• Malformation (congenital) - see also Anomaly

    • adrenal gland Q89.1
      ICD-10-CM Diagnosis Code Q89.1

      Congenital malformations of adrenal gland

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Type 1 Excludes
      • adrenogenital disorders (E25.-)
      • congenital adrenal hyperplasia (E25.0)
    • affecting multiple systems with skeletal changes NEC Q87.5
      ICD-10-CM Diagnosis Code Q87.5

      Other congenital malformation syndromes with other skeletal changes

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • alimentary tract Q45.9
      ICD-10-CM Diagnosis Code Q45.9

      Congenital malformation of digestive system, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of digestive system
      • Congenital deformity of digestive system
      • specified type NEC Q45.8
        ICD-10-CM Diagnosis Code Q45.8

        Other specified congenital malformations of digestive system

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Absence (complete) (partial) of alimentary tract NOS
        • Duplication of digestive system
        • Malposition, congenital of digestive system
      • upper Q40.9
        ICD-10-CM Diagnosis Code Q40.9

        Congenital malformation of upper alimentary tract, unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital anomaly of upper alimentary tract
        • Congenital deformity of upper alimentary tract
        • specified type NEC Q40.8
          ICD-10-CM Diagnosis Code Q40.8

          Other specified congenital malformations of upper alimentary tract

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • aorta Q25.40
      ICD-10-CM Diagnosis Code Q25.40

      Congenital malformation of aorta unspecified

        2017 - New Code 2018 2019 Billable/Specific Code POA Exempt
      • absence Q25.41
        ICD-10-CM Diagnosis Code Q25.41

        Absence and aplasia of aorta

          2017 - New Code 2018 2019 Billable/Specific Code POA Exempt
      • aneurysm, congenital Q25.43
        ICD-10-CM Diagnosis Code Q25.43

        Congenital aneurysm of aorta

          2017 - New Code 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital aneurysm of aortic root
        • Congenital aneurysm of aortic sinus
      • aplasia Q25.41
        ICD-10-CM Diagnosis Code Q25.41

        Absence and aplasia of aorta

          2017 - New Code 2018 2019 Billable/Specific Code POA Exempt
      • atresia Q25.29
        ICD-10-CM Diagnosis Code Q25.29

        Other atresia of aorta

          2017 - New Code 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Atresia of aorta
        • aortic arch Q25.21
          ICD-10-CM Diagnosis Code Q25.21

          Interruption of aortic arch

            2017 - New Code 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Atresia of aortic arch
      • coarctation Q25.1
        (preductal) (postductal)
        ICD-10-CM Diagnosis Code Q25.1

        Coarctation of aorta

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Coarctation of aorta (preductal) (postductal)
        • Stenosis of aorta
      • dilatation, congenital Q25.44
        ICD-10-CM Diagnosis Code Q25.44

        Congenital dilation of aorta

          2017 - New Code 2018 2019 Billable/Specific Code POA Exempt
      • hypoplasia Q25.42
        ICD-10-CM Diagnosis Code Q25.42

        Hypoplasia of aorta

          2017 - New Code 2018 2019 Billable/Specific Code POA Exempt
      • patent ductus arteriosus Q25.0
        ICD-10-CM Diagnosis Code Q25.0

        Patent ductus arteriosus

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Patent ductus Botallo
        • Persistent ductus arteriosus
      • specified type NEC Q25.49
        ICD-10-CM Diagnosis Code Q25.49

        Other congenital malformations of aorta

          2017 - New Code 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Aortic arch
        • Bovine arch
      • stenosis Q25.1
        ICD-10-CM Diagnosis Code Q25.1

        Coarctation of aorta

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Coarctation of aorta (preductal) (postductal)
        • Stenosis of aorta
        • supravalvular Q25.3
          ICD-10-CM Diagnosis Code Q25.3

          Supravalvular aortic stenosis

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Type 1 Excludes
          • congenital aortic stenosis NOS (Q23.0)
          • congenital stenosis of aortic valve (Q23.0)
    • aortic valve Q23.9
      ICD-10-CM Diagnosis Code Q23.9

      Congenital malformation of aortic and mitral valves, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • specified NEC Q23.8
        ICD-10-CM Diagnosis Code Q23.8

        Other congenital malformations of aortic and mitral valves

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • arteriovenous, aneurysmatic (congenital) Q27.30
      ICD-10-CM Diagnosis Code Q27.30

      Arteriovenous malformation, site unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • brain Q28.2
        ICD-10-CM Diagnosis Code Q28.2

        Arteriovenous malformation of cerebral vessels

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Arteriovenous malformation of brain NOS
        • Congenital arteriovenous cerebral aneurysm (nonruptured)
      • cerebral Q28.2
        ICD-10-CM Diagnosis Code Q28.2

        Arteriovenous malformation of cerebral vessels

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Arteriovenous malformation of brain NOS
        • Congenital arteriovenous cerebral aneurysm (nonruptured)
      • peripheral Q27.30
        ICD-10-CM Diagnosis Code Q27.30

        Arteriovenous malformation, site unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • digestive system Q27.33
          ICD-10-CM Diagnosis Code Q27.33

          Arteriovenous malformation of digestive system vessel

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • lower limb Q27.32
          ICD-10-CM Diagnosis Code Q27.32

          Arteriovenous malformation of vessel of lower limb

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • other specified site Q27.39
          ICD-10-CM Diagnosis Code Q27.39

          Arteriovenous malformation, other site

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • renal vessel Q27.34
          ICD-10-CM Diagnosis Code Q27.34

          Arteriovenous malformation of renal vessel

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • upper limb Q27.31
          ICD-10-CM Diagnosis Code Q27.31

          Arteriovenous malformation of vessel of upper limb

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • precerebral vessels Q28.0
        (nonruptured)
        ICD-10-CM Diagnosis Code Q28.0

        Arteriovenous malformation of precerebral vessels

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital arteriovenous precerebral aneurysm (nonruptured)
    • auricle
      • ear (congenital) Q17.3
        ICD-10-CM Diagnosis Code Q17.3

        Other misshapen ear

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Pointed ear
        • acquired H61.119
          ICD-10-CM Diagnosis Code H61.119

          Acquired deformity of pinna, unspecified ear

            2016 2017 2018 2019 Billable/Specific Code
          • left H61.112
            ICD-10-CM Diagnosis Code H61.112

            Acquired deformity of pinna, left ear

              2016 2017 2018 2019 Billable/Specific Code
            • with right H61.113
              ICD-10-CM Diagnosis Code H61.113

              Acquired deformity of pinna, bilateral

                2016 2017 2018 2019 Billable/Specific Code
          • right H61.111
            ICD-10-CM Diagnosis Code H61.111

            Acquired deformity of pinna, right ear

              2016 2017 2018 2019 Billable/Specific Code
            • with left H61.113
              ICD-10-CM Diagnosis Code H61.113

              Acquired deformity of pinna, bilateral

                2016 2017 2018 2019 Billable/Specific Code
    • bile duct Q44.5
      ICD-10-CM Diagnosis Code Q44.5

      Other congenital malformations of bile ducts

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Accessory hepatic duct
      • Biliary duct duplication
      • Congenital malformation of bile duct NOS
      • Cystic duct duplication
    • bladder Q64.79
      ICD-10-CM Diagnosis Code Q64.79

      Other congenital malformations of bladder and urethra

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • aplasia Q64.5
        ICD-10-CM Diagnosis Code Q64.5

        Congenital absence of bladder and urethra

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • diverticulum Q64.6
        ICD-10-CM Diagnosis Code Q64.6

        Congenital diverticulum of bladder

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • exstrophy - see Exstrophy, bladder
      • neck obstruction Q64.31
        ICD-10-CM Diagnosis Code Q64.31

        Congenital bladder neck obstruction

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital obstruction of vesicourethral orifice
    • bone Q79.9
      ICD-10-CM Diagnosis Code Q79.9

      Congenital malformation of musculoskeletal system, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of musculoskeletal system NOS
      • Congenital deformity of musculoskeletal system NOS
      • face Q75.9
        ICD-10-CM Diagnosis Code Q75.9

        Congenital malformation of skull and face bones, unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital anomaly of face bones NOS
        • Congenital anomaly of skull NOS
        • specified type NEC Q75.8
          ICD-10-CM Diagnosis Code Q75.8

          Other specified congenital malformations of skull and face bones

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Absence of skull bone, congenital
          • Congenital deformity of forehead
          • Platybasia
      • skull Q75.9
        ICD-10-CM Diagnosis Code Q75.9

        Congenital malformation of skull and face bones, unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital anomaly of face bones NOS
        • Congenital anomaly of skull NOS
        • specified type NEC Q75.8
          ICD-10-CM Diagnosis Code Q75.8

          Other specified congenital malformations of skull and face bones

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Absence of skull bone, congenital
          • Congenital deformity of forehead
          • Platybasia
    • brain (multiple) Q04.9
      ICD-10-CM Diagnosis Code Q04.9

      Congenital malformation of brain, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly NOS of brain
      • Congenital deformity NOS of brain
      • Congenital disease or lesion NOS of brain
      • Multiple anomalies NOS of brain, congenital
      • arteriovenous Q28.2
        ICD-10-CM Diagnosis Code Q28.2

        Arteriovenous malformation of cerebral vessels

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Arteriovenous malformation of brain NOS
        • Congenital arteriovenous cerebral aneurysm (nonruptured)
      • specified type NEC Q04.8
        ICD-10-CM Diagnosis Code Q04.8

        Other specified congenital malformations of brain

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Arnold-Chiari syndrome, type IV
        • Macrogyria
    • branchial cleft Q18.2
      ICD-10-CM Diagnosis Code Q18.2

      Other branchial cleft malformations

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Branchial cleft malformation NOS
      • Cervical auricle
      • Otocephaly
    • breast Q83.9
      ICD-10-CM Diagnosis Code Q83.9

      Congenital malformation of breast, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • specified type NEC Q83.8
        ICD-10-CM Diagnosis Code Q83.8

        Other congenital malformations of breast

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • broad ligament Q50.6
      ICD-10-CM Diagnosis Code Q50.6

      Other congenital malformations of fallopian tube and broad ligament

        2016 2017 2018 2019 Billable/Specific Code Female Dx POA Exempt
      Applicable To
      • Absence of fallopian tube and broad ligament
      • Accessory fallopian tube and broad ligament
      • Atresia of fallopian tube and broad ligament
      • Congenital malformation of fallopian tube or broad ligament NOS
    • bronchus Q32.4
      ICD-10-CM Diagnosis Code Q32.4

      Other congenital malformations of bronchus

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of bronchus
      • Agenesis of bronchus
      • Atresia of bronchus
      • Congenital diverticulum of bronchus
      • Congenital malformation of bronchus NOS
    • bursa Q79.9
      ICD-10-CM Diagnosis Code Q79.9

      Congenital malformation of musculoskeletal system, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of musculoskeletal system NOS
      • Congenital deformity of musculoskeletal system NOS
    • cardiac
      • chambers Q20.9
        ICD-10-CM Diagnosis Code Q20.9

        Congenital malformation of cardiac chambers and connections, unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • specified type NEC Q20.8
          ICD-10-CM Diagnosis Code Q20.8

          Other congenital malformations of cardiac chambers and connections

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Cor binoculare
      • septum Q21.9
        ICD-10-CM Diagnosis Code Q21.9

        Congenital malformation of cardiac septum, unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Septal (heart) defect NOS
        • specified type NEC Q21.8
          ICD-10-CM Diagnosis Code Q21.8

          Other congenital malformations of cardiac septa

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Eisenmenger's defect
          • Pentalogy of Fallot
          Code Also
          • if applicable:
          • Eisenmenger's complex (I27.83)
          • Eisenmenger's syndrome (I27.83)
    • cerebral Q04.9
      ICD-10-CM Diagnosis Code Q04.9

      Congenital malformation of brain, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly NOS of brain
      • Congenital deformity NOS of brain
      • Congenital disease or lesion NOS of brain
      • Multiple anomalies NOS of brain, congenital
      • vessels Q28.3
        ICD-10-CM Diagnosis Code Q28.3

        Other malformations of cerebral vessels

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital cerebral aneurysm (nonruptured)
        • Congenital malformation of cerebral vessels NOS
        • Developmental venous anomaly
    • cervix uteri Q51.9
      ICD-10-CM Diagnosis Code Q51.9

      Congenital malformation of uterus and cervix, unspecified

        2016 2017 2018 2019 Billable/Specific Code Female Dx POA Exempt
      • specified type NEC Q51.828
        ICD-10-CM Diagnosis Code Q51.828

        Other congenital malformations of cervix

          2016 2017 2018 2019 Billable/Specific Code Female Dx POA Exempt
    • Chiari
      • Type I G93.5
        ICD-10-CM Diagnosis Code G93.5

        Compression of brain

          2016 2017 2018 2019 Billable/Specific Code
        Applicable To
        • Arnold-Chiari type 1 compression of brain
        • Compression of brain (stem)
        • Herniation of brain (stem)
        Type 1 Excludes
        • diffuse traumatic compression of brain (S06.2-)
        • focal traumatic compression of brain (S06.3-)
      • Type II Q07.01
        ICD-10-CM Diagnosis Code Q07.01

        Arnold-Chiari syndrome with spina bifida

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • choroid (congenital) Q14.3
      ICD-10-CM Diagnosis Code Q14.3

      Congenital malformation of choroid

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • plexus Q07.8
        ICD-10-CM Diagnosis Code Q07.8

        Other specified congenital malformations of nervous system

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Agenesis of nerve
        • Displacement of brachial plexus
        • Jaw-winking syndrome
        • Marcus Gunn's syndrome
    • circulatory system Q28.9
      ICD-10-CM Diagnosis Code Q28.9

      Congenital malformation of circulatory system, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • cochlea Q16.5
      ICD-10-CM Diagnosis Code Q16.5

      Congenital malformation of inner ear

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of membranous labyrinth
      • Congenital anomaly of organ of Corti
    • cornea Q13.4
      ICD-10-CM Diagnosis Code Q13.4

      Other congenital corneal malformations

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of cornea NOS
      • Microcornea
      • Peter's anomaly
    • coronary vessels Q24.5
      ICD-10-CM Diagnosis Code Q24.5

      Malformation of coronary vessels

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital coronary (artery) aneurysm
    • corpus callosum Q04.0
      (congenital)
      ICD-10-CM Diagnosis Code Q04.0

      Congenital malformations of corpus callosum

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Agenesis of corpus callosum
    • diaphragm Q79.1
      ICD-10-CM Diagnosis Code Q79.1

      Other congenital malformations of diaphragm

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Absence of diaphragm
      • Congenital malformation of diaphragm NOS
      • Eventration of diaphragm
    • digestive system NEC, specified type NEC Q45.8
      ICD-10-CM Diagnosis Code Q45.8

      Other specified congenital malformations of digestive system

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Absence (complete) (partial) of alimentary tract NOS
      • Duplication of digestive system
      • Malposition, congenital of digestive system
    • dura Q07.9
      ICD-10-CM Diagnosis Code Q07.9

      Congenital malformation of nervous system, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly NOS of nervous system
      • Congenital deformity NOS of nervous system
      • Congenital disease or lesion NOS of nervous system
      • brain Q04.9
        ICD-10-CM Diagnosis Code Q04.9

        Congenital malformation of brain, unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital anomaly NOS of brain
        • Congenital deformity NOS of brain
        • Congenital disease or lesion NOS of brain
        • Multiple anomalies NOS of brain, congenital
      • spinal Q06.9
        ICD-10-CM Diagnosis Code Q06.9

        Congenital malformation of spinal cord, unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital anomaly NOS of spinal cord
        • Congenital deformity NOS of spinal cord
        • Congenital disease or lesion NOS of spinal cord
    • ear Q17.9
      ICD-10-CM Diagnosis Code Q17.9

      Congenital malformation of ear, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of ear NOS
      • causing impairment of hearing Q16.9
        ICD-10-CM Diagnosis Code Q16.9

        Congenital malformation of ear causing impairment of hearing, unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital absence of ear NOS
      • external Q17.9
        ICD-10-CM Diagnosis Code Q17.9

        Congenital malformation of ear, unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital anomaly of ear NOS
        • accessory auricle Q17.0
          ICD-10-CM Diagnosis Code Q17.0

          Accessory auricle

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Accessory tragus
          • Polyotia
          • Preauricular appendage or tag
          • Supernumerary ear
          • Supernumerary lobule
        • causing impairment of hearing Q16.9
          ICD-10-CM Diagnosis Code Q16.9

          Congenital malformation of ear causing impairment of hearing, unspecified

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Congenital absence of ear NOS
          • absence of
            • auditory canal Q16.1
              ICD-10-CM Diagnosis Code Q16.1

              Congenital absence, atresia and stricture of auditory canal (external)

                2016 2017 2018 2019 Billable/Specific Code POA Exempt
              Applicable To
              • Congenital atresia or stricture of osseous meatus
            • auricle Q16.0
              ICD-10-CM Diagnosis Code Q16.0

              Congenital absence of (ear) auricle

                2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • macrotia Q17.1
          ICD-10-CM Diagnosis Code Q17.1

          Macrotia

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • microtia Q17.2
          ICD-10-CM Diagnosis Code Q17.2

          Microtia

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • misplacement Q17.4
          ICD-10-CM Diagnosis Code Q17.4

          Misplaced ear

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Low-set ears
          Type 1 Excludes
        • misshapen NEC Q17.3
          ICD-10-CM Diagnosis Code Q17.3

          Other misshapen ear

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Pointed ear
        • prominence Q17.5
          ICD-10-CM Diagnosis Code Q17.5

          Prominent ear

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Bat ear
        • specified type NEC Q17.8
          ICD-10-CM Diagnosis Code Q17.8

          Other specified congenital malformations of ear

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Congenital absence of lobe of ear
      • inner Q16.5
        ICD-10-CM Diagnosis Code Q16.5

        Congenital malformation of inner ear

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital anomaly of membranous labyrinth
        • Congenital anomaly of organ of Corti
      • middle Q16.4
        ICD-10-CM Diagnosis Code Q16.4

        Other congenital malformations of middle ear

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital malformation of middle ear NOS
        • absence of eustachian tube Q16.2
          ICD-10-CM Diagnosis Code Q16.2

          Absence of eustachian tube

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • ossicles Q16.3
          (fusion)
          ICD-10-CM Diagnosis Code Q16.3

          Congenital malformation of ear ossicles

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Congenital fusion of ear ossicles
      • ossicles Q16.3
        ICD-10-CM Diagnosis Code Q16.3

        Congenital malformation of ear ossicles

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital fusion of ear ossicles
      • specified type NEC Q17.8
        ICD-10-CM Diagnosis Code Q17.8

        Other specified congenital malformations of ear

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital absence of lobe of ear
    • epididymis Q55.4
      ICD-10-CM Diagnosis Code Q55.4

      Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate

        2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
      Applicable To
      • Absence or aplasia of prostate
      • Absence or aplasia of spermatic cord
      • Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
    • esophagus Q39.9
      ICD-10-CM Diagnosis Code Q39.9

      Congenital malformation of esophagus, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • specified type NEC Q39.8
        ICD-10-CM Diagnosis Code Q39.8

        Other congenital malformations of esophagus

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital absence of esophagus
        • Congenital displacement of esophagus
        • Congenital duplication of esophagus
    • eye Q15.9
      ICD-10-CM Diagnosis Code Q15.9

      Congenital malformation of eye, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of eye
      • Congenital deformity of eye
      • lid Q10.3
        ICD-10-CM Diagnosis Code Q10.3

        Other congenital malformations of eyelid

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Ablepharon
        • Blepharophimosis, congenital
        • Coloboma of eyelid
        • Congenital absence or agenesis of cilia
        • Congenital absence or agenesis of eyelid
        • Congenital accessory eyelid
        • Congenital accessory eye muscle
        • Congenital malformation of eyelid NOS
      • specified NEC Q15.8
        ICD-10-CM Diagnosis Code Q15.8

        Other specified congenital malformations of eye

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • fallopian tube Q50.6
      ICD-10-CM Diagnosis Code Q50.6

      Other congenital malformations of fallopian tube and broad ligament

        2016 2017 2018 2019 Billable/Specific Code Female Dx POA Exempt
      Applicable To
      • Absence of fallopian tube and broad ligament
      • Accessory fallopian tube and broad ligament
      • Atresia of fallopian tube and broad ligament
      • Congenital malformation of fallopian tube or broad ligament NOS
    • genital organ - see Anomaly, genitalia
    • great
      • artery Q25.9
        ICD-10-CM Diagnosis Code Q25.9

        Congenital malformation of great arteries, unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • vein Q26.9
        ICD-10-CM Diagnosis Code Q26.9

        Congenital malformation of great vein, unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital anomaly of vena cava (inferior) (superior) NOS
        • anomalous
          • portal venous connection Q26.5
            ICD-10-CM Diagnosis Code Q26.5

            Anomalous portal venous connection

              2016 2017 2018 2019 Billable/Specific Code POA Exempt
          • pulmonary venous connection Q26.4
            ICD-10-CM Diagnosis Code Q26.4

            Anomalous pulmonary venous connection, unspecified

              2016 2017 2018 2019 Billable/Specific Code POA Exempt
            • partial Q26.3
              ICD-10-CM Diagnosis Code Q26.3

              Partial anomalous pulmonary venous connection

                2016 2017 2018 2019 Billable/Specific Code POA Exempt
              Applicable To
              • Partial anomalous pulmonary venous return
            • total Q26.2
              ICD-10-CM Diagnosis Code Q26.2

              Total anomalous pulmonary venous connection

                2016 2017 2018 2019 Billable/Specific Code POA Exempt
              Applicable To
              • Total anomalous pulmonary venous return [TAPVR], subdiaphragmatic
              • Total anomalous pulmonary venous return [TAPVR], supradiaphragmatic
        • persistent left superior vena cava Q26.1
          ICD-10-CM Diagnosis Code Q26.1

          Persistent left superior vena cava

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • portal vein-hepatic artery fistula Q26.6
          ICD-10-CM Diagnosis Code Q26.6

          Portal vein-hepatic artery fistula

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • specified type NEC Q26.8
          ICD-10-CM Diagnosis Code Q26.8

          Other congenital malformations of great veins

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Absence of vena cava (inferior) (superior)
          • Azygos continuation of inferior vena cava
          • Persistent left posterior cardinal vein
          • Scimitar syndrome
        • vena cava stenosis, congenital Q26.0
          ICD-10-CM Diagnosis Code Q26.0

          Congenital stenosis of vena cava

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Congenital stenosis of vena cava (inferior)(superior)
    • gum Q38.6
      ICD-10-CM Diagnosis Code Q38.6

      Other congenital malformations of mouth

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of mouth NOS
    • hair Q84.2
      ICD-10-CM Diagnosis Code Q84.2

      Other congenital malformations of hair

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital hypertrichosis
      • Congenital malformation of hair NOS
      • Persistent lanugo
    • heart Q24.9
      ICD-10-CM Diagnosis Code Q24.9

      Congenital malformation of heart, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of heart
      • Congenital disease of heart
      • specified type NEC Q24.8
        ICD-10-CM Diagnosis Code Q24.8

        Other specified congenital malformations of heart

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital diverticulum of left ventricle
        • Congenital malformation of myocardium
        • Congenital malformation of pericardium
        • Malposition of heart
        • Uhl's disease
    • integument Q84.9
      ICD-10-CM Diagnosis Code Q84.9

      Congenital malformation of integument, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of integument NOS
      • Congenital deformity of integument NOS
      • specified type NEC Q84.8
        ICD-10-CM Diagnosis Code Q84.8

        Other specified congenital malformations of integument

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Aplasia cutis congenita
    • internal ear Q16.5
      ICD-10-CM Diagnosis Code Q16.5

      Congenital malformation of inner ear

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of membranous labyrinth
      • Congenital anomaly of organ of Corti
    • intestine Q43.9
      ICD-10-CM Diagnosis Code Q43.9

      Congenital malformation of intestine, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • specified type NEC Q43.8
        ICD-10-CM Diagnosis Code Q43.8

        Other specified congenital malformations of intestine

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital blind loop syndrome
        • Congenital diverticulitis, colon
        • Congenital diverticulum, intestine
        • Dolichocolon
        • Megaloappendix
        • Megaloduodenum
        • Microcolon
        • Transposition of appendix
        • Transposition of colon
        • Transposition of intestine
    • iris Q13.2
      ICD-10-CM Diagnosis Code Q13.2

      Other congenital malformations of iris

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Anisocoria, congenital
      • Atresia of pupil
      • Congenital malformation of iris NOS
      • Corectopia
    • joint Q74.9
      ICD-10-CM Diagnosis Code Q74.9

      Unspecified congenital malformation of limb(s)

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of limb(s) NOS
      • ankle Q74.2
        ICD-10-CM Diagnosis Code Q74.2

        Other congenital malformations of lower limb(s), including pelvic girdle

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital fusion of sacroiliac joint
        • Congenital malformation of ankle joint
        • Congenital malformation of sacroiliac joint
        Type 1 Excludes
        • anteversion of femur (neck) (Q65.89)
      • lumbosacral Q76.49
        ICD-10-CM Diagnosis Code Q76.49

        Other congenital malformations of spine, not associated with scoliosis

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital absence of vertebra NOS
        • Congenital fusion of spine NOS
        • Congenital malformation of lumbosacral (joint) (region) NOS
        • Congenital malformation of spine NOS
        • Hemivertebra NOS
        • Malformation of spine NOS
        • Platyspondylisis NOS
        • Supernumerary vertebra NOS
      • sacroiliac Q74.2
        ICD-10-CM Diagnosis Code Q74.2

        Other congenital malformations of lower limb(s), including pelvic girdle

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital fusion of sacroiliac joint
        • Congenital malformation of ankle joint
        • Congenital malformation of sacroiliac joint
        Type 1 Excludes
        • anteversion of femur (neck) (Q65.89)
      • specified type NEC Q74.8
        ICD-10-CM Diagnosis Code Q74.8

        Other specified congenital malformations of limb(s)

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • kidney Q63.9
      ICD-10-CM Diagnosis Code Q63.9

      Congenital malformation of kidney, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • accessory Q63.0
        ICD-10-CM Diagnosis Code Q63.0

        Accessory kidney

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • giant Q63.3
        ICD-10-CM Diagnosis Code Q63.3

        Hyperplastic and giant kidney

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Compensatory hypertrophy of kidney
      • horseshoe Q63.1
        ICD-10-CM Diagnosis Code Q63.1

        Lobulated, fused and horseshoe kidney

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • hydronephrosis Q62.0
        ICD-10-CM Diagnosis Code Q62.0

        Congenital hydronephrosis

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • malposition Q63.2
        ICD-10-CM Diagnosis Code Q63.2

        Ectopic kidney

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital displaced kidney
        • Malrotation of kidney
      • specified type NEC Q63.8
        ICD-10-CM Diagnosis Code Q63.8

        Other specified congenital malformations of kidney

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital renal calculi
    • lacrimal apparatus Q10.6
      ICD-10-CM Diagnosis Code Q10.6

      Other congenital malformations of lacrimal apparatus

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of lacrimal apparatus NOS
    • lingual Q38.3
      ICD-10-CM Diagnosis Code Q38.3

      Other congenital malformations of tongue

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Aglossia
      • Bifid tongue
      • Congenital adhesion of tongue
      • Congenital fissure of tongue
      • Congenital malformation of tongue NOS
      • Double tongue
      • Hypoglossia
      • Hypoplasia of tongue
      • Microglossia
    • lip Q38.0
      ICD-10-CM Diagnosis Code Q38.0

      Congenital malformations of lips, not elsewhere classified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital fistula of lip
      • Congenital malformation of lip NOS
      • Van der Woude's syndrome
      Type 1 Excludes
    • liver Q44.7
      ICD-10-CM Diagnosis Code Q44.7

      Other congenital malformations of liver

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Accessory liver
      • Alagille's syndrome
      • Congenital absence of liver
      • Congenital hepatomegaly
      • Congenital malformation of liver NOS
    • lung Q33.9
      ICD-10-CM Diagnosis Code Q33.9

      Congenital malformation of lung, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • meninges or membrane (congenital) Q07.9
      ICD-10-CM Diagnosis Code Q07.9

      Congenital malformation of nervous system, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly NOS of nervous system
      • Congenital deformity NOS of nervous system
      • Congenital disease or lesion NOS of nervous system
      • cerebral Q04.8
        ICD-10-CM Diagnosis Code Q04.8

        Other specified congenital malformations of brain

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Arnold-Chiari syndrome, type IV
        • Macrogyria
      • spinal Q06.9
        (cord)
        ICD-10-CM Diagnosis Code Q06.9

        Congenital malformation of spinal cord, unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital anomaly NOS of spinal cord
        • Congenital deformity NOS of spinal cord
        • Congenital disease or lesion NOS of spinal cord
    • middle ear Q16.4
      ICD-10-CM Diagnosis Code Q16.4

      Other congenital malformations of middle ear

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of middle ear NOS
      • ossicles Q16.3
        ICD-10-CM Diagnosis Code Q16.3

        Congenital malformation of ear ossicles

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital fusion of ear ossicles
    • mitral valve Q23.9
      ICD-10-CM Diagnosis Code Q23.9

      Congenital malformation of aortic and mitral valves, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • specified NEC Q23.8
        ICD-10-CM Diagnosis Code Q23.8

        Other congenital malformations of aortic and mitral valves

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • Mondini's Q16.5
      (congenital) (malformation, cochlea)
      ICD-10-CM Diagnosis Code Q16.5

      Congenital malformation of inner ear

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of membranous labyrinth
      • Congenital anomaly of organ of Corti
    • mouth Q38.6
      (congenital)
      ICD-10-CM Diagnosis Code Q38.6

      Other congenital malformations of mouth

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of mouth NOS
    • multiple types NEC Q89.7
      ICD-10-CM Diagnosis Code Q89.7

      Multiple congenital malformations, not elsewhere classified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Multiple congenital anomalies NOS
      • Multiple congenital deformities NOS
      Type 1 Excludes
      • congenital malformation syndromes affecting multiple systems (Q87.-)
    • musculoskeletal system Q79.9
      ICD-10-CM Diagnosis Code Q79.9

      Congenital malformation of musculoskeletal system, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of musculoskeletal system NOS
      • Congenital deformity of musculoskeletal system NOS
    • myocardium Q24.8
      ICD-10-CM Diagnosis Code Q24.8

      Other specified congenital malformations of heart

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital diverticulum of left ventricle
      • Congenital malformation of myocardium
      • Congenital malformation of pericardium
      • Malposition of heart
      • Uhl's disease
    • nail Q84.6
      ICD-10-CM Diagnosis Code Q84.6

      Other congenital malformations of nails

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital clubnail
      • Congenital koilonychia
      • Congenital malformation of nail NOS
    • nervous system Q07.9
      (central)
      ICD-10-CM Diagnosis Code Q07.9

      Congenital malformation of nervous system, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly NOS of nervous system
      • Congenital deformity NOS of nervous system
      • Congenital disease or lesion NOS of nervous system
    • nose Q30.9
      ICD-10-CM Diagnosis Code Q30.9

      Congenital malformation of nose, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • specified type NEC Q30.8
        ICD-10-CM Diagnosis Code Q30.8

        Other congenital malformations of nose

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Accessory nose
        • Congenital anomaly of nasal sinus wall
    • optic disc Q14.2
      ICD-10-CM Diagnosis Code Q14.2

      Congenital malformation of optic disc

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Coloboma of optic disc
    • orbit Q10.7
      ICD-10-CM Diagnosis Code Q10.7

      Congenital malformation of orbit

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • ovary Q50.39
      ICD-10-CM Diagnosis Code Q50.39

      Other congenital malformation of ovary

        2016 2017 2018 2019 Billable/Specific Code Female Dx POA Exempt
      Applicable To
      • Congenital malformation of ovary NOS
    • palate Q38.5
      ICD-10-CM Diagnosis Code Q38.5

      Congenital malformations of palate, not elsewhere classified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of uvula
      • Congenital malformation of palate NOS
      • Congenital high arched palate
      Type 1 Excludes
      • cleft palate (Q35.-)
      • cleft palate with cleft lip (Q37.-)
    • parathyroid gland Q89.2
      ICD-10-CM Diagnosis Code Q89.2

      Congenital malformations of other endocrine glands

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of parathyroid or thyroid gland
      • Persistent thyroglossal duct
      • Thyroglossal cyst
      Type 1 Excludes
      • congenital goiter (E03.0)
      • congenital hypothyroidism (E03.1)
    • pelvic organs or tissues NEC
      • in pregnancy or childbirth O34.8-
        ICD-10-CM Diagnosis Code O34.8-

        Maternal care for other abnormalities of pelvic organs

          2016 2017 2018 2019 Non-Billable/Non-Specific Code
        • causing obstructed labor O65.5
          ICD-10-CM Diagnosis Code O65.5

          Obstructed labor due to abnormality of maternal pelvic organs

            2016 2017 2018 2019 Billable/Specific Code Maternity Dx (12-55 years) Female Dx
          Applicable To
          • Obstructed labor due to conditions listed in O34.-
          Use Additional
          • code to identify abnormality of pelvic organs O34.-
    • penis Q55.69
      ICD-10-CM Diagnosis Code Q55.69

      Other congenital malformation of penis

        2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
      Applicable To
      • Congenital malformation of penis NOS
      • aplasia Q55.5
        ICD-10-CM Diagnosis Code Q55.5

        Congenital absence and aplasia of penis

          2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
      • curvature Q55.61
        (lateral)
        ICD-10-CM Diagnosis Code Q55.61

        Curvature of penis (lateral)

          2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
      • hypoplasia Q55.62
        ICD-10-CM Diagnosis Code Q55.62

        Hypoplasia of penis

          2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
        Applicable To
        • Micropenis
    • pericardium Q24.8
      ICD-10-CM Diagnosis Code Q24.8

      Other specified congenital malformations of heart

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital diverticulum of left ventricle
      • Congenital malformation of myocardium
      • Congenital malformation of pericardium
      • Malposition of heart
      • Uhl's disease
    • peripheral vascular system Q27.9
      ICD-10-CM Diagnosis Code Q27.9

      Congenital malformation of peripheral vascular system, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Anomaly of artery or vein NOS
      • specified type NEC Q27.8
        ICD-10-CM Diagnosis Code Q27.8

        Other specified congenital malformations of peripheral vascular system

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Absence of peripheral vascular system
        • Atresia of peripheral vascular system
        • Congenital aneurysm (peripheral)
        • Congenital stricture, artery
        • Congenital varix
        Type 1 Excludes
        • arteriovenous malformation (Q27.3-)
    • pharynx Q38.8
      ICD-10-CM Diagnosis Code Q38.8

      Other congenital malformations of pharynx

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of pharynx NOS
      • Imperforate pharynx
    • precerebral vessels Q28.1
      ICD-10-CM Diagnosis Code Q28.1

      Other malformations of precerebral vessels

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of precerebral vessels NOS
      • Congenital precerebral aneurysm (nonruptured)
    • prostate Q55.4
      ICD-10-CM Diagnosis Code Q55.4

      Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate

        2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
      Applicable To
      • Absence or aplasia of prostate
      • Absence or aplasia of spermatic cord
      • Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
    • pulmonary
      • arteriovenous Q25.72
        ICD-10-CM Diagnosis Code Q25.72

        Congenital pulmonary arteriovenous malformation

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital pulmonary arteriovenous aneurysm
      • artery Q25.9
        ICD-10-CM Diagnosis Code Q25.9

        Congenital malformation of great arteries, unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • atresia Q25.5
          ICD-10-CM Diagnosis Code Q25.5

          Atresia of pulmonary artery

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
        • specified type NEC Q25.79
          ICD-10-CM Diagnosis Code Q25.79

          Other congenital malformations of pulmonary artery

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Aberrant pulmonary artery
          • Agenesis of pulmonary artery
          • Congenital aneurysm of pulmonary artery
          • Congenital anomaly of pulmonary artery
          • Hypoplasia of pulmonary artery
        • stenosis Q25.6
          ICD-10-CM Diagnosis Code Q25.6

          Stenosis of pulmonary artery

            2016 2017 2018 2019 Billable/Specific Code POA Exempt
          Applicable To
          • Supravalvular pulmonary stenosis
      • valve Q22.3
        ICD-10-CM Diagnosis Code Q22.3

        Other congenital malformations of pulmonary valve

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital malformation of pulmonary valve NOS
        • Supernumerary cusps of pulmonary valve
    • renal artery Q27.2
      ICD-10-CM Diagnosis Code Q27.2

      Other congenital malformations of renal artery

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of renal artery NOS
      • Multiple renal arteries
    • respiratory system Q34.9
      ICD-10-CM Diagnosis Code Q34.9

      Congenital malformation of respiratory system, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of respiratory system
      • Congenital anomaly of respiratory system NOS
    • retina Q14.1
      ICD-10-CM Diagnosis Code Q14.1

      Congenital malformation of retina

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital retinal aneurysm
    • scrotum - see Malformation, testis and scrotum
    • seminal vesicles Q55.4
      ICD-10-CM Diagnosis Code Q55.4

      Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate

        2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
      Applicable To
      • Absence or aplasia of prostate
      • Absence or aplasia of spermatic cord
      • Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
    • sense organs NEC Q07.9
      ICD-10-CM Diagnosis Code Q07.9

      Congenital malformation of nervous system, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly NOS of nervous system
      • Congenital deformity NOS of nervous system
      • Congenital disease or lesion NOS of nervous system
    • skin Q82.9
      ICD-10-CM Diagnosis Code Q82.9

      Congenital malformation of skin, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • specified NEC Q89.8
      ICD-10-CM Diagnosis Code Q89.8

      Other specified congenital malformations

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Use Additional
      • code(s) to identify all associated manifestations
    • spinal
      • cord Q06.9
        ICD-10-CM Diagnosis Code Q06.9

        Congenital malformation of spinal cord, unspecified

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital anomaly NOS of spinal cord
        • Congenital deformity NOS of spinal cord
        • Congenital disease or lesion NOS of spinal cord
      • nerve root Q07.8
        ICD-10-CM Diagnosis Code Q07.8

        Other specified congenital malformations of nervous system

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Agenesis of nerve
        • Displacement of brachial plexus
        • Jaw-winking syndrome
        • Marcus Gunn's syndrome
    • spine Q76.49
      ICD-10-CM Diagnosis Code Q76.49

      Other congenital malformations of spine, not associated with scoliosis

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital absence of vertebra NOS
      • Congenital fusion of spine NOS
      • Congenital malformation of lumbosacral (joint) (region) NOS
      • Congenital malformation of spine NOS
      • Hemivertebra NOS
      • Malformation of spine NOS
      • Platyspondylisis NOS
      • Supernumerary vertebra NOS
    • spleen Q89.09
      ICD-10-CM Diagnosis Code Q89.09

      Congenital malformations of spleen

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital splenomegaly
    • stomach Q40.3
      ICD-10-CM Diagnosis Code Q40.3

      Congenital malformation of stomach, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • specified type NEC Q40.2
        ICD-10-CM Diagnosis Code Q40.2

        Other specified congenital malformations of stomach

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital displacement of stomach
        • Congenital diverticulum of stomach
        • Congenital hourglass stomach
        • Congenital duplication of stomach
        • Megalogastria
        • Microgastria
    • teeth, tooth K00.9
      ICD-10-CM Diagnosis Code K00.9

      Disorder of tooth development, unspecified

        2016 2017 2018 2019 Billable/Specific Code
      Applicable To
      • Disorder of odontogenesis NOS
    • tendon Q79.9
      ICD-10-CM Diagnosis Code Q79.9

      Congenital malformation of musculoskeletal system, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly of musculoskeletal system NOS
      • Congenital deformity of musculoskeletal system NOS
    • testis and scrotum Q55.20
      ICD-10-CM Diagnosis Code Q55.20

      Unspecified congenital malformations of testis and scrotum

        2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
      Applicable To
      • Congenital malformation of testis or scrotum NOS
      • aplasia Q55.0
        ICD-10-CM Diagnosis Code Q55.0

        Absence and aplasia of testis

          2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
        Applicable To
        • Monorchism
      • hypoplasia Q55.1
        ICD-10-CM Diagnosis Code Q55.1

        Hypoplasia of testis and scrotum

          2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
        Applicable To
        • Fusion of testes
      • polyorchism Q55.21
        ICD-10-CM Diagnosis Code Q55.21

        Polyorchism

          2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
      • retractile testis Q55.22
        ICD-10-CM Diagnosis Code Q55.22

        Retractile testis

          2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
      • scrotal transposition Q55.23
        ICD-10-CM Diagnosis Code Q55.23

        Scrotal transposition

          2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
      • specified NEC Q55.29
        ICD-10-CM Diagnosis Code Q55.29

        Other congenital malformations of testis and scrotum

          2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
    • thorax, bony Q76.9
      ICD-10-CM Diagnosis Code Q76.9

      Congenital malformation of bony thorax, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • throat Q38.8
      ICD-10-CM Diagnosis Code Q38.8

      Other congenital malformations of pharynx

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of pharynx NOS
      • Imperforate pharynx
    • thyroid gland Q89.2
      ICD-10-CM Diagnosis Code Q89.2

      Congenital malformations of other endocrine glands

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital malformation of parathyroid or thyroid gland
      • Persistent thyroglossal duct
      • Thyroglossal cyst
      Type 1 Excludes
      • congenital goiter (E03.0)
      • congenital hypothyroidism (E03.1)
    • tongue (congenital) Q38.3
      ICD-10-CM Diagnosis Code Q38.3

      Other congenital malformations of tongue

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Aglossia
      • Bifid tongue
      • Congenital adhesion of tongue
      • Congenital fissure of tongue
      • Congenital malformation of tongue NOS
      • Double tongue
      • Hypoglossia
      • Hypoplasia of tongue
      • Microglossia
      • hypertrophy Q38.2
        ICD-10-CM Diagnosis Code Q38.2

        Macroglossia

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital hypertrophy of tongue
      • tie Q38.1
        ICD-10-CM Diagnosis Code Q38.1

        Ankyloglossia

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Tongue tie
    • trachea Q32.1
      ICD-10-CM Diagnosis Code Q32.1

      Other congenital malformations of trachea

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Atresia of trachea
      • Congenital anomaly of tracheal cartilage
      • Congenital dilatation of trachea
      • Congenital malformation of trachea
      • Congenital stenosis of trachea
      • Congenital tracheocele
    • tricuspid valve Q22.9
      ICD-10-CM Diagnosis Code Q22.9

      Congenital malformation of tricuspid valve, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • specified type NEC Q22.8
        ICD-10-CM Diagnosis Code Q22.8

        Other congenital malformations of tricuspid valve

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • umbilical cord NEC O69.89
      (complicating delivery)
      ICD-10-CM Diagnosis Code O69.89

      Labor and delivery complicated by other cord complications

        2016 2017 2018 2019 Non-Billable/Non-Specific Code
    • umbilicus Q89.9
      ICD-10-CM Diagnosis Code Q89.9

      Congenital malformation, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly NOS
      • Congenital deformity NOS
    • ureter Q62.8
      ICD-10-CM Diagnosis Code Q62.8

      Other congenital malformations of ureter

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Anomaly of ureter NOS
      • agenesis Q62.4
        ICD-10-CM Diagnosis Code Q62.4

        Agenesis of ureter

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Congenital absence ureter
      • duplication Q62.5
        ICD-10-CM Diagnosis Code Q62.5

        Duplication of ureter

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
        Applicable To
        • Accessory ureter
        • Double ureter
      • malposition - see Malposition, congenital, ureter
      • obstructive defect - see Defect, obstructive, ureter
      • vesico-uretero-renal reflux Q62.7
        ICD-10-CM Diagnosis Code Q62.7

        Congenital vesico-uretero-renal reflux

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • urethra Q64.79
      ICD-10-CM Diagnosis Code Q64.79

      Other congenital malformations of bladder and urethra

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • aplasia Q64.5
        ICD-10-CM Diagnosis Code Q64.5

        Congenital absence of bladder and urethra

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • duplication Q64.74
        ICD-10-CM Diagnosis Code Q64.74

        Double urethra

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • posterior valves Q64.2
        ICD-10-CM Diagnosis Code Q64.2

        Congenital posterior urethral valves

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • prolapse Q64.71
        ICD-10-CM Diagnosis Code Q64.71

        Congenital prolapse of urethra

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
      • stricture Q64.32
        ICD-10-CM Diagnosis Code Q64.32

        Congenital stricture of urethra

          2016 2017 2018 2019 Billable/Specific Code POA Exempt
    • urinary system Q64.9
      ICD-10-CM Diagnosis Code Q64.9

      Congenital malformation of urinary system, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Congenital anomaly NOS of urinary system
      • Congenital deformity NOS of urinary system
    • uterus Q51.9
      ICD-10-CM Diagnosis Code Q51.9

      Congenital malformation of uterus and cervix, unspecified

        2016 2017 2018 2019 Billable/Specific Code Female Dx POA Exempt
      • specified type NEC Q51.818
        ICD-10-CM Diagnosis Code Q51.818

        Other congenital malformations of uterus

          2016 2017 2018 2019 Billable/Specific Code Female Dx POA Exempt
        Applicable To
        • Müllerian anomaly of uterus NEC
    • vagina Q52.4
      ICD-10-CM Diagnosis Code Q52.4

      Other congenital malformations of vagina

        2016 2017 2018 2019 Billable/Specific Code Female Dx POA Exempt
      Applicable To
      • Canal of Nuck cyst, congenital
      • Congenital malformation of vagina NOS
      • Embryonic vaginal cyst
      • Gartner's duct cyst
    • vas deferens Q55.4
      ICD-10-CM Diagnosis Code Q55.4

      Other congenital malformations of vas deferens, epididymis, seminal vesicles and prostate

        2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
      Applicable To
      • Absence or aplasia of prostate
      • Absence or aplasia of spermatic cord
      • Congenital malformation of vas deferens, epididymis, seminal vesicles or prostate NOS
      • atresia Q55.3
        ICD-10-CM Diagnosis Code Q55.3

        Atresia of vas deferens

          2016 2017 2018 2019 Billable/Specific Code Male Dx POA Exempt
        Code First
        • any associated cystic fibrosis (E84.-)
    • vascular system, peripheral Q27.9
      ICD-10-CM Diagnosis Code Q27.9

      Congenital malformation of peripheral vascular system, unspecified

        2016 2017 2018 2019 Billable/Specific Code POA Exempt
      Applicable To
      • Anomaly of artery or vein NOS
    • venous - see Anomaly, vein(s)
    • vulva Q52.70
      ICD-10-CM Diagnosis Code Q52.70

      Unspecified congenital malformations of vulva

        2016 2017 2018 2019 Billable/Specific Code Female Dx POA Exempt
      Applicable To
      • Congenital malformation of vulva NOS