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2021/2022 ICD-10-CM Index
›
'M' Terms
›
Index Terms Starting With 'M' (Mastocytosis)
Index Terms Starting With 'M' (Mastocytosis)
Mastocytosis
D47.09
ICD-10-CM Diagnosis Code
D47.09
Other mast cell neoplasms of uncertain behavior
2018 - New Code
2019
2020
2021
2022
Billable/Specific Code
Applicable To
Extracutaneous mastocytoma
Mast cell tumor NOS
Mastocytoma NOS
Mastocytosis NOS
aggressive systemic
C96.21
ICD-10-CM Diagnosis Code
C96.21
Aggressive systemic mastocytosis
2018 - New Code
2019
2020
2021
2022
Billable/Specific Code
cutaneous (diffuse) (maculopapular)
D47.01
ICD-10-CM Diagnosis Code
D47.01
Cutaneous mastocytosis
2018 - New Code
2019
2020
2021
2022
Billable/Specific Code
Applicable To
Diffuse cutaneous mastocytosis
Maculopapular cutaneous mastocytosis
Solitary mastocytoma
Telangiectasia macularis eruptiva perstans
Urticaria pigmentosa
Type 1 Excludes
congenital (diffuse) (maculopapular) cutaneous mastocytosis (
Q82.2
)
congenital urticaria pigmentosa (
Q82.2
)
extracutaneous mastocytoma (
D47.09
)
congenital
Q82.2
ICD-10-CM Diagnosis Code
Q82.2
Congenital cutaneous mastocytosis
2016
2017
2018 - Revised Code
2019
2020
2021
2022
Billable/Specific Code
POA Exempt
Applicable To
Congenital diffuse cutaneous mastocytosis
Congenital maculopapular cutaneous mastocytosis
Congenital urticaria pigmentosa
Type 1 Excludes
cutaneous mastocytosis NOS (
D47.01
)
diffuse cutaneous mastocytosis (with onset after newborn period) (
D47.01
)
malignant mastocytosis (
C96.2-
)
systemic mastocytosis (
D47.02
)
urticaria pigmentosa (non-congenital) (with onset after newborn period) (
D47.01
)
of neonatal onset
Q82.2
ICD-10-CM Diagnosis Code
Q82.2
Congenital cutaneous mastocytosis
2016
2017
2018 - Revised Code
2019
2020
2021
2022
Billable/Specific Code
POA Exempt
Applicable To
Congenital diffuse cutaneous mastocytosis
Congenital maculopapular cutaneous mastocytosis
Congenital urticaria pigmentosa
Type 1 Excludes
cutaneous mastocytosis NOS (
D47.01
)
diffuse cutaneous mastocytosis (with onset after newborn period) (
D47.01
)
malignant mastocytosis (
C96.2-
)
systemic mastocytosis (
D47.02
)
urticaria pigmentosa (non-congenital) (with onset after newborn period) (
D47.01
)
of newborn onset
Q82.2
ICD-10-CM Diagnosis Code
Q82.2
Congenital cutaneous mastocytosis
2016
2017
2018 - Revised Code
2019
2020
2021
2022
Billable/Specific Code
POA Exempt
Applicable To
Congenital diffuse cutaneous mastocytosis
Congenital maculopapular cutaneous mastocytosis
Congenital urticaria pigmentosa
Type 1 Excludes
cutaneous mastocytosis NOS (
D47.01
)
diffuse cutaneous mastocytosis (with onset after newborn period) (
D47.01
)
malignant mastocytosis (
C96.2-
)
systemic mastocytosis (
D47.02
)
urticaria pigmentosa (non-congenital) (with onset after newborn period) (
D47.01
)
indolent systemic
D47.02
ICD-10-CM Diagnosis Code
D47.02
Systemic mastocytosis
2018 - New Code
2019
2020
2021
2022
Billable/Specific Code
Applicable To
Indolent systemic mastocytosis
Isolated bone marrow mastocytosis
Smoldering systemic mastocytosis
Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
, if applicable, any associated hematological non-mast cell lineage disease, such as:
acute myeloid leukemia (
C92.6-
,
C92.A-
)
chronic myelomonocytic leukemia (
C93.1-
)
essential thrombocytosis (
D47.3
)
hypereosinophilic syndrome (
D72.1
)
myelodysplastic syndrome (
D46.9
)
myeloproliferative syndrome (
D47.1
)
non-Hodgkin lymphoma (
C82
-
C85
)
plasma cell myeloma (
C90.0-
)
polycythemia vera (
D45
)
Type 1 Excludes
aggressive systemic mastocytosis (
C96.21
)
mast cell leukemia (
C94.3-
)
isolated bone marrow
D47.02
ICD-10-CM Diagnosis Code
D47.02
Systemic mastocytosis
2018 - New Code
2019
2020
2021
2022
Billable/Specific Code
Applicable To
Indolent systemic mastocytosis
Isolated bone marrow mastocytosis
Smoldering systemic mastocytosis
Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
, if applicable, any associated hematological non-mast cell lineage disease, such as:
acute myeloid leukemia (
C92.6-
,
C92.A-
)
chronic myelomonocytic leukemia (
C93.1-
)
essential thrombocytosis (
D47.3
)
hypereosinophilic syndrome (
D72.1
)
myelodysplastic syndrome (
D46.9
)
myeloproliferative syndrome (
D47.1
)
non-Hodgkin lymphoma (
C82
-
C85
)
plasma cell myeloma (
C90.0-
)
polycythemia vera (
D45
)
Type 1 Excludes
aggressive systemic mastocytosis (
C96.21
)
mast cell leukemia (
C94.3-
)
malignant
C96.29
ICD-10-CM Diagnosis Code
C96.29
Other malignant mast cell neoplasm
2018 - New Code
2019
2020
2021
2022
Billable/Specific Code
systemic (indolent) (smoldering)
with an associated hematological non-mast cell lineage disease
D47.02
(SM-AHNMD)
ICD-10-CM Diagnosis Code
D47.02
Systemic mastocytosis
2018 - New Code
2019
2020
2021
2022
Billable/Specific Code
Applicable To
Indolent systemic mastocytosis
Isolated bone marrow mastocytosis
Smoldering systemic mastocytosis
Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Code Also
, if applicable, any associated hematological non-mast cell lineage disease, such as:
acute myeloid leukemia (
C92.6-
,
C92.A-
)
chronic myelomonocytic leukemia (
C93.1-
)
essential thrombocytosis (
D47.3
)
hypereosinophilic syndrome (
D72.1
)
myelodysplastic syndrome (
D46.9
)
myeloproliferative syndrome (
D47.1
)
non-Hodgkin lymphoma (
C82
-
C85
)
plasma cell myeloma (
C90.0-
)
polycythemia vera (
D45
)
Type 1 Excludes
aggressive systemic mastocytosis (
C96.21
)
mast cell leukemia (
C94.3-
)