2022 ICD-10-CM Diagnosis Code M35.01

Sjögren syndrome with keratoconjunctivitis

    2016 2017 2018 2019 2020 2021 2022 - Revised Code Billable/Specific Code
  • M35.01 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • Short description: Sjogren syndrome with keratoconjunctivitis
  • ICD-10-CM M35.01 is a revised 2022 ICD-10-CM code that became effective on October 1, 2021.
  • This is the American ICD-10-CM version of M35.01 - other international versions of ICD-10 M35.01 may differ.
The following code(s) above M35.01 contain annotation back-references
Annotation Back-References
In this context, annotation back-references refer to codes that contain:
  • Applicable To annotations, or
  • Code Also annotations, or
  • Code First annotations, or
  • Excludes1 annotations, or
  • Excludes2 annotations, or
  • Includes annotations, or
  • Note annotations, or
  • Use Additional annotations
that may be applicable to M35.01:
  • M00-M99
    2022 ICD-10-CM Range M00-M99

    Diseases of the musculoskeletal system and connective tissue

    Note
    • Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
    Type 2 Excludes
    • arthropathic psoriasis (L40.5-)
    • certain conditions originating in the perinatal period (P04-P96)
    • certain infectious and parasitic diseases (A00-B99)
    • compartment syndrome (traumatic) (T79.A-)
    • complications of pregnancy, childbirth and the puerperium (O00-O9A)
    • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
    • endocrine, nutritional and metabolic diseases (E00-E88)
    • injury, poisoning and certain other consequences of external causes (S00-T88)
    • neoplasms (C00-D49)
    • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
    Diseases of the musculoskeletal system and connective tissue
  • M30-M36
    2022 ICD-10-CM Range M30-M36

    Systemic connective tissue disorders

    Includes
    • autoimmune disease NOS
    • collagen (vascular) disease NOS
    • systemic autoimmune disease
    • systemic collagen (vascular) disease
    Type 1 Excludes
    • autoimmune disease, single organ or single cell-type -code to relevant condition category
    Systemic connective tissue disorders
  • M35
    ICD-10-CM Diagnosis Code M35

    Other systemic involvement of connective tissue

      2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
    Type 1 Excludes
    • reactive perforating collagenosis (L87.1)
    Other systemic involvement of connective tissue
  • M35.0
    ICD-10-CM Diagnosis Code M35.0

    Sjögren syndrome

      2022 - Revised Code Non-Billable/Non-Specific Code
    Applicable To
    • Sicca syndrome
    Type 1 Excludes
    • dry mouth, unspecified (R68.2)
    Use Additional
    • code to identify associated manifestations
    Sjögren syndrome
Approximate Synonyms
  • Keratoconjunctivitis sicca
  • Keratoconjunctivitis sicca due to sjogren's syndrome
  • Keratoconjunctivitis sicca, in sjˆgren's syndrome
  • Keratoconjunctivitis sicca, in sjögren's syndrome
ICD-10-CM M35.01 is grouped within Diagnostic Related Group(s) (MS-DRG v39.0):
  • 545 Connective tissue disorders with mcc
  • 546 Connective tissue disorders with cc
  • 547 Connective tissue disorders without cc/mcc

Convert M35.01 to ICD-9-CM

Code History
  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): Revised code
    • New description: Sjogren syndrome with keratoconjunctivitis
    • 2021 description: Sicca syndrome with keratoconjunctivitis
Code annotations containing back-references to M35.01:
  • Type 1 Excludes: H16.22
    ICD-10-CM Diagnosis Code H16.22

    Keratoconjunctivitis sicca, not specified as Sjögren's

      2016 2017 2018 2019 2020 2021 2022 Non-Billable/Non-Specific Code
    Type 1 Excludes

Diagnosis Index entries containing back-references to M35.01:
  • Syndrome - see also Disease
    • Sjögren M35.00
      ICD-10-CM Diagnosis Code M35.00

      Sjögren syndrome, unspecified

        2022 - Revised Code Billable/Specific Code
      • with
        • keratoconjunctivitis M35.01

ICD-10-CM Codes Adjacent To M35.01
M34.2 Systemic sclerosis induced by drug and chemical
M34.8 Other forms of systemic sclerosis
M34.81 Systemic sclerosis with lung involvement
M34.82 Systemic sclerosis with myopathy
M34.83 Systemic sclerosis with polyneuropathy
M34.89 Other systemic sclerosis
M34.9 Systemic sclerosis, unspecified
M35 Other systemic involvement of connective tissue
M35.0 Sjögren syndrome
M35.00 …… unspecified
M35.01 …… with keratoconjunctivitis
M35.02 …… with lung involvement
M35.03 …… with myopathy
M35.04 …… with tubulo-interstitial nephropathy
M35.05 …… with inflammatory arthritis
M35.06 …… with peripheral nervous system involvement
M35.07 …… with central nervous system involvement
M35.08 …… with gastrointestinal involvement
M35.0A …… with glomerular disease
M35.0B …… with vasculitis
M35.0C …… with dental involvement

Reimbursement claims with a date of service on or after October 1, 2015 require the use of ICD-10-CM codes.