1. 2021 ICD-10-CM Index
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2. 'M' Terms
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3. Index Terms Starting With 'M' (Mastocytosis)

Index Terms Starting With 'M' (Mastocytosis)

• Mastocytosis D47.09

  ICD-10-CM Diagnosis Code D47.09

  Other mast cell neoplasms of uncertain behavior

  2018 - New Code 2019 2020 2021 Billable/Specific Code

  Applicable To

  • Extracutaneous mastocytoma
  • Mast cell tumor NOS
  • Mastocytoma NOS
  • Mastocytosis NOS

  • aggressive systemic C96.21
    ICD-10-CM Diagnosis Code C96.21

    Aggressive systemic mastocytosis

    2018 - New Code 2019 2020 2021 Billable/Specific Code
  • cutaneous (diffuse) (maculopapular) D47.01
    ICD-10-CM Diagnosis Code D47.01

    Cutaneous mastocytosis

    2018 - New Code 2019 2020 2021 Billable/Specific Code

    Applicable To

    • Diffuse cutaneous mastocytosis
    • Maculopapular cutaneous mastocytosis
    • Solitary mastocytoma
    • Telangiectasia macularis eruptiva perstans
    • Urticaria pigmentosa

    Type 1 Excludes

    • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
    • congenital urticaria pigmentosa (Q82.2)
    • extracutaneous mastocytoma (D47.09)
    • congenital Q82.2
      ICD-10-CM Diagnosis Code Q82.2

      Congenital cutaneous mastocytosis

      2016 2017 2018 - Revised Code 2019 2020 2021 Billable/Specific Code POA Exempt

      Applicable To

      • Congenital diffuse cutaneous mastocytosis
      • Congenital maculopapular cutaneous mastocytosis
      • Congenital urticaria pigmentosa

      Type 1 Excludes

      • cutaneous mastocytosis NOS (D47.01)
      • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
      • malignant mastocytosis (C96.2-)
      • systemic mastocytosis (D47.02)
      • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
    • of neonatal onset Q82.2
      ICD-10-CM Diagnosis Code Q82.2

      Congenital cutaneous mastocytosis

      2016 2017 2018 - Revised Code 2019 2020 2021 Billable/Specific Code POA Exempt

      Applicable To

      • Congenital diffuse cutaneous mastocytosis
      • Congenital maculopapular cutaneous mastocytosis
      • Congenital urticaria pigmentosa

      Type 1 Excludes

      • cutaneous mastocytosis NOS (D47.01)
      • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
      • malignant mastocytosis (C96.2-)
      • systemic mastocytosis (D47.02)
      • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
    • of newborn onset Q82.2
      ICD-10-CM Diagnosis Code Q82.2

      Congenital cutaneous mastocytosis

      2016 2017 2018 - Revised Code 2019 2020 2021 Billable/Specific Code POA Exempt

      Applicable To

      • Congenital diffuse cutaneous mastocytosis
      • Congenital maculopapular cutaneous mastocytosis
      • Congenital urticaria pigmentosa

      Type 1 Excludes

      • cutaneous mastocytosis NOS (D47.01)
      • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
      • malignant mastocytosis (C96.2-)
      • systemic mastocytosis (D47.02)
      • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
  • indolent systemic D47.02
    ICD-10-CM Diagnosis Code D47.02

    Systemic mastocytosis

    2018 - New Code 2019 2020 2021 Billable/Specific Code

    Applicable To

    • Indolent systemic mastocytosis
    • Isolated bone marrow mastocytosis
    • Smoldering systemic mastocytosis
    • Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)

    Code Also

    • , if applicable, any associated hematological non-mast cell lineage disease, such as:
    • acute myeloid leukemia (C92.6-, C92.A-)
    • chronic myelomonocytic leukemia (C93.1-)
    • essential thrombocytosis (D47.3)
    • hypereosinophilic syndrome (D72.1)
    • myelodysplastic syndrome (D46.9)
    • myeloproliferative syndrome (D47.1)
    • non-Hodgkin lymphoma (C82-C85)
    • plasma cell myeloma (C90.0-)
    • polycythemia vera (D45)

    Type 1 Excludes

    • aggressive systemic mastocytosis (C96.21)
    • mast cell leukemia (C94.3-)
  • isolated bone marrow D47.02
    ICD-10-CM Diagnosis Code D47.02

    Systemic mastocytosis

    2018 - New Code 2019 2020 2021 Billable/Specific Code

    Applicable To

    • Indolent systemic mastocytosis
    • Isolated bone marrow mastocytosis
    • Smoldering systemic mastocytosis
    • Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)

    Code Also

    • , if applicable, any associated hematological non-mast cell lineage disease, such as:
    • acute myeloid leukemia (C92.6-, C92.A-)
    • chronic myelomonocytic leukemia (C93.1-)
    • essential thrombocytosis (D47.3)
    • hypereosinophilic syndrome (D72.1)
    • myelodysplastic syndrome (D46.9)
    • myeloproliferative syndrome (D47.1)
    • non-Hodgkin lymphoma (C82-C85)
    • plasma cell myeloma (C90.0-)
    • polycythemia vera (D45)

    Type 1 Excludes

    • aggressive systemic mastocytosis (C96.21)
    • mast cell leukemia (C94.3-)
  • malignant C96.29
    ICD-10-CM Diagnosis Code C96.29

    Other malignant mast cell neoplasm

    2018 - New Code 2019 2020 2021 Billable/Specific Code
  • systemic (indolent) (smoldering)
    • with an associated hematological non-mast cell lineage disease D47.02
      (SM-AHNMD)
      ICD-10-CM Diagnosis Code D47.02

      Systemic mastocytosis

      2018 - New Code 2019 2020 2021 Billable/Specific Code

      Applicable To

      • Indolent systemic mastocytosis
      • Isolated bone marrow mastocytosis
      • Smoldering systemic mastocytosis
      • Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)

      Code Also

      • , if applicable, any associated hematological non-mast cell lineage disease, such as:
      • acute myeloid leukemia (C92.6-, C92.A-)
      • chronic myelomonocytic leukemia (C93.1-)
      • essential thrombocytosis (D47.3)
      • hypereosinophilic syndrome (D72.1)
      • myelodysplastic syndrome (D46.9)
      • myeloproliferative syndrome (D47.1)
      • non-Hodgkin lymphoma (C82-C85)
      • plasma cell myeloma (C90.0-)
      • polycythemia vera (D45)

      Type 1 Excludes

      • aggressive systemic mastocytosis (C96.21)
      • mast cell leukemia (C94.3-)