesis of cilia
        • Congenital absence or agenesis of eyelid
        • Congenital accessory eyelid
        • Congenital accessory eye muscle
        • Congenital malformation of eyelid NOS
      • foramen
        • botalli Q21.1
          ICD-10-CM Diagnosis Code Q21.1

          Atrial septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Coronary sinus defect
          • Patent or persistent foramen ovale
          • Patent or persistent ostium secundum defect (type II)
          • Patent or persistent sinus venosus defect
        • ovale Q21.1
          ICD-10-CM Diagnosis Code Q21.1

          Atrial septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Coronary sinus defect
          • Patent or persistent foramen ovale
          • Patent or persistent ostium secundum defect (type II)
          • Patent or persistent sinus venosus defect
      • genitalia, genital organ(s)
        • female Q52.8
          ICD-10-CM Diagnosis Code Q52.8

          Other specified congenital malformations of female genitalia

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          • external Q52.79
            ICD-10-CM Diagnosis Code Q52.79

            Other congenital malformations of vulva

              2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
            Applicable To
            • Congenital cyst of vulva
          • internal NEC Q52.8
            ICD-10-CM Diagnosis Code Q52.8

            Other specified congenital malformations of female genitalia

              2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        • male Q55.8
          ICD-10-CM Diagnosis Code Q55.8

          Other specified congenital malformations of male genital organs

            2016 2017 2018 2019 2020 Billable/Specific Code Male Dx POA Exempt
      • glottis Q31.8
        ICD-10-CM Diagnosis Code Q31.8

        Other congenital malformations of larynx

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Absence of larynx
        • Agenesis of larynx
        • Atresia of larynx
        • Congenital cleft thyroid cartilage
        • Congenital fissure of epiglottis
        • Congenital stenosis of larynx NEC
        • Posterior cleft of cricoid cartilage
      • interatrial ostium or septum Q21.1
        ICD-10-CM Diagnosis Code Q21.1

        Atrial septal defect

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Coronary sinus defect
        • Patent or persistent foramen ovale
        • Patent or persistent ostium secundum defect (type II)
        • Patent or persistent sinus venosus defect
      • interauricular ostium or septum Q21.1
        ICD-10-CM Diagnosis Code Q21.1

        Atrial septal defect

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Coronary sinus defect
        • Patent or persistent foramen ovale
        • Patent or persistent ostium secundum defect (type II)
        • Patent or persistent sinus venosus defect
      • interventricular ostium or septum Q21.0
        ICD-10-CM Diagnosis Code Q21.0

        Ventricular septal defect

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Roger's disease
      • larynx Q31.8
        ICD-10-CM Diagnosis Code Q31.8

        Other congenital malformations of larynx

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Absence of larynx
        • Agenesis of larynx
        • Atresia of larynx
        • Congenital cleft thyroid cartilage
        • Congenital fissure of epiglottis
        • Congenital stenosis of larynx NEC
        • Posterior cleft of cricoid cartilage
      • lip - see Cleft, lip
      • nasal septum Q30.3
        ICD-10-CM Diagnosis Code Q30.3

        Congenital perforated nasal septum

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • nose Q30.2
        ICD-10-CM Diagnosis Code Q30.2

        Fissured, notched and cleft nose

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • omphalomesenteric duct Q43.0
        ICD-10-CM Diagnosis Code Q43.0

        Meckel's diverticulum (displaced) (hypertrophic)

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Persistent omphalomesenteric duct
        • Persistent vitelline duct
      • optic nerve entry Q14.2
        ICD-10-CM Diagnosis Code Q14.2

        Congenital malformation of optic disc

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Coloboma of optic disc
      • organ or site not listed - see Anomaly, by site
      • ostium
        • interatrial Q21.1
          ICD-10-CM Diagnosis Code Q21.1

          Atrial septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Coronary sinus defect
          • Patent or persistent foramen ovale
          • Patent or persistent ostium secundum defect (type II)
          • Patent or persistent sinus venosus defect
        • interauricular Q21.1
          ICD-10-CM Diagnosis Code Q21.1

          Atrial septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Coronary sinus defect
          • Patent or persistent foramen ovale
          • Patent or persistent ostium secundum defect (type II)
          • Patent or persistent sinus venosus defect
        • interventricular Q21.0
          ICD-10-CM Diagnosis Code Q21.0

          Ventricular septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Roger's disease
      • palate - see Cleft, palate
      • preauricular sinus Q18.1
        ICD-10-CM Diagnosis Code Q18.1

        Preauricular sinus and cyst

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Fistula of auricle, congenital
        • Cervicoaural fistula
      • retina Q14.1
        ICD-10-CM Diagnosis Code Q14.1

        Congenital malformation of retina

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital retinal aneurysm
      • roof of orbit Q75.8
        ICD-10-CM Diagnosis Code Q75.8

        Other specified congenital malformations of skull and face bones

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Absence of skull bone, congenital
        • Congenital deformity of forehead
        • Platybasia
      • sclera Q13.5
        ICD-10-CM Diagnosis Code Q13.5

        Blue sclera

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      • septum
        • aorticopulmonary Q21.4
          ICD-10-CM Diagnosis Code Q21.4

          Aortopulmonary septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Aortic septal defect
          • Aortopulmonary window
        • atrial Q21.1
          (secundum)
          ICD-10-CM Diagnosis Code Q21.1

          Atrial septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Coronary sinus defect
          • Patent or persistent foramen ovale
          • Patent or persistent ostium secundum defect (type II)
          • Patent or persistent sinus venosus defect
        • between aorta and pulmonary artery Q21.4
          ICD-10-CM Diagnosis Code Q21.4

          Aortopulmonary septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Aortic septal defect
          • Aortopulmonary window
        • heart Q21.9
          ICD-10-CM Diagnosis Code Q21.9

          Congenital malformation of cardiac septum, unspecified

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Septal (heart) defect NOS
        • interatrial Q21.1
          (secundum)
          ICD-10-CM Diagnosis Code Q21.1

          Atrial septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Coronary sinus defect
          • Patent or persistent foramen ovale
          • Patent or persistent ostium secundum defect (type II)
          • Patent or persistent sinus venosus defect
        • interauricular Q21.1
          (secundum)
          ICD-10-CM Diagnosis Code Q21.1

          Atrial septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Coronary sinus defect
          • Patent or persistent foramen ovale
          • Patent or persistent ostium secundum defect (type II)
          • Patent or persistent sinus venosus defect
        • interventricular Q21.0
          ICD-10-CM Diagnosis Code Q21.0

          Ventricular septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Roger's disease
          • in tetralogy of Fallot Q21.3
            ICD-10-CM Diagnosis Code Q21.3

            Tetralogy of Fallot

              2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
            Applicable To
            • Ventricular septal defect with pulmonary stenosis or atresia, dextroposition of aorta and hypertrophy of right ventricle.
        • nasal Q30.3
          ICD-10-CM Diagnosis Code Q30.3

          Congenital perforated nasal septum

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        • ventricular Q21.0
          ICD-10-CM Diagnosis Code Q21.0

          Ventricular septal defect

            2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          Applicable To
          • Roger's disease
          • in tetralogy of Fallot Q21.3
            ICD-10-CM Diagnosis Code Q21.3

            Tetralogy of Fallot

              2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
            Applicable To
            • Ventricular septal defect with pulmonary stenosis or atresia, dextroposition of aorta and hypertrophy of right ventricle.
          • with pulmonary stenosis or atresia, dextraposition of aorta, and hypertrophy of right ventricle Q21.3
            ICD-10-CM Diagnosis Code Q21.3

            Tetralogy of Fallot

              2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
            Applicable To
            • Ventricular septal defect with pulmonary stenosis or atresia, dextroposition of aorta and hypertrophy of right ventricle.
      • skull Q75.0
        ICD-10-CM Diagnosis Code Q75.0

        Craniosynostosis

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Acrocephaly
        • Imperfect fusion of skull
        • Oxycephaly
        • Trigonocephaly
        • with
          • anencephaly Q00.0
            ICD-10-CM Diagnosis Code Q00.0

            Anencephaly

              2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
            Applicable To
            • Acephaly
            • Acrania
            • Amyelencephaly
            • Hemianencephaly
            • Hemicephaly
          • encephalocele - see Encephalocele
          • hydrocephalus Q03.9
            ICD-10-CM Diagnosis Code Q03.9

            Congenital hydrocephalus, unspecified

              2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
          • microcephaly Q02
            ICD-10-CM Diagnosis Code Q02

            Microcephaly

              2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
            Code First
            • , if applicable, congenital Zika virus disease
            Includes
            • hydromicrocephaly
            • micrencephalon
            Type 1 Excludes
            • Meckel-Gruber syndrome (Q61.9)
      • spine (with meningocele) - see Spina bifida
      • trachea Q32.1
        ICD-10-CM Diagnosis Code Q32.1

        Other congenital malformations of trachea

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Atresia of trachea
        • Congenital anomaly of tracheal cartilage
        • Congenital dilatation of trachea
        • Congenital malformation of trachea
        • Congenital stenosis of trachea
        • Congenital tracheocele
      • tympanic membrane Q16.4
        (causing impairment of hearing)
        ICD-10-CM Diagnosis Code Q16.4

        Other congenital malformations of middle ear

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital malformation of middle ear NOS
      • uterus Q51.818
        ICD-10-CM Diagnosis Code Q51.818

        Other congenital malformations of uterus

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Müllerian anomaly of uterus NEC
      • vitelline duct Q43.0
        ICD-10-CM Diagnosis Code Q43.0

        Meckel's diverticulum (displaced) (hypertrophic)

          2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
        Applicable To
        • Persistent omphalomesenteric duct
        • Persistent vitelline duct
    • erection - see Dysfunction, sexual, male, erectile
    • fusion - see Imperfect, closure
    • inflation, lung (newborn) - see Atelectasis
    • posture R29.3
      ICD-10-CM Diagnosis Code R29.3

      Abnormal posture

        2016 2017 2018 2019 2020 Billable/Specific Code
    • rotation, intestine Q43.3
      ICD-10-CM Diagnosis Code Q43.3

      Congenital malformations of intestinal fixation

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital omental, anomalous adhesions [bands]
      • Congenital peritoneal adhesions [bands]
      • Incomplete rotation of cecum and colon
      • Insufficient rotation of cecum and colon
      • Jackson's membrane
      • Malrotation of colon
      • Rotation failure of cecum and colon
      • Universal mesentery
    • septum, ventricular Q21.0
      ICD-10-CM Diagnosis Code Q21.0

      Ventricular septal defect

        2016 2017 2018 2019 2020 Billable/Specific Code POA Exempt
      Applicable To
      • Roger's disease