Index Terms Starting With 'L' (Lymphoma)

  • Lymphoma (of) (malignant) C85.90
    ICD-10-CM Diagnosis Code C85.90

    Non-Hodgkin lymphoma, unspecified, unspecified site

      2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code

    • adult T-cell C91.5-
      (HTLV-1-associated) (acute variant) (chronic variant) (lymphomatoid variant) (smouldering variant)
      ICD-10-CM Diagnosis Code C91.5-

      Adult T-cell lymphoma/leukemia (HTLV-1-associated)

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Acute variant of adult T-cell lymphoma/leukemia (HTLV-1-associated)
      • Chronic variant of adult T-cell lymphoma/leukemia (HTLV-1-associated)
      • Lymphomatoid variant of adult T-cell lymphoma/leukemia (HTLV-1-associated)
      • Smouldering variant of adult T-cell lymphoma/leukemia (HTLV-1-associated)
    • anaplastic large cell
      • ALK-negative C84.7-
        ICD-10-CM Diagnosis Code C84.7-

        Anaplastic large cell lymphoma, ALK-negative

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Type 1 Excludes
        • primary cutaneous CD30-positive T-cell proliferations (C86.6-)
      • ALK-positive C84.6-
        ICD-10-CM Diagnosis Code C84.6-

        Anaplastic large cell lymphoma, ALK-positive

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Anaplastic large cell lymphoma, CD30-positive
      • breast implant associated C84.7A
        (BIA-ALCL)
        ICD-10-CM Diagnosis Code C84.7A

        Anaplastic large cell lymphoma, ALK-negative, breast

          2022 - New Code 2023 Billable/Specific Code
        Applicable To
        • Breast implant associated anaplastic large cell lymphoma (BIA-ALCL)
        Use Additional
        • code to identify:
        • breast implant status (Z98.82)
        • personal history of breast implant removal (Z98.86)
      • CD30-positive C84.6-
        ICD-10-CM Diagnosis Code C84.6-

        Anaplastic large cell lymphoma, ALK-positive

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Anaplastic large cell lymphoma, CD30-positive
      • primary cutaneous C86.6
        ICD-10-CM Diagnosis Code C86.6

        Primary cutaneous CD30-positive T-cell proliferations

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
        Applicable To
        • Lymphomatoid papulosis
        • Primary cutaneous anaplastic large cell lymphoma
        • Primary cutaneous CD30-positive large T-cell lymphoma
    • angioimmunoblastic T-cell C86.5
      ICD-10-CM Diagnosis Code C86.5

      Angioimmunoblastic T-cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Angioimmunoblastic lymphadenopathy with dysproteinemia (AILD)
    • B-cell C85.1-
      ICD-10-CM Diagnosis Code C85.1-

      Unspecified B-cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Note
      • If B-cell lineage or involvement is mentioned in conjunction with a specific lymphoma, code to the more specific description.
    • B-precursor C83.5-
      ICD-10-CM Diagnosis Code C83.5-

      Lymphoblastic (diffuse) lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • B-precursor lymphoma
      • Lymphoblastic B-cell lymphoma
      • Lymphoblastic lymphoma NOS
      • Lymphoblastic T-cell lymphoma
      • T-precursor lymphoma
    • BALT C88.4
      ICD-10-CM Diagnosis Code C88.4

      Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma]
      • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma]
      Type 1 Excludes
      • high malignant (diffuse large B-cell) lymphoma (C83.3-)
    • blastic NK-cell C86.4
      ICD-10-CM Diagnosis Code C86.4

      Blastic NK-cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Blastic plasmacytoid dendritic cell neoplasm (BPDCN)
    • blastic plasmacytoid dendritic cell neoplasm C86.4
      (BPDCN)
      ICD-10-CM Diagnosis Code C86.4

      Blastic NK-cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Blastic plasmacytoid dendritic cell neoplasm (BPDCN)
    • bronchial-associated lymphoid tissue [BALT-lymphoma] C88.4
      ICD-10-CM Diagnosis Code C88.4

      Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma]
      • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma]
      Type 1 Excludes
      • high malignant (diffuse large B-cell) lymphoma (C83.3-)
    • Burkitt C83.7-
      (atypical)
      ICD-10-CM Diagnosis Code C83.7-

      Burkitt lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Atypical Burkitt lymphoma
      • Burkitt-like lymphoma
      Type 1 Excludes
      • mature B-cell leukemia Burkitt type (C91.A-)
    • Burkitt-like C83.7-
      ICD-10-CM Diagnosis Code C83.7-

      Burkitt lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Atypical Burkitt lymphoma
      • Burkitt-like lymphoma
      Type 1 Excludes
      • mature B-cell leukemia Burkitt type (C91.A-)
    • centrocytic C83.1-
      ICD-10-CM Diagnosis Code C83.1-

      Mantle cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Centrocytic lymphoma
      • Malignant lymphomatous polyposis
    • cutaneous follicle center C82.6-
      ICD-10-CM Diagnosis Code C82.6-

      Cutaneous follicle center lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    • cutaneous T-cell C84.A-
      ICD-10-CM Diagnosis Code C84.A-

      Cutaneous T-cell lymphoma, unspecified

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    • diffuse follicle center C82.5-
      ICD-10-CM Diagnosis Code C82.5-

      Diffuse follicle center lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    • diffuse large cell C83.3-
      ICD-10-CM Diagnosis Code C83.3-

      Diffuse large B-cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Anaplastic diffuse large B-cell lymphoma
      • CD30-positive diffuse large B-cell lymphoma
      • Centroblastic diffuse large B-cell lymphoma
      • Diffuse large B-cell lymphoma, subtype not specified
      • Immunoblastic diffuse large B-cell lymphoma
      • Plasmablastic diffuse large B-cell lymphoma
      • Diffuse large B-cell lymphoma, subtype not specified
      • T-cell rich diffuse large B-cell lymphoma
      Type 1 Excludes
      • mediastinal (thymic) large B-cell lymphoma (C85.2-)
      • mature T/NK-cell lymphomas (C84.-)
      • anaplastic C83.3-
        ICD-10-CM Diagnosis Code C83.3-

        Diffuse large B-cell lymphoma

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Anaplastic diffuse large B-cell lymphoma
        • CD30-positive diffuse large B-cell lymphoma
        • Centroblastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • Immunoblastic diffuse large B-cell lymphoma
        • Plasmablastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • T-cell rich diffuse large B-cell lymphoma
        Type 1 Excludes
        • mediastinal (thymic) large B-cell lymphoma (C85.2-)
        • mature T/NK-cell lymphomas (C84.-)
      • B-cell C83.3-
        ICD-10-CM Diagnosis Code C83.3-

        Diffuse large B-cell lymphoma

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Anaplastic diffuse large B-cell lymphoma
        • CD30-positive diffuse large B-cell lymphoma
        • Centroblastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • Immunoblastic diffuse large B-cell lymphoma
        • Plasmablastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • T-cell rich diffuse large B-cell lymphoma
        Type 1 Excludes
        • mediastinal (thymic) large B-cell lymphoma (C85.2-)
        • mature T/NK-cell lymphomas (C84.-)
      • CD30-positive C83.3-
        ICD-10-CM Diagnosis Code C83.3-

        Diffuse large B-cell lymphoma

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Anaplastic diffuse large B-cell lymphoma
        • CD30-positive diffuse large B-cell lymphoma
        • Centroblastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • Immunoblastic diffuse large B-cell lymphoma
        • Plasmablastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • T-cell rich diffuse large B-cell lymphoma
        Type 1 Excludes
        • mediastinal (thymic) large B-cell lymphoma (C85.2-)
        • mature T/NK-cell lymphomas (C84.-)
      • centroblastic C83.3-
        ICD-10-CM Diagnosis Code C83.3-

        Diffuse large B-cell lymphoma

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Anaplastic diffuse large B-cell lymphoma
        • CD30-positive diffuse large B-cell lymphoma
        • Centroblastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • Immunoblastic diffuse large B-cell lymphoma
        • Plasmablastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • T-cell rich diffuse large B-cell lymphoma
        Type 1 Excludes
        • mediastinal (thymic) large B-cell lymphoma (C85.2-)
        • mature T/NK-cell lymphomas (C84.-)
      • immunoblastic C83.3-
        ICD-10-CM Diagnosis Code C83.3-

        Diffuse large B-cell lymphoma

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Anaplastic diffuse large B-cell lymphoma
        • CD30-positive diffuse large B-cell lymphoma
        • Centroblastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • Immunoblastic diffuse large B-cell lymphoma
        • Plasmablastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • T-cell rich diffuse large B-cell lymphoma
        Type 1 Excludes
        • mediastinal (thymic) large B-cell lymphoma (C85.2-)
        • mature T/NK-cell lymphomas (C84.-)
      • plasmablastic C83.3-
        ICD-10-CM Diagnosis Code C83.3-

        Diffuse large B-cell lymphoma

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Anaplastic diffuse large B-cell lymphoma
        • CD30-positive diffuse large B-cell lymphoma
        • Centroblastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • Immunoblastic diffuse large B-cell lymphoma
        • Plasmablastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • T-cell rich diffuse large B-cell lymphoma
        Type 1 Excludes
        • mediastinal (thymic) large B-cell lymphoma (C85.2-)
        • mature T/NK-cell lymphomas (C84.-)
      • subtype not specified C83.3-
        ICD-10-CM Diagnosis Code C83.3-

        Diffuse large B-cell lymphoma

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Anaplastic diffuse large B-cell lymphoma
        • CD30-positive diffuse large B-cell lymphoma
        • Centroblastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • Immunoblastic diffuse large B-cell lymphoma
        • Plasmablastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • T-cell rich diffuse large B-cell lymphoma
        Type 1 Excludes
        • mediastinal (thymic) large B-cell lymphoma (C85.2-)
        • mature T/NK-cell lymphomas (C84.-)
      • T-cell rich C83.3-
        ICD-10-CM Diagnosis Code C83.3-

        Diffuse large B-cell lymphoma

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Anaplastic diffuse large B-cell lymphoma
        • CD30-positive diffuse large B-cell lymphoma
        • Centroblastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • Immunoblastic diffuse large B-cell lymphoma
        • Plasmablastic diffuse large B-cell lymphoma
        • Diffuse large B-cell lymphoma, subtype not specified
        • T-cell rich diffuse large B-cell lymphoma
        Type 1 Excludes
        • mediastinal (thymic) large B-cell lymphoma (C85.2-)
        • mature T/NK-cell lymphomas (C84.-)
    • enteropathy-type C86.2
      (associated) (intestinal)
      ICD-10-CM Diagnosis Code C86.2

      Enteropathy-type (intestinal) T-cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Enteropathy associated T-cell lymphoma
    • extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] C88.4
      ICD-10-CM Diagnosis Code C88.4

      Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma]
      • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma]
      Type 1 Excludes
      • high malignant (diffuse large B-cell) lymphoma (C83.3-)
    • extranodal NK/T-cell, nasal type C86.0
      ICD-10-CM Diagnosis Code C86.0

      Extranodal NK/T-cell lymphoma, nasal type

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • follicular C82.9-
      ICD-10-CM Diagnosis Code C82.9-

      Follicular lymphoma, unspecified

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      • grade
        • I C82.0-
          ICD-10-CM Diagnosis Code C82.0-

          Follicular lymphoma grade I

            2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        • II C82.1-
          ICD-10-CM Diagnosis Code C82.1-

          Follicular lymphoma grade II

            2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        • III C82.2-
          ICD-10-CM Diagnosis Code C82.2-

          Follicular lymphoma grade III, unspecified

            2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        • IIIa C82.3-
          ICD-10-CM Diagnosis Code C82.3-

          Follicular lymphoma grade IIIa

            2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        • IIIb C82.4-
          ICD-10-CM Diagnosis Code C82.4-

          Follicular lymphoma grade IIIb

            2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      • specified NEC C82.8-
        ICD-10-CM Diagnosis Code C82.8-

        Other types of follicular lymphoma

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    • hepatosplenic T-cell C86.1
      (alpha-beta) (gamma-delta)
      ICD-10-CM Diagnosis Code C86.1

      Hepatosplenic T-cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Alpha-beta and gamma delta types
    • histiocytic C85.9-
      ICD-10-CM Diagnosis Code C85.9-

      Non-Hodgkin lymphoma, unspecified

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Lymphoma NOS
      • Malignant lymphoma NOS
      • Non-Hodgkin lymphoma NOS
      • true C96.A
        ICD-10-CM Diagnosis Code C96.A

        Histiocytic sarcoma

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
        Applicable To
        • Malignant histiocytosis
    • Hodgkin C81.9
      ICD-10-CM Diagnosis Code C81.9

      Hodgkin lymphoma, unspecified

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      • lymphocyte depleted C81.3-
        (classical)
        ICD-10-CM Diagnosis Code C81.3-

        Lymphocyte depleted Hodgkin lymphoma

          2016 2017 - Revised Code 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Lymphocyte depleted classical Hodgkin lymphoma
      • lymphocyte depleted classical C81.3-
        ICD-10-CM Diagnosis Code C81.3-

        Lymphocyte depleted Hodgkin lymphoma

          2016 2017 - Revised Code 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Lymphocyte depleted classical Hodgkin lymphoma
      • lymphocyte-rich C81.4-
        (classical)
        ICD-10-CM Diagnosis Code C81.4-

        Lymphocyte-rich Hodgkin lymphoma

          2016 2017 - Revised Code 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Lymphocyte-rich classical Hodgkin lymphoma
        Type 1 Excludes
        • nodular lymphocyte predominant Hodgkin lymphoma (C81.0-)
      • lymphocyte-rich classical C81.4-
        ICD-10-CM Diagnosis Code C81.4-

        Lymphocyte-rich Hodgkin lymphoma

          2016 2017 - Revised Code 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Lymphocyte-rich classical Hodgkin lymphoma
        Type 1 Excludes
        • nodular lymphocyte predominant Hodgkin lymphoma (C81.0-)
      • mixed cellularity C81.2-
        (classical)
        ICD-10-CM Diagnosis Code C81.2-

        Mixed cellularity Hodgkin lymphoma

          2016 2017 - Revised Code 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Mixed cellularity classical Hodgkin lymphoma
      • mixed cellularity classical C81.2-
        ICD-10-CM Diagnosis Code C81.2-

        Mixed cellularity Hodgkin lymphoma

          2016 2017 - Revised Code 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Mixed cellularity classical Hodgkin lymphoma
      • nodular
        • lymphocyte predominant C81.0-
          ICD-10-CM Diagnosis Code C81.0-

          Nodular lymphocyte predominant Hodgkin lymphoma

            2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        • sclerosis C81.1-
          (classical)
          ICD-10-CM Diagnosis Code C81.1-

          Nodular sclerosis Hodgkin lymphoma

            2016 2017 - Revised Code 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
          Applicable To
          • Nodular sclerosis classical Hodgkin lymphoma
      • nodular sclerosis C81.1-
        (classical)
        ICD-10-CM Diagnosis Code C81.1-

        Nodular sclerosis Hodgkin lymphoma

          2016 2017 - Revised Code 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Nodular sclerosis classical Hodgkin lymphoma
      • specified NEC C81.7-
        (classical)
        ICD-10-CM Diagnosis Code C81.7-

        Other Hodgkin lymphoma

          2016 2017 - Revised Code 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Classical Hodgkin lymphoma NOS
        • Other classical Hodgkin lymphoma
    • intravascular large B-cell C83.8-
      ICD-10-CM Diagnosis Code C83.8-

      Other non-follicular lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Intravascular large B-cell lymphoma
      • Lymphoid granulomatosis
      • Primary effusion B-cell lymphoma
      Type 1 Excludes
      • mediastinal (thymic) large B-cell lymphoma (C85.2-)
      • T-cell rich B-cell lymphoma (C83.3-)
    • Lennert's C84.4-
      ICD-10-CM Diagnosis Code C84.4-

      Peripheral T-cell lymphoma, not elsewhere classified

        2016 2017 2018 2019 2020 2021 2022 2023 - Revised Code Non-Billable/Non-Specific Code
      Applicable To
      • Lennert's lymphoma
      • Lymphoepithelioid lymphoma
      • Mature T-cell lymphoma, not elsewhere classified
    • lymphoblastic C83.5-
      (diffuse)
      ICD-10-CM Diagnosis Code C83.5-

      Lymphoblastic (diffuse) lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • B-precursor lymphoma
      • Lymphoblastic B-cell lymphoma
      • Lymphoblastic lymphoma NOS
      • Lymphoblastic T-cell lymphoma
      • T-precursor lymphoma
    • lymphoblastic B-cell C83.5-
      ICD-10-CM Diagnosis Code C83.5-

      Lymphoblastic (diffuse) lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • B-precursor lymphoma
      • Lymphoblastic B-cell lymphoma
      • Lymphoblastic lymphoma NOS
      • Lymphoblastic T-cell lymphoma
      • T-precursor lymphoma
    • lymphoblastic T-cell C83.5-
      ICD-10-CM Diagnosis Code C83.5-

      Lymphoblastic (diffuse) lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • B-precursor lymphoma
      • Lymphoblastic B-cell lymphoma
      • Lymphoblastic lymphoma NOS
      • Lymphoblastic T-cell lymphoma
      • T-precursor lymphoma
    • lymphoepithelioid C84.4-
      ICD-10-CM Diagnosis Code C84.4-

      Peripheral T-cell lymphoma, not elsewhere classified

        2016 2017 2018 2019 2020 2021 2022 2023 - Revised Code Non-Billable/Non-Specific Code
      Applicable To
      • Lennert's lymphoma
      • Lymphoepithelioid lymphoma
      • Mature T-cell lymphoma, not elsewhere classified
    • lymphoplasmacytic C83.0-
      ICD-10-CM Diagnosis Code C83.0-

      Small cell B-cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Lymphoplasmacytic lymphoma
      • Nodal marginal zone lymphoma
      • Non-leukemic variant of B-CLL
      • Splenic marginal zone lymphoma
      Type 1 Excludes
      • chronic lymphocytic leukemia (C91.1)
      • mature T/NK-cell lymphomas (C84.-)
      • Waldenström macroglobulinemia (C88.0)
      • with IgM-production C88.0
        ICD-10-CM Diagnosis Code C88.0

        Waldenström macroglobulinemia

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
        Applicable To
        • Lymphoplasmacytic lymphoma with IgM-production
        • Macroglobulinemia (idiopathic) (primary)
        Type 1 Excludes
        • small cell B-cell lymphoma (C83.0)
    • MALT C88.4
      ICD-10-CM Diagnosis Code C88.4

      Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma]
      • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma]
      Type 1 Excludes
      • high malignant (diffuse large B-cell) lymphoma (C83.3-)
    • mantle cell C83.1-
      ICD-10-CM Diagnosis Code C83.1-

      Mantle cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Centrocytic lymphoma
      • Malignant lymphomatous polyposis
    • mature T-cell NEC C84.4-
      ICD-10-CM Diagnosis Code C84.4-

      Peripheral T-cell lymphoma, not elsewhere classified

        2016 2017 2018 2019 2020 2021 2022 2023 - Revised Code Non-Billable/Non-Specific Code
      Applicable To
      • Lennert's lymphoma
      • Lymphoepithelioid lymphoma
      • Mature T-cell lymphoma, not elsewhere classified
    • mature T/NK-cell C84.9-
      ICD-10-CM Diagnosis Code C84.9-

      Mature T/NK-cell lymphomas, unspecified

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • NK/T cell lymphoma NOS
      Type 1 Excludes
      • mature T-cell lymphoma, not elsewhere classified (C84.4-)
      • specified NEC C84.Z-
        ICD-10-CM Diagnosis Code C84.Z-

        Other mature T/NK-cell lymphomas

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Note
        • If T-cell lineage or involvement is mentioned in conjunction with a specific lymphoma, code to the more specific description.
        Type 1 Excludes
        • angioimmunoblastic T-cell lymphoma (C86.5)
        • blastic NK-cell lymphoma (C86.4)
        • enteropathy-type T-cell lymphoma (C86.2)
        • extranodal NK-cell lymphoma, nasal type (C86.0)
        • hepatosplenic T-cell lymphoma (C86.1)
        • primary cutaneous CD30-positive T-cell proliferations (C86.6)
        • subcutaneous panniculitis-like T-cell lymphoma (C86.3)
        • T-cell leukemia (C91.1-)
    • mediastinal C85.2-
      (thymic)
      ICD-10-CM Diagnosis Code C85.2-

      Mediastinal (thymic) large B-cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    • Mediterranean C88.3
      ICD-10-CM Diagnosis Code C88.3

      Immunoproliferative small intestinal disease

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Alpha heavy chain disease
      • Mediterranean lymphoma
    • mucosa-associated lymphoid tissue [MALT-lymphoma] C88.4
      ICD-10-CM Diagnosis Code C88.4

      Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma]
      • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma]
      Type 1 Excludes
      • high malignant (diffuse large B-cell) lymphoma (C83.3-)
    • NK/T cell C84.9-
      ICD-10-CM Diagnosis Code C84.9-

      Mature T/NK-cell lymphomas, unspecified

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • NK/T cell lymphoma NOS
      Type 1 Excludes
      • mature T-cell lymphoma, not elsewhere classified (C84.4-)
    • nodal marginal zone C83.0-
      ICD-10-CM Diagnosis Code C83.0-

      Small cell B-cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Lymphoplasmacytic lymphoma
      • Nodal marginal zone lymphoma
      • Non-leukemic variant of B-CLL
      • Splenic marginal zone lymphoma
      Type 1 Excludes
      • chronic lymphocytic leukemia (C91.1)
      • mature T/NK-cell lymphomas (C84.-)
      • Waldenström macroglobulinemia (C88.0)
    • non-follicular (diffuse) C83.9-
      ICD-10-CM Diagnosis Code C83.9-

      Non-follicular (diffuse) lymphoma, unspecified

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      • specified NEC C83.8-
        ICD-10-CM Diagnosis Code C83.8-

        Other non-follicular lymphoma

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
        Applicable To
        • Intravascular large B-cell lymphoma
        • Lymphoid granulomatosis
        • Primary effusion B-cell lymphoma
        Type 1 Excludes
        • mediastinal (thymic) large B-cell lymphoma (C85.2-)
        • T-cell rich B-cell lymphoma (C83.3-)
    • non-Hodgkin C85.9-
      - see also Lymphoma, by type
      ICD-10-CM Diagnosis Code C85.9-

      Non-Hodgkin lymphoma, unspecified

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Lymphoma NOS
      • Malignant lymphoma NOS
      • Non-Hodgkin lymphoma NOS
      • specified NEC C85.8-
        ICD-10-CM Diagnosis Code C85.8-

        Other specified types of non-Hodgkin lymphoma

          2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
    • non-leukemic variant of B-CLL C83.0-
      ICD-10-CM Diagnosis Code C83.0-

      Small cell B-cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Lymphoplasmacytic lymphoma
      • Nodal marginal zone lymphoma
      • Non-leukemic variant of B-CLL
      • Splenic marginal zone lymphoma
      Type 1 Excludes
      • chronic lymphocytic leukemia (C91.1)
      • mature T/NK-cell lymphomas (C84.-)
      • Waldenström macroglobulinemia (C88.0)
    • peripheral T-cell NEC C84.4-
      ICD-10-CM Diagnosis Code C84.4-

      Peripheral T-cell lymphoma, not elsewhere classified

        2016 2017 2018 2019 2020 2021 2022 2023 - Revised Code Non-Billable/Non-Specific Code
      Applicable To
      • Lennert's lymphoma
      • Lymphoepithelioid lymphoma
      • Mature T-cell lymphoma, not elsewhere classified
    • primary cutaneous
      • anaplastic large cell C86.6
        ICD-10-CM Diagnosis Code C86.6

        Primary cutaneous CD30-positive T-cell proliferations

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
        Applicable To
        • Lymphomatoid papulosis
        • Primary cutaneous anaplastic large cell lymphoma
        • Primary cutaneous CD30-positive large T-cell lymphoma
      • CD30-positive large T-cell C86.6
        ICD-10-CM Diagnosis Code C86.6

        Primary cutaneous CD30-positive T-cell proliferations

          2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
        Applicable To
        • Lymphomatoid papulosis
        • Primary cutaneous anaplastic large cell lymphoma
        • Primary cutaneous CD30-positive large T-cell lymphoma
    • primary effusion B-cell C83.8-
      ICD-10-CM Diagnosis Code C83.8-

      Other non-follicular lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Intravascular large B-cell lymphoma
      • Lymphoid granulomatosis
      • Primary effusion B-cell lymphoma
      Type 1 Excludes
      • mediastinal (thymic) large B-cell lymphoma (C85.2-)
      • T-cell rich B-cell lymphoma (C83.3-)
    • SALT C88.4
      ICD-10-CM Diagnosis Code C88.4

      Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma]
      • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma]
      Type 1 Excludes
      • high malignant (diffuse large B-cell) lymphoma (C83.3-)
    • skin-associated lymphoid tissue [SALT-lymphoma] C88.4
      ICD-10-CM Diagnosis Code C88.4

      Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Lymphoma of skin-associated lymphoid tissue [SALT-lymphoma]
      • Lymphoma of bronchial-associated lymphoid tissue [BALT-lymphoma]
      Type 1 Excludes
      • high malignant (diffuse large B-cell) lymphoma (C83.3-)
    • small cell B-cell C83.0-
      ICD-10-CM Diagnosis Code C83.0-

      Small cell B-cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Lymphoplasmacytic lymphoma
      • Nodal marginal zone lymphoma
      • Non-leukemic variant of B-CLL
      • Splenic marginal zone lymphoma
      Type 1 Excludes
      • chronic lymphocytic leukemia (C91.1)
      • mature T/NK-cell lymphomas (C84.-)
      • Waldenström macroglobulinemia (C88.0)
    • splenic marginal zone C83.0-
      ICD-10-CM Diagnosis Code C83.0-

      Small cell B-cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • Lymphoplasmacytic lymphoma
      • Nodal marginal zone lymphoma
      • Non-leukemic variant of B-CLL
      • Splenic marginal zone lymphoma
      Type 1 Excludes
      • chronic lymphocytic leukemia (C91.1)
      • mature T/NK-cell lymphomas (C84.-)
      • Waldenström macroglobulinemia (C88.0)
    • subcutaneous panniculitis-like T-cell C86.3
      ICD-10-CM Diagnosis Code C86.3

      Subcutaneous panniculitis-like T-cell lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
    • T-precursor C83.5-
      ICD-10-CM Diagnosis Code C83.5-

      Lymphoblastic (diffuse) lymphoma

        2016 2017 2018 2019 2020 2021 2022 2023 Non-Billable/Non-Specific Code
      Applicable To
      • B-precursor lymphoma
      • Lymphoblastic B-cell lymphoma
      • Lymphoblastic lymphoma NOS
      • Lymphoblastic T-cell lymphoma
      • T-precursor lymphoma
    • true histiocytic C96.A
      ICD-10-CM Diagnosis Code C96.A

      Histiocytic sarcoma

        2016 2017 2018 2019 2020 2021 2022 2023 Billable/Specific Code
      Applicable To
      • Malignant histiocytosis